Functional defects of a muscle-specific calpain, p94, caused by mutations associated with limb-girdle muscular dystrophy type 2A

Journal of Biological Chemistry

Volumn 273, Issue 27, 1998, Pages 17073-17078

  Ono, Yasuko ^a   Shimada, Hiroko ^a   Sorimach, Hiroyuki ^a   Richard, Isabelle ^b   Saido, Takaomi C ^c   Beckmann, Jacques S ^b   Ishiura, Shoichi ^a   Suzuki, Koichi ^a  

^a UNIVERSITY OF TOKYO   (Japan)

^b GÉNÉTHON   (France)

^c TOKYO METROPOLITAN INSTITUTE OF MEDICAL SCIENCE   (Japan)

Author keywords

[No Author keywords available]

Indexed keywords

CALPAIN; CONNECTIN; FODRIN;

ANIMAL CELL; ARTICLE; AUTOLYSIS; CONTROLLED STUDY; ENZYME SUBSTRATE; IMMUNOBLOTTING; LIMB GIRDLE MUSCULAR DYSTROPHY; MISSENSE MUTATION; NONHUMAN; PHENOTYPE; POINT MUTATION; PRIORITY JOURNAL; PROTEIN BINDING; PROTEIN DEGRADATION;

EID: 0032479445     PISSN: 00219258     EISSN: None     Source Type: Journal    
DOI: 10.1074/jbc.273.27.17073     Document Type: Article

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