Mutations in copper-zinc superoxide dismutase that cause amyotrophic lateral sclerosis alter the zinc binding site and the redox behavior of the protein

Proceedings of the National Academy of Sciences of the United States of America

Volumn 93, Issue 22, 1996, Pages 12240-12244

  Lyons, Thomas J ^a   Liu, Hongbin ^a   Goto, Joy J ^a   Nersissian, Aram ^a   Roe, James A ^b   Graden, Janet A ^a,d   Café, Carla ^c   Ellerby, Lisa M ^c   Bredesen, Dale E ^c   Gralla, Edith Butler ^a   Valentine, Joan Selverstone ^a  

^a UNIVERSITY OF CALIFORNIA   (United States)

^b LOYOLA MARYMOUNT UNIVERSITY   (United States)

^c BURNHAM INSTITUTE   (United States)

^d UNIVERSITY OF UTAH HEALTH SCIENCES CENTER   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

COBALT; COPPER ION; COPPER ZINC SUPEROXIDE DISMUTASE; ZINC;

AMYOTROPHIC LATERAL SCLEROSIS; CONFERENCE PAPER; CONTROLLED STUDY; ENZYME ACTIVITY; ENZYME CHEMISTRY; GENE MUTATION; HUMAN; OXIDATION REDUCTION REACTION; PRIORITY JOURNAL;

EID: 16044366720     PISSN: 00278424     EISSN: None     Source Type: Journal    
DOI: 10.1073/pnas.93.22.12240     Document Type: Article

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