A ΔF508 mutation in mouse cystic fibrosis transmembrane conductance regulator results in a temperature-sensitive processing defect in vivo

Journal of Clinical Investigation

Volumn 98, Issue 6, 1996, Pages 1304-1312

  French, Pim J ^a   Van Doorninck, J Hikke ^a   Peters, Richard H P C ^a   Verbeek, Elly ^b   Ameen, Nadia A ^c   Marino, Christopher R ^d   De Jonge, Hugo R ^b   Bijman, Jan ^a   Scholte, Bob J ^a,b  

^a ERASMUS MEDICAL CENTER   (Netherlands)

^b ERASMUS UNIVERSITY ROTTERDAM   (Netherlands)

^c UNIVERSITY OF MIAMI   (United States)

^d UNIVERSITY OF TENNESSEE HEALTH SCIENCE CENTER   (United States)

Author keywords

animal models; antibody; chloride channel; cystic fibrosis; patch clamp

Indexed keywords

CHLORIDE CHANNEL; TRANSMEMBRANE CONDUCTANCE REGULATOR;

ANIMAL CELL; ANIMAL EXPERIMENT; ANIMAL MODEL; ARTICLE; COMPLEX FORMATION; CONTROLLED STUDY; CYSTIC FIBROSIS; EPITHELIUM CELL; GENE DELETION; GENE MUTATION; GENETIC TRANSCRIPTION; IN VIVO STUDY; INTESTINE CRYPT; INTRON; MOUSE; NONHUMAN; PATCH CLAMP; PRIORITY JOURNAL; TEMPERATURE SENSITIVE MUTANT;

EID: 0029785795     PISSN: 00219738     EISSN: None     Source Type: Journal    
DOI: 10.1172/JCI118917     Document Type: Article

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