Lipid thioesters derived from acylated proteins accumulate in infantile neuronal ceroid lipofuscinosis: Correction of the defect in lymphoblasts by recombinant palmitoyl-protein thioesterase

Proceedings of the National Academy of Sciences of the United States of America

Volumn 93, Issue 19, 1996, Pages 10046-10050

  Lu, Jui Yun ^a   Verkruyse, Linda A ^a   Hofmann, Sandra L ^a  

^a UNIVERSITY OF TEXAS SOUTHWESTERN MEDICAL CENTER   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

CYSTEINE; HYDROXYLAMINE; LIPID; PALMITOYL COENZYME A HYDROLASE; RECOMBINANT PROTEIN; SOMATOMEDIN B RECEPTOR; SULFUR 35; THIOESTER; THIOL ESTER HYDROLASE;

ACYLATION; ANIMAL CELL; ARTICLE; CELL IMMORTALIZATION; CELL LINE; CONTROLLED STUDY; CULTURE MEDIUM; ENZYME ASSAY; HUMAN; HUMAN CELL; ISOTOPE LABELING; LYMPHOBLASTOID CELL LINE; NEURONAL CEROID LIPOFUSCINOSIS; NONHUMAN; PRIORITY JOURNAL; PROTEIN DEGRADATION; THIN LAYER CHROMATOGRAPHY;

ANIMALS; B-LYMPHOCYTES; CELL LINE, TRANSFORMED; CERCOPITHECUS AETHIOPS; CHILD, PRESCHOOL; COS CELLS; CYSTEINE; HERPESVIRUS 4, HUMAN; HUMANS; HYDROXYLAMINE; HYDROXYLAMINES; KINETICS; LIPID METABOLISM; NEURONAL CEROID-LIPOFUSCINOSES; POLYMERASE CHAIN REACTION; RECOMBINANT PROTEINS; SULFHYDRYL COMPOUNDS; THIOLESTER HYDROLASES; TRANSFECTION;

ANIMALIA;

EID: 0029788513     PISSN: 00278424     EISSN: None     Source Type: Journal    
DOI: 10.1073/pnas.93.19.10046     Document Type: Article

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