Radixin deficiency causes deafness associated with progressive degeneration of cochlear stereocilia

Journal of Cell Biology

Volumn 166, Issue 4, 2004, Pages 559-570

  Kitajiri, Shin Ichiro ^a,b   Fukumoto, Kanehisa ^a,c   Hata, Masaki ^d   Sasaki, Hiroyuki ^d,e   Katsuno, Tatsuya ^a,f   Nakagawa, Takayuki ^a   Ito, Juichi ^a   Tsukita, Shoichiro ^a,b   Tsukita, Sachiko ^a,b,g  

^a KYOTO UNIVERSITY   (Japan)

^b JAPAN SCIENCE AND TECHNOLOGY AGENCY   (Japan)

^c KYOTO PREFECTURAL UNIVERSITY OF MEDICINE   (Japan)

^d Kyoto Research Park ^*  (Japan)

^e JIKEI UNIVERSITY SCHOOL OF MEDICINE   (Japan)

^f NAGOYA UNIVERSITY   (Japan)

^g KYOTO UNIVERSITY FACULTY OF MEDICINE   (Japan)

Author keywords

Cochlea; Deafness; ERM; Radixin; Stereocilia

Indexed keywords

EZRIN; MOESIN; RADIXIN;

ACTIN FILAMENT; ANIMAL CELL; ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; AUDITORY CORTEX; CELL DEGENERATION; CELL MEMBRANE; CONTROLLED STUDY; HAIR CELL; HEARING; HEARING IMPAIRMENT; INNER EAR DISEASE; MICROVILLUS; MOUSE; NONHUMAN; PRIORITY JOURNAL; PROTEIN CROSS LINKING; PROTEIN DEFICIENCY; PROTEIN LOCALIZATION; PROTEIN STRUCTURE; STEREOCILIUM; STRUCTURE ACTIVITY RELATION;

ANIMALS; BLOOD PROTEINS; CELL MEMBRANE; CILIA; COCHLEA; CYTOSKELETAL PROTEINS; CYTOSKELETON; DEAFNESS; HAIR CELLS; IMMUNOBLOTTING; MEMBRANE PROTEINS; MICE; MICE, INBRED C57BL; MICE, TRANSGENIC; MICROSCOPY, ELECTRON; MICROSCOPY, ELECTRON, SCANNING; MICROSCOPY, FLUORESCENCE; MICROVILLI; MUTATION; PHOSPHOPROTEINS; TIME FACTORS;

ANIMALIA;

EID: 4143152925     PISSN: 00219525     EISSN: None     Source Type: Journal    
DOI: 10.1083/jcb.200402007     Document Type: Article

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