-
1
-
-
84941049266
-
CFTR, bicarbonate, and the pathophysiology of cystic fibrosis
-
Borowitz, D. (2015). CFTR, bicarbonate, and the pathophysiology of cystic fibrosis. Pediatr. Pulmonol. 40, S24–S30. doi: 10.1002/ppul.23247
-
(2015)
Pediatr. Pulmonol.
, vol.40
, pp. S24-S30
-
-
Borowitz, D.1
-
2
-
-
84990855968
-
Cystic fibrosis: A clinical view
-
Castellani, C., and Assael, B. M. (2017). Cystic fibrosis: a clinical view. Cell. Mol. Life Sci. 74, 129–140. doi: 10.1007/s00018-016-2393-9
-
(2017)
Cell. Mol. Life Sci.
, vol.74
, pp. 129-140
-
-
Castellani, C.1
Assael, B.M.2
-
3
-
-
16644381108
-
Well-differentiated human airway epithelial cell cultures
-
Fulcher, M. L., Gabriel, S., Burns, K. A., Yankaskas, J. R., and Randell, S. H. (2005). Well-differentiated human airway epithelial cell cultures. Methods Mol. Med. 2005, 183–206.
-
(2005)
Methods Mol. Med.
, vol.2005
, pp. 183-206
-
-
Fulcher, M.L.1
Gabriel, S.2
Burns, K.A.3
Yankaskas, J.R.4
Randell, S.H.5
-
4
-
-
0032418043
-
An improved method to obtain highly differentiated monolayers of human bronchial epithelial cells
-
Galietta, L. J., Lantero, S., Gazzolo, A., Sacco, O., Romano, L., Rossi, G. A., et al. (1998). An improved method to obtain highly differentiated monolayers of human bronchial epithelial cells. In Vitro Cell. Dev. Biol. Anim. 34, 478–481.
-
(1998)
Vitro Cell. Dev. Biol. Anim.
, vol.34
, pp. 478-481
-
-
Galietta, L.J.1
Lantero, S.2
Gazzolo, A.3
Sacco, O.4
Romano, L.5
Rossi, G.A.6
-
5
-
-
85018371743
-
Pharmacological rescue of conditionally reprogrammed cystic fibrosis bronchial epithelial cells
-
Gentzsch, M., Boyles, S. E., Cheluvaraju, C., Chaudhry, I. G., Quinney, N. L., Cho, C., et al. (2017). Pharmacological rescue of conditionally reprogrammed cystic fibrosis bronchial epithelial cells. Am. J. Respir. Cell Mol. Biol. 56, 568–574. doi: 10.1165/rcmb.2016-0276MA
-
(2017)
Am. J. Respir. Cell Mol. Biol.
, vol.56
, pp. 568-574
-
-
Gentzsch, M.1
Boyles, S.E.2
Cheluvaraju, C.3
Chaudhry, I.G.4
Quinney, N.L.5
Cho, C.6
-
6
-
-
84960908845
-
Pharmacological rescue of mutant CFTR protein improves the viscoelastic properties of CF mucus
-
Gianotti, A., Capurro, V., Scudieri, P., Galietta, L. J. V., Moran, O., and Zegarra-Moran, O. (2016). Pharmacological rescue of mutant CFTR protein improves the viscoelastic properties of CF mucus. J. Cyst. Fibros. 15, 295–301. doi: 10.1016/j.jcf.2015.11.003
-
(2016)
J. Cyst. Fibros.
, vol.15
, pp. 295-301
-
-
Gianotti, A.1
Capurro, V.2
Scudieri, P.3
Galietta, L.J.V.4
Moran, O.5
Zegarra-Moran, O.6
-
7
-
-
33846016908
-
Basal cells of the human adult airway surface epithelium retain transit-amplifying cell properties
-
Hajj, R., Baranek, T., Le Naour, R., Lesimple, P., Puchelle, E., and Coraux, C. (2007). Basal cells of the human adult airway surface epithelium retain transit-amplifying cell properties. Stem Cells 25, 139–148.
-
(2007)
Stem Cells
, vol.25
, pp. 139-148
-
-
Hajj, R.1
Baranek, T.2
Le Naour, R.3
Lesimple, P.4
Puchelle, E.5
Coraux, C.6
-
8
-
-
11044236102
-
Transepithelial electrical measurements with the Ussing chamber
-
Li, H., Sheppard, D. N., and Hug, M. J. (2004). Transepithelial electrical measurements with the Ussing chamber. J. Cyst. Fibros 3(Suppl. 2), 123–126. doi: 10.1016/j.jcf.2004.05.026
-
(2004)
J. Cyst. Fibros
, vol.3
, pp. 123-126
-
-
Li, H.1
Sheppard, D.N.2
Hug, M.J.3
-
9
-
-
53749097483
-
Nasal epithelial cells as surrogates for bronchial epithelial cells in airway inflammation studies
-
McDougall, C. M., Blaylock, M. G., Douglas, J. G., Brooker, R. J., Helms, P. J., and Walsh, G. M. (2008). Nasal epithelial cells as surrogates for bronchial epithelial cells in airway inflammation studies. Am. J. Respir. Cell Mol. Biol. 39, 560–568. doi: 10.1165/rcmb.2007-0325OC
-
(2008)
Am. J. Respir. Cell Mol. Biol.
, vol.39
, pp. 560-568
-
-
McDougall, C.M.1
Blaylock, M.G.2
Douglas, J.G.3
Brooker, R.J.4
Helms, P.J.5
Walsh, G.M.6
-
10
-
-
38049068170
-
Feasibility of nasal epithelial brushing for the study of airway epithelial functions in CF infants
-
Mosler, K., Coraux, C., Fragaki, K., Zahm, J., Bajolet, O., Bessaci-Kabouya, K., et al. (2008). Feasibility of nasal epithelial brushing for the study of airway epithelial functions in CF infants. J. Cyst. Fibros. 7, 44–53.
-
(2008)
J. Cyst. Fibros.
, vol.7
, pp. 44-53
-
-
Mosler, K.1
Coraux, C.2
Fragaki, K.3
Zahm, J.4
Bajolet, O.5
Bessaci-Kabouya, K.6
-
11
-
-
84990922590
-
Dual SMAD signaling inhibition enables long-term expansion of diverse epithelial basal cells
-
Mou, H., Vinarsky, V., Tata, P. R., Brazauskas, K., Choi, S. H., Crooke, A. K., et al. (2016). Dual SMAD signaling inhibition enables long-term expansion of diverse epithelial basal cells. Cell Stem Cell 19, 217–231. doi: 10.1016/j.stem.2016.05.012
-
(2016)
Cell Stem Cell
, vol.19
, pp. 217-231
-
-
Mou, H.1
Vinarsky, V.2
Tata, P.R.3
Brazauskas, K.4
Choi, S.H.5
Crooke, A.K.6
-
12
-
-
84886865193
-
Culturing of human nasal epithelial cells at the air liquid interface
-
Müller, L., Brighton, L. E., Carson, J. L., Fischer, W. A. II, and Jaspers, I. (2013). Culturing of human nasal epithelial cells at the air liquid interface. J. Vis. Exp. 8:80.
-
(2013)
J. Vis. Exp.
, vol.8
, pp. 80
-
-
Müller, L.1
Brighton, L.E.2
Carson, J.L.3
Fischer, W.A.4
Jaspers, I.5
-
13
-
-
80052327898
-
Use of primary cultures of human bronchial epithelial cells isolated from cystic fibrosis patients for the pre-clinical testing of CFTR modulators
-
Neuberger, T., Burton, T., Clark, H., and Van Goor, F. (2011). Use of primary cultures of human bronchial epithelial cells isolated from cystic fibrosis patients for the pre-clinical testing of CFTR modulators. Methods Mol. Biol. 741, 39–54. doi: 10.1007/978-1-61779-117-8_4
-
(2011)
Methods Mol. Biol.
, vol.741
, pp. 39-54
-
-
Neuberger, T.1
Burton, T.2
Clark, H.3
Van Goor, F.4
-
14
-
-
84879410121
-
Mechanism-based corrector combination restores ΔF508-CFTR folding and function
-
Okiyoneda, T., Veit, G., Dekkers, J. F., Bagdany, M., Soya, N., Xu, H., et al. (2013). Mechanism-based corrector combination restores ΔF508-CFTR folding and function. Nat. Chem. Biol. 9, 444–454. doi: 10.1038/nchembio.1253
-
(2013)
Nat. Chem. Biol.
, vol.9
, pp. 444-454
-
-
Okiyoneda, T.1
Veit, G.2
Dekkers, J.F.3
Bagdany, M.4
Soya, N.5
Xu, H.6
-
15
-
-
84888266885
-
Radiation induces diffusible feeder cell factor(s) that cooperate with ROCK Inhibitor to conditionally reprogram and immortalize epithelial cells
-
Palechor-Ceron, N., Suprynowicz, F. A., Upadhyay, G., Dakic, A., Minas, T., Simic, V., et al. (2013). Radiation induces diffusible feeder cell factor(s) that cooperate with ROCK Inhibitor to conditionally reprogram and immortalize epithelial cells. Am. J. Pathol. 183, 1862–1870. doi: 10.1016/j.ajpath.2013.08.009
-
(2013)
Am. J. Pathol.
, vol.183
, pp. 1862-1870
-
-
Palechor-Ceron, N.1
Suprynowicz, F.A.2
Upadhyay, G.3
Dakic, A.4
Minas, T.5
Simic, V.6
-
16
-
-
24644464284
-
Small-molecule correctors of defective ΔF508-CFTR cellular processing identified by high-throughput screening
-
Pedemonte, N., Lukacs, G. L., Du, K., Caci, E., Zegarra-Moran, O., Galietta, L. J. V., et al. (2005). Small-molecule correctors of defective ΔF508-CFTR cellular processing identified by high-throughput screening. J. Clin. Invest. 115, 2564–2571.
-
(2005)
J. Clin. Invest.
, vol.115
, pp. 2564-2571
-
-
Pedemonte, N.1
Lukacs, G.L.2
Du, K.3
Caci, E.4
Zegarra-Moran, O.5
Galietta, L.J.V.6
-
17
-
-
85027236424
-
Correction of CFTR function in nasal epithelial cells from cystic fibrosis patients predicts improvement of respiratory function by CFTR modulators
-
Pranke, I. M., Hatton, A., Simonin, J., Jais, J. P., Le Pimpec-Barthes, F., Carsin, A., et al. (2017). Correction of CFTR function in nasal epithelial cells from cystic fibrosis patients predicts improvement of respiratory function by CFTR modulators. Sci. Rep. 7:7375. doi: 10.1038/s41598-017-07504-1
-
(2017)
Sci. Rep.
, vol.7
, pp. 7375
-
-
Pranke, I.M.1
Hatton, A.2
Simonin, J.3
Jais, J.P.4
Le Pimpec-Barthes, F.5
Carsin, A.6
-
18
-
-
48149090717
-
Cystic fibrosis: Impaired bicarbonate secretion and mucoviscidosis
-
Quinton, P. M. (2008). Cystic fibrosis: impaired bicarbonate secretion and mucoviscidosis. Lancet 372, 415–417. doi: 10.1016/S0140-6736(08)61162-9
-
(2008)
Lancet
, vol.372
, pp. 415-417
-
-
Quinton, P.M.1
-
19
-
-
0026497359
-
Spontaneous production of transforming growth factor-beta 2 by primary cultures of bronchial epithelial cells. Effects on cell behavior in vitro
-
Sacco, O., Romberger, D., Rizzino, A., Beckmann, J. D., Rennard, S. I., and Spurzem, J. R. (1992). Spontaneous production of transforming growth factor-beta 2 by primary cultures of bronchial epithelial cells. Effects on cell behavior in vitro. J. Clin. Invest. 90, 1379–1385.
-
(1992)
J. Clin. Invest.
, vol.90
, pp. 1379-1385
-
-
Sacco, O.1
Romberger, D.2
Rizzino, A.3
Beckmann, J.D.4
Rennard, S.I.5
Spurzem, J.R.6
-
20
-
-
84990988081
-
Role of CFTR in epithelial physiology
-
Saint-Criq, V., and Gray, M. A. (2017). Role of CFTR in epithelial physiology. Cell. Mol. Life Sci. 74, 93–115.
-
(2017)
Cell. Mol. Life Sci.
, vol.74
, pp. 93-115
-
-
Saint-Criq, V.1
Gray, M.A.2
-
21
-
-
84870370950
-
Association of TMEM16A chloride channel overexpression with airway goblet cell metaplasia
-
Scudieri, P., Caci, E., Bruno, S., Ferrera, L., Schiavon, M., Sondo, E., et al. (2012). Association of TMEM16A chloride channel overexpression with airway goblet cell metaplasia. J. Physiol. 590, 6141–6155. doi: 10.1113/jphysiol.2012.240838
-
(2012)
J. Physiol.
, vol.590
, pp. 6141-6155
-
-
Scudieri, P.1
Caci, E.2
Bruno, S.3
Ferrera, L.4
Schiavon, M.5
Sondo, E.6
-
22
-
-
84930710029
-
TEER measurement techniques for in vitro barrier model systems
-
Srinivasan, B., Kolli, A. R., Esch, M. B., Abaci, H. E., Shuler, M. L., and Hickman, J. J. (2015). TEER measurement techniques for in vitro barrier model systems. J. Lab. Autom. 20, 107–126. doi: 10.1177/2211068214561025
-
(2015)
J. Lab. Autom.
, vol.20
, pp. 107-126
-
-
Srinivasan, B.1
Kolli, A.R.2
Esch, M.B.3
Abaci, H.E.4
Shuler, M.L.5
Hickman, J.J.6
-
23
-
-
84906069624
-
Comparison of three different brushing techniques to isolate and culture primary nasal epithelial cells from human subjects
-
Stokes, A. B., Kieninger, E., Schogler, A., Kopf, B. S., Casaulta, C., Geiser, T., et al. (2014). Comparison of three different brushing techniques to isolate and culture primary nasal epithelial cells from human subjects. Exp. Lung Res. 40, 327–332. doi: 10.3109/01902148.2014.925987
-
(2014)
Exp. Lung Res.
, vol.40
, pp. 327-332
-
-
Stokes, A.B.1
Kieninger, E.2
Schogler, A.3
Kopf, B.S.4
Casaulta, C.5
Geiser, T.6
-
24
-
-
70350070383
-
Nanomolar potency pyrimido-pyrrolo-quinoxalinedione CFTR inhibitor reduces cyst size in a polycystic kidney disease model
-
Tradtrantip, L., Sonawane, N. D., Namkung, W., and Verkman, A. S. (2009). Nanomolar potency pyrimido-pyrrolo-quinoxalinedione CFTR inhibitor reduces cyst size in a polycystic kidney disease model. J. Med. Chem. 52, 6447–6455. doi: 10.1021/jm9009873
-
(2009)
J. Med. Chem.
, vol.52
, pp. 6447-6455
-
-
Tradtrantip, L.1
Sonawane, N.D.2
Namkung, W.3
Verkman, A.S.4
-
25
-
-
73249114731
-
Rescue of CF airway epithelial cell function in vitro by a CFTR potentiator. VX-770
-
Van Goor, F., Hadida, S., Grootenhuis, P. D., Burton, B., Cao, D., Neuberger, T., et al. (2009). Rescue of CF airway epithelial cell function in vitro by a CFTR potentiator. VX-770. Proc. Natl. Acad. Sci. U.S.A. 106, 18825–18830. doi: 10.1073/pnas.0904709106
-
(2009)
Proc. Natl. Acad. Sci. U.S.A.
, vol.106
, pp. 18825-18830
-
-
Van Goor, F.1
Hadida, S.2
Grootenhuis, P.D.3
Burton, B.4
Cao, D.5
Neuberger, T.6
-
26
-
-
81755163563
-
Correction of the F508del-CFTR protein processing defect in vitro by the investigational drug VX-809
-
Van Goor, F., Hadida, S., Grootenhuis, P. D., Burton, B., Stack, J. H., Straley, K. S., et al. (2011). Correction of the F508del-CFTR protein processing defect in vitro by the investigational drug VX-809. Proc. Natl. Acad. Sci. U.S.A. 108, 18843–18848. doi: 10.1073/pnas.1105787108
-
(2011)
Proc. Natl. Acad. Sci. U.S.A.
, vol.108
, pp. 18843-18848
-
-
Van Goor, F.1
Hadida, S.2
Grootenhuis, P.D.3
Burton, B.4
Stack, J.H.5
Straley, K.S.6
-
27
-
-
84937035647
-
Lumacaftor-Ivacaftor in Patients with Cystic Fibrosis Homozygous for Phe508del CFTR
-
Wainwright, C. E., Elborn, J. S., Ramsey, B. W., Marigowda, G., Huang, X., Cipolli, M., et al. (2015). Lumacaftor-Ivacaftor in Patients with Cystic Fibrosis Homozygous for Phe508del CFTR. N. Engl. J. Med. 373, 220–231. doi: 10.1056/NEJMoa1409547
-
(2015)
N. Engl. J. Med.
, vol.373
, pp. 220-231
-
-
Wainwright, C.E.1
Elborn, J.S.2
Ramsey, B.W.3
Marigowda, G.4
Huang, X.5
Cipolli, M.6
-
28
-
-
80055103786
-
Primary human bronchial epithelial cells grown from explants
-
Yaghi, A., Zaman, A., and Dolovich, M. (2010). Primary human bronchial epithelial cells grown from explants. J. Vis. Exp. 26:37.
-
(2010)
J. Vis. Exp.
, vol.26
, pp. 37
-
-
Yaghi, A.1
Zaman, A.2
Dolovich, M.3
|