Absence of heterogeneous nuclear ribonucleoproteins and survival motor neuron protein in TDP-43 positive inclusions in frontotemporal lobar degeneration

Acta Neuropathologica

Volumn 113, Issue 5, 2007, Pages 543-548

  Neumann, Manuela ^a   Igaz, Lionel M ^b   Kwong, Linda K ^b   Nakashima Yasuda, Hanae ^b   Kolb, Stephen J ^b   Dreyfuss, Gideon ^b   Kretzschmar, Hans A ^a   Trojanowski, John Q ^b,c   Lee, Virginia M Y ^b,c  

^a UNIVERSITY OF MUNICH   (Germany)

^b UNIVERSITY OF PENNSYLVANIA   (United States)

^c UNIVERSITY OF PENNSYLVANIA   (United States)

Author keywords

FTD; hnRNP; SMN; TDP 43; Ubiquitin

Indexed keywords

BIOLOGICAL MARKER; HETEROGENEOUS NUCLEAR RIBONUCLEOPROTEIN; NUCLEAR PROTEIN; SURVIVAL MOTOR NEURON PROTEIN; TDP 43; UBIQUITIN; UNCLASSIFIED DRUG;

ARTICLE; BRAIN DEGENERATION; BRAIN REGION; CARBOXY TERMINAL SEQUENCE; CELL INCLUSION; CELL NUCLEUS; CELL NUCLEUS INCLUSION BODY; CELLULAR DISTRIBUTION; CHEMICAL ANALYSIS; CHEMICAL LABELING; CONTROLLED STUDY; CYTOPLASM; EXON; FRONTOTEMPORAL LOBAR DEGENERATION; HUMAN; HUMAN TISSUE; IMMUNOHISTOCHEMISTRY; NERVE CELL; PATHOGENESIS; PRIORITY JOURNAL; PROTEIN DEGRADATION; PROTEIN EXPRESSION; PROTEIN FUNCTION; PROTEIN LOCALIZATION; PROTEIN METABOLISM; PROTEIN PHOSPHORYLATION; PROTEIN PROTEIN INTERACTION; TRANSCRIPTION REGULATION; UBIQUITINATION;

CYCLIC AMP RESPONSE ELEMENT-BINDING PROTEIN; DEMENTIA; DNA-BINDING PROTEINS; HETEROGENEOUS-NUCLEAR RIBONUCLEOPROTEINS; HUMANS; INCLUSION BODIES; MOTOR NEURONS; NERVE TISSUE PROTEINS; RNA-BINDING PROTEINS; UBIQUITIN;

EID: 34247595383     PISSN: 00016322     EISSN: None     Source Type: Journal    
DOI: 10.1007/s00401-007-0221-x     Document Type: Article

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