From neuronal inclusions to neurodegeneration: Neuropathological investigation of a transgenic mouse model of Huntington's disease

Philosophical Transactions of the Royal Society B: Biological Sciences

Volumn 354, Issue 1386, 1999, Pages 971-979

  Davies, Stephen W ^a   Turmaine, Mark ^a   Cozens, Barbara A ^a   Raza, Aysha S ^a   Mahal, Amarbirpal ^b   Mangiarini, Laura ^b   Bates, Gillian P ^b  

^a UNIVERSITY COLLEGE LONDON   (United Kingdom)

^b KING'S COLLEGE LONDON   (United Kingdom)

Author keywords

Cell death; Huntington's disease; Neurodegeneration; Neuronal intranuclear inclusions; Neuropathology; Transgenic mouse

Indexed keywords

ANIMAL MODEL; CELL DEATH; DISEASE MODEL; EXON; GLUTAMINE; HUNTINGTON CHOREA; MUTANT PROTEIN; NERVE CELL; NERVE DEGENERATION; PATHOGENESIS; PROTEIN AGGREGATION; REPETITIVE DNA; TRANSGENIC MOUSE;

ANIMALIA; MUS MUSCULUS;

EID: 0033614760     PISSN: 09628436     EISSN: None     Source Type: Journal    
DOI: 10.1098/rstb.1999.0448     Document Type: Article

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