Partial external biliary diversion for intractable pruritus and xanthomas in Alagille syndrome

Hepatology

Volumn 35, Issue 6, 2002, Pages 1501-1506

  Emerick, Karan M ^a   Whitington, Peter F ^a  

^a NORTHWESTERN UNIVERSITY   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

BILE ACID; BILE SALT; CHOLESTEROL;

ALAGILLE SYNDROME; ARTICLE; BILE ACID BLOOD LEVEL; CHILD; CHOLESTEROL BLOOD LEVEL; CLINICAL ARTICLE; FEMALE; FOLLOW UP; HUMAN; LIVER CIRRHOSIS; LIVER TRANSPLANTATION; MALE; PRIORITY JOURNAL; PRURITUS; SCORING SYSTEM; XANTHOMA;

EID: 0036614010     PISSN: 02709139     EISSN: None     Source Type: Journal    
DOI: 10.1053/jhep.2002.33332     Document Type: Article

References (32)

1. Outcome of liver disease in children with Alagille syndrome: A study of 163 patients
2. Rifampin relieves pruritus in children with cholestatic liver disease
3. Management of the pruritus of cholestasis: Potential role of opiate antagonists
4. Relief of the pruritus of jaundice with a bile-acid sequestering resin
5. The pruritus of cholestasis: Potential pathogenic and therapeutic implications of opioids
6. Bile acid therapy in pediatric hepatobiliary disease: The role of ursodeoxycholic acid
7. Biochemical and clinical response to ursodeoxycholic acid administration in pediatric patients with chronic cholestasis
8. Liver transplantation in children with Alagille syndrome - A study of twelve cases
9. Resolution of xanthomas in Alagille syndrome after liver transplantation
10. Outcome of syndromic paucity of interlobular bile ducts (Alagille syndrome) with onset of cholestasis in infancy
11. Features of Alagille syndrome in 92 patients: Frequency and relation to prognosis
12. Partial external diversion of bile for the treatment of intractable pruritus associated with intrahepatic cholestasis
13. Selective surgical management of progressive familial intrahepatic cholestasis (Byler's disease)
14. Treatment of progressive familial intrahepatic cholestasis: Liver transplantation or partial external biliary diversion
15. Long-term outcome after partial external biliary diversion for intractable pruritus in patients with intrahepatic cholestasis
16. Ileal exclusion for Byler's disease: An alternative surgical approach with promising early resuits for pruritus
17. Progressive familial intrahepatic cholestasis (Bylers disease)
18. Histologic pathology of the liver in progressive familial intrahepatic cholestasis
19. Genetic and morphological findings in progressive familial intrahepatic cholestasis (Byler disease [PFIC-1] and Byler syndrome): Evidence for heterogeneity
20. A gene encoding a P-type ATPase mutated in two forms of hereditary cholestasis
21. A gene encoding a liver-specific ABC transporter is mutated in progressive familial intrahepatic cholestasis
22. Evidence for defective primary bile acid secretion in children with progressive familial intrahepatic cholestasis (Byler disease)
23. Alagille syndrome is caused by mutations in human Jagged1, which encodes a ligand for Notch 1
24. Mutations in the human Jagged1 gene are responsible for Alagille syndrome
25. Hepatic JAGGED 1 expression studies
26. JAGGED1 gene expression during human embryogenesis elucidates the wide phenotypic spectrum of Alagille syndrome
27. Normal organ weights of infants and children
28. Experimental atrophy/hypertrophy complex (AHC) of the liver: Portal vein, but not bile duct obstruction, is the main driving force for the development of AHC in the rat
29. Variable morbidity in Alagille syndrome: A review of 43 cases
30. Does liver transplantation affect growth pattern in Alagille syndrome?
31. Liver transplantation for arteriohepatic dysplasia (Alagille's syndrome)
32. Liver transplantation for Alagille syndrome