Palmitoyl-protein thioesterase and the molecular pathogenesis of infantile neuronal ceroid lipofuscinosis

Neuropediatrics

Volumn 28, Issue 1, 1997, Pages 27-30

  Hofmann, Sandra L ^a   Lee, Laura A ^a   Lu, Jui Yun ^a   Verkruyse, Linda A ^a  

^a UNIVERSITY OF TEXAS SOUTHWESTERN MEDICAL CENTER   (United States)

Author keywords

Infantile neuronal ceroid lipofuscinosis; Lysosomal enzymes; Neurodegeneration; Protein acylation; Thioesterases

Indexed keywords

LYSOSOME ENZYME; PALMITOYL PROTEIN THIOESTERASE; THIOL ESTER HYDROLASE; UNCLASSIFIED DRUG;

ARTICLE; AUTOPHAGY; ENZYME ACTIVITY; ENZYME DEFICIENCY; ENZYME LOCALIZATION; ENZYMOLOGY; HUMAN; LYMPHOBLAST; LYSOSOME; METABOLISM; NEURONAL CEROID LIPOFUSCINOSIS; PATHOGENESIS; PRIORITY JOURNAL; PROTEIN DEGRADATION;

EID: 0030739514     PISSN: 0174304X     EISSN: None     Source Type: Journal    
DOI: 10.1055/s-2007-973661     Document Type: Article

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