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Volumn 36, Issue 1, 2003, Pages 50-53

Lack of cholesterol-lowering effect of graded doses of cholestyramine in children with Alagille syndrome: A pilot study

Author keywords

Alagille syndrome; Cholestyramine; Hypercholesterolemia

Indexed keywords

BILE ACID; CHOLESTEROL; COLESTYRAMINE; HIGH DENSITY LIPOPROTEIN; HYPOCHOLESTEROLEMIC AGENT; LOW DENSITY LIPOPROTEIN; TRIACYLGLYCEROL;

EID: 19044362111     PISSN: 02772116     EISSN: None     Source Type: Journal    
DOI: 10.1097/00005176-200301000-00011     Document Type: Article
Times cited : (5)

References (21)
  • 1
    • 0030914459 scopus 로고    scopus 로고
    • Mutations in the human Jagged1 gene are responsible for Alasille syndrome
    • Oda T, Elkahloun AG, Pike BL, et al. Mutations in the human Jagged1 gene are responsible for Alasille syndrome. Nature Genet 1997;16:235-12.
    • (1997) Nature Genet , vol.16 , pp. 235-312
    • Oda, T.1    Elkahloun, A.G.2    Pike, B.L.3
  • 2
    • 0023148932 scopus 로고
    • Syndromic paucity of interlobular bile ducts (Alagille syndrome or arteriohepatic dysplasia): Review of 80 cases
    • Alagille D, Estrada A, Hadchuel M, Gautier M, Odièvre M, Dommergues JP. Syndromic paucity of interlobular bile ducts (Alagille syndrome or arteriohepatic dysplasia): Review of 80 cases. J Pediatr 1987;110:195-200.
    • (1987) J Pediatr , vol.110 , pp. 195-200
    • Alagille, D.1    Estrada, A.2    Hadchuel, M.3    Gautier, M.4    Odièvre, M.5    Dommergues, J.P.6
  • 3
    • 0029018141 scopus 로고
    • Lipoprotein pattern and plasma lecithin cholesterol acyl transferase activity in children with Alagille syndrome
    • Gottrand F, Clavey V, Fruchart JC, Farriaux JP. Lipoprotein pattern and plasma lecithin cholesterol acyl transferase activity in children with Alagille syndrome. Atherosclerosis 1995;115:233-41.
    • (1995) Atherosclerosis , vol.115 , pp. 233-241
    • Gottrand, F.1    Clavey, V.2    Fruchart, J.C.3    Farriaux, J.P.4
  • 5
    • 0031752929 scopus 로고    scopus 로고
    • Lipoprotein-X in patients with cirrhosis: Its relationship to cholestasis and hypercholesterolemia
    • Soros P, Bottcher J, Maschek H, Selberg O, Muller MJ. Lipoprotein-X in patients with cirrhosis: Its relationship to cholestasis and hypercholesterolemia. Hepatology 1998;28:1199-205.
    • (1998) Hepatology , vol.28 , pp. 1199-1205
    • Soros, P.1    Bottcher, J.2    Maschek, H.3    Selberg, O.4    Muller, M.J.5
  • 6
    • 10144243678 scopus 로고
    • Medical management of neonatal cholestasis
    • Balistreri W, Stocker JT, eds. New York: Hemisphere Publishing Corporation
    • Sokol RJ. Medical management of neonatal cholestasis. In: Balistreri W, Stocker JT, eds. Pediatric hepatology. New York: Hemisphere Publishing Corporation, 1990:41-76.
    • (1990) Pediatric Hepatology , pp. 41-76
    • Sokol, R.J.1
  • 7
    • 0033512356 scopus 로고    scopus 로고
    • Variable morbidity in Alagille syndrome: A review of 43 cases
    • Quiros-Tejeira RE, Ament ME, et al. Variable morbidity in Alagille syndrome: A review of 43 cases. J Pediatr Gastroenterol Nutr 1999;29:431-7.
    • (1999) J Pediatr Gastroenterol Nutr , vol.29 , pp. 431-437
    • Quiros-Tejeira, R.E.1    Ament, M.E.2
  • 8
    • 0029016136 scopus 로고
    • Aortic calcification and renal cysts demonstrated by CT in a teenager with Alagille syndrome
    • Pombo F, Isla C, Gayol A, Bargiela A. Aortic calcification and renal cysts demonstrated by CT in a teenager with Alagille syndrome. Pediatr Radiol 1995;25:314-5.
    • (1995) Pediatr Radiol , vol.25 , pp. 314-315
    • Pombo, F.1    Isla, C.2    Gayol, A.3    Bargiela, A.4
  • 9
    • 0031713693 scopus 로고    scopus 로고
    • The pharmacoeconomic benefits of cholesterol reduction
    • Gonzalez ER. The pharmacoeconomic benefits of cholesterol reduction. Am J Manag Care 1998;4:223-30.
    • (1998) Am J Manag Care , vol.4 , pp. 223-230
    • Gonzalez, E.R.1
  • 11
    • 0014146848 scopus 로고
    • Cholestyramine therapy in patients with a paucity of intrahepatic bile ducts
    • Sharp HL, Carey JB, White JG, Krivit W. Cholestyramine therapy in patients with a paucity of intrahepatic bile ducts. J Pediatr 1967;71:723-36.
    • (1967) J Pediatr , vol.71 , pp. 723-736
    • Sharp, H.L.1    Carey, J.B.2    White, J.G.3    Krivit, W.4
  • 12
    • 0015848081 scopus 로고
    • Cholestatic syndromes in infancy: Diagnostic value of serum bile acid pattern and cholestyramine administration
    • Javitt NB, Morrissey KP, Siegel E, et al. Cholestatic syndromes in infancy: Diagnostic value of serum bile acid pattern and cholestyramine administration. Pediatr Res 1973;7:119-25.
    • (1973) Pediatr Res , vol.7 , pp. 119-125
    • Javitt, N.B.1    Morrissey, K.P.2    Siegel, E.3
  • 13
    • 0018447805 scopus 로고
    • Prolonged neonatal cholestasis: Bile acid pattern and response to cholestyramine
    • Levy JS, Gelb AM, Stenger RJ, Javitt NB. Prolonged neonatal cholestasis: Bile acid pattern and response to cholestyramine. Mt Sinai J Med 1979;46:169.
    • (1979) Mt Sinai J Med , vol.46 , pp. 169
    • Levy, J.S.1    Gelb, A.M.2    Stenger, R.J.3    Javitt, N.B.4
  • 15
    • 27944491705 scopus 로고
    • Escaséz congénita sindromática de los conductos biliares intrahepáticos: Síndrome de Alagille. Informe de dos casos tratados con colestiramina
    • Martínez R, Espinoza M, González A, Cantú JM. Escaséz congénita sindromática de los conductos biliares intrahepáticos: Síndrome de Alagille. Informe de dos casos tratados con colestiramina. Rev Med IMSS 1986;24:265-72.
    • (1986) Rev Med IMSS , vol.24 , pp. 265-272
    • Martínez, R.1    Espinoza, M.2    González, A.3    Cantú, J.M.4
  • 16
    • 0030722513 scopus 로고    scopus 로고
    • Acceptability and compliance with two forms of cholestyramine in the treatment of hypercholesterolemia in children: A randomized, crossover trial
    • McCrindle BW, O'Neill MB, Cullen-Dean G, Helden E. Acceptability and compliance with two forms of cholestyramine in the treatment of hypercholesterolemia in children: A randomized, crossover trial. J Pediatr 1997;130:266-73.
    • (1997) J Pediatr , vol.130 , pp. 266-273
    • McCrindle, B.W.1    O'Neill, M.B.2    Cullen-Dean, G.3    Helden, E.4
  • 17
    • 0027243348 scopus 로고
    • Summary of the second report of the National Cholesterol Education Program Expert Panel on Detection, Evaluation, and Treatment of High Blood Cholesterol in Adults (Adult Treatment Panel II)
    • Expert Panel on Detection, Evaluation and Treatment of High Blood Cholesterol in Adults. Summary of the second report of the National Cholesterol Education Program Expert Panel on Detection, Evaluation, and Treatment of High Blood Cholesterol in Adults (Adult Treatment Panel II). JAMA 1993;269:1015-23.
    • (1993) JAMA , vol.269 , pp. 1015-1023
  • 18
    • 0029816227 scopus 로고    scopus 로고
    • Abnormal lipoprotein pattern in patients with Alagille syndrome depends on icterus severity
    • Davit-Spraul A, Pourci ML, Atger V, et al. Abnormal lipoprotein pattern in patients with Alagille syndrome depends on icterus severity. Gastroenterology 1996;111:1023-32.
    • (1996) Gastroenterology , vol.111 , pp. 1023-1032
    • Davit-Spraul, A.1    Pourci, M.L.2    Atger, V.3
  • 19
    • 0024852215 scopus 로고
    • Cholesterol and prostaglandin synthesis by cultured human skin fibroblasts in the Alagille syndrome involving paucity of interlobular bile ducts
    • Dupont J, Raulin J, Gautier M, et al. Cholesterol and prostaglandin synthesis by cultured human skin fibroblasts in the Alagille syndrome involving paucity of interlobular bile ducts. J Inherit Metab Dis 1989;12:436-44.
    • (1989) J Inherit Metab Dis , vol.12 , pp. 436-444
    • Dupont, J.1    Raulin, J.2    Gautier, M.3
  • 20
    • 0031985271 scopus 로고    scopus 로고
    • Cholesterol in childhood
    • American Academy of Pediatrics, Comitee on Nutrition. Cholesterol in childhood. Pediatrics 1998;101:141-7.
    • (1998) Pediatrics , vol.101 , pp. 141-147
  • 21
    • 0031876986 scopus 로고    scopus 로고
    • Comparison of atorvastatin alone versus simvastatin +/- cholestyramine in the management of severe primary hypercholesterolaemia (the six cities study)
    • Simons LA. Comparison of atorvastatin alone versus simvastatin +/- cholestyramine in the management of severe primary hypercholesterolaemia (the six cities study). Aust N Z J Med 1998;28:327-33.
    • (1998) Aust N Z J Med , vol.28 , pp. 327-333
    • Simons, L.A.1


* 이 정보는 Elsevier사의 SCOPUS DB에서 KISTI가 분석하여 추출한 것입니다.