Cholesterol reutilization during myelination of regenerating PNS axons is impaired in niemann-pick disease type C mice

Journal of Neuroscience Research

Volumn 49, Issue 3, 1997, Pages 389-392

  Goodrum, Jeffry F ^a   Pentchev, Peter G ^b  

^a UNIVERSITY OF NORTH CAROLINA SCHOOL OF MEDICINE   (United States)

^b NATIONAL INSTITUTE OF NEUROLOGICAL DISORDERS AND STROKE   (United States)

Author keywords

Cholesterol; Lipidosis; Nerve regeneration; Neuropathy; Remyelination

Indexed keywords

CHOLESTEROL; LOW DENSITY LIPOPROTEIN CHOLESTEROL;

ANIMAL CELL; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; CHOLESTEROL ESTERIFICATION; CHOLESTEROL METABOLISM; ELECTRON MICROSCOPY; MOUSE; MYELIN SHEATH; NERVE FIBER REGENERATION; NIEMANN PICK DISEASE; NONHUMAN; PRIORITY JOURNAL; REMYELINIZATION; SCIATIC NERVE;

ANIMALS; AUTORADIOGRAPHY; AXONS; CHOLESTEROL; HUMANS; MICE; MICE, INBRED BALB C; MICE, TRANSGENIC; MICROSCOPY, ELECTRON; MYELIN SHEATH; NERVE CRUSH; NERVE REGENERATION; NIEMANN-PICK DISEASES; PERIPHERAL NERVOUS SYSTEM; SCIATIC NERVE;

EID: 0030800371     PISSN: 03604012     EISSN: None     Source Type: Journal    
DOI: 10.1002/(SICI)1097-4547(19970801)49:3<389::AID-JNR14>3.0.CO;2-V     Document Type: Article

References (9)

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9. Pentchev PG, Varnier MT, Suzuki K, Patterson MC (1995): Niemann-Pick disease type C: A cellular cholesterol lipidosis. In Scriver CR, Beaudet AL, Sly WS, Valle D (eds): 'Metabolic and Molecular Bases of Inherited Disease.' 7th ed. New York: McGraw-Hill Inc., pp 2625-2640.