Cryopyrinopathies: Update on pathogenesis and treatment

Nature Clinical Practice Rheumatology

Volumn 4, Issue 9, 2008, Pages 481-489

  Neven, Bénédicte ^a,b   Prieur, Anne Marie ^a   dit Maire, Pierre Quartier ^a  

^a HÔPITAL NECKER ENFANTS MALADES   (France)

^b INSERM   (France)

Author keywords

[No Author keywords available]

Indexed keywords

ACZ 885; ANTIINFLAMMATORY AGENT; CELL PROTEIN; CORTICOSTEROID; IMMUNOGLOBULIN G1 ANTIBODY; INTERLEUKIN 1 ANTIBODY; INTERLEUKIN 1BETA; NONSTEROID ANTIINFLAMMATORY AGENT; NUCLEOTIDE BINDING OLIGOMERIZATION DOMAIN LEUCINE RICH REPEAT FAMILY PYRIN DOMAIN CONTAINING PROTEIN 3; RECOMBINANT INTERLEUKIN 1 RECEPTOR BLOCKING AGENT; RILONACEPT; THALIDOMIDE; TUMOR NECROSIS FACTOR INHIBITOR; VX 765;

ANTIINFLAMMATORY ACTIVITY; AUTOINFLAMMATORY DISEASE; CINCA SYNDROME; CLINICAL FEATURE; COLD EXPOSURE; CORONARY ARTERY ATHEROSCLEROSIS; CRYOPYRINOPATHY; DRUG DOSE REDUCTION; DRUG EFFICACY; DRUG FATALITY; DRUG HALF LIFE; DRUG RESPONSE; FAMILIAL COLD AUTOINFLAMMATORY SYNDROME; GENE MUTATION; HUMAN; IMMUNOPATHOGENESIS; INFECTION; INJECTION SITE ERYTHEMA; INJECTION SITE PAIN; INJECTION SITE REACTION; MENINGITIS; MUCKLE WELLS SYNDROME; NONHUMAN; PRIORITY JOURNAL; REVIEW; RISK FACTOR; SYMPTOMATOLOGY; UPPER RESPIRATORY TRACT INFECTION;

AUTOIMMUNE DISEASES; CARRIER PROTEINS; HUMANS; INFLAMMATION; NEUROCUTANEOUS SYNDROMES; SKIN DISEASES; URTICARIA;

EID: 51149087862     PISSN: 17458382     EISSN: 17458390     Source Type: Journal    
DOI: 10.1038/ncprheum0874     Document Type: Review

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