Structure of human Wilson protein domains 5 and 6 and their interplay with domain 4 and the copper chaperone HAH1 in copper uptake

Proceedings of the National Academy of Sciences of the United States of America

Volumn 103, Issue 15, 2006, Pages 5729-5734

  Achila, David ^a   Banci, Lucia ^b   Bertini, Ivano ^b   Bunce, Jennifer ^a   Ciofi Baffoni, Simone ^b   Huffman, David L ^a  

^a WESTERN MICHIGAN UNIVERSITY   (United States)

^b UNIVERSITY OF FLORENCE   (Italy)

Author keywords

ATPase function; Copper transport; Metal binding domain; Metallochaperone; Wilson disease protein

Indexed keywords

ADENOSINE TRIPHOSPHATASE; CERULOPLASMIN; CHAPERONE; CHAPERONE HAH1; COPPER; FERREDOXIN; UNCLASSIFIED DRUG; WILSON DISEASE PROTEIN;

ARTICLE; BIOACCUMULATION; COMPLEX FORMATION; COPPER METABOLISM; CRYSTAL STRUCTURE; DNA DAMAGE; ENZYME INACTIVATION; GOLGI COMPLEX; HYDROPHOBICITY; LIPID PEROXIDATION; METAL BINDING; MISSENSE MUTATION; MOLECULAR CLONING; NUCLEAR MAGNETIC RESONANCE SPECTROSCOPY; NUCLEAR OVERHAUSER EFFECT; PRIORITY JOURNAL; PROTEIN DOMAIN; PROTEIN PURIFICATION; PROTEIN SECONDARY STRUCTURE; PROTEIN STRUCTURE; TITRIMETRY; WILSON DISEASE;

ADENOSINE TRIPHOSPHATASES; BINDING SITES; BIOLOGICAL TRANSPORT; CATION TRANSPORT PROTEINS; COPPER; HEPATOLENTICULAR DEGENERATION; HUMANS; MAGNETIC RESONANCE SPECTROSCOPY; MODELS, MOLECULAR; MOLECULAR CHAPERONES; PROTEIN STRUCTURE, SECONDARY;

EID: 33645821051     PISSN: 00278424     EISSN: None     Source Type: Journal    
DOI: 10.1073/pnas.0504472103     Document Type: Article

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