Mitochondrial abnormalities in CLN2 and CLN3 forms of Batten disease

Molecular and Chemical Neuropathology

Volumn 29, Issue 2-3, 1996, Pages 227-235

  Dawson, Glyn ^a   Kilkus, John ^a   Siakotos, Aristotle N ^b   Singh, Inderjit ^c  

^a UNIVERSITY OF CHICAGO   (United States)

^b INDIANA UNIVERSITY   (United States)

^c MEDICAL UNIVERSITY OF SOUTH CAROLINA   (United States)

Author keywords

fatty acid transport and oxidation; mitochondria; Neuronal ceroid lipofuscinosis; peroxisomes

Indexed keywords

ADENOSINE TRIPHOSPHATASE; CARNITINE; CATALASE; FATTY ACID; LIGNOCERIC ACID; MITOCHONDRIAL ENZYME; PALMITIC ACID; PHYTANIC ACID;

ADRENOLEUKODYSTROPHY; ARTICLE; BRAIN MITOCHONDRION; CONTROLLED STUDY; ENZYME ACTIVITY; ENZYME SUBUNIT; FATTY ACID OXIDATION; HUMAN; HUMAN CELL; MITOCHONDRIAL MEMBRANE; NEURONAL CEROID LIPOFUSCINOSIS; PRIORITY JOURNAL; SKIN FIBROBLAST; ZELLWEGER SYNDROME;

EID: 0030477041     PISSN: 10447393     EISSN: None     Source Type: Journal    
DOI: 10.1007/BF02815004     Document Type: Article

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