Myopathy phenotype of transgenic mice expressing active site-mutated inactive p94 skeletal muscle-specific calpain, the gene product responsible for limb girdle muscular dystrophy type 2A

Human Molecular Genetics

Volumn 9, Issue 9, 2000, Pages 1393-1402

  Tagawa, Kazuhiko ^a,b,c   Taya, Choji ^d   Hayashi, Yukiko ^c   Nakagawa, Masahiro ^c   Ono, Yasuko ^a   Fukuda, Rie ^a   Karasuyama, Hajime ^d   Toyama Sorimachi, Noriko ^d   Katsui, Yukiko ^a   Hata, Shoji ^a   Ishiura, Shoichi ^a   Nonaka, Ikuya ^c   Seyama, Yosuke ^b   Arahata, Kiichi ^c   Yonekawa, Hiromichi ^d   Sorimachi, Hiroyuki ^a   Suzuki, Koichi ^a  

^a UNIVERSITY OF TOKYO   (Japan)

^b UNIVERSITY OF TOKYO   (Japan)

^c NATIONAL INSTITUTE OF NEUROSCIENCE   (Japan)

^d TOKYO METROPOLITAN INSTITUTE OF MEDICAL SCIENCE   (Japan)

Author keywords

[No Author keywords available]

Indexed keywords

CALPAIN; MESSENGER RNA; MUTANT PROTEIN;

ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; CONTROLLED STUDY; ENZYME ACTIVE SITE; EXTENSOR DIGITORUM LONGUS MUSCLE; FEMALE; GRIP STRENGTH; HISTOPATHOLOGY; LIMB GIRDLE MUSCULAR DYSTROPHY; MALE; MOUSE; MYOPATHY; NONHUMAN; NUCLEOTIDE SEQUENCE; PHENOTYPE; PRIORITY JOURNAL; PROTEIN DEGRADATION; SOLEUS MUSCLE; TRANSGENIC MOUSE;

ANIMALIA; MUS MUSCULUS;

EID: 0001634301     PISSN: 09646906     EISSN: None     Source Type: Journal    
DOI: 10.1093/hmg/9.9.1393     Document Type: Article

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