-
1
-
-
0026735060
-
-
Van den Bosch, H., Schutgens, R. B. H., Wanders, R. J. A., and Tager, J. M. (1992) Annu. Rev. Biochem. 61, 157-197
-
(1992)
Annu. Rev. Biochem.
, vol.61
, pp. 157-197
-
-
Van Den Bosch, H.1
Schutgens, R.B.H.2
Wanders, R.J.A.3
Tager, J.M.4
-
3
-
-
0023664229
-
-
Van Veldhoven, P. P., Just, W. W., and Mannaerts, G. P (1987) J. Biol. Chem. 262, 4310-4318
-
(1987)
J. Biol. Chem.
, vol.262
, pp. 4310-4318
-
-
Van Veldhoven, P.P.1
Just, W.W.2
Mannaerts, G.P.3
-
4
-
-
0029064219
-
-
Van Roermund, C. W. T., Elgersma, Y., Singh, N., Wanders, R. J. A., and Tabak, H. F. (1995) EMBO. J. 14, 3480-3486
-
(1995)
EMBO. J.
, vol.14
, pp. 3480-3486
-
-
Van Roermund, C.W.T.1
Elgersma, Y.2
Singh, N.3
Wanders, R.J.A.4
Tabak, H.F.5
-
5
-
-
0025045656
-
-
Wolvetang, E. J., Tager, J. M., and Wanders, R. J. A. (1990) Biochem. Biophys. Res. Commun. 170, 1135-1143
-
(1990)
Biochem. Biophys. Res. Commun.
, vol.170
, pp. 1135-1143
-
-
Wolvetang, E.J.1
Tager, J.M.2
Wanders, R.J.A.3
-
6
-
-
0022761273
-
-
Hashimoto, T., Kuwabara, T., Usuda, N., and Nagata, T. (1986) J. Biochem. (Tokyo) 100, 301-310
-
(1986)
J. Biochem. (Tokyo)
, vol.100
, pp. 301-310
-
-
Hashimoto, T.1
Kuwabara, T.2
Usuda, N.3
Nagata, T.4
-
8
-
-
0025255475
-
-
Kamijo, K., Taketani, S., Yokota, S., Osumi, T., and Hashimoto, T. (1990) J. Biol. Chem. 265, 4534-4540
-
(1990)
J. Biol. Chem.
, vol.265
, pp. 4534-4540
-
-
Kamijo, K.1
Taketani, S.2
Yokota, S.3
Osumi, T.4
Hashimoto, T.5
-
11
-
-
0026500670
-
-
Kamijo, K., Kamijo, T., Ueno, I., Osumi, T., and Hashimoto, T. (1992) Biochim. Biophys. Acta 1129, 323-327
-
(1992)
Biochim. Biophys. Acta
, vol.1129
, pp. 323-327
-
-
Kamijo, K.1
Kamijo, T.2
Ueno, I.3
Osumi, T.4
Hashimoto, T.5
-
12
-
-
0026849933
-
-
Gärtner, J., Moser, H., and Valle, D. (1992) Nat. Genet. 1, 16-23
-
(1992)
Nat. Genet.
, vol.1
, pp. 16-23
-
-
Gärtner, J.1
Moser, H.2
Valle, D.3
-
13
-
-
0027532282
-
-
Mosser, J., Douar, A.-M., Sarde, C.-O., Kioschis, P., Feil, R., Moser, H., Poustka, A.-M., Mandel, J.-L., and Aubourg, P. (1993) Nature 381, 726-730
-
(1993)
Nature
, vol.381
, pp. 726-730
-
-
Mosser, J.1
Douar, A.-M.2
Sarde, C.-O.3
Kioschis, P.4
Feil, R.5
Moser, H.6
Poustka, A.-M.7
Mandel, J.-L.8
Aubourg, P.9
-
14
-
-
0030034602
-
-
Lombard-Platet, G., Savary, S., Sarde, C.-O., Mandel, J.-L., and Chimini, G. (1996) Proc. Natl. Acad. Sci. U. S. A. 93, 1265-1269
-
(1996)
Proc. Natl. Acad. Sci. U. S. A.
, vol.93
, pp. 1265-1269
-
-
Lombard-Platet, G.1
Savary, S.2
Sarde, C.-O.3
Mandel, J.-L.4
Chimini, G.5
-
15
-
-
0031561433
-
-
Holzinger, A., Kammerer, S., Berger, J., and Roscher, A. A. (1997) Biochem. Biophys. Res. Commun. 239, 261-264
-
(1997)
Biochem. Biophys. Res. Commun.
, vol.239
, pp. 261-264
-
-
Holzinger, A.1
Kammerer, S.2
Berger, J.3
Roscher, A.A.4
-
16
-
-
0031559581
-
-
Holzinger, A., Kammerer, S., and Roscher, A. A. (1997) Biochem. Biophys. Res. Commun. 237, 152-157
-
(1997)
Biochem. Biophys. Res. Commun.
, vol.237
, pp. 152-157
-
-
Holzinger, A.1
Kammerer, S.2
Roscher, A.A.3
-
17
-
-
0030776037
-
-
Shani, N., Jimenez-Sanchez, G., Steel, G., Dean, M., and Valle, D. (1997) Hum. Mol. Genet. 6, 1925-1931
-
(1997)
Hum. Mol. Genet.
, vol.6
, pp. 1925-1931
-
-
Shani, N.1
Jimenez-Sanchez, G.2
Steel, G.3
Dean, M.4
Valle, D.5
-
19
-
-
0002277381
-
-
(Scriver, C. R., Beaudet, A. L., Sly, W. S., and Valle, D., eds) 7th Ed., McGraw-Hill Inc., New York
-
Moser, H. M., Smith, K. D., and Moser, A. B. (1995) in The Metabolic and Molecular Basis of Inherited Disease (Scriver, C. R., Beaudet, A. L., Sly, W. S., and Valle, D., eds) 7th Ed., pp. 2325-2349, McGraw-Hill Inc., New York
-
(1995)
The Metabolic and Molecular Basis of Inherited Disease
, pp. 2325-2349
-
-
Moser, H.M.1
Smith, K.D.2
Moser, A.B.3
-
20
-
-
0030910241
-
-
Paton, B. C., Heron, S. E., Nelson, P. V., Morris, C. P., and Poulos, A. (1997) Am. J. Hum. Genet. 60, 1535-1539
-
(1997)
Am. J. Hum. Genet.
, vol.60
, pp. 1535-1539
-
-
Paton, B.C.1
Heron, S.E.2
Nelson, P.V.3
Morris, C.P.4
Poulos, A.5
-
21
-
-
0030021833
-
-
Imanaka, T., Shiina, Y., Takano, T., Hashimoto, T., and Osumi, T. (1996) J. Biol. Chem. 271, 3706-3713
-
(1996)
J. Biol. Chem.
, vol.271
, pp. 3706-3713
-
-
Imanaka, T.1
Shiina, Y.2
Takano, T.3
Hashimoto, T.4
Osumi, T.5
-
22
-
-
0028108279
-
-
Tsukamoto, T., Hata, S., Yokota, S., Miura, S., Fujiki, Y., Hijikata, M. Miyazawa, S., Hashimoto, T., and Osumi, T. (1994) J. Biol. Chem. 269, 6001-6010
-
(1994)
J. Biol. Chem.
, vol.269
, pp. 6001-6010
-
-
Tsukamoto, T.1
Hata, S.2
Yokota, S.3
Miura, S.4
Fujiki, Y.5
Hijikata, M.6
Miyazawa, S.7
Hashimoto, T.8
Osumi, T.9
-
24
-
-
0029958652
-
-
Sato, R., Inoue, J., Kawabe, Y., Kodama, T., Takano, T., and Maeda, M. (1996) J. Biol. Chem. 271, 26461-26464
-
(1996)
J. Biol. Chem.
, vol.271
, pp. 26461-26464
-
-
Sato, R.1
Inoue, J.2
Kawabe, Y.3
Kodama, T.4
Takano, T.5
Maeda, M.6
-
25
-
-
0031764039
-
-
Kawabe, Y., Imanaka, T., Kodama, T., Takano, T., and Sato, R. (1998) Cell Struct. Funct. 23, 187-192
-
(1998)
Cell Struct. Funct.
, vol.23
, pp. 187-192
-
-
Kawabe, Y.1
Imanaka, T.2
Kodama, T.3
Takano, T.4
Sato, R.5
-
26
-
-
0026326482
-
-
Osumi, T., Tsukamoto, T., Hata, S., Yokota, S., Miura, S., Fujiki, Y., Hijikata, M., Miyazawa, S., and Hashimoto, T. (1991) Biochem. Biophys. Res. Commun. 181, 947-954
-
(1991)
Biochem. Biophys. Res. Commun.
, vol.181
, pp. 947-954
-
-
Osumi, T.1
Tsukamoto, T.2
Hata, S.3
Yokota, S.4
Miura, S.5
Fujiki, Y.6
Hijikata, M.7
Miyazawa, S.8
Hashimoto, T.9
-
27
-
-
0025977715
-
-
Suzuki, Y., Shimozawa, N., Yajima, S., Yamaguchi, S., Orii, T., and Hashimoto, T. (1991) Biochem. Pharmacol. 41, 453-456
-
(1991)
Biochem. Pharmacol.
, vol.41
, pp. 453-456
-
-
Suzuki, Y.1
Shimozawa, N.2
Yajima, S.3
Yamaguchi, S.4
Orii, T.5
Hashimoto, T.6
-
28
-
-
0018356140
-
-
Mannaerts, G. P., Debeer, L. J., Thomas, J., and De Schepper, P. J. (1979) J. Biol. Chem. 254, 4585-4595
-
(1979)
J. Biol. Chem.
, vol.254
, pp. 4585-4595
-
-
Mannaerts, G.P.1
Debeer, L.J.2
Thomas, J.3
De Schepper, P.J.4
-
29
-
-
0019325999
-
-
Thomas, J., Debeer, L. J., De Schepper, P. J., and Mannaerts, G. P. (1980) Biochem. J. 190, 485-494
-
(1980)
Biochem. J.
, vol.190
, pp. 485-494
-
-
Thomas, J.1
Debeer, L.J.2
De Schepper, P.J.3
Mannaerts, G.P.4
-
30
-
-
0023882203
-
-
Small, G. M., Imanaka, T., and Lazarow, P. B. (1988) Anal. Biochem. 169, 405-409
-
(1988)
Anal. Biochem.
, vol.169
, pp. 405-409
-
-
Small, G.M.1
Imanaka, T.2
Lazarow, P.B.3
-
31
-
-
0021346563
-
-
Turnbull, D. M., Bartlett, K., Younan, S. I. M., and Sherratt, H. S. A. (1984) Biochem. Pharmacol. 33, 475-481
-
(1984)
Biochem. Pharmacol.
, vol.33
, pp. 475-481
-
-
Turnbull, D.M.1
Bartlett, K.2
Younan, S.I.M.3
Sherratt, H.S.A.4
-
34
-
-
0001607723
-
-
Walker, J. E., Saraste, M., Runswick, M. J., and Gay, N. J. (1982) EMBO J. 1, 945-951
-
(1982)
EMBO J.
, vol.1
, pp. 945-951
-
-
Walker, J.E.1
Saraste, M.2
Runswick, M.J.3
Gay, N.J.4
-
35
-
-
0025048136
-
-
Saraste, M., Sibbald, P. R., and Wittinghofer, A. (1990) Trends Biochem. Sci. 15, 430-434
-
(1990)
Trends Biochem. Sci.
, vol.15
, pp. 430-434
-
-
Saraste, M.1
Sibbald, P.R.2
Wittinghofer, A.3
-
36
-
-
0026700075
-
-
Omote, H., Maeda, M., and Futai, M. (1992) J. Biol. Chem. 267, 20571-20576
-
(1992)
J. Biol. Chem.
, vol.267
, pp. 20571-20576
-
-
Omote, H.1
Maeda, M.2
Futai, M.3
-
37
-
-
0025973236
-
-
Imanaka, T., Lazarow, P. B., and Takano, T. (1991) Biochim. Biophys. Acta 1062, 264-270
-
(1991)
Biochim. Biophys. Acta
, vol.1062
, pp. 264-270
-
-
Imanaka, T.1
Lazarow, P.B.2
Takano, T.3
-
38
-
-
0020483106
-
-
Mannaerts, G. P., Van Veldhoven, P., Van Broekhoven, A., Vandebroek, G., and Debeer, L. J. (1982) Biochem. J. 204, 17-23
-
(1982)
Biochem. J.
, vol.204
, pp. 17-23
-
-
Mannaerts, G.P.1
Van Veldhoven, P.2
Van Broekhoven, A.3
Vandebroek, G.4
Debeer, L.J.5
-
39
-
-
0028308841
-
-
Bossier, P., Fernandes, L., Vilela, C., and Rodrigues-Pousada, C. (1994) Yeast 10, 681-686
-
(1994)
Yeast
, vol.10
, pp. 681-686
-
-
Bossier, P.1
Fernandes, L.2
Vilela, C.3
Rodrigues-Pousada, C.4
-
40
-
-
0029883155
-
-
Shani, N., Sapag, A., and Valle, D. (1996) J. Biol. Chem. 271, 8725-8730
-
(1996)
J. Biol. Chem.
, vol.271
, pp. 8725-8730
-
-
Shani, N.1
Sapag, A.2
Valle, D.3
-
41
-
-
0029011568
-
-
Shani, N., Watkins, P. A., and Valle, D. (1995) Proc. Natl. Acad. Sci. U. S. A. 92, 6012-6016
-
(1995)
Proc. Natl. Acad. Sci. U. S. A.
, vol.92
, pp. 6012-6016
-
-
Shani, N.1
Watkins, P.A.2
Valle, D.3
-
42
-
-
0030066019
-
-
Swartzman, E. E., Viswanathan, M. N., and Thorner, J. (1996) J. Cell Biol. 132, 549-563
-
(1996)
J. Cell Biol.
, vol.132
, pp. 549-563
-
-
Swartzman, E.E.1
Viswanathan, M.N.2
Thorner, J.3
-
43
-
-
0029783210
-
-
Hettema, E. H., van Roermund, C. W. T., Distel, B., van den Berg, M., Vilela, C., Rodrigues-Pousada, C., Wanders, R. J. A., and Tabak, H. F. (1996) EMBO J. 15, 3813-3822
-
(1996)
EMBO J.
, vol.15
, pp. 3813-3822
-
-
Hettema, E.H.1
Van Roermund, C.W.T.2
Distel, B.3
Van Den Berg, M.4
Vilela, C.5
Rodrigues-Pousada, C.6
Wanders, R.J.A.7
Tabak, H.F.8
-
44
-
-
0030662714
-
-
Verleur, N., Hettema, E. H., Van Roermund, C. W. T., Tabak, H. F., and Wanders, R. J. A. (1997) Eur. J. Biochem. 249, 657-661
-
(1997)
Eur. J. Biochem.
, vol.249
, pp. 657-661
-
-
Verleur, N.1
Hettema, E.H.2
Van Roermund, C.W.T.3
Tabak, H.F.4
Wanders, R.J.A.5
-
46
-
-
0026333365
-
-
Jedlitschky, G., Huber, M., Völkl, A., Müller, M., Leier, I., Müller, J., Lehmann, W.-D., Fahimi, H. D., and Keppler, D. (1991) J. Biol. Chem. 266, 24763-24772
-
(1991)
J. Biol. Chem.
, vol.266
, pp. 24763-24772
-
-
Jedlitschky, G.1
Huber, M.2
Völkl, A.3
Müller, M.4
Leier, I.5
Müller, J.6
Lehmann, W.-D.7
Fahimi, H.D.8
Keppler, D.9
-
47
-
-
0024208541
-
-
Draye, J.-P., Veitch, K., Vamecq, J., and Van Hoof, F. (1988) Eur. J. Biochem. 178, 183-189
-
(1988)
Eur. J. Biochem.
, vol.178
, pp. 183-189
-
-
Draye, J.-P.1
Veitch, K.2
Vamecq, J.3
Van Hoof, F.4
-
48
-
-
0024554625
-
-
Ostlund-Farrants, A.-K., Björkhem, I., and Pedersen, J. I. (1989) Biochim. Biophys. Acta 1002, 198-202
-
(1989)
Biochim. Biophys. Acta
, vol.1002
, pp. 198-202
-
-
Ostlund-Farrants, A.-K.1
Björkhem, I.2
Pedersen, J.I.3
-
50
-
-
0030725292
-
-
Verhoeven, N. M., Wanders, R. J. A., Schor, D. S. M., Jansen, G. A., and Jakobs, C. (1997) J. Lipid Res. 38, 2062-2070
-
(1997)
J. Lipid Res.
, vol.38
, pp. 2062-2070
-
-
Verhoeven, N.M.1
Wanders, R.J.A.2
Schor, D.S.M.3
Jansen, G.A.4
Jakobs, C.5
|