Cystic kidney diseases and planar cell polarity signaling

Clinical Genetics

Volumn 75, Issue 2, 2009, Pages 107-117

  Bacallao, R L ^a   Mcneill, H ^b,c  

^a INDIANA UNIVERSITY SCHOOL OF MEDICINE   (United States)

^b MOUNT SINAI HOSPITAL   (Canada)

^c UNIVERSITY OF TORONTO   (Canada)

Author keywords

Development kidney; Nephronophthisis; Planar polarity; Polycystic kidney disease; Spindle orientation

Indexed keywords

APC PROTEIN; AXIN; BETA CATENIN; CASEIN KINASE; DISHEVELLED PROTEIN; FRIZZLED PROTEIN; GLYCOGEN SYNTHASE KINASE 3; PHOSPHOPROTEIN PHOSPHATASE 2A; POLYCYSTIN 1; POLYCYSTIN 2; T CELL FACTOR PROTEIN; WNT1 PROTEIN;

CELL POLARITY; CILIARY MOTILITY; CLINICAL FEATURE; DISEASE COURSE; DROSOPHILA; GENE LOCUS; GENE MUTATION; GENETIC CONSERVATION; GENETIC TRANSCRIPTION; HUMAN; KIDNEY FAILURE; KIDNEY POLYCYSTIC DISEASE; KIDNEY SURGERY; LIVER FAILURE; LIVER TRANSPLANTATION; NEPHRONOPHTHISIS; NONHUMAN; PATHOGENESIS; PREVALENCE; PRIORITY JOURNAL; REVIEW; SIGNAL TRANSDUCTION;

ANIMALS; BODY PATTERNING; CELL POLARITY; CILIA; DROSOPHILA; HUMANS; KIDNEY DISEASES, CYSTIC; MODELS, BIOLOGICAL; SIGNAL TRANSDUCTION;

EID: 58849164887     PISSN: 00099163     EISSN: 13990004     Source Type: Journal    
DOI: 10.1111/j.1399-0004.2008.01148.x     Document Type: Review

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