Molecular basis of inherited skin-blistering disorders, and therapeutic implications

Expert Reviews in Molecular Medicine

Volumn 8, Issue 24, 2006, Pages 1-21

  Aumailley, Monique ^a   Has, Cristina ^b   Tunggal, Lucy ^a   Bruckner Tuderman, Leena ^b  

^a UNIVERSITY OF COLOGNE   (Germany)

^b UNIVERSITY OF FREIBURG   (Germany)

Author keywords

[No Author keywords available]

Indexed keywords

CELL PROTEIN; COLLAGEN TYPE 7; CYTOKERATIN 14; LAMININ; LAMININ 332; LENTIVIRUS VECTOR; PLECTIN; RECOMBINANT COLLAGEN TYPE 7; RECOMBINANT LAMININ 332; RECOMBINANT PROTEIN; RETROVIRUS VECTOR; UNCLASSIFIED DRUG;

ARTICLE; BONE MARROW TRANSPLANTATION; BULLOUS SKIN DISEASE; BURN; CELL BASED GENE THERAPY; CELL TRANSPLANTATION; CLINICAL FEATURE; DERMOEPIDERMAL JUNCTION; DISEASE ASSOCIATION; DISEASE CLASSIFICATION; DISEASE SEVERITY; ECTODERMAL DYSPLASIA; EPIDERMIS CELL; EPIDERMOLYSIS BULLOSA; EPIDERMOLYSIS BULLOSA DYSTROPHICA; EVIDENCE BASED MEDICINE; FIBROBLAST; GENE MUTATION; GENE REPLACEMENT THERAPY; GENE TRANSFER; GENETIC MODEL; HEALTH CARE COST; HUMAN; IN VITRO STUDY; KERATINOCYTE; MOLECULAR GENETICS; NONHUMAN; NONVIRAL GENE DELIVERY SYSTEM; PATHOPHYSIOLOGY; PRIORITY JOURNAL; PROTEIN EXPRESSION; PROTEIN FUNCTION; RNA INTERFERENCE; SKIN FRAGILITY; SYSTEMATIC REVIEW; TRANSMISSION ELECTRON MICROSCOPY; TRANSPOSON; ULTRASTRUCTURE; VIRAL GENE DELIVERY SYSTEM;

ANIMALS; BLISTER; DERMIS; EPIDERMIS; EPIDERMOLYSIS BULLOSA; HUMANS; SKIN DISEASES, GENETIC;

EID: 33750212860     PISSN: 14623994     EISSN: 14623994     Source Type: Journal    
DOI: 10.1017/S1462399406000123     Document Type: Article

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