Interaction of the copper chaperone HAH1 with the Wilson disease protein is essential for copper homeostasis

Proceedings of the National Academy of Sciences of the United States of America

Volumn 96, Issue 23, 1999, Pages 13363-13368

  Hamza, Iqbal ^b   Schaefer, Mark ^b   Klomp, Leo W J ^b   Gitlin, Jonathan D ^a,b  

^a ST LOUIS CHILDREN S HOSPITAL   (United States)

^b WASHINGTON UNIVERSITY SCHOOL OF MEDICINE   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

CARRIER PROTEIN; CHAPERONE; COPPER; GLUTATHIONE TRANSFERASE; PROTEIN; PROTEIN HAH 1; UNCLASSIFIED DRUG;

AMINO ACID SEQUENCE; AMINO TERMINAL SEQUENCE; ARTICLE; HOMEOSTASIS; HUMAN; HUMAN TISSUE; IMMUNOBLOTTING; IMMUNOPRECIPITATION; INTRACELLULAR TRANSPORT; MENKES SYNDROME; PRIORITY JOURNAL; PROTEIN LOCALIZATION; PROTEIN PROTEIN INTERACTION; SITE DIRECTED MUTAGENESIS; WILSON DISEASE;

ADENOSINE TRIPHOSPHATASES; AMINO ACID SEQUENCE; CARRIER PROTEINS; CATION TRANSPORT PROTEINS; CELL LINE; COPPER; FLUORESCENT ANTIBODY TECHNIQUE, INDIRECT; HOMEOSTASIS; HUMANS; MOLECULAR CHAPERONES; MOLECULAR SEQUENCE DATA; MUTAGENESIS; SEQUENCE HOMOLOGY, AMINO ACID;

MAMMALIA; SACCHAROMYCES CEREVISIAE;

EID: 0033539566     PISSN: 00278424     EISSN: None     Source Type: Journal    
DOI: 10.1073/pnas.96.23.13363     Document Type: Article

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