Selective changes in mitochondria respiratory properties in oxidative or glycolytic muscle fibers isolated from G93AhumanSOD1 transgenic mice

Neuromuscular Disorders

Volumn 11, Issue 8, 2001, Pages 722-727

  Leclerc, Nathalie ^a   Ribera, Florence ^b   Zoll, Joffrey ^b   Warter, Jean Marie ^b   Poindron, Philippe ^a   Lampert, Eliane ^b   Borg, Jacques ^c  

^a Centre de Recherches Pharmaceutiques   (France)

^b UNIVERSITY HOSPITAL OF STRASBOURG   (France)

^c UNIVERSITÉ DE STRASBOURG   (France)

Author keywords

Amyotrophic lateral sclerosis; Mitochondria; Muscle function; Oxidative stress; Superoxide dismutase; Transgenic mouse

Indexed keywords

ADENOSINE DIPHOSPHATE; COPPER ZINC SUPEROXIDE DISMUTASE;

AMYOTROPHIC LATERAL SCLEROSIS; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; CONTROLLED STUDY; DIAPHRAGM MUSCLE; DISEASE COURSE; ENERGY METABOLISM; ENZYME ACTIVITY; EXTENSOR DIGITORUM LONGUS MUSCLE; FEMALE; MALE; MITOCHONDRIAL RESPIRATION; MOTONEURON; MOUSE; MUSCLE CELL; MUSCLE MITOCHONDRION; MUSCLE TISSUE; NERVOUS TISSUE; NONHUMAN; OXIDATIVE STRESS; OXYGEN CONSUMPTION; PRIORITY JOURNAL; SOLEUS MUSCLE; TRANSGENIC MOUSE;

ADENOSINE DIPHOSPHATE; AMINO ACID SUBSTITUTION; AMYOTROPHIC LATERAL SCLEROSIS; ANIMALS; BRAIN; CELL RESPIRATION; DIAPHRAGM; DISEASE MODELS, ANIMAL; DISEASE PROGRESSION; ENZYME ACTIVATION; GLYCOLYSIS; HUMANS; MICE; MICE, TRANSGENIC; MITOCHONDRIA, MUSCLE; MUSCLE, SKELETAL; ORGAN SPECIFICITY; OXIDATION-REDUCTION; OXIDATIVE PHOSPHORYLATION; OXYGEN CONSUMPTION; SPINAL CORD; SUPEROXIDE DISMUTASE;

EID: 0034811135     PISSN: 09608966     EISSN: None     Source Type: Journal    
DOI: 10.1016/S0960-8966(01)00240-1     Document Type: Article

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