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Volumn 59, Issue 1, 2007, Pages 57-72

New perspective in long QT syndrome;Nuevas perspectivas en el síndrome de QT largo

Author keywords

Arrhythmias; Cardiac channelopathies; Long QT syndrome; Sudden death

Indexed keywords

AMANTADINE; AMIODARONE; AMITRIPTYLINE; AZITHROMYCIN; CIPROFLOXACIN; CITALOPRAM; CLARITHROMYCIN; CLINDAMYCIN; DOBUTAMINE; DOPAMINE; DROPERIDOL; EPHEDRINE; FLUOXETINE; FOSCARNET; HALOPERIDOL; IMIPRAMINE; ION CHANNEL; LEVOFLOXACIN; NORADRENALIN; OCTREOTIDE; ONDANSETRON; PAROXETINE; QUINIDINE; RISPERIDONE; SALBUTAMOL; SALMETEROL; SIBUTRAMINE; SOTALOL; TERBUTALINE; UNINDEXED DRUG;

EID: 34249100209     PISSN: 00348376     EISSN: 00348376     Source Type: Journal    
DOI: None     Document Type: Review
Times cited : (3)

References (126)
  • 1
    • 1842425821 scopus 로고    scopus 로고
    • Sudden death in patients without structural heart disease
    • Wever EF, Robles de Medina EO. Sudden death in patients without structural heart disease. J Am Coll Cardiol 2004; 43: 1137-44.
    • (2004) J Am Coll Cardiol , vol.43 , pp. 1137-1144
    • Wever, E.F.1    Robles de Medina, E.O.2
  • 3
    • 0034622658 scopus 로고    scopus 로고
    • Sudden cardiac death with apparently normal heart
    • Chugh SS, Kelly KL, Titus JL. Sudden cardiac death with apparently normal heart. Circulation. 2000; 102: 649-54.
    • (2000) Circulation , vol.102 , pp. 649-654
    • Chugh, S.S.1    Kelly, K.L.2    Titus, J.L.3
  • 5
    • 25444529765 scopus 로고    scopus 로고
    • Molecular physiology of cardiac repolarization
    • Nerbonne JM, Kass RS. Molecular physiology of cardiac repolarization. Physiol Rev 2005; 85: 1205-53.
    • (2005) Physiol Rev , vol.85 , pp. 1205-1253
    • Nerbonne, J.M.1    Kass, R.S.2
  • 8
    • 0029116230 scopus 로고
    • Cardiac sodium channel mutations in patients with long QT syndrome, an inherited cardiac arrhythmia
    • Wang Q, Shen J, Li Z, et al. Cardiac sodium channel mutations in patients with long QT syndrome, an inherited cardiac arrhythmia. Hum Mol Genet 1995; 4: 1603-7.
    • (1995) Hum Mol Genet , vol.4 , pp. 1603-1607
    • Wang, Q.1    Shen, J.2    Li, Z.3
  • 9
    • 0024917731 scopus 로고
    • Torsade de pointes during an atropine sulfate test in a patient with congenital long QT syndrome
    • Beccaria E, Brun S, Gaita F, Giustetto C, Conti M. Torsade de pointes during an atropine sulfate test in a patient with congenital long QT syndrome. Cardiología 1989; 34: 1039-43.
    • (1989) Cardiología , vol.34 , pp. 1039-1043
    • Beccaria, E.1    Brun, S.2    Gaita, F.3    Giustetto, C.4    Conti, M.5
  • 10
    • 49749174698 scopus 로고
    • Congenital deaf-mutism, functional heart disease with prolongation of the Q-T interval and sudden death
    • Jervell A, Lange-Nielsen F. Congenital deaf-mutism, functional heart disease with prolongation of the Q-T interval and sudden death. Am Heart J 1957; 54: 59-68.
    • (1957) Am Heart J , vol.54 , pp. 59-68
    • Jervell, A.1    Lange-Nielsen, F.2
  • 11
    • 34249065662 scopus 로고
    • Rare cardiac arrhythmias of the pediatric age. I. Repetitive Paroxysmal Tachycardia
    • Romano C, Gemme G, Pongiglione R. Rare cardiac arrhythmias of the pediatric age. I. Repetitive Paroxysmal Tachycardia. Minerva Pediatr 1963; 15: 1155-64.
    • (1963) Minerva Pediatr , vol.15 , pp. 1155-1164
    • Romano, C.1    Gemme, G.2    Pongiglione, R.3
  • 12
    • 0028905566 scopus 로고
    • SCN5A mutations associated with an inherited cardiac arrhythmia, long QT syndrome
    • Wang Q, Shen J, Splawski I, et al. SCN5A mutations associated with an inherited cardiac arrhythmia, long QT syndrome. Cell 1995; 80: 805-11.
    • (1995) Cell , vol.80 , pp. 805-811
    • Wang, Q.1    Shen, J.2    Splawski, I.3
  • 13
    • 29144494740 scopus 로고    scopus 로고
    • Genetic testing in the long QT syndrome: Development and validation of an efficient approach to genotyping in clinical practice
    • Napolitano C, Priori SG, Schwartz PJ, et al. Genetic testing in the long QT syndrome: development and validation of an efficient approach to genotyping in clinical practice. JAMA 2005; 294: 2975-80.
    • (2005) JAMA , vol.294 , pp. 2975-2980
    • Napolitano, C.1    Priori, S.G.2    Schwartz, P.J.3
  • 14
    • 0034213745 scopus 로고    scopus 로고
    • Molecular basis of functional voltage-gated K+ channel diversity in the mammalian myocardium
    • Nerbonne JM. Molecular basis of functional voltage-gated K+ channel diversity in the mammalian myocardium. J Physiol 2000; 525 Pt 2: 285-98.
    • (2000) J Physiol , vol.525 , Issue.PART 2 , pp. 285-298
    • Nerbonne, J.M.1
  • 17
    • 0008530413 scopus 로고    scopus 로고
    • Potassium channel subunits encoded by the KCNE gene family: Physiology and pathophysiology of the MinK-related peptides (MiRPs)
    • Abbott GW, Goldstein SA. Potassium channel subunits encoded by the KCNE gene family: physiology and pathophysiology of the MinK-related peptides (MiRPs). Mol Interv 2001; 1: 95-107.
    • (2001) Mol Interv , vol.1 , pp. 95-107
    • Abbott, G.W.1    Goldstein, S.A.2
  • 18
    • 0037127028 scopus 로고    scopus 로고
    • Requirement of a macromolecular signaling complex for beta adrenergic receptor modulation of the KCNQ1-KCNE1 potassium channel
    • Marx SO, Kurokawa J, Reiken S, et al. Requirement of a macromolecular signaling complex for beta adrenergic receptor modulation of the KCNQ1-KCNE1 potassium channel. Science 2002; 295: 496-9.
    • (2002) Science , vol.295 , pp. 496-499
    • Marx, S.O.1    Kurokawa, J.2    Reiken, S.3
  • 19
    • 0035043779 scopus 로고    scopus 로고
    • Another role for the sympathetic nervous system in the long QT syndrome?
    • Schwartz PJ. Another role for the sympathetic nervous system in the long QT syndrome? J Cardiovasc Electrophysiol 2001; 12: 500-2.
    • (2001) J Cardiovasc Electrophysiol , vol.12 , pp. 500-502
    • Schwartz, P.J.1
  • 20
    • 0033636506 scopus 로고    scopus 로고
    • Nomenclature of voltage-gated sodium channels
    • Goldin AL, Barchi RL, Caldwell JH, et al. Nomenclature of voltage-gated sodium channels. Neuron 2000; 28: 365-8.
    • (2000) Neuron , vol.28 , pp. 365-368
    • Goldin, A.L.1    Barchi, R.L.2    Caldwell, J.H.3
  • 21
    • 0026530472 scopus 로고
    • Primary structure and functional expression of the human cardiac tetrodotoxin-insensitive voltage-dependent sodium channel
    • Gellens ME, George AL, Jr., Chen LQ, et al. Primary structure and functional expression of the human cardiac tetrodotoxin-insensitive voltage-dependent sodium channel. Proc Natl Acad Sci USA 1992; 89: 554-8.
    • (1992) Proc Natl Acad Sci USA , vol.89 , pp. 554-558
    • Gellens, M.E.1    George Jr., A.L.2    Chen, L.Q.3
  • 22
    • 15044340142 scopus 로고    scopus 로고
    • Modulation of Na(v)1.5 by beta1- and beta3-subunit co-expression in mammalian cells
    • Ko SH, Lenkowski PW, Lee HC, Mounsey JP, Patel MK. Modulation of Na(v)1.5 by beta1- and beta3-subunit co-expression in mammalian cells. Pflugers Arch 2005; 449: 403-12.
    • (2005) Pflugers Arch , vol.449 , pp. 403-412
    • Ko, S.H.1    Lenkowski, P.W.2    Lee, H.C.3    Mounsey, J.P.4    Patel, M.K.5
  • 23
    • 1642370591 scopus 로고    scopus 로고
    • Distinct subcellular localization of different sodium channel alpha and beta subunits in single ventricular myocytes from mouse heart
    • Maier SK, Westenbroek RE, McCormick KA, Curtis R, Scheuer T, Catterall WA. Distinct subcellular localization of different sodium channel alpha and beta subunits in single ventricular myocytes from mouse heart. Circulation 2004; 109: 1421-7.
    • (2004) Circulation , vol.109 , pp. 1421-1427
    • Maier, S.K.1    Westenbroek, R.E.2    McCormick, K.A.3    Curtis, R.4    Scheuer, T.5    Catterall, W.A.6
  • 24
    • 0023276525 scopus 로고
    • Beta 2 subunits of sodium channels from vertebrate brain. Studies with subunit-specific antibodies
    • Wollner DA, Messner DJ, Catterall WA. Beta 2 subunits of sodium channels from vertebrate brain. Studies with subunit-specific antibodies. J Biol Chem 1987; 262: 14709-15.
    • (1987) J Biol Chem , vol.262 , pp. 14709-14715
    • Wollner, D.A.1    Messner, D.J.2    Catterall, W.A.3
  • 25
    • 0028972374 scopus 로고
    • Structure and function of the beta 2 subunit of brain sodium channels, a transmembrane glycoprotein with a CAM motif
    • Isom LL, Ragsdale DS, De Jongh KS, et al. Structure and function of the beta 2 subunit of brain sodium channels, a transmembrane glycoprotein with a CAM motif. Cell 1995; 83: 433-42.
    • (1995) Cell , vol.83 , pp. 433-442
    • Isom, L.L.1    Ragsdale, D.S.2    De Jongh, K.S.3
  • 26
    • 12944260700 scopus 로고    scopus 로고
    • Beta 3: An additional auxiliary subunit of the voltage-sensitive sodium channel that modulates channel gating with distinct kinetics
    • Morgan K, Stevens EB, Shah B, et al. Beta 3: an additional auxiliary subunit of the voltage-sensitive sodium channel that modulates channel gating with distinct kinetics. Proc Natl Acad Sci USA 2000; 97: 2308-13.
    • (2000) Proc Natl Acad Sci USA , vol.97 , pp. 2308-2313
    • Morgan, K.1    Stevens, E.B.2    Shah, B.3
  • 27
    • 0041419702 scopus 로고    scopus 로고
    • Sodium channel beta4, a new disulfide-linked auxiliary subunit with similarity to beta2
    • Yu FH, Westenbroek RE, Silos-Santiago I, et al. Sodium channel beta4, a new disulfide-linked auxiliary subunit with similarity to beta2. J Neurosci 2003; 23: 7577-85.
    • (2003) J Neurosci , vol.23 , pp. 7577-7585
    • Yu, F.H.1    Westenbroek, R.E.2    Silos-Santiago, I.3
  • 28
    • 0035830365 scopus 로고    scopus 로고
    • Genotype-phenotype correlation in the long-QT syndrome: Gene-specific triggers for life-threatening arrhythmias
    • Schwartz PJ, Priori SG, Spazzolini C, et al. Genotype-phenotype correlation in the long-QT syndrome: gene-specific triggers for life-threatening arrhythmias. Circulation 2001; 103: 89-95.
    • (2001) Circulation , vol.103 , pp. 89-95
    • Schwartz, P.J.1    Priori, S.G.2    Spazzolini, C.3
  • 29
    • 22044453803 scopus 로고    scopus 로고
    • Developmental aspects of long QT syndrome type 3 and Brugada syndrome on the basis of a single SCN5A mutation in childhood
    • Beaufort-Krol GC, van den Berg MP, Wilde AA, et al. Developmental aspects of long QT syndrome type 3 and Brugada syndrome on the basis of a single SCN5A mutation in childhood. J Am Coll Cardiol 2005; 46: 331-7.
    • (2005) J Am Coll Cardiol , vol.46 , pp. 331-337
    • Beaufort-Krol, G.C.1    van den Berg, M.P.2    Wilde, A.A.3
  • 30
    • 0242464931 scopus 로고    scopus 로고
    • Ankyrin-B mutation causes type 4 long-QT cardiac arrhythmia and sudden cardiac death
    • Mohler PJ, Schott JJ, Gramolini AO, et al. Ankyrin-B mutation causes type 4 long-QT cardiac arrhythmia and sudden cardiac death. Nature 2003; 421: 634-9.
    • (2003) Nature , vol.421 , pp. 634-639
    • Mohler, P.J.1    Schott, J.J.2    Gramolini, A.O.3
  • 31
    • 18944397275 scopus 로고    scopus 로고
    • Ankyrin-based cardiac arrhythmias: A new class of channelopathies due to loss of cellular targeting
    • Mohler PJ, Bennett V. Ankyrin-based cardiac arrhythmias: a new class of channelopathies due to loss of cellular targeting. Curr Opin Cardiol 2005; 20: 189-93.
    • (2005) Curr Opin Cardiol , vol.20 , pp. 189-193
    • Mohler, P.J.1    Bennett, V.2
  • 32
    • 2942695712 scopus 로고    scopus 로고
    • A cardiac arrhythmia syndrome caused by loss of ankyrin-B function
    • Mohler PJ, Splawski I, Napolitano C, et al. A cardiac arrhythmia syndrome caused by loss of ankyrin-B function. Proc Natl Acad Sci USA 2004; 101: 9137-42.
    • (2004) Proc Natl Acad Sci USA , vol.101 , pp. 9137-9142
    • Mohler, P.J.1    Splawski, I.2    Napolitano, C.3
  • 34
    • 0033574273 scopus 로고    scopus 로고
    • MiRP1 forms IKr potassium channels with HERG and is associated with cardiac arrhythmia
    • Abbott GW, Sesti F, Splawski I, et al. MiRP1 forms IKr potassium channels with HERG and is associated with cardiac arrhythmia. Cell 1999; 97: 175-87.
    • (1999) Cell , vol.97 , pp. 175-187
    • Abbott, G.W.1    Sesti, F.2    Splawski, I.3
  • 35
    • 0035907032 scopus 로고    scopus 로고
    • Mutations in Kir2.1 cause the developmental and episodic electrical phenotypes of Andersen's syndrome
    • Plaster NM, Tawil R, Tristani-Firouzi M, et al. Mutations in Kir2.1 cause the developmental and episodic electrical phenotypes of Andersen's syndrome. Cell 2001; 105: 511-19.
    • (2001) Cell , vol.105 , pp. 511-519
    • Plaster, N.M.1    Tawil, R.2    Tristani-Firouzi, M.3
  • 36
    • 32444450201 scopus 로고    scopus 로고
    • Andersen-Tawil syndrome: Prospective cohort analysis and expansion of the phenotype
    • Yoon G, Oberoi S, Tristani-Firouzi M, et al. Andersen-Tawil syndrome: Prospective cohort analysis and expansion of the phenotype. Am J Med Genet A 2006; 140: 312-21.
    • (2006) Am J Med Genet A , vol.140 , pp. 312-321
    • Yoon, G.1    Oberoi, S.2    Tristani-Firouzi, M.3
  • 37
    • 5344223383 scopus 로고    scopus 로고
    • Ca(V)1.2 calcium channel dysfunction causes a multisystem disorder including arrhythmia and autism
    • Splawski I, Timothy KW, Sharpe LM, et al. Ca(V)1.2 calcium channel dysfunction causes a multisystem disorder including arrhythmia and autism. Cell 2004; 119: 19-31.
    • (2004) Cell , vol.119 , pp. 19-31
    • Splawski, I.1    Timothy, K.W.2    Sharpe, L.M.3
  • 38
    • 20444426877 scopus 로고    scopus 로고
    • Severe arrhythmia disorder caused by cardiac L-type calcium channel mutations
    • discussion 8086-8
    • Splawski I, Timothy KW, Decher N, et al. Severe arrhythmia disorder caused by cardiac L-type calcium channel mutations. Proc Natl Acad Sci USA 2005; 102: 8089-96; discussion 8086-8.
    • (2005) Proc Natl Acad Sci USA , vol.102 , pp. 8089-8096
    • Splawski, I.1    Timothy, K.W.2    Decher, N.3
  • 40
    • 33644853794 scopus 로고    scopus 로고
    • The Jervell and Lange-Nielsen Syndrome
    • Natural History, Molecular Basis, and Clinical Outcome
    • Schwartz PJ, Spazzolini C, Crotti L, et al. The Jervell and Lange-Nielsen Syndrome. Natural History, Molecular Basis, and Clinical Outcome. Circulation 2006.
    • (2006) Circulation
    • Schwartz, P.J.1    Spazzolini, C.2    Crotti, L.3
  • 42
    • 21144457928 scopus 로고    scopus 로고
    • Inaccurate electrocardiographic interpretation of long QT: The majority of physicians cannot recognize a long QT when they see one
    • Viskin S, Rosovski U, Sands AJ, et al. Inaccurate electrocardiographic interpretation of long QT: the majority of physicians cannot recognize a long QT when they see one. Heart Rhythm 2005; 2: 569-74.
    • (2005) Heart Rhythm , vol.2 , pp. 569-574
    • Viskin, S.1    Rosovski, U.2    Sands, A.J.3
  • 43
    • 0345969487 scopus 로고
    • Importance of lead selection in QT interval measurement
    • Cowan JC, Yusoff K, Moore M, et al. Importance of lead selection in QT interval measurement. Am J Cardiol 1988; 61: 83-7.
    • (1988) Am J Cardiol , vol.61 , pp. 83-87
    • Cowan, J.C.1    Yusoff, K.2    Moore, M.3
  • 45
    • 33645997040 scopus 로고    scopus 로고
    • The role of sodium channel current in modulating transmural dispersion of repolarization and arrhythmogenesis
    • Antzelevitch C, Belardinelli L. The role of sodium channel current in modulating transmural dispersion of repolarization and arrhythmogenesis. J Cardiovasc Electrophysiol 2006; 17 (Suppl. 1): S79-S85.
    • (2006) J Cardiovasc Electrophysiol , vol.17 , Issue.SUPPL. 1
    • Antzelevitch, C.1    Belardinelli, L.2
  • 46
    • 10744226665 scopus 로고    scopus 로고
    • T wave peak-to-end interval and QT dispersion in acquired long QT syndrome: A new index for arrhythmogenicity
    • Yamaguchi M, Shimizu M, Ino H, et al. T wave peak-to-end interval and QT dispersion in acquired long QT syndrome: a new index for arrhythmogenicity. Clin Sci (Lond) 2003; 105: 671-6.
    • (2003) Clin Sci (Lond) , vol.105 , pp. 671-676
    • Yamaguchi, M.1    Shimizu, M.2    Ino, H.3
  • 47
    • 0028209226 scopus 로고
    • Dispersion of the QT interval. A marker of therapeutic efficacy in the idiopathic long QT syndrome
    • Priori SG, Napolitano C, Diehl L, Schwartz PJ. Dispersion of the QT interval. A marker of therapeutic efficacy in the idiopathic long QT syndrome. Circulation 1994; 89: 1681-9.
    • (1994) Circulation , vol.89 , pp. 1681-1689
    • Priori, S.G.1    Napolitano, C.2    Diehl, L.3    Schwartz, P.J.4
  • 51
    • 30344485732 scopus 로고    scopus 로고
    • T-wave alternans and the susceptibility to ventricular arrhythmias
    • Narayan SM. T-wave alternans and the susceptibility to ventricular arrhythmias. J Am Coll Cardiol 2006; 47: 269-81.
    • (2006) J Am Coll Cardiol , vol.47 , pp. 269-281
    • Narayan, S.M.1
  • 53
    • 10744225310 scopus 로고    scopus 로고
    • Long QT syndrome in neonates: Conduction disorders associated with HERG mutations and sinus bradycardia with KCNQ1 mutations
    • Lupoglazoff JM, Denjoy I, Villain E, et al. Long QT syndrome in neonates: conduction disorders associated with HERG mutations and sinus bradycardia with KCNQ1 mutations. J Am Coll Cardiol 2004; 43: 826-30.
    • (2004) J Am Coll Cardiol , vol.43 , pp. 826-830
    • Lupoglazoff, J.M.1    Denjoy, I.2    Villain, E.3
  • 54
    • 0023624610 scopus 로고    scopus 로고
    • Scott WA, Dick M, 2nd. Two:one atrioventricular block in infants with congenital long QT syndrome. Am J Cardiol 1987; 60: 1409-10.
    • Scott WA, Dick M, 2nd. Two:one atrioventricular block in infants with congenital long QT syndrome. Am J Cardiol 1987; 60: 1409-10.
  • 55
    • 0027273764 scopus 로고
    • The long QT syndrome in children. An international study of 287 patients
    • Garson A Jr., Dick M, 2nd, Fournier A, et al. The long QT syndrome in children. An international study of 287 patients. Circulation 1993; 87: 1866-72.
    • (1993) Circulation , vol.87 , pp. 1866-1872
    • Garson Jr., A.1    Dick 2nd, M.2    Fournier, A.3
  • 56
    • 0028877407 scopus 로고
    • Infants with long-QT syndrome and 2:1 atrioventricular block
    • Trippel DL, Parsons MK, Gillette PC. Infants with long-QT syndrome and 2:1 atrioventricular block. Am Heart J 1995; 130: 1130-4.
    • (1995) Am Heart J , vol.130 , pp. 1130-1134
    • Trippel, D.L.1    Parsons, M.K.2    Gillette, P.C.3
  • 58
    • 0025358150 scopus 로고
    • Persistent functional atrioventricular block in two patients with prolonged QT intervals: Elucidation of the mechanism of block
    • van Hare GF, Franz MR, Roge C, Scheinman MM. Persistent functional atrioventricular block in two patients with prolonged QT intervals: elucidation of the mechanism of block. Pacing Clin Electrophysiol 1990; 13: 608-18.
    • (1990) Pacing Clin Electrophysiol , vol.13 , pp. 608-618
    • van Hare, G.F.1    Franz, M.R.2    Roge, C.3    Scheinman, M.M.4
  • 59
    • 0033592362 scopus 로고    scopus 로고
    • Homozygous premature truncation of the HERG protein: The human HERG knockout
    • Hoorntje T, Alders M, van Tintelen P, et al. Homozygous premature truncation of the HERG protein: the human HERG knockout. Circulation 1999; 100: 1264-7.
    • (1999) Circulation , vol.100 , pp. 1264-1267
    • Hoorntje, T.1    Alders, M.2    van Tintelen, P.3
  • 60
    • 17144442716 scopus 로고    scopus 로고
    • Homozygosity for a HERG potassium channel mutation causes a severe form of long QT syndrome: Identification of an apparent founder mutation in the Finns
    • Pilippo K, Laitinen P, Swan H, et al. Homozygosity for a HERG potassium channel mutation causes a severe form of long QT syndrome: identification of an apparent founder mutation in the Finns. J Am Coll Cardiol 2000; 35: 1919-25.
    • (2000) J Am Coll Cardiol , vol.35 , pp. 1919-1925
    • Pilippo, K.1    Laitinen, P.2    Swan, H.3
  • 61
    • 0007519279 scopus 로고    scopus 로고
    • Homozygous SCN5A mutation in long-QT syndrome with functional two-to-one atrioventricular block
    • Lupoglazoff JM, Cheav T, Baroudi G, et al. Homozygous SCN5A mutation in long-QT syndrome with functional two-to-one atrioventricular block. Circ Res 2001; 89: E16-E21.
    • (2001) Circ Res , vol.89
    • Lupoglazoff, J.M.1    Cheav, T.2    Baroudi, G.3
  • 62
    • 9644264340 scopus 로고    scopus 로고
    • Classification and mechanism of Torsade de Pointes initiation in patients with congenital long QT syndrome
    • Noda T, Shimizu W, Satomi K, et al. Classification and mechanism of Torsade de Pointes initiation in patients with congenital long QT syndrome. Eur Heart J 2004; 25: 2149-54.
    • (2004) Eur Heart J , vol.25 , pp. 2149-2154
    • Noda, T.1    Shimizu, W.2    Satomi, K.3
  • 63
    • 32944461884 scopus 로고    scopus 로고
    • The mechanism of pause-induced torsade de pointes in long QT syndrome
    • Liu J, Laurita KR. The mechanism of pause-induced torsade de pointes in long QT syndrome. J Cardiovasc Electrophysiol 2005; 16: 981-7.
    • (2005) J Cardiovasc Electrophysiol , vol.16 , pp. 981-987
    • Liu, J.1    Laurita, K.R.2
  • 64
    • 0034082381 scopus 로고    scopus 로고
    • Arrhythmias in the congenital long QT syndrome: How often is torsade de pointes pause dependent?
    • Viskin S, Fish R, Zeltser D, et al. Arrhythmias in the congenital long QT syndrome: how often is torsade de pointes pause dependent? Heart 2000; 83: 661-6.
    • (2000) Heart , vol.83 , pp. 661-666
    • Viskin, S.1    Fish, R.2    Zeltser, D.3
  • 66
    • 0034610404 scopus 로고    scopus 로고
    • Spectrum of ST-T-wave patterns and repolarization parameters in congenital long-QT syndrome: ECG findings identify genotypes
    • Zhang L, Timothy KW, Vincent GM, et al. Spectrum of ST-T-wave patterns and repolarization parameters in congenital long-QT syndrome: ECG findings identify genotypes. Circulation 2000; 102: 2849-55.
    • (2000) Circulation , vol.102 , pp. 2849-2855
    • Zhang, L.1    Timothy, K.W.2    Vincent, G.M.3
  • 67
    • 0036936530 scopus 로고    scopus 로고
    • Prenatal diagnosis and treatment of fetal long QT syndrome: A case report
    • Chang IK, Shyu MK, Lee CN, et al. Prenatal diagnosis and treatment of fetal long QT syndrome: a case report. Prenat Diagn 2002; 22: 1209-12.
    • (2002) Prenat Diagn , vol.22 , pp. 1209-1212
    • Chang, I.K.1    Shyu, M.K.2    Lee, C.N.3
  • 68
    • 3042611768 scopus 로고    scopus 로고
    • Recurrent third-trimester fetal loss and maternal mosaicism for long-QT syndrome
    • Miller TE, Estrella E, Myerburg RJ, et al. Recurrent third-trimester fetal loss and maternal mosaicism for long-QT syndrome. Circulation 2004; 109: 3029-34.
    • (2004) Circulation , vol.109 , pp. 3029-3034
    • Miller, T.E.1    Estrella, E.2    Myerburg, R.J.3
  • 69
    • 1542722281 scopus 로고    scopus 로고
    • Prenatal molecular genetic diagnosis of congenital long QT syndrome by strategic genotyping
    • Tester DJ, McCormack J, Ackerman MJ. Prenatal molecular genetic diagnosis of congenital long QT syndrome by strategic genotyping. Am J Cardiol 2004; 93: 788-91.
    • (2004) Am J Cardiol , vol.93 , pp. 788-791
    • Tester, D.J.1    McCormack, J.2    Ackerman, M.J.3
  • 70
    • 27744471093 scopus 로고    scopus 로고
    • Drug-induced torsades de pointes: The evolving role of pharmacogenetics
    • Fitzgerald PT, Ackerman MI. Drug-induced torsades de pointes: the evolving role of pharmacogenetics. Heart Rhythm 2005; 2: S30-7.
    • (2005) Heart Rhythm , vol.2
    • Fitzgerald, P.T.1    Ackerman, M.I.2
  • 71
    • 1442306232 scopus 로고    scopus 로고
    • Drug-induced prolongation of the QT interval
    • Roden DM. Drug-induced prolongation of the QT interval. N Engl J Med 2004; 350: 1013-22.
    • (2004) N Engl J Med , vol.350 , pp. 1013-1022
    • Roden, D.M.1
  • 73
    • 11144320454 scopus 로고    scopus 로고
    • Molecular and clinical determinants of drug-induced long QT syndrome: An iatrogenic channelopathy
    • Abriel H, Schlapfer J, Keller DI, et al. Molecular and clinical determinants of drug-induced long QT syndrome: an iatrogenic channelopathy. Swiss Med Wkly 2004; 134: 685-94.
    • (2004) Swiss Med Wkly , vol.134 , pp. 685-694
    • Abriel, H.1    Schlapfer, J.2    Keller, D.I.3
  • 74
    • 7444251759 scopus 로고    scopus 로고
    • Role of a KCNH2 polymorphism (R1047 L) in dofetilide-induced Torsades de Pointes
    • Sun Z, Milos PM, Thompson JF, et al. Role of a KCNH2 polymorphism (R1047 L) in dofetilide-induced Torsades de Pointes. J Mol Cell Cardiol 2004; 37: 1031-9.
    • (2004) J Mol Cell Cardiol , vol.37 , pp. 1031-1039
    • Sun, Z.1    Milos, P.M.2    Thompson, J.F.3
  • 75
    • 0345690174 scopus 로고    scopus 로고
    • Ethnic differences in cardiac potassium channel variants: Implications for genetic susceptibility to sudden cardiac death and genetic testing for congenital long QT syndrome
    • Ackerman MJ, Tester DJ, Jones GS, Will ML, Burrow CR, Curran ME. Ethnic differences in cardiac potassium channel variants: implications for genetic susceptibility to sudden cardiac death and genetic testing for congenital long QT syndrome. Mayo Clin Proc 2003; 78: 1479-87.
    • (2003) Mayo Clin Proc , vol.78 , pp. 1479-1487
    • Ackerman, M.J.1    Tester, D.J.2    Jones, G.S.3    Will, M.L.4    Burrow, C.R.5    Curran, M.E.6
  • 76
    • 7744243863 scopus 로고    scopus 로고
    • Spectrum and prevalence of cardiac sodium channel variants among black, white, Asian, and Hispanic individuals: Implications for arrhythmogenic susceptibility and Brugada/ long QT syndrome genetic testing
    • Ackerman MJ, Splawski I, Makielski JC, et al. Spectrum and prevalence of cardiac sodium channel variants among black, white, Asian, and Hispanic individuals: implications for arrhythmogenic susceptibility and Brugada/ long QT syndrome genetic testing. Heart Rhythm. 2004; 1: 600-7.
    • (2004) Heart Rhythm , vol.1 , pp. 600-607
    • Ackerman, M.J.1    Splawski, I.2    Makielski, J.C.3
  • 77
    • 0037421629 scopus 로고    scopus 로고
    • A common human SCN5A polymorphism modifies expression of an arrhythmia causing mutation
    • Ye B, Valdivia CR, Ackerman MJ, Makielski JC. A common human SCN5A polymorphism modifies expression of an arrhythmia causing mutation. Physiol Genomics 2003; 12: 187-93.
    • (2003) Physiol Genomics , vol.12 , pp. 187-193
    • Ye, B.1    Valdivia, C.R.2    Ackerman, M.J.3    Makielski, J.C.4
  • 78
    • 0242330187 scopus 로고    scopus 로고
    • A ubiquitous splice variant and a common polymorphism affect heterologous expression of recombinant human SCN5A heart sodium channels
    • Makielski JC, Ye B, Valdivia CR, et al. A ubiquitous splice variant and a common polymorphism affect heterologous expression of recombinant human SCN5A heart sodium channels. Circ Res 2003; 93: 821-8.
    • (2003) Circ Res , vol.93 , pp. 821-828
    • Makielski, J.C.1    Ye, B.2    Valdivia, C.R.3
  • 79
    • 33644832519 scopus 로고    scopus 로고
    • Roden DM. Long QT syndrome: reduced repolarization reserve and the genetic link. J Intern Med 2006; 259: 59-69.
    • Roden DM. Long QT syndrome: reduced repolarization reserve and the genetic link. J Intern Med 2006; 259: 59-69.
  • 80
    • 32444436881 scopus 로고    scopus 로고
    • A common cardiac sodium channel variant associated with sudden infant death in African Americans, SCN5A S1103Y
    • Plant LD, Bowers PN, Liu Q, et al. A common cardiac sodium channel variant associated with sudden infant death in African Americans, SCN5A S1103Y. J Clin Invest 2006; 116: 430-5.
    • (2006) J Clin Invest , vol.116 , pp. 430-435
    • Plant, L.D.1    Bowers, P.N.2    Liu, Q.3
  • 81
    • 27744551049 scopus 로고    scopus 로고
    • Burst bicycle exercise facilitates diagnosis of latent long QT syndrome
    • Walker BD, Krahn AD, Klein GJ, Skanes AC, Yee R. Burst bicycle exercise facilitates diagnosis of latent long QT syndrome. Am Heart J 2005; 150: 1059-63.
    • (2005) Am Heart J , vol.150 , pp. 1059-1063
    • Walker, B.D.1    Krahn, A.D.2    Klein, G.J.3    Skanes, A.C.4    Yee, R.5
  • 82
    • 0025883918 scopus 로고    scopus 로고
    • Vincent GM, Jaiswal D, Timothy KW. Effects of exercise on heart rate, QT, QTc and QT/QS2 in the Romano-Ward inherited long QT syndrome. Am J Cardiol 1991; 68: 498-503.
    • Vincent GM, Jaiswal D, Timothy KW. Effects of exercise on heart rate, QT, QTc and QT/QS2 in the Romano-Ward inherited long QT syndrome. Am J Cardiol 1991; 68: 498-503.
  • 83
    • 0037448805 scopus 로고    scopus 로고
    • Exercise stress test amplifies genotype-phenotype correlation in the LQT1 and LQT2 forms of the long-QT syndrome
    • Takenaka K, Ai T, Shimizu W, et al. Exercise stress test amplifies genotype-phenotype correlation in the LQT1 and LQT2 forms of the long-QT syndrome. Circulation 2003; 107: 838-44.
    • (2003) Circulation , vol.107 , pp. 838-844
    • Takenaka, K.1    Ai, T.2    Shimizu, W.3
  • 84
    • 0032831603 scopus 로고    scopus 로고
    • Sinus node function and ventricular repolarization during exercise stress test in long QT syndrome patients with KvLQT1 and HERG potassium channel defects
    • Swan H, Viitasalo M, Piippo K, Laitinen P, Kontula K, Toivonen L. Sinus node function and ventricular repolarization during exercise stress test in long QT syndrome patients with KvLQT1 and HERG potassium channel defects. J Am Coll Cardiol 1999; 34: 823-9.
    • (1999) J Am Coll Cardiol , vol.34 , pp. 823-829
    • Swan, H.1    Viitasalo, M.2    Piippo, K.3    Laitinen, P.4    Kontula, K.5    Toivonen, L.6
  • 85
    • 0028874658 scopus 로고
    • Long QT syndrome patients with mutations of the SCN5A and HERG genes have differential responses to Na+ channel blockade and to increases in heart rate. Implications for gene-specific therapy
    • Schwartz PJ, Priori SG, Locati EH, et al. Long QT syndrome patients with mutations of the SCN5A and HERG genes have differential responses to Na+ channel blockade and to increases in heart rate. Implications for gene-specific therapy. Circulation 1995; 92: 3381-6.
    • (1995) Circulation , vol.92 , pp. 3381-3386
    • Schwartz, P.J.1    Priori, S.G.2    Locati, E.H.3
  • 87
    • 17144415220 scopus 로고    scopus 로고
    • Compendium of cardiac channel mutations in 541 consecutive unrelated patients referred for long QT syndrome genetic testing
    • Tester DJ, Will ML, Haglund CM, Ackerman MI. Compendium of cardiac channel mutations in 541 consecutive unrelated patients referred for long QT syndrome genetic testing. Heart Rhythm 2005; 2: 507-17.
    • (2005) Heart Rhythm , vol.2 , pp. 507-517
    • Tester, D.J.1    Will, M.L.2    Haglund, C.M.3    Ackerman, M.I.4
  • 88
    • 4444273245 scopus 로고    scopus 로고
    • An intronic mutation causes long QT syndrome
    • Zhang L, Vincent GM, Baralle M, et al. An intronic mutation causes long QT syndrome. J Am Coll Cardiol 2004; 44: 1283-91.
    • (2004) J Am Coll Cardiol , vol.44 , pp. 1283-1291
    • Zhang, L.1    Vincent, G.M.2    Baralle, M.3
  • 89
    • 1042268063 scopus 로고    scopus 로고
    • Inherited arrhythmogenic diseases: The complexity beyond monogenic disorders
    • Priori SG. Inherited arrhythmogenic diseases: the complexity beyond monogenic disorders. Circ Res 2004; 94: 140-5.
    • (2004) Circ Res , vol.94 , pp. 140-145
    • Priori, S.G.1
  • 90
    • 0033514263 scopus 로고    scopus 로고
    • Low penetrance in the long-QT syndrome: Clinical impact
    • Priori SG, Napolitano C, Schwartz PJ. Low penetrance in the long-QT syndrome: clinical impact. Circulation 1999; 99: 529-33.
    • (1999) Circulation , vol.99 , pp. 529-533
    • Priori, S.G.1    Napolitano, C.2    Schwartz, P.J.3
  • 91
    • 0034468875 scopus 로고    scopus 로고
    • Clinical applicability of molecular biology: The case of the long QT syndrome
    • Schwartz PJ. Clinical applicability of molecular biology: the case of the long QT syndrome. Curr Control Trials Cardiovasc Med 2000; 1: 88-91.
    • (2000) Curr Control Trials Cardiovasc Med , vol.1 , pp. 88-91
    • Schwartz, P.J.1
  • 92
    • 0037133307 scopus 로고    scopus 로고
    • Increased risk of arrhythmic events in long-QT syndrome with mutations in the pore region of the human ether-a-go-go-related gene pota-ssium channel
    • Moss AJ, Zareba W, Kaufman ES, et al. Increased risk of arrhythmic events in long-QT syndrome with mutations in the pore region of the human ether-a-go-go-related gene pota-ssium channel. Circulation 2002; 105: 794-9.
    • (2002) Circulation , vol.105 , pp. 794-799
    • Moss, A.J.1    Zareba, W.2    Kaufman, E.S.3
  • 93
    • 0036302646 scopus 로고    scopus 로고
    • Congenital long QT syndrome with functionally impaired atrioventricular conduction: Successful treatment by mexiletine and propranolol
    • Yao CT, Wang JN, Tsai YC, Lin CS, Wu JM. Congenital long QT syndrome with functionally impaired atrioventricular conduction: successful treatment by mexiletine and propranolol. J Formos Med Assoc 2002; 101: 291-3.
    • (2002) J Formos Med Assoc , vol.101 , pp. 291-293
    • Yao, C.T.1    Wang, J.N.2    Tsai, Y.C.3    Lin, C.S.4    Wu, J.M.5
  • 94
    • 0036237833 scopus 로고    scopus 로고
    • Epinephrine-induced QT interval prolongation: A gene-specific paradoxical response in congenital long QT syndrome
    • Ackerman MJ, Khositseth A, Tester DJ, Hejlik JB, Shen WK, Porter CB. Epinephrine-induced QT interval prolongation: a gene-specific paradoxical response in congenital long QT syndrome. Mayo Clin Proc 2002; 77: 413-21.
    • (2002) Mayo Clin Proc , vol.77 , pp. 413-421
    • Ackerman, M.J.1    Khositseth, A.2    Tester, D.J.3    Hejlik, J.B.4    Shen, W.K.5    Porter, C.B.6
  • 95
    • 13544271952 scopus 로고    scopus 로고
    • Epinephrine-induced T-wave notching in congenital long QT syndrome
    • Khositseth A, Hejlik J, Shen WK, Ackerman MJ. Epinephrine-induced T-wave notching in congenital long QT syndrome. Heart Rhythm 2005; 2: 141-6.
    • (2005) Heart Rhythm , vol.2 , pp. 141-146
    • Khositseth, A.1    Hejlik, J.2    Shen, W.K.3    Ackerman, M.J.4
  • 96
    • 9244245287 scopus 로고    scopus 로고
    • Diagnostic value of epinephrine test for genotyping LQT1, LQT2, and LQT3 forms of congenital long QT syndrome
    • Shimizu W, Noda T, Takaki H, et al. Diagnostic value of epinephrine test for genotyping LQT1, LQT2, and LQT3 forms of congenital long QT syndrome. Heart Rhythm 2004; 1: 276-83.
    • (2004) Heart Rhythm , vol.1 , pp. 276-283
    • Shimizu, W.1    Noda, T.2    Takaki, H.3
  • 97
    • 0038415858 scopus 로고    scopus 로고
    • Risk stratification in the long-QT syndrome
    • Priori SG, Schwartz PJ, Napolitano C, et al. Risk stratification in the long-QT syndrome. N Engl J Med 2003; 348: 1866-74.
    • (2003) N Engl J Med , vol.348 , pp. 1866-1874
    • Priori, S.G.1    Schwartz, P.J.2    Napolitano, C.3
  • 98
    • 0032499656 scopus 로고    scopus 로고
    • Age- and sex-related differences in clinical manifestations in patients with congenital long-QT syndrome: Findings from the International LQTS Registry
    • Locati EH, Zareba W, Moss AJ, et al. Age- and sex-related differences in clinical manifestations in patients with congenital long-QT syndrome: findings from the International LQTS Registry. Circulation 1998; 97: 2237-44.
    • (1998) Circulation , vol.97 , pp. 2237-2244
    • Locati, E.H.1    Zareba, W.2    Moss, A.J.3
  • 99
    • 0032189139 scopus 로고    scopus 로고
    • Influence of genotype on the clinical course of the long-QT syndrome. International Long-QT Syndrome Registry Research Group
    • Zareba W, Moss Al, Schwartz PJ, et al. Influence of genotype on the clinical course of the long-QT syndrome. International Long-QT Syndrome Registry Research Group. N Engl J Med 1998; 339: 960-5.
    • (1998) N Engl J Med , vol.339 , pp. 960-965
    • Zareba, W.1    Moss, A.2    Schwartz, P.J.3
  • 100
    • 2442532568 scopus 로고    scopus 로고
    • Identification of a common genetic substrate underlying postpartum cardiac events in congenital long QT syndrome
    • Khositseth A, Tester DJ, Will ML, Bell CM, Ackerman MJ. Identification of a common genetic substrate underlying postpartum cardiac events in congenital long QT syndrome. Heart Rhythm 2004; 1: 60-4.
    • (2004) Heart Rhythm , vol.1 , pp. 60-64
    • Khositseth, A.1    Tester, D.J.2    Will, M.L.3    Bell, C.M.4    Ackerman, M.J.5
  • 101
    • 0032502041 scopus 로고    scopus 로고
    • Influence of pregnancy on the risk for cardiac events in patients with hereditary long QT syndrome. LQTS Investigators
    • Rashba EJ, Zareba W, Moss AJ, et al. Influence of pregnancy on the risk for cardiac events in patients with hereditary long QT syndrome. LQTS Investigators. Circulation 1998; 97: 451-6.
    • (1998) Circulation , vol.97 , pp. 451-456
    • Rashba, E.J.1    Zareba, W.2    Moss, A.J.3
  • 102
    • 17744384482 scopus 로고    scopus 로고
    • Correlation of genetic etiology with response to beta-adrenergic blockade among symptomatic patients with familial long-QT syndrome
    • Itoh T, Kikuchi K, Odagawa Y, et al. Correlation of genetic etiology with response to beta-adrenergic blockade among symptomatic patients with familial long-QT syndrome. J Hum Genet 2001; 46: 38-40.
    • (2001) J Hum Genet , vol.46 , pp. 38-40
    • Itoh, T.1    Kikuchi, K.2    Odagawa, Y.3
  • 103
    • 6044273765 scopus 로고    scopus 로고
    • Beta-blocker therapy failures in symptomatic probands with genotyped long-QT syndrome
    • Chatrath R, Bell CM, Ackerman MJ. Beta-blocker therapy failures in symptomatic probands with genotyped long-QT syndrome. Pediatr Cardiol 2004; 25: 459-65.
    • (2004) Pediatr Cardiol , vol.25 , pp. 459-465
    • Chatrath, R.1    Bell, C.M.2    Ackerman, M.J.3
  • 104
    • 0032786115 scopus 로고    scopus 로고
    • Long-term follow-up of patients with long-QT syndrome treated with beta-blockers and continuous pacing
    • Dorostkar PC, Eldar M, Belhassen B, Scheinman MM. Long-term follow-up of patients with long-QT syndrome treated with beta-blockers and continuous pacing. Circulation 1999; 100: 2431-6.
    • (1999) Circulation , vol.100 , pp. 2431-2436
    • Dorostkar, P.C.1    Eldar, M.2    Belhassen, B.3    Scheinman, M.M.4
  • 105
    • 4544387969 scopus 로고    scopus 로고
    • Association of long QT syndrome loci and cardiac events among patients treated with beta-blockers
    • Priori SG, Napolitano C, Schwartz PJ, et al. Association of long QT syndrome loci and cardiac events among patients treated with beta-blockers. JAMA 2004; 292: 1341-4.
    • (2004) JAMA , vol.292 , pp. 1341-1344
    • Priori, S.G.1    Napolitano, C.2    Schwartz, P.J.3
  • 106
    • 0034636115 scopus 로고    scopus 로고
    • Effects of flecainide in patients with new SCN5A mutation: Mutation-specific therapy for long-QT syndrome?
    • Benhorin J, Taub R, Goldmit M, et al. Effects of flecainide in patients with new SCN5A mutation: mutation-specific therapy for long-QT syndrome? Circulation 2000; 101: 1698-706.
    • (2000) Circulation , vol.101 , pp. 1698-1706
    • Benhorin, J.1    Taub, R.2    Goldmit, M.3
  • 107
    • 0347951001 scopus 로고    scopus 로고
    • Long QT syndrome and life threatening arrhythmia in a newborn: Molecular diagnosis and treatment response
    • Schulze-Bahr E, Fenge H, Etzrodt D, et al. Long QT syndrome and life threatening arrhythmia in a newborn: molecular diagnosis and treatment response. Heart 2004; 90: 13-6.
    • (2004) Heart , vol.90 , pp. 13-16
    • Schulze-Bahr, E.1    Fenge, H.2    Etzrodt, D.3
  • 108
    • 4644325716 scopus 로고    scopus 로고
    • Images in cardiovascular medicine. Life-threatening neonatal arrhythmia: Successful treatment and confirmation of clinically suspected extreme long QT-syndrome-3
    • Kehl HG, Haverkamp W, Rellensmann G, et al. Images in cardiovascular medicine. Life-threatening neonatal arrhythmia: successful treatment and confirmation of clinically suspected extreme long QT-syndrome-3. Circulation 2004; 109: e205-e206.
    • (2004) Circulation , vol.109
    • Kehl, H.G.1    Haverkamp, W.2    Rellensmann, G.3
  • 109
    • 0032574657 scopus 로고    scopus 로고
    • Improvement of repolarization abnormalities by a K+ channel opener in the LQT1 form of congenital long-QT syndrome
    • Shimizu W, Kurita T, Matsuo K, et al. Improvement of repolarization abnormalities by a K+ channel opener in the LQT1 form of congenital long-QT syndrome. Circulation 1998; 97: 1581-8.
    • (1998) Circulation , vol.97 , pp. 1581-1588
    • Shimizu, W.1    Kurita, T.2    Matsuo, K.3
  • 110
    • 0242713010 scopus 로고    scopus 로고
    • A new oral therapy for long QT syndrome: Long-term oral potassium improves repolarization in patients with BERG mutations
    • Etheridge SP, Compton SJ, Tristani-Firouzi M, Mason JW. A new oral therapy for long QT syndrome: long-term oral potassium improves repolarization in patients with BERG mutations. J Am Coll Cardiol 2003; 42: 1777-82.
    • (2003) J Am Coll Cardiol , vol.42 , pp. 1777-1782
    • Etheridge, S.P.1    Compton, S.J.2    Tristani-Firouzi, M.3    Mason, J.W.4
  • 111
    • 2442662544 scopus 로고    scopus 로고
    • Novel therapeutics for treatment of long-QT syndrome and torsade de pointes
    • Khan IA, Gowda RM. Novel therapeutics for treatment of long-QT syndrome and torsade de pointes. Int J Cardiol 2004; 95: 1-6.
    • (2004) Int J Cardiol , vol.95 , pp. 1-6
    • Khan, I.A.1    Gowda, R.M.2
  • 112
    • 0034084919 scopus 로고    scopus 로고
    • Cardiac pacing in the long QT syndrome: Review of available data and practical recommendations
    • Viskin S. Cardiac pacing in the long QT syndrome: review of available data and practical recommendations. J Cardiovasc Electrophysiol 2000; 11: 593-600.
    • (2000) J Cardiovasc Electrophysiol , vol.11 , pp. 593-600
    • Viskin, S.1
  • 113
  • 114
    • 20244385009 scopus 로고    scopus 로고
    • Implantable cardioverter-defibrillator therapy in patients with congenital long-QT syndrome: A long-term follow-up
    • Monnig G, Kobe J, Loher A, et al. Implantable cardioverter-defibrillator therapy in patients with congenital long-QT syndrome: a long-term follow-up. Heart Rhythm 2005; 2: 497-504.
    • (2005) Heart Rhythm , vol.2 , pp. 497-504
    • Monnig, G.1    Kobe, J.2    Loher, A.3
  • 116
    • 0038298806 scopus 로고    scopus 로고
    • Saving lives in congenital long QT syndrome: Who benefits from implantable cardioverter defibrillator therapy?
    • Kaufman ES. Saving lives in congenital long QT syndrome: who benefits from implantable cardioverter defibrillator therapy? J Cardiovasc Electrophysiol 2003; 14: 342-3.
    • (2003) J Cardiovasc Electrophysiol , vol.14 , pp. 342-343
    • Kaufman, E.S.1
  • 117
    • 0015223506 scopus 로고
    • Unilateral cervicothoracic sympathetic ganglionectomy for the treatment of long QT interval syndrome
    • Moss AJ, McDonald J. Unilateral cervicothoracic sympathetic ganglionectomy for the treatment of long QT interval syndrome. N Engl J Med 1971; 285: 903-4.
    • (1971) N Engl J Med , vol.285 , pp. 903-904
    • Moss, A.J.1    McDonald, J.2
  • 118
    • 0025769189 scopus 로고
    • Left cardiac sympathetic denervation in the therapy of congenital long QT syndrome. A worldwide report
    • Schwartz PJ, Locati EH, Moss AJ, Crampton RS, Trazzi R, Ruberti U. Left cardiac sympathetic denervation in the therapy of congenital long QT syndrome. A worldwide report. Circulation 1991; 84: 503-11.
    • (1991) Circulation , vol.84 , pp. 503-511
    • Schwartz, P.J.1    Locati, E.H.2    Moss, A.J.3    Crampton, R.S.4    Trazzi, R.5    Ruberti, U.6
  • 119
    • 0042129888 scopus 로고    scopus 로고
    • Role of left cardiac sympathetic denervation in the management of congenital long QT syndrome
    • Wang LX. Role of left cardiac sympathetic denervation in the management of congenital long QT syndrome. J Postgrad Med 2003; 49: 179-81.
    • (2003) J Postgrad Med , vol.49 , pp. 179-181
    • Wang, L.X.1
  • 120
    • 3342905299 scopus 로고    scopus 로고
    • Left cardiac sympathetic denervation as the first-line therapy for congenital long QT syndrome
    • Wang L, Feng G. Left cardiac sympathetic denervation as the first-line therapy for congenital long QT syndrome. Med Hypotheses 2004; 63: 438-41.
    • (2004) Med Hypotheses , vol.63 , pp. 438-441
    • Wang, L.1    Feng, G.2
  • 121
    • 11144356780 scopus 로고    scopus 로고
    • Left cardiac sympathetic denervation in the management of high-risk patients affected by the long-QT syndrome
    • Schwartz PJ, Priori SG, Cerrone M, et al. Left cardiac sympathetic denervation in the management of high-risk patients affected by the long-QT syndrome. Circulation 2004; 109: 1826-33.
    • (2004) Circulation , vol.109 , pp. 1826-1833
    • Schwartz, P.J.1    Priori, S.G.2    Cerrone, M.3
  • 122
    • 0041857898 scopus 로고    scopus 로고
    • Mapping and ablation of ventricular fibrillation associated with long-QT and Brugada syndromes
    • Haissaguerre M, Extramiana F, Hocini M, et al. Mapping and ablation of ventricular fibrillation associated with long-QT and Brugada syndromes. Circulation 2003; 108: 925-8.
    • (2003) Circulation , vol.108 , pp. 925-928
    • Haissaguerre, M.1    Extramiana, F.2    Hocini, M.3
  • 124
    • 0033533770 scopus 로고    scopus 로고
    • Molecular diagnosis of the inherited long-QT syndrome in a woman who died after near-drowning
    • Ackerman MJ, Tester DJ, Porter CJ, Edwards WD. Molecular diagnosis of the inherited long-QT syndrome in a woman who died after near-drowning. N Engl J Med 1999; 341: 1121-5.
    • (1999) N Engl J Med , vol.341 , pp. 1121-1125
    • Ackerman, M.J.1    Tester, D.J.2    Porter, C.J.3    Edwards, W.D.4
  • 125
    • 2342440911 scopus 로고    scopus 로고
    • Postmortem molecular screening in unexplained sudden death
    • Chugh SS, Senashova O, Watts A, et al. Postmortem molecular screening in unexplained sudden death. J Am Coll Cardiol 2004; 43: 1625-9.
    • (2004) J Am Coll Cardiol , vol.43 , pp. 1625-1629
    • Chugh, S.S.1    Senashova, O.2    Watts, A.3
  • 126
    • 22544474319 scopus 로고    scopus 로고
    • Sudden infant death syndrome: How significant are the cardiac channelopathies?
    • Tester DJ, Ackerman MJ. Sudden infant death syndrome: how significant are the cardiac channelopathies? Cardiavasc Res 2005; 67: 388-96.
    • (2005) Cardiavasc Res , vol.67 , pp. 388-396
    • Tester, D.J.1    Ackerman, M.J.2


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