Accumulation of protease-resistant prion protein (PrP) and apoptosis of cerebellar granule cells in transgenic mice expressing a PrP insertional mutation

Proceedings of the National Academy of Sciences of the United States of America

Volumn 97, Issue 10, 2000, Pages 5574-5579

  Chiesa, Roberto ^a   Drisaldi, Bettina ^a   Quaglio, Elena ^a   Migheli, Antonio ^b   Piccardo, Pedro ^c   Ghetti, Bernardino ^c   Harris, David A ^a  

^a WASHINGTON UNIVERSITY SCHOOL OF MEDICINE   (United States)

^b UNIVERSITY OF TURIN   (Italy)

^c INDIANA UNIVERSITY   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

PRION PROTEIN;

ANIMAL MODEL; ANIMAL TISSUE; APOPTOSIS; ARTICLE; ATAXIA; GENE MUTATION; GRANULE CELL; HEMIZYGOSITY; HOMOZYGOSITY; MOUSE; NONHUMAN; PRIORITY JOURNAL; SCRAPIE; TRANSGENIC MOUSE;

ANIMALS; APOPTOSIS; CEREBELLUM; ENDOPEPTIDASES; HOMOZYGOTE; HUMANS; MICE; MICE, INBRED C57BL; MICE, INBRED CBA; MICE, INBRED STRAINS; MICE, TRANSGENIC; MUTAGENESIS, INSERTIONAL; NEURONS; PRION DISEASES; PRIONS; RECOMBINANT PROTEINS; SCRAPIE;

ANIMALIA; ATAXIA; MUS MUSCULUS;

EID: 0034625069     PISSN: 00278424     EISSN: None     Source Type: Journal    
DOI: 10.1073/pnas.97.10.5574     Document Type: Article

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