-
1
-
-
0030937857
-
Fenofibrate differently alters expression of genes encoding ATP-binding transporter proteins of the peroxisomal membrane
-
S. Albet, C. Causeret, M. Bentejac, J.-L. Mandel, P. Aubourg and B. Maurice (1997) Fenofibrate differently alters expression of genes encoding ATP-binding transporter proteins of the peroxisomal membrane. FEBS Lett. 405 394-397.
-
(1997)
FEBS Lett.
, vol.405
, pp. 394-397
-
-
Albet, S.1
Causeret, C.2
Bentejac, M.3
Mandel, J.-L.4
Aubourg, P.5
Maurice, B.6
-
2
-
-
0033569840
-
The four murine peroxisomal ABC-transporter genes differ in constitutive, inducible and developmental expression
-
J. Berger, S. Albet, M. Bentejac, A. Netik, A. Holzinger, A.A. Roscher, M. Bugaut and S. Forss-Petter (1999) The four murine peroxisomal ABC-transporter genes differ in constitutive, inducible and developmental expression. Eur. J. Biochem. 265 719-727.
-
(1999)
Eur. J. Biochem.
, vol.265
, pp. 719-727
-
-
Berger, J.1
Albet, S.2
Bentejac, M.3
Netik, A.4
Holzinger, A.5
Roscher, A.A.6
Bugaut, M.7
Forss-Petter, S.8
-
3
-
-
0029932602
-
Characterization of a partial pseudogene homologous to the adrenoleukodystrophy gene and application of mutation detection
-
A. Braun, S. Kammerer, H. Ambach and A.A. Roscher (1996) Characterization of a partial pseudogene homologous to the adrenoleukodystrophy gene and application of mutation detection. Hum. Mutat. 7 105-108.
-
(1996)
Hum. Mutat.
, vol.7
, pp. 105-108
-
-
Braun, A.1
Kammerer, S.2
Ambach, H.3
Roscher, A.A.4
-
4
-
-
0030946632
-
Human PEX7 encodes the peroxisomal PTS2 receptor and is responsible for rhizomelic chondrodysplasia punctata
-
N. Braverman, G. Steel, C. Obie, A. Moser, H. Moser, S.J. Gould and D. Valle (1997) Human PEX7 encodes the peroxisomal PTS2 receptor and is responsible for rhizomelic chondrodysplasia punctata. Nat. Genet. 15 369-376.
-
(1997)
Nat. Genet.
, vol.15
, pp. 369-376
-
-
Braverman, N.1
Steel, G.2
Obie, C.3
Moser, A.4
Moser, H.5
Gould, S.J.6
Valle, D.7
-
5
-
-
0031854532
-
An isoform of Pex5p, the human PTS1 receptor, is required for the import of PTS2 proteins into peroxisomes
-
N. Braverman, G. Dodt, S.J. Gould and D. Valle (1998) An isoform of Pex5p, the human PTS1 receptor, is required for the import of PTS2 proteins into peroxisomes. Hum. Mol. Genet. 7 1195-1205.
-
(1998)
Hum. Mol. Genet.
, vol.7
, pp. 1195-1205
-
-
Braverman, N.1
Dodt, G.2
Gould, S.J.3
Valle, D.4
-
6
-
-
0037016760
-
Two different targeting signals direct human peroxisomal membrane protein 22 to peroxisomes
-
U. Brosius, T. Dehmel and J. Gärtner (2002) Two different targeting signals direct human peroxisomal membrane protein 22 to peroxisomes. J. Biol. Chem. 277 774-784.
-
(2002)
J. Biol. Chem.
, vol.277
, pp. 774-784
-
-
Brosius, U.1
Dehmel, T.2
Gärtner, J.3
-
7
-
-
0033047785
-
Metabolic control of peroxisome abundance
-
C.C. Chang, S. South, D. Warren, J. Jones, A.B. Moser, H.W. Moser and S.J. Gould (1999) Metabolic control of peroxisome abundance. J. Cell Sci. 112 1579-1590.
-
(1999)
J. Cell Sci.
, vol.112
, pp. 1579-1590
-
-
Chang, C.C.1
South, S.2
Warren, D.3
Jones, J.4
Moser, A.B.5
Moser, H.W.6
Gould, S.J.7
-
8
-
-
0030588321
-
Topology of ATP-binding domain of adrenoleukodystrophy gene product in peroxisomes
-
M. Contreras, T.K. Sengupta, F. Sheikh, P. Aubourg and I. Singh (1996) Topology of ATP-binding domain of adrenoleukodystrophy gene product in peroxisomes. Arch. Biochem. Biophys. 334 369-379.
-
(1996)
Arch. Biochem. Biophys.
, vol.334
, pp. 369-379
-
-
Contreras, M.1
Sengupta, T.K.2
Sheikh, F.3
Aubourg, P.4
Singh, I.5
-
10
-
-
10144261887
-
A unified nomenclature for peroxisome biogenesis factors
-
B. Distel, R. Erdmann, S.J. Gould, G. Blobel, D.I. Crane, J.M. Cregg, et al. (1996) A unified nomenclature for peroxisome biogenesis factors. J. Cell Biol. 135 1-3.
-
(1996)
J. Cell Biol.
, vol.135
, pp. 1-3
-
-
Distel, B.1
Erdmann, R.2
Gould, S.J.3
Blobel, G.4
Crane, D.I.5
Cregg, J.M.6
-
11
-
-
0030459304
-
Multiple PEX genes are required for proper subcellular distribution and stability of Pex5p, the PTS1 receptor: evidence that PTS1 protein import is mediated by a cycling receptor
-
G. Dodt and S.J. Gould (1996) Multiple PEX genes are required for proper subcellular distribution and stability of Pex5p, the PTS1 receptor: evidence that PTS1 protein import is mediated by a cycling receptor. J. Cell Biol. 135 1763-1774.
-
(1996)
J. Cell Biol.
, vol.135
, pp. 1763-1774
-
-
Dodt, G.1
Gould, S.J.2
-
12
-
-
0028817372
-
Mutations in the PTS1 receptor gene, PXR1, define complementation group 2 of the peroxisome biogenesis disorders
-
G. Dodt, N. Braverman, C. Wong, A. Moser, H.W. Moser, P. Watkins, D. Valle and S.J. Gould (1995) Mutations in the PTS1 receptor gene, PXR1, define complementation group 2 of the peroxisome biogenesis disorders. Nat. Genet. 9 115-124.
-
(1995)
Nat. Genet.
, vol.9
, pp. 115-124
-
-
Dodt, G.1
Braverman, N.2
Wong, C.3
Moser, A.4
Moser, H.W.5
Watkins, P.6
Valle, D.7
Gould, S.J.8
-
13
-
-
0029879509
-
The sorting sequence of the peroxisomal integral membrane protein PMP47 is contained within a short hydrophilic loop
-
J.M. Dyer, J.A. McNew and J.M. Goodman (1996) The sorting sequence of the peroxisomal integral membrane protein PMP47 is contained within a short hydrophilic loop. J. Cell Biol. 133 269-280.
-
(1996)
J. Cell Biol.
, vol.133
, pp. 269-280
-
-
Dyer, J.M.1
McNew, J.A.2
Goodman, J.M.3
-
14
-
-
0036176213
-
Identification of ligand-binding regions of P-glycoprotein by activated-pharmacophore photoaffinity labeling and matrix-assisted laser desorption/ionization time-of-flight mass spectrometry
-
G.F. Ecker, E. Csaszar, S. Kopp, B. Plagens, W.E. Holzer, W. Ernst and P. Chiba (2002) Identification of ligand-binding regions of P-glycoprotein by activated-pharmacophore photoaffinity labeling and matrix-assisted laser desorption/ionization time-of-flight mass spectrometry. Mol. Pharmacol. 61 637-648.
-
(2002)
Mol. Pharmacol.
, vol.61
, pp. 637-648
-
-
Ecker, G.F.1
Csaszar, E.2
Kopp, S.3
Plagens, B.4
Holzer, W.E.5
Ernst, W.6
Chiba, P.7
-
15
-
-
0030757906
-
Interchromosomal duplications of the adrenoleukodystrophy locus: a phenomenon of pericentromeric plasticity
-
E.E. Eichler, M.L. Budarf, M. Rocchi, L.L. Deaven, N.A. Doggett, A. Baldini, D.L. Nelson and H.W. Mohrenweiser (1997) Interchromosomal duplications of the adrenoleukodystrophy locus: a phenomenon of pericentromeric plasticity. Hum. Mol. Genet. 6 991-1002.
-
(1997)
Hum. Mol. Genet.
, vol.6
, pp. 991-1002
-
-
Eichler, E.E.1
Budarf, M.L.2
Rocchi, M.3
Deaven, L.L.4
Doggett, N.A.5
Baldini, A.6
Nelson, D.L.7
Mohrenweiser, H.W.8
-
16
-
-
0030689779
-
Targeted inactivation of the X-linked adrenoleukodystrophy gene in mice
-
S. Forss-Petter, H. Werner, J. Berger, H. Lassmann, B. Molzer, M.H. Schwab, H. Bernheimer, F. Zimmermann and K.A. Nave (1997) Targeted inactivation of the X-linked adrenoleukodystrophy gene in mice. J. Neurosci. Res. 50 829-843.
-
(1997)
J. Neurosci. Res.
, vol.50
, pp. 829-843
-
-
Forss-Petter, S.1
Werner, H.2
Berger, J.3
Lassmann, H.4
Molzer, B.5
Schwab, M.H.6
Bernheimer, H.7
Zimmermann, F.8
Nave, K.A.9
-
17
-
-
0034819367
-
Fibrate induction of the adrenoleukodystrophy-related gene (ABCD2) promoter analysis and role of the peroxisome proliferator-activated receptor PPARalpha
-
S. Fourcade, S. Savary, S. Albet, D. Gauthe, C. Gondcaille, T. Pineau, et al. (2001) Fibrate induction of the adrenoleukodystrophy-related gene (ABCD2) promoter analysis and role of the peroxisome proliferator-activated receptor PPARalpha. Eur. J. Biochem. 268 3490-3500.
-
(2001)
Eur. J. Biochem.
, vol.268
, pp. 3490-3500
-
-
Fourcade, S.1
Savary, S.2
Albet, S.3
Gauthe, D.4
Gondcaille, C.5
Pineau, T.6
-
18
-
-
0028916868
-
Identification and characterization of the putative human peroxisomal C-terminal targeting signal import receptor
-
M. Fransen, C. Brees, E. Baumgart, J.C.T. Vanhooren, M. Baes, G.P. Mannaerts and P.P. Van Veldhoven (1995) Identification and characterization of the putative human peroxisomal C-terminal targeting signal import receptor. J. Biol. Chem. 270 7731-7736.
-
(1995)
J. Biol. Chem.
, vol.270
, pp. 7731-7736
-
-
Fransen, M.1
Brees, C.2
Baumgart, E.3
Vanhooren, J.C.T.4
Baes, M.5
Mannaerts, G.P.6
Van Veldhoven, P.P.7
-
19
-
-
0026849933
-
Mutations in the 70 kD peroxisomal membrane protein gene in Zellweger syndrome
-
J. Gärtner, H. Moser and D. Valle (1992) Mutations in the 70 kD peroxisomal membrane protein gene in Zellweger syndrome. Nat. Genet. 1 16-23.
-
(1992)
Nat. Genet.
, vol.1
, pp. 16-23
-
-
Gärtner, J.1
Moser, H.2
Valle, D.3
-
20
-
-
0027483134
-
Localization of the 70 kD peroxisomal membrane protein to human 1p21-22 and mouse 3
-
J. Gärtner, W. Kearns, C. Rosenberg, P. Pearson, N.G. Copeland, D.J. Gilbert, N. Jenkins and D. Valle (1993) Localization of the 70 kD peroxisomal membrane protein to human 1p21-22 and mouse 3. Genomics 15 412-414.
-
(1993)
Genomics
, vol.15
, pp. 412-414
-
-
Gärtner, J.1
Kearns, W.2
Rosenberg, C.3
Pearson, P.4
Copeland, N.G.5
Gilbert, D.J.6
Jenkins, N.7
Valle, D.8
-
21
-
-
0032033152
-
Genomic organization of the 70-kDa peroxisomal membrane protein gene (PXMP1)
-
J. Gärtner, G. Jimenez-Sanchez, P. Roerig and D. Valle (1998) Genomic organization of the 70-kDa peroxisomal membrane protein gene (PXMP1). Genomics 48 203-208.
-
(1998)
Genomics
, vol.48
, pp. 203-208
-
-
Gärtner, J.1
Jimenez-Sanchez, G.2
Roerig, P.3
Valle, D.4
-
22
-
-
0342576245
-
A proposed model for the PEX5-peroxisomal targeting signal-1 recognition complex
-
G.J. Gatto Jr., B.V. Geisbrecht, S.J. Gould and J.M. Berg (2000) A proposed model for the PEX5-peroxisomal targeting signal-1 recognition complex. Proteins 38 241-246.
-
(2000)
Proteins
, vol.38
, pp. 241-246
-
-
Gatto, G.J.1
Geisbrecht, B.V.2
Gould, S.J.3
Berg, J.M.4
-
23
-
-
0033664345
-
Peroxisomal targeting signal-1 recognition by the TPR domains of human PEX5
-
G.J. Gatto Jr., B.V. Geisbrecht, S.J. Gould and J.M. Berg (2000) Peroxisomal targeting signal-1 recognition by the TPR domains of human PEX5. Nat. Struct. Biol. 7 1091-1095.
-
(2000)
Nat. Struct. Biol.
, vol.7
, pp. 1091-1095
-
-
Gatto, G.J.1
Geisbrecht, B.V.2
Gould, S.J.3
Berg, J.M.4
-
24
-
-
0033804750
-
PEX3 is the causal gene responsible for peroxisome membrane assembly-defective Zellweger syndrome of complementation group G
-
K. Ghaedi, M. Honsho, N. Shimozawa, Y. Suzuki, N. Kondo and Y. Fujiki (2000) PEX3 is the causal gene responsible for peroxisome membrane assembly-defective Zellweger syndrome of complementation group G. Am. J. Hum. Genet. 67 976-981.
-
(2000)
Am. J. Hum. Genet.
, vol.67
, pp. 976-981
-
-
Ghaedi, K.1
Honsho, M.2
Shimozawa, N.3
Suzuki, Y.4
Kondo, N.5
Fujiki, Y.6
-
25
-
-
0034728796
-
Human adrenoleukodystrophy protein and related peroxisomal ABC transporters interact with the peroxisomal assembly protein PEX19p
-
C.J. Gloeckner, P.U. Mayerhofer, P. Landgraf, A.C. Muntau, A. Holzinger, J.-K. Gerber, S. Kammerer, J. Adamski and A.A. Roscher (2000) Human adrenoleukodystrophy protein and related peroxisomal ABC transporters interact with the peroxisomal assembly protein PEX19p. Biochem. Biophys. Res. Commun. 271 144-150.
-
(2000)
Biochem. Biophys. Res. Commun.
, vol.271
, pp. 144-150
-
-
Gloeckner, C.J.1
Mayerhofer, P.U.2
Landgraf, P.3
Muntau, A.C.4
Holzinger, A.5
Gerber, J.-K.6
Kammerer, S.7
Adamski, J.8
Roscher, A.A.9
-
26
-
-
0242392537
-
Pex19p, a farnesylated protein essential for peroxisome biogenesis
-
K. Gotte, W. Girzalsky, M. Linkert, E. Baumgart, S. Kammerer, W.H. Kunau and R. Erdmann (1998) Pex19p, a farnesylated protein essential for peroxisome biogenesis. Mol. Cell Biol. 18 616-628.
-
(1998)
Mol. Cell Biol.
, vol.18
, pp. 616-628
-
-
Gotte, K.1
Girzalsky, W.2
Linkert, M.3
Baumgart, E.4
Kammerer, S.5
Kunau, W.H.6
Erdmann, R.7
-
27
-
-
0034255179
-
The genetics and cell biology of the peroxisome biogenesis disorders
-
S.J. Gould and D. Valle (2000) The genetics and cell biology of the peroxisome biogenesis disorders. Trends Genet. 16 340-344.
-
(2000)
Trends Genet.
, vol.16
, pp. 340-344
-
-
Gould, S.J.1
Valle, D.2
-
28
-
-
0034255179
-
Peroxisome biogenesis disorders: genetics and cell biology
-
S.J. Gould and D. Valle (2000) Peroxisome biogenesis disorders: genetics and cell biology. TIGS 16 340-344.
-
(2000)
TIGS
, vol.16
, pp. 340-344
-
-
Gould, S.J.1
Valle, D.2
-
29
-
-
0001687866
-
The peroxisome biogenesis disorders
-
C.R. Scriver, A.L. Beaudet, W.S. Sly, D. Valle (Eds), New York: McGraw-Hill
-
S.J. Gould, G.V. Raymond and D. Valle (2001) The peroxisome biogenesis disorders. C.R. Scriver, A.L. Beaudet, W.S. Sly, D. Valle (Eds) The Metabolic and Molecular Basis of Inherited Disease New York: McGraw-Hill 3181-3217.
-
(2001)
The Metabolic and Molecular Basis of Inherited Disease
, pp. 3181-3217
-
-
Gould, S.J.1
Raymond, G.V.2
Valle, D.3
-
30
-
-
0034717895
-
Transport of fatty acids and metabolites across the peroxisomal membrane
-
E.H. Hettema and H.F. Tabak (2000) Transport of fatty acids and metabolites across the peroxisomal membrane. Biochim. Biophys. Acta 1486 18-27.
-
(2000)
Biochim. Biophys. Acta
, vol.1486
, pp. 18-27
-
-
Hettema, E.H.1
Tabak, H.F.2
-
31
-
-
0029783210
-
The ABC transporter proteins Pat1 and Pat2 are required for import of long-chain fatty acids into peroxisomes of Saccharomyces cerevisiae
-
E.H. Hettema, C.W.T. van Roermund, B. Distel, M. van den Berg, C. Vilela, C. Rodrigues-Pousada, R.J.A. Wanders and H.F. Tabak (1996) The ABC transporter proteins Pat1 and Pat2 are required for import of long-chain fatty acids into peroxisomes of Saccharomyces cerevisiae. EMBO J. 15 3813-3822.
-
(1996)
EMBO J.
, vol.15
, pp. 3813-3822
-
-
Hettema, E.H.1
van Roermund, C.W.T.2
Distel, B.3
van den Berg, M.4
Vilela, C.5
Rodrigues-Pousada, C.6
Wanders, R.J.A.7
Tabak, H.F.8
-
32
-
-
0034677197
-
Saccharomyces cerevisiae pex3p and pex19p are required for proper localization and stability of peroxisomal membrane proteins
-
E.H. Hettema, W. Girzalsky, M. van Den Berg, R. Erdmann and B. Distel (2000) Saccharomyces cerevisiae pex3p and pex19p are required for proper localization and stability of peroxisomal membrane proteins. EMBO J. 19 223-233.
-
(2000)
EMBO J.
, vol.19
, pp. 223-233
-
-
Hettema, E.H.1
Girzalsky, W.2
van Den Berg, M.3
Erdmann, R.4
Distel, B.5
-
33
-
-
0031561433
-
cDNA cloning and mRNA expression of the human adrenoleukodystrophy related protein (ALDP) a peroxisomal ABC transporter
-
A. Holzinger, S. Kammerer, J. Berger and A.A. Roscher (1997) cDNA cloning and mRNA expression of the human adrenoleukodystrophy related protein (ALDP) a peroxisomal ABC transporter. Biochem. Biophys. Res. Commun. 239 261-264.
-
(1997)
Biochem. Biophys. Res. Commun.
, vol.239
, pp. 261-264
-
-
Holzinger, A.1
Kammerer, S.2
Berger, J.3
Roscher, A.A.4
-
34
-
-
0031559581
-
Primary structure of human PMP69, a putative peroxisomal ABC-transporter
-
A. Holzinger, S. Kammerer and A.A. Roscher (1997) Primary structure of human PMP69, a putative peroxisomal ABC-transporter. Biochem. Biophys. Res. Commun. 237 152-157.
-
(1997)
Biochem. Biophys. Res. Commun.
, vol.237
, pp. 152-157
-
-
Holzinger, A.1
Kammerer, S.2
Roscher, A.A.3
-
35
-
-
0032540497
-
Genomic organization and chromosomal localization of the human peroxisomal membrane protein-1-like protein (PXMP1-L) gene encoding a peroxisomal ABC transporter
-
A. Holzinger, A.A. Roscher, P. Landgraf, P. Lichtner and S. Kammerer (1998) Genomic organization and chromosomal localization of the human peroxisomal membrane protein-1-like protein (PXMP1-L) gene encoding a peroxisomal ABC transporter. FEBS Lett. 426 238-242.
-
(1998)
FEBS Lett.
, vol.426
, pp. 238-242
-
-
Holzinger, A.1
Roscher, A.A.2
Landgraf, P.3
Lichtner, P.4
Kammerer, S.5
-
36
-
-
0032471611
-
Mutation in PEX16 is causal in the peroxisome-deficient Zellweger syndrome of complementation group D
-
M. Honsho, S. Tamura, N. Shimozawa, Y. Suzuki, N. Kondo and Y. Fujiki (1998) Mutation in PEX16 is causal in the peroxisome-deficient Zellweger syndrome of complementation group D. Am. J. Hum. Genet. 63 1622-1630.
-
(1998)
Am. J. Hum. Genet.
, vol.63
, pp. 1622-1630
-
-
Honsho, M.1
Tamura, S.2
Shimozawa, N.3
Suzuki, Y.4
Kondo, N.5
Fujiki, Y.6
-
37
-
-
0034685825
-
2) determined by site-directed chemical cross-linking
-
S. Hunke, M. Mourez, M. Jéhanno, E. Dassa and E. Schneider (2000) ATP modulates subunit-subunit interactions in an ATP-binding cassette transporter (MalFGK2) determined by site-directed chemical cross-linking. J. Biol. Chem. 275 15526-15534.
-
(2000)
J. Biol. Chem.
, vol.275
, pp. 15526-15534
-
-
Hunke, S.1
Mourez, M.2
Jéhanno, M.3
Dassa, E.4
Schneider, E.5
-
38
-
-
0033597211
-
Characterization of the 70 kDa peroxisomal membrane protein, an ATP binding cassette transporter
-
T. Imanaka, K. Aihara, T. Takano, A. Yamashita, R. Sato, Y. Suzuki, S. Yokota and T. Osumi (1999) Characterization of the 70 kDa peroxisomal membrane protein, an ATP binding cassette transporter. J. Biol. Chem. 274 11968-11976.
-
(1999)
J. Biol. Chem.
, vol.274
, pp. 11968-11976
-
-
Imanaka, T.1
Aihara, K.2
Takano, T.3
Yamashita, A.4
Sato, R.5
Suzuki, Y.6
Yokota, S.7
Osumi, T.8
-
39
-
-
0028227288
-
PxF, a prenylated protein of peroxisomes
-
G.L. James, J.L. Goldstein, R.K.W. Pathak, R.G. Anderson and M.S. Brown (1994) PxF, a prenylated protein of peroxisomes. J. Biol. Chem. 269 14182-14190.
-
(1994)
J. Biol. Chem.
, vol.269
, pp. 14182-14190
-
-
James, G.L.1
Goldstein, J.L.2
Pathak, R.K.W.3
Anderson, R.G.4
Brown, M.S.5
-
40
-
-
0035966061
-
In situ measurements of the pH of mammalian peroxisomes using the fluorescent protein pHluorin
-
A. Jankowski, J.H. Kim, R.F. Collins, R. Daneman, P. Walton and S. Grinstein (2001) In situ measurements of the pH of mammalian peroxisomes using the fluorescent protein pHluorin. J. Biol. Chem. 276 48748-48753.
-
(2001)
J. Biol. Chem.
, vol.276
, pp. 48748-48753
-
-
Jankowski, A.1
Kim, J.H.2
Collins, R.F.3
Daneman, R.4
Walton, P.5
Grinstein, S.6
-
41
-
-
0004721783
-
Fasting fuel homeostasis triggered by defective phytanic and pristanic acids metabolism in the 70 kDA peroxisomal protein deficient mice
-
G. Jimenez-Sanchez, K. Hebron, I. Silva-Zolezzi, S.J. Mihalik, P.A. Watkins, M. Espeel, A. Moser, G. Thomas, F. Röels and D. Valle (2000) Fasting fuel homeostasis triggered by defective phytanic and pristanic acids metabolism in the 70 kDA peroxisomal protein deficient mice. Am. J. Hum. Genet. 67 A65.
-
(2000)
Am. J. Hum. Genet.
, vol.67
, pp. A65
-
-
Jimenez-Sanchez, G.1
Hebron, K.2
Silva-Zolezzi, I.3
Mihalik, S.J.4
Watkins, P.A.5
Espeel, M.6
Moser, A.7
Thomas, G.8
Röels, F.9
Valle, D.10
-
42
-
-
0035844874
-
Multiple distinct targeting signals in integral peroxisomal membrane proteins
-
J.M. Jones, J.C. Morrell and S.J. Gould (2001) Multiple distinct targeting signals in integral peroxisomal membrane proteins. J. Cell Biol. 153 1141-1149.
-
(2001)
J. Cell Biol.
, vol.153
, pp. 1141-1149
-
-
Jones, J.M.1
Morrell, J.C.2
Gould, S.J.3
-
43
-
-
0030771852
-
DNA binding properties of peroxisome proliferator-activated receptor subtypes on various natural peroxisome proliferator response elements
-
C. Juge-Aubry, A. Pernin, T. Favez, A.G. Burger, W. Wahli, C.A. Meier and B. Desvergnee (1997) DNA binding properties of peroxisome proliferator-activated receptor subtypes on various natural peroxisome proliferator response elements. J. Biol. Chem. 272 25252-25259.
-
(1997)
J. Biol. Chem.
, vol.272
, pp. 25252-25259
-
-
Juge-Aubry, C.1
Pernin, A.2
Favez, T.3
Burger, A.G.4
Wahli, W.5
Meier, C.A.6
Desvergnee, B.7
-
44
-
-
0025255475
-
The 70 kDa peroxisomal membrane protein is a member of the Mdr (P-glycoprotein)-related ATP-binding protein superfamily
-
K. Kamijo, S. Taketani, S. Yokata, T. Osumi and T. Hashimoto (1990) The 70 kDa peroxisomal membrane protein is a member of the Mdr (P-glycoprotein)-related ATP-binding protein superfamily. J. Biol. Chem. 265 4534-4540.
-
(1990)
J. Biol. Chem.
, vol.265
, pp. 4534-4540
-
-
Kamijo, K.1
Taketani, S.2
Yokata, S.3
Osumi, T.4
Hashimoto, T.5
-
45
-
-
0031730433
-
Gene redundancy and pharmacologic gene therapy: Implications for X-linked adrenoleukodystrophy
-
S. Kemp, H.M. Wei, J.F. Lu, L.T. Braiterman, M.C. McGuinness, A.B. Moser, P.A. Watkins and K.D. Smith (1998) Gene redundancy and pharmacologic gene therapy: Implications for X-linked adrenoleukodystrophy. Nat. Med. 4 1261-1268.
-
(1998)
Nat. Med.
, vol.4
, pp. 1261-1268
-
-
Kemp, S.1
Wei, H.M.2
Lu, J.F.3
Braiterman, L.T.4
McGuinness, M.C.5
Moser, A.B.6
Watkins, P.A.7
Smith, K.D.8
-
46
-
-
0034713444
-
Roles of PPARs in health and disease
-
S. Kersten, B. Desvergne and W. Wahli (2000) Roles of PPARs in health and disease. Nature 405 421-424.
-
(2000)
Nature
, vol.405
, pp. 421-424
-
-
Kersten, S.1
Desvergne, B.2
Wahli, W.3
-
47
-
-
0035805574
-
Recognition of peroxisomal targeting signal type 1 by the import receptor Pex5p
-
A.T.J. Klein, P. Barnett, G. Bottger, D. Konings, H.F. Tabak and B. Distel (2001) Recognition of peroxisomal targeting signal type 1 by the import receptor Pex5p. J. Biol. Chem. 276 15034-15041.
-
(2001)
J. Biol. Chem.
, vol.276
, pp. 15034-15041
-
-
Klein, A.T.J.1
Barnett, P.2
Bottger, G.3
Konings, D.4
Tabak, H.F.5
Distel, B.6
-
48
-
-
0027299142
-
Two complementary approaches to study peroxisome biogenesis in Saccharomyces cerevisiae: forward and reversed genetics
-
W.H. Kunau, A. Beyer, T. Franken, K. Gotte, M. Marzioch, J. Saidowsky, A. Skaletz-Rorowski and F.F. Wiebel (1993) Two complementary approaches to study peroxisome biogenesis in Saccharomyces cerevisiae: forward and reversed genetics. Biochimie 75 209-224.
-
(1993)
Biochimie
, vol.75
, pp. 209-224
-
-
Kunau, W.H.1
Beyer, A.2
Franken, T.3
Gotte, K.4
Marzioch, M.5
Saidowsky, J.6
Skaletz-Rorowski, A.7
Wiebel, F.F.8
-
49
-
-
0025332595
-
Topographical localization of peroxisomal acyl-CoA ligases: differential localization of palmitoyl-CoA and lignoceroyl-CoA ligases
-
O. Lazo, M. Contreras and I. Singh (1990) Topographical localization of peroxisomal acyl-CoA ligases: differential localization of palmitoyl-CoA and lignoceroyl-CoA ligases. Biochemistry 29 3981-3986.
-
(1990)
Biochemistry
, vol.29
, pp. 3981-3986
-
-
Lazo, O.1
Contreras, M.2
Singh, I.3
-
50
-
-
0000470358
-
Homo- and heterodimerization of peroxisomal ATP-binding cassette half-transporters
-
L.-S. Liu, K. Janvier, V. Berteaux-Lecellier, N. Cartier, R. Benarous and P. Aubourg (1999) Homo- and heterodimerization of peroxisomal ATP-binding cassette half-transporters. J. Biol. Chem. 274 32738-32743.
-
(1999)
J. Biol. Chem.
, vol.274
, pp. 32738-32743
-
-
Liu, L.-S.1
Janvier, K.2
Berteaux-Lecellier, V.3
Cartier, N.4
Benarous, R.5
Aubourg, P.6
-
51
-
-
0030793307
-
A mouse model for X-linked adrenoleukodystrophy
-
J.F. Lu, A.M. Lawler, P.A. Watkins, J.M. Powers, A.B. Moser, H.W. Moser and K.D. Smith (1997) A mouse model for X-linked adrenoleukodystrophy. Proc. Natl Acad. Sci. USA 94 9366-9371.
-
(1997)
Proc. Natl Acad. Sci. USA
, vol.94
, pp. 9366-9371
-
-
Lu, J.F.1
Lawler, A.M.2
Watkins, P.A.3
Powers, J.M.4
Moser, A.B.5
Moser, H.W.6
Smith, K.D.7
-
52
-
-
13044312086
-
Human PEX19: cDNA cloning by functional complementation, mutation analysis in a patient with Zellweger syndrome and potential role in peroxisomal membrane assembly
-
Y. Matsuzono, N. Kinoshita, S. Tamura, N. Shimozawa, M. Hamasaki, K. Ghaedi, R.J.A. Wanders, Y. Suzuki, N. Kondo and Y. Fujiki (1999) Human PEX19: cDNA cloning by functional complementation, mutation analysis in a patient with Zellweger syndrome and potential role in peroxisomal membrane assembly. Proc. Natl Acad. Sci. USA 96 2116-2121.
-
(1999)
Proc. Natl Acad. Sci. USA
, vol.96
, pp. 2116-2121
-
-
Matsuzono, Y.1
Kinoshita, N.2
Tamura, S.3
Shimozawa, N.4
Hamasaki, M.5
Ghaedi, K.6
Wanders, R.J.A.7
Suzuki, Y.8
Kondo, N.9
Fujiki, Y.10
-
53
-
-
0002277381
-
X-linked adrenoleukodystrophy
-
C.R. Scriver, A.L. Beaudet, W.S. Sly, D. Valle (Eds), New York: McGraw-Hill
-
H.W. Moser, K.D. Smith, P.A. Watkins, J.M. Powers and A.B. Moser (2001) X-linked adrenoleukodystrophy. C.R. Scriver, A.L. Beaudet, W.S. Sly, D. Valle (Eds) The Metabolic and Molecular Basis of Inherited Disease New York: McGraw-Hill 3257-3302.
-
(2001)
The Metabolic and Molecular Basis of Inherited Disease
, pp. 3257-3302
-
-
Moser, H.W.1
Smith, K.D.2
Watkins, P.A.3
Powers, J.M.4
Moser, A.B.5
-
54
-
-
0028006093
-
The gene responsible for adrenoleukodystrophy encodes a peroxisomal membrane protein
-
J. Mosser, Y. Lutz, M.E. Stoeckel, C.O. Sarde, C. Kretz, A.M. Douar, J. Lopez, P. Aubourg and J.L. Mandel (1994) The gene responsible for adrenoleukodystrophy encodes a peroxisomal membrane protein. Hum. Mol. Genet. 3 265-271.
-
(1994)
Hum. Mol. Genet.
, vol.3
, pp. 265-271
-
-
Mosser, J.1
Lutz, Y.2
Stoeckel, M.E.3
Sarde, C.O.4
Kretz, C.5
Douar, A.M.6
Lopez, J.7
Aubourg, P.8
Mandel, J.L.9
-
55
-
-
0031003680
-
Rhizomelic chondrodysplasia punctata is a peroxisomal protein targeting disease caused by a non-functional PTS2 receptor
-
A.M. Motley, E.H. Hettema, E.M. Hogenhout, P. Brites, A.L.M.A. ten Asbroek, F.A. Wijburg, et al. (1997) Rhizomelic chondrodysplasia punctata is a peroxisomal protein targeting disease caused by a non-functional PTS2 receptor. Nat. Genet. 15 377-380.
-
(1997)
Nat. Genet.
, vol.15
, pp. 377-380
-
-
Motley, A.M.1
Hettema, E.H.2
Hogenhout, E.M.3
Brites, P.4
ten Asbroek, A.L.M.A.5
Wijburg, F.A.6
-
56
-
-
0030910930
-
Subunit interactions in ABC transporters: a conserved sequence in hydrophobic membrane proteins of periplasmic permeases defines an important site of interaction with the ATPase subunits
-
M. Mourez, M. Hofnung and E. Dassa (1997) Subunit interactions in ABC transporters: a conserved sequence in hydrophobic membrane proteins of periplasmic permeases defines an important site of interaction with the ATPase subunits. EMBO J. 16 3066-3077.
-
(1997)
EMBO J.
, vol.16
, pp. 3066-3077
-
-
Mourez, M.1
Hofnung, M.2
Dassa, E.3
-
57
-
-
0033794897
-
Defective peroxisome membrane synthesis due to mutations in human PEX3 causes Zellweger Syndrome, complementation group G
-
A.C. Muntau, P.U. Mayerhofer, B.C. Paton, S. Kammerer and A.A. Roscher (2000) Defective peroxisome membrane synthesis due to mutations in human PEX3 causes Zellweger Syndrome, complementation group G. Am. J. Hum. Genet. 67 967-975.
-
(2000)
Am. J. Hum. Genet.
, vol.67
, pp. 967-975
-
-
Muntau, A.C.1
Mayerhofer, P.U.2
Paton, B.C.3
Kammerer, S.4
Roscher, A.A.5
-
58
-
-
0031962116
-
Peroxisome targeting signal type 1 (PTS1) receptor is involved in import of both PTS1 and PTS2: Studies with PEX5-defective CHO cell mutants
-
H. Otera, K. Okumoto, K. Tateishi, Y. Ikoma, E. Matsuda, M. Nishimura, et al. (1998) Peroxisome targeting signal type 1 (PTS1) receptor is involved in import of both PTS1 and PTS2: Studies with PEX5-defective CHO cell mutants. Mol. Cell Biol. 18 388-399.
-
(1998)
Mol. Cell Biol.
, vol.18
, pp. 388-399
-
-
Otera, H.1
Okumoto, K.2
Tateishi, K.3
Ikoma, Y.4
Matsuda, E.5
Nishimura, M.6
-
59
-
-
0034647937
-
The mammalian peroxin Pex5pL, the longer isoform of the mobile peroxisome targeting signal (PTS) type 1 transporter, translocates the Pex7p PTS2 protein complex into peroxisomes via its initial docking site, Pex14p
-
H. Otera, T. Harano, M. Honsho, K. Ghaedi, S. Mukai, A. Tanaka, A. Kawai, N. Shimizu and Y. Fujiki (2000) The mammalian peroxin Pex5pL, the longer isoform of the mobile peroxisome targeting signal (PTS) type 1 transporter, translocates the Pex7p PTS2 protein complex into peroxisomes via its initial docking site, Pex14p. J. Biol. Chem. 275 21703-21714.
-
(2000)
J. Biol. Chem.
, vol.275
, pp. 21703-21714
-
-
Otera, H.1
Harano, T.2
Honsho, M.3
Ghaedi, K.4
Mukai, S.5
Tanaka, A.6
Kawai, A.7
Shimizu, N.8
Fujiki, Y.9
-
60
-
-
0034616064
-
Targeting of the 22 kDa integral peroxisomal membrane protein
-
B. Pause, R. Saffrich, A. Hunziker, W. Ansorge and W.W. Just (2000) Targeting of the 22 kDa integral peroxisomal membrane protein. FEBS Lett. 471 23-28.
-
(2000)
FEBS Lett.
, vol.471
, pp. 23-28
-
-
Pause, B.1
Saffrich, R.2
Hunziker, A.3
Ansorge, W.4
Just, W.W.5
-
61
-
-
0028841420
-
Localization of mRNAs for adrenoleukodystrophy and the 70 kDa peroxisomal (PMP70) proteins in the rat brain during post-natal development
-
H. Pollard, J. Moreau and P. Aubourg (1995) Localization of mRNAs for adrenoleukodystrophy and the 70 kDa peroxisomal (PMP70) proteins in the rat brain during post-natal development. J. Neurosci. Res. 42 433-437.
-
(1995)
J. Neurosci. Res.
, vol.42
, pp. 433-437
-
-
Pollard, H.1
Moreau, J.2
Aubourg, P.3
-
62
-
-
0034672587
-
Characterization of the adrenoleukodystrophy-related (ALDR, ABCD2) gene promoters: Inductibility by retinoic acid and forskolin
-
A. Pujol, N. Troffer-Charlier, E. Metzger, G. Chimini and J.L. Mandel (2000) Characterization of the adrenoleukodystrophy-related (ALDR, ABCD2) gene promoters: Inductibility by retinoic acid and forskolin. Genomics 70 131-139.
-
(2000)
Genomics
, vol.70
, pp. 131-139
-
-
Pujol, A.1
Troffer-Charlier, N.2
Metzger, E.3
Chimini, G.4
Mandel, J.L.5
-
64
-
-
1842335689
-
Rhizomelic chondrodysplasia punctata is caused by deficiency of human PEX7, a homologue of the yeast PTS2 receptor
-
P.E. Purdue, J.W. Zhang, M. Skoneczny and P.B. Lazarow (1997) Rhizomelic chondrodysplasia punctata is caused by deficiency of human PEX7, a homologue of the yeast PTS2 receptor. Nat. Genet. 15 381-384.
-
(1997)
Nat. Genet.
, vol.15
, pp. 381-384
-
-
Purdue, P.E.1
Zhang, J.W.2
Skoneczny, M.3
Lazarow, P.B.4
-
65
-
-
0022446395
-
Transcriptional regulation of peroxisomal fatty acyl-CoA oxidase and enoyl-CoA hydratase/3-hydroxyacyl-CoA dehydrogenase in rat liver by peroxisome proliferators
-
J.K. Reddy, S.K. Goel, M.R. Nemali, J.J. Carrino, T.G. Laffer, M.K. Reddy, et al. (1986) Transcriptional regulation of peroxisomal fatty acyl-CoA oxidase and enoyl-CoA hydratase/3-hydroxyacyl-CoA dehydrogenase in rat liver by peroxisome proliferators. Proc. Natl Acad. Sci. USA 83 1747-1751.
-
(1986)
Proc. Natl Acad. Sci. USA
, vol.83
, pp. 1747-1751
-
-
Reddy, J.K.1
Goel, S.K.2
Nemali, M.R.3
Carrino, J.J.4
Laffer, T.G.5
Reddy, M.K.6
-
66
-
-
0034515057
-
The genetics of peroxisome biogenesis
-
K.A. Sacksteder and S.J. Gould (2000) The genetics of peroxisome biogenesis. Annu. Rev. Genet. 34 623-652.
-
(2000)
Annu. Rev. Genet.
, vol.34
, pp. 623-652
-
-
Sacksteder, K.A.1
Gould, S.J.2
-
67
-
-
0034611003
-
PEX19 binds multiple peroxisomal membrane proteins, is predominantly cytoplasmic, and is required for peroxisome membrane synthesis
-
K.A. Sacksteder, J.M. Jones, S.T. South, X. Li, Y. Liu and S.J. Gould (2000) PEX19 binds multiple peroxisomal membrane proteins, is predominantly cytoplasmic, and is required for peroxisome membrane synthesis. J. Cell Biol. 148 931-944.
-
(2000)
J. Cell Biol.
, vol.148
, pp. 931-944
-
-
Sacksteder, K.A.1
Jones, J.M.2
South, S.T.3
Li, X.4
Liu, Y.5
Gould, S.J.6
-
68
-
-
0027933788
-
Genomic organization of the adrenoleukodystrophy gene
-
C.O. Sarde, J. Mosser, P. Kioschis, C. Kretz, S. Vicaire, P. Aubourg, A. Poustka and J.L. Mandel (1994) Genomic organization of the adrenoleukodystrophy gene. Genomics 22 13-20.
-
(1994)
Genomics
, vol.22
, pp. 13-20
-
-
Sarde, C.O.1
Mosser, J.2
Kioschis, P.3
Kretz, C.4
Vicaire, S.5
Aubourg, P.6
Poustka, A.7
Mandel, J.L.8
-
69
-
-
0028240216
-
Bacterial binding protein-dependent permeases: characterization of distinctive signatures for functionally related integral cytoplasmic membrane proteins
-
W. Saurin, W. Koster and E. Dassa (1994) Bacterial binding protein-dependent permeases: characterization of distinctive signatures for functionally related integral cytoplasmic membrane proteins. Mol. Microbiol. 12 993-1004.
-
(1994)
Mol. Microbiol.
, vol.12
, pp. 993-1004
-
-
Saurin, W.1
Koster, W.2
Dassa, E.3
-
70
-
-
0034843468
-
Identification of peroxisomal membrane proteins of Saccharomyces cerevisiae by mass spectrometry
-
H. Schäfer, K. Nau, A. Sickmann, R. Erdmann and H.E. Meyer (2001) Identification of peroxisomal membrane proteins of Saccharomyces cerevisiae by mass spectrometry. Electrophoresis 22 2955-2968.
-
(2001)
Electrophoresis
, vol.22
, pp. 2955-2968
-
-
Schäfer, H.1
Nau, K.2
Sickmann, A.3
Erdmann, R.4
Meyer, H.E.5
-
71
-
-
0029969114
-
A Saccharomyces cerevisiae homolog of the human adrenoleukodystrophy transporter is a heterodimer of two half ATP-binding cassette transporter
-
N. Shani and D. Valle (1996) A Saccharomyces cerevisiae homolog of the human adrenoleukodystrophy transporter is a heterodimer of two half ATP-binding cassette transporter. Proc. Natl Acad. Sci. USA 93 11901-11906.
-
(1996)
Proc. Natl Acad. Sci. USA
, vol.93
, pp. 11901-11906
-
-
Shani, N.1
Valle, D.2
-
72
-
-
0029011568
-
PXA1, a putative S. cerevisiae homolog of the human adrenoleukodystrophy gene
-
N. Shani, P.A. Watkins and D. Valle (1995) PXA1, a putative S. cerevisiae homolog of the human adrenoleukodystrophy gene. Proc. Natl Acad. Sci. USA 92 6012-6016.
-
(1995)
Proc. Natl Acad. Sci. USA
, vol.92
, pp. 6012-6016
-
-
Shani, N.1
Watkins, P.A.2
Valle, D.3
-
73
-
-
0029883155
-
Characterization and analysis of conserved motifs in a peroxisomal ATP-binding cassette transporter
-
N. Shani, A. Sapag and D. Valle (1996) Characterization and analysis of conserved motifs in a peroxisomal ATP-binding cassette transporter. J. Biol. Chem. 271 8725-8730.
-
(1996)
J. Biol. Chem.
, vol.271
, pp. 8725-8730
-
-
Shani, N.1
Sapag, A.2
Valle, D.3
-
74
-
-
0345575773
-
Four half ABC transporters may heterodimerize in the peroxisome membrane
-
N. Shani, G. Steel, M. Dean and D. Valle (1996) Four half ABC transporters may heterodimerize in the peroxisome membrane. Am. J. Hum. Genet. 59 A42.
-
(1996)
Am. J. Hum. Genet.
, vol.59
, pp. A42
-
-
Shani, N.1
Steel, G.2
Dean, M.3
Valle, D.4
-
75
-
-
0030776037
-
Identification of a fourth half ABC transporter in the human peroxisomal membrane
-
N. Shani, G. Jimenez-Sanchez, G. Steel, M. Dean and D. Valle (1997) Identification of a fourth half ABC transporter in the human peroxisomal membrane. Hum. Mol. Genet. 6 1925-1931.
-
(1997)
Hum. Mol. Genet.
, vol.6
, pp. 1925-1931
-
-
Shani, N.1
Jimenez-Sanchez, G.2
Steel, G.3
Dean, M.4
Valle, D.5
-
76
-
-
0032893407
-
X-linked adrenoleukodystrophy: Genes, mutations and phenotypes
-
K.D. Smith, S. Kemp, L.T. Braiterman, J.-F. Lu, H.-M. Wei, M. Geraghty, G. Stetten, J.S. Bergin, J. Pevsner and P.A. Watkins (1999) X-linked adrenoleukodystrophy: Genes, mutations and phenotypes. Neurochem. Res. 24 521-535.
-
(1999)
Neurochem. Res.
, vol.24
, pp. 521-535
-
-
Smith, K.D.1
Kemp, S.2
Braiterman, L.T.3
Lu, J.-F.4
Wei, H.-M.5
Geraghty, M.6
Stetten, G.7
Bergin, J.S.8
Pevsner, J.9
Watkins, P.A.10
-
77
-
-
0033015535
-
Pex19p interacts with pex3p and pex10p and is essential for peroxisome biogenesis in Pichia pastoris
-
W.B. Snyder, K.N. Faber, T.J. Wenzel, A. Koller, G.H. Luers, L. Rangell, G.A. Keller and S. Subramani (1999) Pex19p interacts with pex3p and pex10p and is essential for peroxisome biogenesis in Pichia pastoris. Mol. Biol. Cell 10 1745-1761.
-
(1999)
Mol. Biol. Cell
, vol.10
, pp. 1745-1761
-
-
Snyder, W.B.1
Faber, K.N.2
Wenzel, T.J.3
Koller, A.4
Luers, G.H.5
Rangell, L.6
Keller, G.A.7
Subramani, S.8
-
78
-
-
0034641098
-
The peroxin Pex19p interacts with multiple, integral membrane proteins at the peroxisomal membrane
-
W.B. Snyder, A. Koller, A.J. Choy and S. Subramani (2000) The peroxin Pex19p interacts with multiple, integral membrane proteins at the peroxisomal membrane. J. Cell Biol. 149 1171-1178.
-
(2000)
J. Cell Biol.
, vol.149
, pp. 1171-1178
-
-
Snyder, W.B.1
Koller, A.2
Choy, A.J.3
Subramani, S.4
-
79
-
-
0033601767
-
Peroxisome synthesis in the absence of preexisting peroxisomes
-
S.T. South and S.J. Gould (1999) Peroxisome synthesis in the absence of preexisting peroxisomes. J. Cell Biol. 144 255-266.
-
(1999)
J. Cell Biol.
, vol.144
, pp. 255-266
-
-
South, S.T.1
Gould, S.J.2
-
80
-
-
0034717704
-
Inhibitors of COPI and COPII do not block PEX3-mediated peroxisome synthesis
-
S.T. South, K.A. Sacksteder, X. Li, Y. Liu, M. Santos and S.J. Gould (2000) Inhibitors of COPI and COPII do not block PEX3-mediated peroxisome synthesis. J. Cell Biol. 149 1345-1360.
-
(2000)
J. Cell Biol.
, vol.149
, pp. 1345-1360
-
-
South, S.T.1
Sacksteder, K.A.2
Li, X.3
Liu, Y.4
Santos, M.5
Gould, S.J.6
-
81
-
-
0032869224
-
Role of very long chain acyl-coenzyme A synthetase in X-linked adrenoleukodystrophy
-
S.J. Steinberg, S. Kemp, L.T. Braiterman and P.A. Watkins (1999) Role of very long chain acyl-coenzyme A synthetase in X-linked adrenoleukodystrophy. Ann. Neurol. 46 409-412.
-
(1999)
Ann. Neurol.
, vol.46
, pp. 409-412
-
-
Steinberg, S.J.1
Kemp, S.2
Braiterman, L.T.3
Watkins, P.A.4
-
82
-
-
0032887065
-
Human liver-specific very long chain acyl-coenzyme A synthetase: cDNA cloning and characterization of a second enzymatically active protein
-
S.J. Steinberg, S.J. Wang, M.C. McGuinness and P.A. Watkins (1999) Human liver-specific very long chain acyl-coenzyme A synthetase: cDNA cloning and characterization of a second enzymatically active protein. Mol. Genet. Metab. 68 32-42.
-
(1999)
Mol. Genet. Metab.
, vol.68
, pp. 32-42
-
-
Steinberg, S.J.1
Wang, S.J.2
McGuinness, M.C.3
Watkins, P.A.4
-
83
-
-
0031941276
-
Components involved in peroxisome import, biogenesis, proliferation, turnover and movement
-
S. Subramani (1998) Components involved in peroxisome import, biogenesis, proliferation, turnover and movement. Physiol. Rev. 78 171-188.
-
(1998)
Physiol. Rev.
, vol.78
, pp. 171-188
-
-
Subramani, S.1
-
84
-
-
0030066019
-
The PAL1 gene product is a peroxisomal ATP-binding cassette transporter in the yeast Saccharomyces cerevisiae
-
E.E. Swartzman, M.N. Viswanathan and J. Thorner (1996) The PAL1 gene product is a peroxisomal ATP-binding cassette transporter in the yeast Saccharomyces cerevisiae. J. Cell Biol. 132 549-563.
-
(1996)
J. Cell Biol.
, vol.132
, pp. 549-563
-
-
Swartzman, E.E.1
Viswanathan, M.N.2
Thorner, J.3
-
85
-
-
0033231876
-
Peroxisomes: simple function but complex in maintenance
-
H.F. Tabak, I. Braakman and B. Distel (1999) Peroxisomes: simple function but complex in maintenance. Trends Cell Biol. 9 447-453.
-
(1999)
Trends Cell Biol.
, vol.9
, pp. 447-453
-
-
Tabak, H.F.1
Braakman, I.2
Distel, B.3
-
86
-
-
0034967980
-
Identification of a peroxisomal ATP carrier required for medium-chain fatty acid β-oxidation and normal peroxisome proliferation in Saccharomyces cerevisiae
-
C.W. van Roermund, R. Drissen, M. van den Berg, L. Ijlst, E.H. Hettema, H.F. Tabak, H.R. Waterham and R.J. Wanders (2001) Identification of a peroxisomal ATP carrier required for medium-chain fatty acid β-oxidation and normal peroxisome proliferation in Saccharomyces cerevisiae. Mol. Cell Biol. 21 4321-4329.
-
(2001)
Mol. Cell Biol.
, vol.21
, pp. 4321-4329
-
-
van Roermund, C.W.1
Drissen, R.2
van den Berg, M.3
Ijlst, L.4
Hettema, E.H.5
Tabak, H.F.6
Waterham, H.R.7
Wanders, R.J.8
-
87
-
-
0030662714
-
Transport of activated fatty acids by the peroxisomal ATP-binding cassette transporter Pxa2 in a semi-intact yeast system
-
N. Verleur, E.H. Hettema, C.W.T. Van Roermund, H.F. Tabak and R.J.A. Wanders (1997) Transport of activated fatty acids by the peroxisomal ATP-binding cassette transporter Pxa2 in a semi-intact yeast system. Eur. J. Biochem. 249 657-661.
-
(1997)
Eur. J. Biochem.
, vol.249
, pp. 657-661
-
-
Verleur, N.1
Hettema, E.H.2
Van Roermund, C.W.T.3
Tabak, H.F.4
Wanders, R.J.A.5
-
88
-
-
0033278397
-
Fatty acids, eicosanoids, and hypolipidemic agents regulate gene expression through direct binding to peroxisome proliferator-activated receptors
-
W. Wahli, P.R. Devchand, A. Ijpenberg and B. Desvergne (1999) Fatty acids, eicosanoids, and hypolipidemic agents regulate gene expression through direct binding to peroxisome proliferator-activated receptors. Adv. Exp. Med. Biol. 447 199-209.
-
(1999)
Adv. Exp. Med. Biol.
, vol.447
, pp. 199-209
-
-
Wahli, W.1
Devchand, P.R.2
Ijpenberg, A.3
Desvergne, B.4
-
89
-
-
0001168899
-
Single peroxisomal enzyme deficiencies
-
C.R. Scriver, A.L. Beaudet, W.S. Sly, D. Valle (Eds), New York: McGraw-Hill
-
R.J. Wanders, P.G. Barth and H.S.A. Heymans (2001) Single peroxisomal enzyme deficiencies. C.R. Scriver, A.L. Beaudet, W.S. Sly, D. Valle (Eds) The Metabolic and Molecular Basis of Inherited Disease New York: McGraw-Hill 3219-3256.
-
(2001)
The Metabolic and Molecular Basis of Inherited Disease
, pp. 3219-3256
-
-
Wanders, R.J.1
Barth, P.G.2
Heymans, H.S.A.3
-
90
-
-
0035815693
-
Discrete targeting signals direct PmP47 to oleate-induced peroxisomes in Saccharomyces cerevisiae
-
X. Wang, M.J. Unruh and J.M. Goodman (2001) Discrete targeting signals direct PmP47 to oleate-induced peroxisomes in Saccharomyces cerevisiae. J. Biol. Chem. 276 10897-10905.
-
(2001)
J. Biol. Chem.
, vol.276
, pp. 10897-10905
-
-
Wang, X.1
Unruh, M.J.2
Goodman, J.M.3
-
91
-
-
0029024783
-
Human peroxisomal targeting signal-1 receptor restores peroxisomal protein import in cells from patients with fatal peroxisomal disorders
-
E.A.C. Wiemer, W.M. Nuttley, B.L. Bertolaet, X. Li, U. Franke, M.J. Wheelock, U.K. Anné, K.R. Johnson and S. Subramani (1995) Human peroxisomal targeting signal-1 receptor restores peroxisomal protein import in cells from patients with fatal peroxisomal disorders. J. Cell Biol. 130 51-65.
-
(1995)
J. Cell Biol.
, vol.130
, pp. 51-65
-
-
Wiemer, E.A.C.1
Nuttley, W.M.2
Bertolaet, B.L.3
Li, X.4
Franke, U.5
Wheelock, M.J.6
Anné, U.K.7
Johnson, K.R.8
Subramani, S.9
-
92
-
-
0033051826
-
Adrenoleukodystrophy protein enhances association of very long chain acyl-coenzyme A synthetase with the peroxisome
-
T. Yamada, T. Taniwaki, N. Shinnoh, A. Uchiyama, N. Shimozawa, Y. Ohyagi, H. Asahara and J. Kira (1999) Adrenoleukodystrophy protein enhances association of very long chain acyl-coenzyme A synthetase with the peroxisome. Neurology 52 614-616.
-
(1999)
Neurology
, vol.52
, pp. 614-616
-
-
Yamada, T.1
Taniwaki, T.2
Shinnoh, N.3
Uchiyama, A.4
Shimozawa, N.5
Ohyagi, Y.6
Asahara, H.7
Kira, J.8
-
93
-
-
0034569801
-
Very long chain fatty acid metabolism in adrenoleukodystrophy protein-deficient mice
-
T. Yamada, N. Shinnoh, A. Kondo, A. Uchiyama, N. Shimozawa, J. Kira and T. Kobayashi (2000) Very long chain fatty acid metabolism in adrenoleukodystrophy protein-deficient mice. Cell Biochem. Biophys. 32 239-246.
-
(2000)
Cell Biochem. Biophys.
, vol.32
, pp. 239-246
-
-
Yamada, T.1
Shinnoh, N.2
Kondo, A.3
Uchiyama, A.4
Shimozawa, N.5
Kira, J.6
Kobayashi, T.7
-
94
-
-
0033739281
-
Pristanic acid acid and phytanic acid: Naturally occurring ligands for the nuclear receptor peroxisome proliferator-activated receptor α
-
A.W.M. Zomer, B. van der Burg, G.A. Jansen, R.J. Wanders, B.T. Poll-The and P.T. van der Saag (2000) Pristanic acid acid and phytanic acid: Naturally occurring ligands for the nuclear receptor peroxisome proliferator-activated receptor α. J. Lipid Res. 41 1801-1807.
-
(2000)
J. Lipid Res.
, vol.41
, pp. 1801-1807
-
-
Zomer, A.W.M.1
van der Burg, B.2
Jansen, G.A.3
Wanders, R.J.4
Poll-The, B.T.5
van der Saag, P.T.6
|