Progressive muscular dystrophy in α-sarcoglycan-deficient mice

Journal of Cell Biology

Volumn 142, Issue 6, 1998, Pages 1461-1471

  Duclos, Franck ^a   Straub, Volker ^a   Moore, Steven A ^a   Venzke, David P ^a   Hrstka, Ron F ^a   Crosbie, Rachelle H ^a   Durbeej, Madeleine ^a   Lebakken, Connie S ^a   Ettinger, Audrey J ^b   Van Der Meulen, Jack ^c   Holt, Kathleen H ^a   Lim, Leland E ^a   Sanes, Joshua R ^b   Davidson, Beverly L ^a   Faulkner, John A ^c   Williamson, Roger ^a   Campbell, Kevin P ^a  

^a UNIVERSITY OF IOWA   (United States)

^b WASHINGTON UNIVERSITY SCHOOL OF MEDICINE   (United States)

^c UNIVERSITY OF MICHIGAN HEALTH SYSTEM   (United States)

Author keywords

Dystroglycan; Gene targeting; Muscular dystrophy; Sacospan; Sarcoglycan

Indexed keywords

DYSTROGLYCAN; MUSCLE ENZYME; SARCOGLYCAN;

ANIMAL CELL; ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; AUTOSOMAL RECESSIVE DISORDER; CONTROLLED STUDY; EXPERIMENTAL MODEL; GENE MUTATION; GENE TARGETING; MOUSE; MUSCLE CELL; MUSCLE CONTRACTILITY; MUSCLE NECROSIS; MUSCULAR DYSTROPHY; NONHUMAN; NORTHERN BLOTTING; NUCLEOTIDE SEQUENCE; PRIORITY JOURNAL; PROTEIN EXPRESSION; PROTEIN PROTEIN INTERACTION;

AMINO ACID SEQUENCE; ANIMALS; BASE SEQUENCE; CARRIER PROTEINS; CYTOSKELETAL PROTEINS; DISEASE PROGRESSION; DNA, COMPLEMENTARY; DYSTROPHIN; GENE TRANSFER TECHNIQUES; GLYCOPROTEINS; MEMBRANE GLYCOPROTEINS; MEMBRANE PROTEINS; MICE; MICE, INBRED C57BL; MICE, KNOCKOUT; MOLECULAR SEQUENCE DATA; MUSCLE CONTRACTION; MUSCULAR DYSTROPHY, ANIMAL; NEOPLASM PROTEINS; SARCOGLYCANS; SARCOLEMMA;

EID: 19244372467     PISSN: 00219525     EISSN: None     Source Type: Journal    
DOI: 10.1083/jcb.142.6.1461     Document Type: Article

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