Medical management of alagille syndrome

Journal of Pediatric Gastroenterology and Nutrition

Volumn 50, Issue 6, 2010, Pages 580-586

  Kamath, Binita M ^a   Loomes, Kathleen M ^b   Piccoli, David A ^b  

^a HOSPITAL FOR SICK CHILDREN   (Canada)

^b CHILDREN S HOSPITAL OF PHILADELPHIA   (United States)

Author keywords

Alagille; Cholestasis; JAGGED1; Liver

Indexed keywords

ATORVASTATIN; COLESEVELAM; COLESTYRAMINE; DIPHENHYDRAMINE; HYDROXYZINE; JAGGED1; NALTREXONE; PHENOBARBITAL; RIFAMPICIN; URSODEOXYCHOLIC ACID;

ABDOMINAL PAIN; ALAGILLE SYNDROME; BILE DUCT ATRESIA; CEREBROVASCULAR MALFORMATION; CHOLESTASIS; CLINICAL EVALUATION; CLINICAL TRIAL; CONSTIPATION; DIARRHEA; DIET SUPPLEMENTATION; DROWSINESS; GENE MUTATION; GROWTH DISORDER; HEADACHE; HEART DISEASE; HEPATITIS; HEPATOBILIARY SCINTISCANNING; HUMAN; HYPERCHLOREMIC ACIDOSIS; HYPERSENSITIVITY REACTION; KIDNEY DISEASE; KIDNEY FAILURE; LABORATORY TEST; LIVER BIOPSY; LIVER CELL CARCINOMA; LIVER DISEASE; MALNUTRITION; METABOLIC BONE DISEASE; NEUROLOGICAL COMPLICATION; NUTRITIONAL INTOLERANCE; PATHOLOGIC FRACTURE; PRIORITY JOURNAL; PRURITUS; REVIEW; SEDATION; SIDE EFFECT; URINE; VITAMIN SUPPLEMENTATION; WITHDRAWAL SYNDROME;

ALAGILLE SYNDROME; CALCIUM-BINDING PROTEINS; CHOLAGOGUES AND CHOLERETICS; HUMANS; INFANT, NEWBORN; INTERCELLULAR SIGNALING PEPTIDES AND PROTEINS; MEMBRANE PROTEINS; MUTATION;

EID: 77953129356     PISSN: 02772116     EISSN: None     Source Type: Journal    
DOI: 10.1097/MPG.0b013e3181d98ea8     Document Type: Review

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