-
1
-
-
10944273371
-
Specificity of prion assembly in vivo
-
Bagriantsev, S., and S. W. Liebman. 2004. Specificity of prion assembly in vivo. J. Biol. Chem. 279:51042-51048.
-
(2004)
J. Biol. Chem
, vol.279
, pp. 51042-51048
-
-
Bagriantsev, S.1
Liebman, S.W.2
-
2
-
-
0028997297
-
Non-genetic propagation of strain-specific properties of scrapie prion protein
-
Bessen, R. A., D. A. Kocisko, G. J. Raymond, S. Nandan, P. T. Lansbury, and B. Caughey. 1995. Non-genetic propagation of strain-specific properties of scrapie prion protein. Nature 375:698-700.
-
(1995)
Nature
, vol.375
, pp. 698-700
-
-
Bessen, R.A.1
Kocisko, D.A.2
Raymond, G.J.3
Nandan, S.4
Lansbury, P.T.5
Caughey, B.6
-
3
-
-
0026558780
-
Identification of two biologically distinct strains of transmissible mink encephalopathy in hamsters
-
Bessen, R. A., and R. F. Marsh. 1992. Identification of two biologically distinct strains of transmissible mink encephalopathy in hamsters. J. Gen. Virol. 73(Pt. 2):329-334.
-
(1992)
J. Gen. Virol
, vol.73
, Issue.PART. 2
, pp. 329-334
-
-
Bessen, R.A.1
Marsh, R.F.2
-
4
-
-
31044445005
-
Prion variant maintained only at high levels of the Hsp104 disaggregase
-
Borchsenius, A. S., S. Muller, G. P. Newnam, S. G. Inge-Vechtomov, and Y. O. Chernoff. 2006. Prion variant maintained only at high levels of the Hsp104 disaggregase. Curr. Genet. 49:21-29.
-
(2006)
Curr. Genet
, vol.49
, pp. 21-29
-
-
Borchsenius, A.S.1
Muller, S.2
Newnam, G.P.3
Inge-Vechtomov, S.G.4
Chernoff, Y.O.5
-
5
-
-
0035803490
-
-
Borchsenius, A. S., R. D. Wegrzyn, G. P. Newnam, S. G. Inge-Vechtomov, and Y. O. Chernoff. 2001. Yeast prion protein derivative defective in aggregate shearing and production of new 'seeds'. EMBO J. 20:6683-6691.
-
Borchsenius, A. S., R. D. Wegrzyn, G. P. Newnam, S. G. Inge-Vechtomov, and Y. O. Chernoff. 2001. Yeast prion protein derivative defective in aggregate shearing and production of new 'seeds'. EMBO J. 20:6683-6691.
-
-
-
-
6
-
-
0036215385
-
Similar and divergent features in mammalian and yeast prions
-
Bousset, L., and R. Melki. 2002. Similar and divergent features in mammalian and yeast prions. Microbes Infect. 4:461-469.
-
(2002)
Microbes Infect
, vol.4
, pp. 461-469
-
-
Bousset, L.1
Melki, R.2
-
7
-
-
0028235176
-
Human spongiform encephalopathy: The National Institutes of Health series of 300 cases of experimentally transmitted disease
-
Brown, P., C. J. Gibbs, Jr., P. Rodgers-Johnson, D. M. Asher, M. P. Sulima, A. Bacote, L. G. Goldfarb, and D. C. Gajdusek. 1994. Human spongiform encephalopathy: the National Institutes of Health series of 300 cases of experimentally transmitted disease. Ann. Neurol. 35:513-529.
-
(1994)
Ann. Neurol
, vol.35
, pp. 513-529
-
-
Brown, P.1
Gibbs Jr., C.J.2
Rodgers-Johnson, P.3
Asher, D.M.4
Sulima, M.P.5
Bacote, A.6
Goldfarb, L.G.7
Gajdusek, D.C.8
-
8
-
-
27544439092
-
Transgenic mice expressing bovine PrP with a four extra repeat octapeptide insert mutation show a spontaneous, non-transmissible, neurodegenerative disease and an expedited course of BSE infection
-
Castilla, J., A. Gutierrez-Adan, A. Bran, B. Pintado, F. J. Salguero, B. Parra, F. D. Segundo, M. A. Ramirez, A. Rabano, M. J. Cano, and J. M. Torres. 2005. Transgenic mice expressing bovine PrP with a four extra repeat octapeptide insert mutation show a spontaneous, non-transmissible, neurodegenerative disease and an expedited course of BSE infection. FEBS Lett. 579:6237-6246.
-
(2005)
FEBS Lett
, vol.579
, pp. 6237-6246
-
-
Castilla, J.1
Gutierrez-Adan, A.2
Bran, A.3
Pintado, B.4
Salguero, F.J.5
Parra, B.6
Segundo, F.D.7
Ramirez, M.A.8
Rabano, A.9
Cano, M.J.10
Torres, J.M.11
-
9
-
-
0030768832
-
Allelic origin of the abnormal prion protein isoform in familial prion diseases
-
Chen, S. G., P. Parchi, P. Brown, S. Capellari, W. Zou, E. J. Cochran, C. L. Vnencak-Jones, J. Julien, C. Vital, J. Mikol, E. Lugaresi, L. Autilio-Gambetti, and P. Gambetti. 1997. Allelic origin of the abnormal prion protein isoform in familial prion diseases. Nat. Med. 3:1009-1015.
-
(1997)
Nat. Med
, vol.3
, pp. 1009-1015
-
-
Chen, S.G.1
Parchi, P.2
Brown, P.3
Capellari, S.4
Zou, W.5
Cochran, E.J.6
Vnencak-Jones, C.L.7
Julien, J.8
Vital, C.9
Mikol, J.10
Lugaresi, E.11
Autilio-Gambetti, L.12
Gambetti, P.13
-
12
-
-
0034625069
-
Accumulation of protease-resistant prion protein (PrP) and apoptosis of cerebellar granule cells in transgenic mice expressing a PrP insertional mutation
-
Chiesa, R., B. Drisaldi, E. Quaglio, A. Migheli, P. Piccardo, B. Ghetti, and D. A. Harris. 2000. Accumulation of protease-resistant prion protein (PrP) and apoptosis of cerebellar granule cells in transgenic mice expressing a PrP insertional mutation. Proc. Natl. Acad. Sci. USA 97:5574-5579.
-
(2000)
Proc. Natl. Acad. Sci. USA
, vol.97
, pp. 5574-5579
-
-
Chiesa, R.1
Drisaldi, B.2
Quaglio, E.3
Migheli, A.4
Piccardo, P.5
Ghetti, B.6
Harris, D.A.7
-
13
-
-
0032427904
-
Neurological illness in transgenic mice expressing a prion protein with an insertional mutation
-
Chiesa, R., P. Piccardo, B. Ghetti, and D. A. Harris. 1998. Neurological illness in transgenic mice expressing a prion protein with an insertional mutation. Neuron 21:1339-1351.
-
(1998)
Neuron
, vol.21
, pp. 1339-1351
-
-
Chiesa, R.1
Piccardo, P.2
Ghetti, B.3
Harris, D.A.4
-
14
-
-
0038128629
-
Molecular distinction between pathogenic and infectious properties of the prion protein
-
Chiesa, R., P. Piccardo, E. Quaglio, B. Drisaldi, S. L. Si-Hoe, M. Takao, B. Ghetti, and D. A. Harris. 2003. Molecular distinction between pathogenic and infectious properties of the prion protein. J. Virol. 77:7611-7622.
-
(2003)
J. Virol
, vol.77
, pp. 7611-7622
-
-
Chiesa, R.1
Piccardo, P.2
Quaglio, E.3
Drisaldi, B.4
Si-Hoe, S.L.5
Takao, M.6
Ghetti, B.7
Harris, D.A.8
-
15
-
-
0034916581
-
Prion diseases of humans and animals: Their causes and molecular basis
-
Collinge, J. 2001. Prion diseases of humans and animals: their causes and molecular basis. Annu. Rev. Neurosci. 24:519-550.
-
(2001)
Annu. Rev. Neurosci
, vol.24
, pp. 519-550
-
-
Collinge, J.1
-
16
-
-
3442890339
-
Octapeptide repeat insertions in the prion protein gene and early onset dementia
-
Croes, E. A., J. Theuns, J. J. Houwing-Duistermaat, B. Dermaut, K. Sleegers, G. Roks, M. Van den Broeck, B. van Harten, J. C. van Swieten, M. Cruts, C. Van Broeckhoven, and C. M. van Duijn. 2004. Octapeptide repeat insertions in the prion protein gene and early onset dementia. J. Neurol. Neurosurg. Psychiatry 75:1166-1170.
-
(2004)
J. Neurol. Neurosurg. Psychiatry
, vol.75
, pp. 1166-1170
-
-
Croes, E.A.1
Theuns, J.2
Houwing-Duistermaat, J.J.3
Dermaut, B.4
Sleegers, K.5
Roks, G.6
Van den Broeck, M.7
van Harten, B.8
van Swieten, J.C.9
Cruts, M.10
Van Broeckhoven, C.11
van Duijn, C.M.12
-
17
-
-
0032568793
-
A critical role for amino-terminal glutamine/asparagine repeats in the formation and propagation of a yeast prion
-
DePace, A. H., A. Santoso, P. Hillner, and J. S. Weissman. 1998. A critical role for amino-terminal glutamine/asparagine repeats in the formation and propagation of a yeast prion. Cell 93:1241-1252.
-
(1998)
Cell
, vol.93
, pp. 1241-1252
-
-
DePace, A.H.1
Santoso, A.2
Hillner, P.3
Weissman, J.S.4
-
21
-
-
0030482356
-
Genesis and variability of [PSI] prion factors in Saccharomyces cerevisiae
-
Derkatch, I. L., Y. O. Chernoff, V. V. Kushnirov, S. G. Inge-Vechtomov, and S. W. Liebman. 1996. Genesis and variability of [PSI] prion factors in Saccharomyces cerevisiae. Genetics 144:1375-1386.
-
(1996)
Genetics
, vol.144
, pp. 1375-1386
-
-
Derkatch, I.L.1
Chernoff, Y.O.2
Kushnirov, V.V.3
Inge-Vechtomov, S.G.4
Liebman, S.W.5
-
22
-
-
0003666095
-
-
Elsevier Academic Press, San Diego, CA
-
Guthrie, C., and G. Fink. 2004. Guide to yeast genetics and molecular and cell biology, vol. 194. Elsevier Academic Press, San Diego, CA.
-
(2004)
Guide to yeast genetics and molecular and cell biology
, vol.194
-
-
Guthrie, C.1
Fink, G.2
-
23
-
-
33244468109
-
Distinct glycoform ratios of protease resistant prion protein associated with PRNP point mutations
-
Hill, A. F., S. Joiner, J. A. Beck, T. A. Campbell, A. Dickinson, M. Poulter, J. D. Wadsworth, and J. Collinge. 2006. Distinct glycoform ratios of protease resistant prion protein associated with PRNP point mutations. Brain 129: 676-685.
-
(2006)
Brain
, vol.129
, pp. 676-685
-
-
Hill, A.F.1
Joiner, S.2
Beck, J.A.3
Campbell, T.A.4
Dickinson, A.5
Poulter, M.6
Wadsworth, J.D.7
Collinge, J.8
-
24
-
-
0037385558
-
Phenotypic variability in the brains of a family with a prion disease characterized by a 144-base pair insertion in the prion protein gene
-
King, A., L. Doey, M. Rossor, S. Mead, J. Collinge, and P. Lantos. 2003. Phenotypic variability in the brains of a family with a prion disease characterized by a 144-base pair insertion in the prion protein gene. Neuropathol. Appl. Neurobiol. 29:98-105.
-
(2003)
Neuropathol. Appl. Neurobiol
, vol.29
, pp. 98-105
-
-
King, A.1
Doey, L.2
Rossor, M.3
Mead, S.4
Collinge, J.5
Lantos, P.6
-
25
-
-
1642617641
-
Protein-only transmission of three yeast prion strains
-
King, C. Y., and R. Diaz-Avalos. 2004. Protein-only transmission of three yeast prion strains. Nature 428:319-323.
-
(2004)
Nature
, vol.428
, pp. 319-323
-
-
King, C.Y.1
Diaz-Avalos, R.2
-
27
-
-
0036459944
-
Mutations of the prion protein gene phenotypic spectrum
-
Kovács, G. G., G. Trabattoni, J. A. Hainfellner, J. W. Ironside, R. S. Knight, and H. Budka. 2002. Mutations of the prion protein gene phenotypic spectrum. J. Neurol. 249:1567-1582.
-
(2002)
J. Neurol
, vol.249
, pp. 1567-1582
-
-
Kovács, G.G.1
Trabattoni, G.2
Hainfellner, J.A.3
Ironside, J.W.4
Knight, R.S.5
Budka, H.6
-
28
-
-
20444474976
-
Structural insights into a yeast prion illuminate nucleation and strain diversity
-
Krishnan, R., and S. L. Lindquist. 2005. Structural insights into a yeast prion illuminate nucleation and strain diversity. Nature 435:765-772.
-
(2005)
Nature
, vol.435
, pp. 765-772
-
-
Krishnan, R.1
Lindquist, S.L.2
-
30
-
-
0034723391
-
Creating a protein-based element of inheritance
-
Li, L., and S. Lindquist. 2000. Creating a protein-based element of inheritance. Science 287:661-664.
-
(2000)
Science
, vol.287
, pp. 661-664
-
-
Li, L.1
Lindquist, S.2
-
31
-
-
0033527045
-
Oligopeptide-repeat expansions modulate 'protein-only' inheritance in yeast
-
Liu, J. J., and S. Lindquist. 1999. Oligopeptide-repeat expansions modulate 'protein-only' inheritance in yeast. Nature 400:573-576.
-
(1999)
Nature
, vol.400
, pp. 573-576
-
-
Liu, J.J.1
Lindquist, S.2
-
33
-
-
34249941302
-
Copper and the prion protein: Methods, structures, function, and disease
-
Millhauser, G. L. 2007. Copper and the prion protein: methods, structures, function, and disease. Annu. Rev. Phys. Chem. 58:299-320.
-
(2007)
Annu. Rev. Phys. Chem
, vol.58
, pp. 299-320
-
-
Millhauser, G.L.1
-
34
-
-
33644540192
-
Octapeptide repeat insertions increase the rate of protease-resistant prion protein formation
-
Moore, R. A., C. Herzog, J. Errett, D. A. Kocisko, K. M. Arnold, S. F. Hayes, and S. A. Priola. 2006. Octapeptide repeat insertions increase the rate of protease-resistant prion protein formation. Protein Sci. 15:609-619.
-
(2006)
Protein Sci
, vol.15
, pp. 609-619
-
-
Moore, R.A.1
Herzog, C.2
Errett, J.3
Kocisko, D.A.4
Arnold, K.M.5
Hayes, S.F.6
Priola, S.A.7
-
35
-
-
0028953840
-
Yeast vectors for the controlled expression of heterologous proteins in different genetic backgrounds
-
Mumberg, D., R. Muller, and M. Funk. 1995. Yeast vectors for the controlled expression of heterologous proteins in different genetic backgrounds. Gene 156:119-122.
-
(1995)
Gene
, vol.156
, pp. 119-122
-
-
Mumberg, D.1
Muller, R.2
Funk, M.3
-
36
-
-
0036310663
-
Guanidine hydrochloride inhibits the generation of prion "seeds" but not prion protein aggregation in yeast
-
Ness, F., P. Ferreira, B. S. Cox, and M. F. Tuite. 2002. Guanidine hydrochloride inhibits the generation of prion "seeds" but not prion protein aggregation in yeast. Mol. Cell. Biol. 22:5593-5605.
-
(2002)
Mol. Cell. Biol
, vol.22
, pp. 5593-5605
-
-
Ness, F.1
Ferreira, P.2
Cox, B.S.3
Tuite, M.F.4
-
38
-
-
0035341212
-
Oligopeptide repeats in the yeast protein Sup35p stabilize intermolecular prion interactions
-
Parham, S. N., C. G. Resende, and M. F. Tuite. 2001. Oligopeptide repeats in the yeast protein Sup35p stabilize intermolecular prion interactions. EMBO J. 20:2111-2119.
-
(2001)
EMBO J
, vol.20
, pp. 2111-2119
-
-
Parham, S.N.1
Resende, C.G.2
Tuite, M.F.3
-
39
-
-
0029780647
-
Support for the prion hypothesis for inheritance of a phenotypic trait in yeast
-
Patino, M. M., J. J. Liu, J. R. Glover, and S. Lindquist. 1996. Support for the prion hypothesis for inheritance of a phenotypic trait in yeast. Science 273: 622-626.
-
(1996)
Science
, vol.273
, pp. 622-626
-
-
Patino, M.M.1
Liu, J.J.2
Glover, J.R.3
Lindquist, S.4
-
41
-
-
0027520888
-
Conversion of truncated and elongated prion proteins into the scrapie isoform in cultured cells
-
Rogers, M., F. Yehiely, M. Scott, and S. B. Prusiner. 1993. Conversion of truncated and elongated prion proteins into the scrapie isoform in cultured cells. Proc. Natl. Acad. Sci. USA 90:3182-3186.
-
(1993)
Proc. Natl. Acad. Sci. USA
, vol.90
, pp. 3182-3186
-
-
Rogers, M.1
Yehiely, F.2
Scott, M.3
Prusiner, S.B.4
-
42
-
-
0034758487
-
The role of conformational flexibility in prion propagation and maintenance for Sup35p
-
Scheibel, T., and S. L. Lindquist. 2001. The role of conformational flexibility in prion propagation and maintenance for Sup35p. Nat. Struct. Biol. 8:958-962.
-
(2001)
Nat. Struct. Biol
, vol.8
, pp. 958-962
-
-
Scheibel, T.1
Lindquist, S.L.2
-
43
-
-
1642633056
-
Conformational variations in an infectious protein determine prion strain differences
-
Tanaka, M., P. Chien, N. Naber, R. Cooke, and J. S. Weissman. 2004. Conformational variations in an infectious protein determine prion strain differences. Nature 428:323-328.
-
(2004)
Nature
, vol.428
, pp. 323-328
-
-
Tanaka, M.1
Chien, P.2
Naber, N.3
Cooke, R.4
Weissman, J.S.5
-
44
-
-
17044435107
-
Mechanism of cross-species prion transmission: An infectious conformation compatible with two highly divergent yeast prion proteins
-
Tanaka, M., P. Chien, K. Yonekura, and J. S. Weissman. 2005. Mechanism of cross-species prion transmission: an infectious conformation compatible with two highly divergent yeast prion proteins. Cell 121:49-62.
-
(2005)
Cell
, vol.121
, pp. 49-62
-
-
Tanaka, M.1
Chien, P.2
Yonekura, K.3
Weissman, J.S.4
-
45
-
-
0030011971
-
Experimental transmission of Creutzfeldt-Jakob disease and related diseases to rodents
-
Tateishi, J., T. Kitamoto, M. Z. Hoque, and H. Furukawa. 1996. Experimental transmission of Creutzfeldt-Jakob disease and related diseases to rodents. Neurology 46:532-537.
-
(1996)
Neurology
, vol.46
, pp. 532-537
-
-
Tateishi, J.1
Kitamoto, T.2
Hoque, M.Z.3
Furukawa, H.4
-
47
-
-
31444452768
-
The battle of the fold: Chaperones take on prions
-
True, H. L. 2006. The battle of the fold: chaperones take on prions. Trends Genet. 22:110-117.
-
(2006)
Trends Genet
, vol.22
, pp. 110-117
-
-
True, H.L.1
-
49
-
-
0036403732
-
Prions as protein-based genetic elements
-
Uptain, S. M., and S. Lindquist. 2002. Prions as protein-based genetic elements. Annu. Rev. Microbiol. 56:703-741.
-
(2002)
Annu. Rev. Microbiol
, vol.56
, pp. 703-741
-
-
Uptain, S.M.1
Lindquist, S.2
-
50
-
-
0035890264
-
+] are distinguished by their efficiencies of prion-mediated conformational conversion
-
+] are distinguished by their efficiencies of prion-mediated conformational conversion. EMBO J. 20:6236-6245.
-
(2001)
EMBO J
, vol.20
, pp. 6236-6245
-
-
Uptain, S.M.1
Sawicki, G.J.2
Caughey, B.3
Lindquist, S.4
-
51
-
-
0035814903
-
Local structural plasticity of the prion protein. Analysis of NMR relaxation dynamics
-
Viles, J. H., D. Donne, G. Kroon, S. B. Prasiner, F. E. Cohen, H. J. Dyson, and P. E. Wright. 2001. Local structural plasticity of the prion protein. Analysis of NMR relaxation dynamics. Biochemistry 40:2743-2753.
-
(2001)
Biochemistry
, vol.40
, pp. 2743-2753
-
-
Viles, J.H.1
Donne, D.2
Kroon, G.3
Prasiner, S.B.4
Cohen, F.E.5
Dyson, H.J.6
Wright, P.E.7
-
52
-
-
0141849458
-
Molecular and clinical classification of human prion disease
-
Wadsworth, J. D., A. F. Hill, J. A. Beck, and J. Collinge. 2003. Molecular and clinical classification of human prion disease. Br. Med. Bull. 66:241-254.
-
(2003)
Br. Med. Bull
, vol.66
, pp. 241-254
-
-
Wadsworth, J.D.1
Hill, A.F.2
Beck, J.A.3
Collinge, J.4
-
53
-
-
33744959528
-
Prion proteins with insertion mutations have altered N-terminal conformation and increased ligand binding activity and are more susceptible to oxidative attack
-
Yin, S., S. Yu, C. Li, P. Wong, B. Chang, F. Xiao, S. C. Kang, H. Yan, G. Xiao, J. Grassi, P. Tien, and M. S. Sy. 2006. Prion proteins with insertion mutations have altered N-terminal conformation and increased ligand binding activity and are more susceptible to oxidative attack. J. Biol. Chem. 281: 10698-10705.
-
(2006)
J. Biol. Chem
, vol.281
, pp. 10698-10705
-
-
Yin, S.1
Yu, S.2
Li, C.3
Wong, P.4
Chang, B.5
Xiao, F.6
Kang, S.C.7
Yan, H.8
Xiao, G.9
Grassi, J.10
Tien, P.11
Sy, M.S.12
-
54
-
-
0010496389
-
To stick or not to stick: Prion domains from yeast to mammals
-
Zhouravleva, G., V. V. Alenin, S. Inge-Vechtomov, and Y. O. Chernoff. 2002. To stick or not to stick: prion domains from yeast to mammals. Recent Res. Dev. Mol. Cell. Biol. 3:185-218.
-
(2002)
Recent Res. Dev. Mol. Cell. Biol
, vol.3
, pp. 185-218
-
-
Zhouravleva, G.1
Alenin, V.V.2
Inge-Vechtomov, S.3
Chernoff, Y.O.4
|