Intracellular trafficking of the human Wilson protein: The role of the six N-terminal metal-binding sites

Biochemical Journal

Volumn 380, Issue 3, 2004, Pages 805-813

  Cater, Michael A ^a   Forbes, John ^b   La Fontaine, Sharon ^a   Cox, Diane ^b   Mercer, Julian F B ^a  

^a DEAKIN UNIVERSITY   (Australia)

^b UNIVERSITY OF ALBERTA   (Canada)

Author keywords

ATP7B; Copper; P type ATPase; Trafficking; Wilson disease; WND

Indexed keywords

CELLS; COPPER; DISEASE CONTROL; FUNCTIONS; PROTEINS; TOXICITY;

BILES; COPPER-TRANSPORTING;

BIOCHEMISTRY;

MENKES PROTEIN; PROTEIN; UNCLASSIFIED DRUG; WILSON PROTEIN;

AMINO TERMINAL SEQUENCE; ANIMAL CELL; ARTICLE; CONTROLLED STUDY; GENE DELETION; GENE LOCATION; GENE MUTATION; MEMBRANE CHANNEL; METAL BINDING; NONHUMAN; PRIORITY JOURNAL; SITE DIRECTED MUTAGENESIS;

ADENOSINE TRIPHOSPHATASES; ALTERNATIVE SPLICING; ANIMALS; BINDING SITES; CATION TRANSPORT PROTEINS; CHO CELLS; COPPER; CRICETINAE; CRICETULUS; INTRACELLULAR MEMBRANES; INTRACELLULAR SPACE; ISOENZYMES; MUTAGENESIS, SITE-DIRECTED; PEPTIDES; PROTEIN STRUCTURE, TERTIARY; SEQUENCE DELETION;

ANIMALIA;

EID: 3042781148     PISSN: 02646021     EISSN: None     Source Type: Journal    
DOI: 10.1042/BJ20031804     Document Type: Article

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