Classical late infantile neuronal ceroid lipofuscinosis fibroblasts are deficient in lysosomal tripeptidyl peptidase I

FEBS Letters

Volumn 443, Issue 2, 1999, Pages 131-135

  Vines, David J ^a   Warburton, Michael J ^a  

^a ST GEORGE'S UNIVERSITY OF LONDON   (United Kingdom)

Author keywords

Carboxyl proteinase; Late infantile neuronal ceroid lipofuscinosis; Peptide degradation; Tripeptidyl peptidase I

Indexed keywords

PEPTIDASE; PROTEINASE;

ADOLESCENT; AMINO ACID SEQUENCE; ARTICLE; CELL CULTURE; CHILD; CONTROLLED STUDY; ENZYME DEFICIENCY; FIBROBLAST; HUMAN; HUMAN CELL; MALE; MOUSE; MUTANT; NEURONAL CEROID LIPOFUSCINOSIS; NONHUMAN; PRESCHOOL CHILD; PRIORITY JOURNAL; PROTEIN DEGRADATION; RAT;

ADOLESCENT; AMINO ACID SEQUENCE; ANIMALS; CELLS, CULTURED; CHILD, PRESCHOOL; ENDOPEPTIDASES; FEMALE; FIBROBLASTS; HUMANS; HYDROGEN-ION CONCENTRATION; HYDROLYSIS; LYSOSOMES; MALE; MOLECULAR SEQUENCE DATA; NEURONAL CEROID-LIPOFUSCINOSES; SEQUENCE HOMOLOGY, AMINO ACID;

EID: 0033052570     PISSN: 00145793     EISSN: None     Source Type: Journal    
DOI: 10.1016/S0014-5793(98)01683-4     Document Type: Article

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