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Volumn 14, Issue 20, 2007, Pages 1492-1501

Expression of CFTR from a ciliated cell-specific promoter is ineffective at correcting nasal potential difference in CF mice

Author keywords

[No Author keywords available]

Indexed keywords

RNA; TRANSMEMBRANE CONDUCTANCE REGULATOR;

EID: 34848847214     PISSN: 09697128     EISSN: 14765462     Source Type: Journal    
DOI: 10.1038/sj.gt.3302994     Document Type: Article
Times cited : (31)

References (46)
  • 1
    • 0024424270 scopus 로고
    • Identification of the cystic fibrosis gene:cLoning and characterization of complementary DNA
    • Riordan JR, Rommens JM, Kerem B-S, Alon N, Rozmahel R, Grzelczak Z et al. Identification of the cystic fibrosis gene:cLoning and characterization of complementary DNA. Science 1989; 245: 1066-1073.
    • (1989) Science , vol.245 , pp. 1066-1073
    • Riordan, J.R.1    Rommens, J.M.2    Kerem, B.-S.3    Alon, N.4    Rozmahel, R.5    Grzelczak, Z.6
  • 2
  • 6
    • 18244377969 scopus 로고    scopus 로고
    • Characterization of wild-type and deltaF508 cystic fibrosis transmembrane regulator in human respiratory epithelia
    • Kreda SM, Mall M, Mengos A, Rochelle L, Yankaskas J, Riordan JR et al. Characterization of wild-type and deltaF508 cystic fibrosis transmembrane regulator in human respiratory epithelia. Mol Biol Cell 2005; 16: 2154-2167.
    • (2005) Mol Biol Cell , vol.16 , pp. 2154-2167
    • Kreda, S.M.1    Mall, M.2    Mengos, A.3    Rochelle, L.4    Yankaskas, J.5    Riordan, J.R.6
  • 7
    • 0026954365 scopus 로고
    • Differential localization of the cystic fibrosis transmembrane conductance regulator in normal and cystic fibrosis airway epithelium
    • Puchelle E, Gaillard D, Ploton D, Hinnrasky J, Fuchey C, Boutterin MC et al. Differential localization of the cystic fibrosis transmembrane conductance regulator in normal and cystic fibrosis airway epithelium. Am J Respir Cell Mol Biol 1992; 7: 485-491.
    • (1992) Am J Respir Cell Mol Biol , vol.7 , pp. 485-491
    • Puchelle, E.1    Gaillard, D.2    Ploton, D.3    Hinnrasky, J.4    Fuchey, C.5    Boutterin, M.C.6
  • 9
    • 21444440910 scopus 로고    scopus 로고
    • The CFTR gene and regulation of its expression
    • Harris A, McCarthy V. The CFTR gene and regulation of its expression. Pediatr Pulmonol 2005; 40: 1-8.
    • (2005) Pediatr Pulmonol , vol.40 , pp. 1-8
    • Harris, A.1    McCarthy, V.2
  • 10
    • 0026625385 scopus 로고
    • Expression of the human cystic fibrosis transmembrane conductance regulator gene in the mouse lung after in vivo intratracheal plasmid-mediated gene transfer
    • Yoshimura K, Rosenfeld MA, Nakamura H, Scherer EM, Pavirani A, Lecocq JP et al. Expression of the human cystic fibrosis transmembrane conductance regulator gene in the mouse lung after in vivo intratracheal plasmid-mediated gene transfer. Nucleic Acids Res 1992; 20: 3233-3240.
    • (1992) Nucleic Acids Res , vol.20 , pp. 3233-3240
    • Yoshimura, K.1    Rosenfeld, M.A.2    Nakamura, H.3    Scherer, E.M.4    Pavirani, A.5    Lecocq, J.P.6
  • 12
    • 0035166381 scopus 로고    scopus 로고
    • Increased persistence of lung gene expression using plasmids containing the ubiquitin C or elongation factor 1alpha promoter
    • Gill DR, Smyth SE, Goddard CA, Pringle IA, Higgins CF, Colledge WH et al. Increased persistence of lung gene expression using plasmids containing the ubiquitin C or elongation factor 1alpha promoter. Gene Therapy 2001; 8: 1539-1546.
    • (2001) Gene Therapy , vol.8 , pp. 1539-1546
    • Gill, D.R.1    Smyth, S.E.2    Goddard, C.A.3    Pringle, I.A.4    Higgins, C.F.5    Colledge, W.H.6
  • 13
    • 0346505482 scopus 로고    scopus 로고
    • New concepts of the pathogenesis of cystic fibrosis lung disease
    • Boucher RC. New concepts of the pathogenesis of cystic fibrosis lung disease. Eur Respir J 2004; 23: 146-158.
    • (2004) Eur Respir J , vol.23 , pp. 146-158
    • Boucher, R.C.1
  • 15
    • 0142244084 scopus 로고    scopus 로고
    • Targeting expression of a transgene to the airway surface epithelium using a ciliated cell-specific promoter
    • Ostrowski LE, Hutchins JR, Zakel K, O'Neal WK. Targeting expression of a transgene to the airway surface epithelium using a ciliated cell-specific promoter. Mol Ther 2003; 8: 637-645.
    • (2003) Mol Ther , vol.8 , pp. 637-645
    • Ostrowski, L.E.1    Hutchins, J.R.2    Zakel, K.3    O'Neal, W.K.4
  • 17
    • 0025094612 scopus 로고
    • Correction of the cystic fibrosis defect in vitro by retrovirus-mediated gene transfer
    • Drumm ML, Pope HA, Cliff WH, Rommens JM, Marvin SA, Tsui LC et al. Correction of the cystic fibrosis defect in vitro by retrovirus-mediated gene transfer. Cell 1990; 62: 1227-1233.
    • (1990) Cell , vol.62 , pp. 1227-1233
    • Drumm, M.L.1    Pope, H.A.2    Cliff, W.H.3    Rommens, J.M.4    Marvin, S.A.5    Tsui, L.C.6
  • 18
    • 0347361558 scopus 로고    scopus 로고
    • The DeltaF508 mutation results in loss of CFTR function and mature protein in native human colon
    • Mall M, Kreda SM, Mengos A, Jensen TJ, Hirtz S, Seydewitz HH et al. The DeltaF508 mutation results in loss of CFTR function and mature protein in native human colon. Gastroenterology 2004; 126: 32-41.
    • (2004) Gastroenterology , vol.126 , pp. 32-41
    • Mall, M.1    Kreda, S.M.2    Mengos, A.3    Jensen, T.J.4    Hirtz, S.5    Seydewitz, H.H.6
  • 19
    • 0028111842 scopus 로고
    • Anomalies in ion transport in CF mouse tracheal epithelium
    • Grubb BR, Paradiso AM, Boucher RC. Anomalies in ion transport in CF mouse tracheal epithelium. Am J Physiol 1994; 267: C293-C300.
    • (1994) Am J Physiol , vol.267
    • Grubb, B.R.1    Paradiso, A.M.2    Boucher, R.C.3
  • 20
    • 17344382237 scopus 로고    scopus 로고
    • Chloride secretion in the trachea of null cystic fibrosis mice: The effects of transfection with pTrial10-CFTR2
    • MacVinish LJ, Gill DR, Hyde SC, Mofford KA, Evans MJ, Higgins CF et al. Chloride secretion in the trachea of null cystic fibrosis mice: the effects of transfection with pTrial10-CFTR2. J Physiol 1997; 499: 677-687.
    • (1997) J Physiol , vol.499 , pp. 677-687
    • MacVinish, L.J.1    Gill, D.R.2    Hyde, S.C.3    Mofford, K.A.4    Evans, M.J.5    Higgins, C.F.6
  • 21
    • 0035479148 scopus 로고    scopus 로고
    • Mouse models of cystic fibrosis
    • Davidson DJ, Rolfe M. Mouse models of cystic fibrosis. Trends Genet 2001; 17: S29-S37.
    • (2001) Trends Genet , vol.17
    • Davidson, D.J.1    Rolfe, M.2
  • 22
    • 0032962320 scopus 로고    scopus 로고
    • Pathophysiology of gene-targeted mouse models for cystic fibrosis
    • Grubb BR, Boucher RC. Pathophysiology of gene-targeted mouse models for cystic fibrosis. Physiol Rev 1999; 79: S193-S214.
    • (1999) Physiol Rev , vol.79
    • Grubb, B.R.1    Boucher, R.C.2
  • 25
    • 0033571594 scopus 로고    scopus 로고
    • Yes-associated protein 65 localizes p62(c-Yes) to the apical compartment of airway epithelia by association with EBP50
    • Mohler PJ, Kreda SM, Boucher RC, Sudol M, Stutts MJ, Milgram SL. Yes-associated protein 65 localizes p62(c-Yes) to the apical compartment of airway epithelia by association with EBP50. J Cell Biol 1999; 147: 879-890.
    • (1999) J Cell Biol , vol.147 , pp. 879-890
    • Mohler, P.J.1    Kreda, S.M.2    Boucher, R.C.3    Sudol, M.4    Stutts, M.J.5    Milgram, S.L.6
  • 26
    • 0031569416 scopus 로고    scopus 로고
    • The human hepatocyte nuclear factor 3/fork head gene FKHL13: Genomic structure and pattern of expression
    • Murphy DB, Seemann S, Wiese S, Kirschner R, Grzeschik KH, Thies U. The human hepatocyte nuclear factor 3/fork head gene FKHL13: Genomic structure and pattern of expression. Genomics 1997; 40: 462-469.
    • (1997) Genomics , vol.40 , pp. 462-469
    • Murphy, D.B.1    Seemann, S.2    Wiese, S.3    Kirschner, R.4    Grzeschik, K.H.5    Thies, U.6
  • 27
    • 34848857509 scopus 로고    scopus 로고
    • The development of paramyxovirus vectors for efficient delivery of CFTR to ciliated airway epithelium
    • Pickles RJ. The development of paramyxovirus vectors for efficient delivery of CFTR to ciliated airway epithelium. Pediatr Pulmonol 2004; Suppl 27: 137-138.
    • (2004) Pediatr Pulmonol , Issue.SUPPL. 27 , pp. 137-138
    • Pickles, R.J.1
  • 28
    • 33751185518 scopus 로고    scopus 로고
    • Real-time analysis of cAMP-mediated regulation of ciliary motility in single primary human airway epithelial cells
    • Schmid A, Bai G, Schmid N, Zaccolo M, Ostrowski LE, Conner GE et al. Real-time analysis of cAMP-mediated regulation of ciliary motility in single primary human airway epithelial cells. J Cell Sci 2006; 119: 4176-4186.
    • (2006) J Cell Sci , vol.119 , pp. 4176-4186
    • Schmid, A.1    Bai, G.2    Schmid, N.3    Zaccolo, M.4    Ostrowski, L.E.5    Conner, G.E.6
  • 29
    • 33846275259 scopus 로고    scopus 로고
    • Inaugural article: Lung development and repair: Contribution of the ciliated lineage
    • Rawlins EL, Ostrowski LE, Randell SH, Hogan BL. Inaugural article: Lung development and repair: Contribution of the ciliated lineage. Proc Natl Acad Sci USA 2007; 104: 410-417.
    • (2007) Proc Natl Acad Sci USA , vol.104 , pp. 410-417
    • Rawlins, E.L.1    Ostrowski, L.E.2    Randell, S.H.3    Hogan, B.L.4
  • 31
    • 0036222250 scopus 로고    scopus 로고
    • Functional evidence of CFTR gene transfer in nasal epithelium of cystic fibrosis mice in vivo following luminal application of DNA complexes targeted to the serpin-enzyme complex receptor
    • Ziady AG, Kelley TJ, Milliken E, Ferkol T, Davis PB. Functional evidence of CFTR gene transfer in nasal epithelium of cystic fibrosis mice in vivo following luminal application of DNA complexes targeted to the serpin-enzyme complex receptor. Mol Ther 2002; 5: 413-419.
    • (2002) Mol Ther , vol.5 , pp. 413-419
    • Ziady, A.G.1    Kelley, T.J.2    Milliken, E.3    Ferkol, T.4    Davis, P.B.5
  • 32
    • 0036431592 scopus 로고    scopus 로고
    • Recovery of airway cystic fibrosis transmembrane conductance regulator function in mice with cystic fibrosis after single-dose lentivirus-mediated gene transfer
    • Limberis M, Anson DS, Fuller M, Parsons DW. Recovery of airway cystic fibrosis transmembrane conductance regulator function in mice with cystic fibrosis after single-dose lentivirus-mediated gene transfer. Hum Gene Ther 2002; 13: 1961-1970.
    • (2002) Hum Gene Ther , vol.13 , pp. 1961-1970
    • Limberis, M.1    Anson, D.S.2    Fuller, M.3    Parsons, D.W.4
  • 33
    • 0027967986 scopus 로고
    • Inefficient gene transfer by adenovirus vector to cystic fibrosis airway epithelia of mice and humans
    • Grubb BR, Pickles RJ, Ye H, Yankaskas JR, Vick RN, Engelhardt JF et al. Inefficient gene transfer by adenovirus vector to cystic fibrosis airway epithelia of mice and humans. Nature 1994; 371: 802-806.
    • (1994) Nature , vol.371 , pp. 802-806
    • Grubb, B.R.1    Pickles, R.J.2    Ye, H.3    Yankaskas, J.R.4    Vick, R.N.5    Engelhardt, J.F.6
  • 34
    • 0032506749 scopus 로고    scopus 로고
    • Enhanced in vivo airway gene transfer via transient modification of host barrier properties with a surface-active agent
    • Parsons DW, Grubb BR, Johnson LG, Boucher RC. Enhanced in vivo airway gene transfer via transient modification of host barrier properties with a surface-active agent. Hum Gene Ther 1998; 9 2661-2672.
    • (1998) Hum Gene Ther , vol.9 , pp. 2661-2672
    • Parsons, D.W.1    Grubb, B.R.2    Johnson, L.G.3    Boucher, R.C.4
  • 35
    • 0025789705 scopus 로고
    • Molecular cloning and sequence analysis of the murine cDNA for the cystic fibrosis transmembrane conductance regulator
    • Yorifuji T, Lemna WK, Ballard CF, Rosenbloom CL, Rozmahel R, Plavsic N et al. Molecular cloning and sequence analysis of the murine cDNA for the cystic fibrosis transmembrane conductance regulator. Genomics 1991; 10: 547-550.
    • (1991) Genomics , vol.10 , pp. 547-550
    • Yorifuji, T.1    Lemna, W.K.2    Ballard, C.F.3    Rosenbloom, C.L.4    Rozmahel, R.5    Plavsic, N.6
  • 36
    • 0032522598 scopus 로고    scopus 로고
    • Comparison of the gating behaviour of human and murine cystic fibrosis transmembrane conductance regulator Cla channels expressed in mammalian cells
    • Lansdell KA, Delaney SJ, Lunn DP, Thomson SA, Sheppard DN, Wainwright BJ. Comparison of the gating behaviour of human and murine cystic fibrosis transmembrane conductance regulator Cla channels expressed in mammalian cells. J Physiol 1998; 508 (Part 2): 379-392.
    • (1998) J Physiol , vol.508 , Issue.PART 2 , pp. 379-392
    • Lansdell, K.A.1    Delaney, S.J.2    Lunn, D.P.3    Thomson, S.A.4    Sheppard, D.N.5    Wainwright, B.J.6
  • 37
    • 2542500548 scopus 로고    scopus 로고
    • Cystic fibrosis transmembrane conductance regulator differentially regulates human and mouse epithelial sodium channels in Xenopus oocytes
    • Yan W, Samaha FF, Ramkumar M, Kleyman TR, Rubenstein RC. Cystic fibrosis transmembrane conductance regulator differentially regulates human and mouse epithelial sodium channels in Xenopus oocytes. J Biol Chem 2004; 279: 23183-23192.
    • (2004) J Biol Chem , vol.279 , pp. 23183-23192
    • Yan, W.1    Samaha, F.F.2    Ramkumar, M.3    Kleyman, T.R.4    Rubenstein, R.C.5
  • 38
    • 0030799599 scopus 로고    scopus 로고
    • Incomplete rescue of cystic fibrosis transmembrane conductance regulator deficient mice by the human CFTR cDNA
    • Rozmahel R, Gyomorey K, Plyte S, Nguyen V, Wilschanski M, Durie P et al. Incomplete rescue of cystic fibrosis transmembrane conductance regulator deficient mice by the human CFTR cDNA. Hum Mol Genet 1997; 6: 1153-1162.
    • (1997) Hum Mol Genet , vol.6 , pp. 1153-1162
    • Rozmahel, R.1    Gyomorey, K.2    Plyte, S.3    Nguyen, V.4    Wilschanski, M.5    Durie, P.6
  • 39
    • 0028557095 scopus 로고
    • Correction of lethal intestinal defect in a mouse model of cystic fibrosis by human CFTR
    • Zhou L, Dey CR, Wert SE, DuVall MD, Frizzell RA, Whitsett JA. Correction of lethal intestinal defect in a mouse model of cystic fibrosis by human CFTR. Science 1994; 266: 1705-1708.
    • (1994) Science , vol.266 , pp. 1705-1708
    • Zhou, L.1    Dey, C.R.2    Wert, S.E.3    DuVall, M.D.4    Frizzell, R.A.5    Whitsett, J.A.6
  • 40
    • 0029785795 scopus 로고    scopus 로고
    • A delta F508 mutation in mouse cystic fibrosis transmembrane conductance regulator results in a temperature-sensitive processing defect in vivo
    • French PJ, van Doorninck JH, Peters RH, Verbeek E, Ameen NA, Marino CR et al. A delta F508 mutation in mouse cystic fibrosis transmembrane conductance regulator results in a temperature-sensitive processing defect in vivo. J Clin Invest 1996; 98: 1304-1312.
    • (1996) J Clin Invest , vol.98 , pp. 1304-1312
    • French, P.J.1    van Doorninck, J.H.2    Peters, R.H.3    Verbeek, E.4    Ameen, N.A.5    Marino, C.R.6
  • 41
    • 0033600763 scopus 로고    scopus 로고
    • Development of substituted Benzo[c]quinolizinium compounds as novel activators of the cystic fibrosis chloride channel
    • Becq F, Mettey Y, Gray MA, Galietta LJ, Dormer RL, Merten M et al. Development of substituted Benzo[c]quinolizinium compounds as novel activators of the cystic fibrosis chloride channel. J Biol Chem 1999; 274: 27415-27425.
    • (1999) J Biol Chem , vol.274 , pp. 27415-27425
    • Becq, F.1    Mettey, Y.2    Gray, M.A.3    Galietta, L.J.4    Dormer, R.L.5    Merten, M.6
  • 43
    • 0033721158 scopus 로고    scopus 로고
    • Airway gene transfer in mouse nasal-airways: Importance of identification of epithelial type for assessment of gene transfer
    • Parsons DW, Hopkins PJ, Bourne AJ, Boucher RC, Martin AJ. Airway gene transfer in mouse nasal-airways: Importance of identification of epithelial type for assessment of gene transfer. Gene Therapy 2000; 7: 1810-1815.
    • (2000) Gene Therapy , vol.7 , pp. 1810-1815
    • Parsons, D.W.1    Hopkins, P.J.2    Bourne, A.J.3    Boucher, R.C.4    Martin, A.J.5
  • 44
    • 0030920951 scopus 로고    scopus 로고
    • Increased contact time improves adenovirus-mediated CFTR gene transfer to nasal epithelium of CF mice
    • Jiang C, Akita GY, Colledge WH, Ratcliff RA, Evans MJ, Hehir KM et al. Increased contact time improves adenovirus-mediated CFTR gene transfer to nasal epithelium of CF mice. Hum Gene Ther 1997; 8 671-680.
    • (1997) Hum Gene Ther , vol.8 , pp. 671-680
    • Jiang, C.1    Akita, G.Y.2    Colledge, W.H.3    Ratcliff, R.A.4    Evans, M.J.5    Hehir, K.M.6
  • 46
    • 0036012525 scopus 로고    scopus 로고
    • Bioelectric measurement of CFTR function in mice
    • Grubb BR. Bioelectric measurement of CFTR function in mice. Methods Mol Med 2002; 70: 525-535.
    • (2002) Methods Mol Med , vol.70 , pp. 525-535
    • Grubb, B.R.1


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