Conditional expression of mutant M-line titins results in cardiomyopathy with altered sarcomere structure

Journal of Biological Chemistry

Volumn 278, Issue 8, 2003, Pages 6059-6065

  Gotthardt, Michael ^a,d   Hammer, Robert E ^a   Hübner, Norbert ^b   Monti, Jan ^b   Witt, Christian C ^c   McNabb, Mark ^d   Richardson, James A ^a   Granzier, Henk ^d   Labeit, Siegfried ^c   Herz, Joachim ^a  

^a UNIVERSITY OF TEXAS SOUTHWESTERN MEDICAL CENTER   (United States)

^b MAX DELBRÜCK CENTER FOR MOLECULAR MEDICINE   (Germany)

^c UNIVERSITY OF HEIDELBERG   (Germany)

^d WASHINGTON STATE UNIVERSITY   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

ELASTICITY; MUSCLE; PROTEINS;

MUSCLE ELASTICITY;

BIOCHEMISTRY;

CONNECTIN; MUSCLE PROTEIN; PROTEIN SERINE THREONINE KINASE; ACTIN; MYOSIN HEAVY CHAIN; PROTEIN KINASE;

ANIMAL EXPERIMENT; ANIMAL TISSUE; ARTICLE; CARDIOMYOPATHY; CATALYSIS; CONTROLLED STUDY; ELASTICITY; EMBRYO; EMBRYO DEVELOPMENT; EXON; FEMALE; GENE DISRUPTION; GENE MUTATION; MALE; MORTALITY; MUSCLE; MUSCLE WEAKNESS; MYOPATHY; NONHUMAN; PRIORITY JOURNAL; PROTEIN DOMAIN; PROTEIN EXPRESSION; PROTEIN STRUCTURE; SARCOMERE; SEQUENCE ANALYSIS; ANIMAL; ANTIBODY SPECIFICITY; BACTERIAL ARTIFICIAL CHROMOSOME; BINDING SITE; CHEMISTRY; GENE EXPRESSION REGULATION; GENETIC RECOMBINATION; GENETICS; MAJOR HISTOCOMPATIBILITY COMPLEX; METABOLISM; MOLECULAR CLONING; MOUSE; MOUSE MUTANT; PATHOLOGY; PHYSIOLOGY; PROMOTER REGION; SKELETAL MUSCLE; STEM CELL; ULTRASTRUCTURE;

ANIMALIA;

ACTINS; ANIMALS; BINDING SITES; CARDIOMYOPATHIES; CHROMOSOMES, ARTIFICIAL, BACTERIAL; CLONING, MOLECULAR; ELASTICITY; GENE EXPRESSION REGULATION; MAJOR HISTOCOMPATIBILITY COMPLEX; MICE; MICE, KNOCKOUT; MUSCLE PROTEINS; MUSCLE, SKELETAL; MYOSIN HEAVY CHAINS; ORGAN SPECIFICITY; PROMOTER REGIONS (GENETICS); PROTEIN KINASES; RECOMBINATION, GENETIC; SARCOMERES; STEM CELLS;

EID: 0037458739     PISSN: 00219258     EISSN: None     Source Type: Journal    
DOI: 10.1074/jbc.M211723200     Document Type: Article

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