-
1
-
-
0027433553
-
Neurochemical and histologic characterization of excitotoxic lesions produced by the mitochondrial toxin 3-nitropropionic acid
-
Beal M. F., Brouillet E., Jenkins B. G., Ferrante R. J., Kowall N. W., Miller J. M., Storey E., Srivastava R., Rosen B. R., and Hyman B. (1993) Neurochemical and histologic characterization of excitotoxic lesions produced by the mitochondrial toxin 3-nitropropionic acid. J. Neurosci. 13, 4181-4191.
-
(1993)
J. Neurosci.
, vol.13
, pp. 4181-4191
-
-
Beal, M.F.1
Brouillet, E.2
Jenkins, B.G.3
Ferrante, R.J.4
Kowall, N.W.5
Miller, J.M.6
Storey, E.7
Srivastava, R.8
Rosen, B.R.9
Hyman, B.10
-
2
-
-
0029088957
-
3-Nitropropionic acid neurotoxicity is attenuated in copper/zinc superoxide dismutase transgenic mice
-
Beal M. F., Ferrante R. J., Henshaw R., Matthews R. T., Chan P. H., Kowall N. W., Epstein C. J., and Schulz J. B. (1995) 3-Nitropropionic acid neurotoxicity is attenuated in copper/zinc superoxide dismutase transgenic mice. J. Neurochem. 65, 919-922.
-
(1995)
J. Neurochem.
, vol.65
, pp. 919-922
-
-
Beal, M.F.1
Ferrante, R.J.2
Henshaw, R.3
Matthews, R.T.4
Chan, P.H.5
Kowall, N.W.6
Epstein, C.J.7
Schulz, J.B.8
-
3
-
-
0031868461
-
Elevated "hydroxyl radical" generation in vivo in an animal model of amyotrophic lateral sclerosis
-
Bogdanov M. B., Ramos L. E., Xu X., and Beal M. F. (1998) Elevated "hydroxyl radical" generation in vivo in an animal model of amyotrophic lateral sclerosis. J. Neurochem. 71, 1321-1324.
-
(1998)
J. Neurochem.
, vol.71
, pp. 1321-1324
-
-
Bogdanov, M.B.1
Ramos, L.E.2
Xu, X.3
Beal, M.F.4
-
4
-
-
0029118136
-
Chronic mitochondrial energy impairment produces selective striatal degeneration and abnormal choreiform movements in primates
-
Brouillet E., Hantraye P., Ferrante R. J., Dolan R., Leroy-Willig A., Kowall N. W., and Beal M. F. (1995) Chronic mitochondrial energy impairment produces selective striatal degeneration and abnormal choreiform movements in primates. Proc. Natl. Acad. Sci. USA 92, 7105-7109.
-
(1995)
Proc. Natl. Acad. Sci. USA
, vol.92
, pp. 7105-7109
-
-
Brouillet, E.1
Hantraye, P.2
Ferrante, R.J.3
Dolan, R.4
Leroy-Willig, A.5
Kowall, N.W.6
Beal, M.F.7
-
5
-
-
0030919567
-
Oxidative damage and metabolic dysfunction in Huntington's disease: Selective vulnerability of the basal ganglia
-
Browne S. E., Bowling A. C., MacGarvey U., Baik M. J., Berger S. C., Muqit M. M. K., Bird E. D., and Beal M. F. (1997) Oxidative damage and metabolic dysfunction in Huntington's disease: selective vulnerability of the basal ganglia. Ann. Neurol. 41, 646-653.
-
(1997)
Ann. Neurol.
, vol.41
, pp. 646-653
-
-
Browne, S.E.1
Bowling, A.C.2
MacGarvey, U.3
Baik, M.J.4
Berger, S.C.5
Muqit, M.M.K.6
Bird, E.D.7
Beal, M.F.8
-
6
-
-
18544410106
-
Formation of neuronal intranuclear inclusions underlies the neurological dysfunction in mice transgenic for the HD mutation
-
Davies S. W., Turmaine M., Cozens B. A., DiFiglia M., Sharp A. H., Ross C. A., Scherzinger E., Wanker E. E., Mangiarini L., and Bates G. P. (1997) Formation of neuronal intranuclear inclusions underlies the neurological dysfunction in mice transgenic for the HD mutation. Cell 90, 537-548.
-
(1997)
Cell
, vol.90
, pp. 537-548
-
-
Davies, S.W.1
Turmaine, M.2
Cozens, B.A.3
DiFiglia, M.4
Sharp, A.H.5
Ross, C.A.6
Scherzinger, E.7
Wanker, E.E.8
Mangiarini, L.9
Bates, G.P.10
-
7
-
-
0029875381
-
Mitochondrial defect in Huntington's disease caudate nucleus
-
Gu M., Gash M. T., Mann V. M., Javoy-Agid F., Cooper J. M., and Schapira A. H. V. (1996) Mitochondrial defect in Huntington's disease caudate nucleus. Ann. Neurol. 39, 385-389.
-
(1996)
Ann. Neurol.
, vol.39
, pp. 385-389
-
-
Gu, M.1
Gash, M.T.2
Mann, V.M.3
Javoy-Agid, F.4
Cooper, J.M.5
Schapira, A.H.V.6
-
8
-
-
0027480960
-
A novel gene containing a trinucleotide repeat that is expanded and unstable on Huntington's disease chromosomes
-
Huntington's Disease Collaborative Research Group (1993) A novel gene containing a trinucleotide repeat that is expanded and unstable on Huntington's disease chromosomes. Cell 72, 971-983.
-
(1993)
Cell
, vol.72
, pp. 971-983
-
-
-
9
-
-
0031596998
-
1H NMR spectroscopy in Huntington's. Striatal asymmetries and correlations with CAG repeats
-
1H NMR spectroscopy in Huntington's. Striatal asymmetries and correlations with CAG repeats. Neurology 50, 1357-1365.
-
(1998)
Neurology
, vol.50
, pp. 1357-1365
-
-
Jenkins, B.G.1
Rosas, H.D.2
Chen, Y.-C.3
Makabe, T.4
Myers, R.5
MacDonald, M.6
Rosen, B.R.7
Beal, M.F.8
Koroshetz, W.J.9
-
11
-
-
0026357457
-
3-Nitropropionic acid: Exogenous animal neurotoxin and possible human striatal toxin
-
Ludolph A., Seelig M., Ludolph A., Novitt P., Allen C. N., Spencer P. S., and Sabri M. I. (1992) 3-Nitropropionic acid: exogenous animal neurotoxin and possible human striatal toxin. Can. J. Neural Sci. 18, 492-498.
-
(1992)
Can. J. Neural Sci.
, vol.18
, pp. 492-498
-
-
Ludolph, A.1
Seelig, M.2
Ludolph, A.3
Novitt, P.4
Allen, C.N.5
Spencer, P.S.6
Sabri, M.I.7
-
12
-
-
16044373842
-
Exon 1 of the HD gene with an expanded CAG repeat is sufficient to cause a progressive neurological phenotype in transgenic mice
-
Mangiarini L., Sathasivam K., Seller M., Cozens B., Harper A., Hetherington C., Lawton M., Trottier Y., Lehrach H., Davies S. W., and Bates G. P. (1996) Exon 1 of the HD gene with an expanded CAG repeat is sufficient to cause a progressive neurological phenotype in transgenic mice. Cell 87, 493-506.
-
(1996)
Cell
, vol.87
, pp. 493-506
-
-
Mangiarini, L.1
Sathasivam, K.2
Seller, M.3
Cozens, B.4
Harper, A.5
Hetherington, C.6
Lawton, M.7
Trottier, Y.8
Lehrach, H.9
Davies, S.W.10
Bates, G.P.11
-
13
-
-
0031964359
-
Neuroprotective effects of creatine and cyclocreatine in animal models of Huntington's disease
-
Matthews R. T., Yang L., Jenkins B. G., Ferrante R. J., Rosen B. R., Kaddurah-Daouk R., and Beal M. F. (1998) Neuroprotective effects of creatine and cyclocreatine in animal models of Huntington's disease. J. Neurosci. 18, 156-163.
-
(1998)
J. Neurosci.
, vol.18
, pp. 156-163
-
-
Matthews, R.T.1
Yang, L.2
Jenkins, B.G.3
Ferrante, R.J.4
Rosen, B.R.5
Kaddurah-Daouk, R.6
Beal, M.F.7
-
14
-
-
0028900092
-
Involvement of free radicals in excitotoxicity in vivo
-
Schulz J. B., Henshaw D. R., Siwek D., Jenkins B. G., Ferrante R. J., Cipolloni P. B., Kowall N. W., Rosen B. R., and Beal M. F. (1995a) Involvement of free radicals in excitotoxicity in vivo. J. Neurochem. 64, 2239-2247.
-
(1995)
J. Neurochem.
, vol.64
, pp. 2239-2247
-
-
Schulz, J.B.1
Henshaw, D.R.2
Siwek, D.3
Jenkins, B.G.4
Ferrante, R.J.5
Cipolloni, P.B.6
Kowall, N.W.7
Rosen, B.R.8
Beal, M.F.9
-
15
-
-
13344261420
-
Blockade of neuronal nitric oxide synthase protects against excitotoxicity in vivo
-
Schulz J. B., Matthews R. T., Jenkins B. G., Ferrante R. J., Siwek D., Henshaw D. R., Cipolloni P. B., Mecocci P., Kowall N. W., Rosen B. R., and Beal M. F. (1995b) Blockade of neuronal nitric oxide synthase protects against excitotoxicity in vivo. J. Neurosci. 15, 8419-8429.
-
(1995)
J. Neurosci.
, vol.15
, pp. 8419-8429
-
-
Schulz, J.B.1
Matthews, R.T.2
Jenkins, B.G.3
Ferrante, R.J.4
Siwek, D.5
Henshaw, D.R.6
Cipolloni, P.B.7
Mecocci, P.8
Kowall, N.W.9
Rosen, B.R.10
Beal, M.F.11
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