Increased risk of arrhythmic events in long-QT syndrome with mutations in the pore region of the human ether-a-go-go-related gene potassium channel

Circulation

Volumn 105, Issue 7, 2002, Pages 794-799

  Moss, Arthur J ^a   Zareba, Wojciech ^a   Kaufman, Elizabeth S ^b   Gartman, Eric ^a   Peterson, Derick R ^a   Benhorin, Jesaia ^c   Towbin, Jeffrey A ^d   Keating, Mark T ^e   Priori, Silvia G ^f,g   Schwartz, Peter J ^f   Vincent, G Michael ^h   Robinson, Jennifer L ^a   Andrews, Mark L ^a   Feng, Changyong ^a   Hall, W Jackson ^a   Medina, Aharon ^c   Zhang, Li ^h   Wang, Zhiqing ^d  

^a UNIVERSITY OF ROCHESTER MEDICAL CENTER   (United States)

^b CASE WESTERN RESERVE UNIVERSITY   (United States)

^c BIKUR CHOLIM HOSPITAL   (Israel)

^d BAYLOR COLLEGE OF MEDICINE   (United States)

^e BOSTON CHILDREN S HOSPITAL   (United States)

^f UNIVERSITY OF PAVIA   (Italy)

^g School of Medicine ^*

^h UNIVERSITY OF UTAH SCHOOL OF MEDICINE   (United States)

Author keywords

Arrhythmia; Genes; Long QT syndrome

Indexed keywords

POTASSIUM CHANNEL; POTASSIUM CHANNEL HERG;

ADOLESCENT; ADULT; ARTICLE; CARDIOVASCULAR RISK; CLINICAL FEATURE; CONTROLLED STUDY; DISEASE COURSE; FEMALE; GENE; GENE LOCATION; GENE MUTATION; HEART ARRHYTHMIA; HUMAN; LONG QT SYNDROME; MAJOR CLINICAL STUDY; MALE; PRIORITY JOURNAL; PROGNOSIS; REGRESSION ANALYSIS;

ADOLESCENT; ADULT; ARRHYTHMIA; BINDING SITES; CATION TRANSPORT PROTEINS; DISEASE PROGRESSION; DNA MUTATIONAL ANALYSIS; DNA-BINDING PROTEINS; ELECTROCARDIOGRAPHY; ETHER-A-GO-GO POTASSIUM CHANNELS; FEMALE; FOLLOW-UP STUDIES; HUMANS; LONG QT SYNDROME; MALE; MODELS, MOLECULAR; MUTATION; ODDS RATIO; PHENOTYPE; POTASSIUM CHANNELS; POTASSIUM CHANNELS, VOLTAGE-GATED; PROGNOSIS; PROPORTIONAL HAZARDS MODELS; REGISTRIES; REGRESSION ANALYSIS; RISK ASSESSMENT; SURVIVAL ANALYSIS; TRANS-ACTIVATORS;

EID: 0037133307     PISSN: 00097322     EISSN: None     Source Type: Journal    
DOI: 10.1161/hc0702.105124     Document Type: Article

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