Vascular Anomalies in Alagille Syndrome: A Significant Cause of Morbidity and Mortality

Circulation

Volumn 109, Issue 11, 2004, Pages 1354-1358

  Kamath, Binita M ^a   Spinner, Nancy B ^a   Emerick, Karan M ^b   Chudley, Albert E ^c   Booth, Carol ^d   Piccoli, David A ^a   Krantz, Ian D ^a,e  

^a UNIVERSITY OF PENNSYLVANIA   (United States)

^b NORTHWESTERN UNIVERSITY   (United States)

^c CHILDREN S HOSPITAL RESEARCH INSTITUTE OF MANITOBA   (Canada)

^d Lutheran General Children's Hospital   (United States)

^e CHILDREN S HOSPITAL OF PHILADELPHIA   (United States)

Author keywords

Aneurysm; Angiogenesis; Cerebrovascular disorders; Vasculature

Indexed keywords

NOTCH RECEPTOR;

ADOLESCENT; ADULT; ALAGILLE SYNDROME; ANEURYSM; AORTA ANEURYSM; BASILAR ARTERY; BRAIN HEMORRHAGE; CAROTID ARTERY ANOMALY; CHILD; CONGENITAL BLOOD VESSEL MALFORMATION; FEMALE; GENE; GENE MUTATION; HUMAN; INFANT; JAGGED1 GENE; KIDNEY ARTERY STENOSIS; MAJOR CLINICAL STUDY; MALE; MIDDLE CEREBRAL ARTERY; MORBIDITY; MORTALITY; MOYAMOYA DISEASE; PRIORITY JOURNAL; RETROSPECTIVE STUDY; REVIEW;

ABNORMALITIES, MULTIPLE; ADULT; ALAGILLE SYNDROME; ANEURYSM; AORTIC ANEURYSM; AORTIC COARCTATION; BLOOD VESSELS; CALCIUM-BINDING PROTEINS; CAROTID ARTERY DISEASES; CHILD; COHORT STUDIES; HUMANS; INTERCELLULAR SIGNALING PEPTIDES AND PROTEINS; INTRACRANIAL ANEURYSM; MEMBRANE PROTEINS; MOYAMOYA DISEASE; NEOVASCULARIZATION, PHYSIOLOGIC; PROTEINS; RECEPTORS, NOTCH; RENAL ARTERY OBSTRUCTION; RETROSPECTIVE STUDIES; SIGNAL TRANSDUCTION;

EID: 1642271395     PISSN: 00097322     EISSN: None     Source Type: Journal    
DOI: 10.1161/01.CIR.0000121361.01862.A4     Document Type: Review

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