Defects in neuromuscular junction structure in dystrophic muscle are corrected by expression of a NOS transgene in dystrophin-deficient muscles, but not in muscles lacking α- and β1-syntrophins

Human Molecular Genetics

Volumn 13, Issue 17, 2004, Pages 1873-1884

  Shiao, Terry ^a   Fond, Andrew ^a   Deng, Bo ^a   Wehling Henricks, Michelle ^a   Adams, Marvin E ^b   Froehner, Stanley C ^b   Tidball, James G ^a  

^a UNIVERSITY OF CALIFORNIA   (United States)

^b UNIVERSITY OF WASHINGTON   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

ALPHA SYNTROPHIN; BETA1 SYNTROPHIN; CHOLINERGIC RECEPTOR; DYSTROPHIN; LAMININ; LECTIN; NITRIC OXIDE; NITRIC OXIDE SYNTHASE; SYNTROPHIN; UNCLASSIFIED DRUG;

ANIMAL CELL; ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; CELL CULTURE; CONCENTRATION (PARAMETERS); CONTROLLED STUDY; ENZYME ACTIVITY; ENZYME INHIBITION; GENE CLUSTER; GENE EXPRESSION; GENE EXPRESSION PROFILING; GENE MUTATION; IMMUNOHISTOCHEMISTRY; IN VITRO STUDY; MOUSE; MUSCULAR DYSTROPHY; NEUROMUSCULAR JUNCTION DISORDER; NEUROMUSCULAR SYNAPSE; NONHUMAN; POSTSYNAPTIC MEMBRANE; PRIORITY JOURNAL; TRANSGENE; WESTERN BLOTTING;

ANIMALS; DYSTROPHIN; DYSTROPHIN-ASSOCIATED PROTEINS; ELECTROPHORESIS, POLYACRYLAMIDE GEL; FLUORESCENCE; GENE EXPRESSION; IMMUNOHISTOCHEMISTRY; LAMININ; LECTINS; MICE; MICE, TRANSGENIC; MUSCLE, SKELETAL; MUSCULAR DYSTROPHIES; NEUROMUSCULAR JUNCTION; NEUROMUSCULAR JUNCTION DISEASES; NITRIC OXIDE; NITRIC OXIDE SYNTHASE; RECEPTORS, CHOLINERGIC; SYNAPSES; TRANSGENES;

EID: 4344568541     PISSN: 09646906     EISSN: None     Source Type: Journal    
DOI: 10.1093/hmg/ddh204     Document Type: Article

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