-
1
-
-
84933673160
-
Practices in prescribing protein substitutes for PKU in Europe: no uniformity of approach
-
Epub 2015 Mar 26, et al
-
Aguiar A, Ahring K, Almeida MF, Assoun M, Belanger Quintana A, Bigot S, Bihet G, Blom Malmberg K, Burlina A, Bushueva T, et al. 2015. Practices in prescribing protein substitutes for PKU in Europe: no uniformity of approach. Mol Genet Metab. 115(1):17–22. Epub 2015 Mar 26. doi:10.1016/j.ymgme.2015.03.006
-
(2015)
Mol Genet Metab
, vol.115
, Issue.1
, pp. 17-22
-
-
Aguiar, A.1
Ahring, K.2
Almeida, M.F.3
Assoun, M.4
Belanger Quintana, A.5
Bigot, S.6
Bihet, G.7
Blom Malmberg, K.8
Burlina, A.9
Bushueva, T.10
-
2
-
-
67349226845
-
Dietary management practices in phenylketonuria across European centres
-
Ahring K, Bélanger-Quintana A, Dokoupil K, Gokmen Ozel H, Lammardo AM, MacDonald A, Motzfeldt K, Nowacka M, Robert M, van Rijn M., 2009. Dietary management practices in phenylketonuria across European centres. Clin Nutr. 28(3):231–236.
-
(2009)
Clin Nutr
, vol.28
, Issue.3
, pp. 231-236
-
-
Ahring, K.1
Bélanger-Quintana, A.2
Dokoupil, K.3
Gokmen Ozel, H.4
Lammardo, A.M.5
MacDonald, A.6
Motzfeldt, K.7
Nowacka, M.8
Robert, M.9
van Rijn, M.10
-
3
-
-
73749088607
-
Management of phenylketonuria in Europe: survey results from 19 countries
-
Epub 2009 Sep 13
-
Blau N, Bélanger-Quintana A, Demirkol M, Feillet F, Giovannini M, MacDonald A, Trefz FK, van Spronsen F,; European PKU centers. 2010b. Management of phenylketonuria in Europe: survey results from 19 countries. Mol Genet Metab. 99(2):109–115. Epub 2009 Sep 13. doi:10.1016/j.ymgme.2009.09.005
-
(2010)
Mol Genet Metab
, vol.99
, Issue.2
, pp. 109-115
-
-
Blau, N.1
Bélanger-Quintana, A.2
Demirkol, M.3
Feillet, F.4
Giovannini, M.5
MacDonald, A.6
Trefz, F.K.7
van Spronsen, F.8
-
5
-
-
31344482675
-
Intellectual development of the patients of the German Collaborative Study of children treated for phenylketonuria
-
Burgard P, Schmidt E, Rupp A, Schneider W, Bremer HJ. 1996. Intellectual development of the patients of the German Collaborative Study of children treated for phenylketonuria. Eur J Pediatr. 155(Suppl1):S33–S38.
-
(1996)
Eur J Pediatr
, vol.155
, pp. S33-S38
-
-
Burgard, P.1
Schmidt, E.2
Rupp, A.3
Schneider, W.4
Bremer, H.J.5
-
6
-
-
85030713904
-
-
accessed, 2016, Dec, v3.6
-
Creme Global [Internet]. 2016. ‘Creme Global’, Creme Global Ltd. [accessed 2016 Dec 23]. v3.6 http://www.cremeglobal.com/modelling-software/creme-food.
-
(2016)
‘Creme Global’, Creme Global Ltd
-
-
-
7
-
-
25144435430
-
Behavioural factors related to metabolic control in patients with phenylketonuria
-
Crone MR, van Spronsen FJ, Oudshoorn K, Bekhof J, van Rijn G, Verkerk PH. 2005. Behavioural factors related to metabolic control in patients with phenylketonuria. J Inherit Metab Dis. 28(5):627–637.
-
(2005)
J Inherit Metab Dis
, vol.28
, Issue.5
, pp. 627-637
-
-
Crone, M.R.1
van Spronsen, F.J.2
Oudshoorn, K.3
Bekhof, J.4
van Rijn, G.5
Verkerk, P.H.6
-
8
-
-
0004036764
-
-
London: HMSO
-
Department of Health, Dietary reference values for food, energy and nutrients for the United Kingdom. 1991. Report on Health and Social Subjects. No. 41. London: HMSO.
-
(1991)
Report on Health and Social Subjects. No. 41
-
-
-
10
-
-
3042830029
-
Assessment of intakes of Artificial Sweeteners in Children with Type 1 Diabetes Mellitus
-
Devitt L, Daneman D, Buccino J. 2004. Assessment of intakes of Artificial Sweeteners in Children with Type 1 Diabetes Mellitus. Can J Diabetes. 28(2):1–5.
-
(2004)
Can J Diabetes
, vol.28
, Issue.2
, pp. 1-5
-
-
Devitt, L.1
Daneman, D.2
Buccino, J.3
-
11
-
-
85075072827
-
General principles for the collection of national food consumption data in the view of a pan-European dietary survey
-
accessed, 2015, Jul
-
[EFSA] European Food Safety Authority. 2009. General principles for the collection of national food consumption data in the view of a pan-European dietary survey. EFSA J. 7(12):1435. [accessed 2015 Jul 23]. http://www.efsa.europa.eu/en/efsajournal/pub/1435.
-
(2009)
EFSA J
, vol.7
, Issue.12
, pp. 1435
-
-
-
12
-
-
0003192196
-
Commission Directive 1999/21/EC of 25 March 1999 on dietary foods for special medical purposes
-
Apr
-
European Commission. 1999. Commission Directive 1999/21/EC of 25 March 1999 on dietary foods for special medical purposes. OJ No. 91 Apr 7:29.
-
(1999)
OJ No
, vol.91
, pp. 29
-
-
-
16
-
-
69049113182
-
Directive 2003/115/EC of the European Parliament and of the Council of 22 December 2003 amending Directive 94/35/EC on sweeteners for use in foodstuffs
-
accessed, 2004, Jan
-
European Commission. 2003. Directive 2003/115/EC of the European Parliament and of the Council of 22 December 2003 amending Directive 94/35/EC on sweeteners for use in foodstuffs. OJ L. 24:65 [accessed 2004 Jan 29].
-
(2003)
OJ L
, vol.24
, pp. 65
-
-
-
17
-
-
65449149705
-
Commission Directive 2006/125/EC of 5 December 2006 on processed cereal-based foods and baby foods for infants and young children
-
Dec
-
European Commission. 2006. Commission Directive 2006/125/EC of 5 December 2006 on processed cereal-based foods and baby foods for infants and young children. OJ L. 339 Dec 6:16–35.
-
(2006)
OJ L
, vol.339
, pp. 16-35
-
-
-
18
-
-
77956639583
-
Regulation (EC) No 1333/2008 of the European Parliament and of the Council of 16 December 2008 on food additives
-
Dec
-
European Commission. 2008. Regulation (EC) No 1333/2008 of the European Parliament and of the Council of 16 December 2008 on food additives. OJ L. 354 Dec 31:16–33.
-
(2008)
OJ L
, vol.354
, pp. 16-33
-
-
-
19
-
-
84881412136
-
Commission Regulation (EU) No 1129/2011 of 11 November 2011 amending Annex II to Regulation (EC) No 1333/2008 of the European Parliament and of the Council by establishing a Union list of food additives
-
Nov
-
European Commission. 2011. Commission Regulation (EU) No 1129/2011 of 11 November 2011 amending Annex II to Regulation (EC) No 1333/2008 of the European Parliament and of the Council by establishing a Union list of food additives. OJ No. 295 Nov 12:1.
-
(2011)
OJ No
, vol.295
, pp. 1
-
-
-
20
-
-
85018049422
-
Regulation (EU) No 609/2013 of the European Parliament and of the Council of 12 June 2013 on food intended for infants and young children, food for special medical purposes, and total diet replacement for weight control and repealing Council Directive 92/52/EEC, Commission Directives 96/8/EC, 1999/21/EC, 2006/125/EC and 2006/141/EC, Directive 2009/39/EC of the European Parliament and of the Council and Commission Regulations (EC) No 41/2009 and (EC) No 953/2009
-
Jun
-
European Commission. 2013. Regulation (EU) No 609/2013 of the European Parliament and of the Council of 12 June 2013 on food intended for infants and young children, food for special medical purposes, and total diet replacement for weight control and repealing Council Directive 92/52/EEC, Commission Directives 96/8/EC, 1999/21/EC, 2006/125/EC and 2006/141/EC, Directive 2009/39/EC of the European Parliament and of the Council and Commission Regulations (EC) No 41/2009 and (EC) No 953/2009. OJ L. 181 Jun 29:35–56.
-
(2013)
OJ L
, vol.181
, pp. 35-56
-
-
-
26
-
-
0034990831
-
Calculation of the intake of three intense sweeteners in young insulin-dependent diabetics
-
Garnier-Sagne I, Leblanc JC, Verger P. 2001. Calculation of the intake of three intense sweeteners in young insulin-dependent diabetics. Food Chem Toxicol. 39:745–749.
-
(2001)
Food Chem Toxicol
, vol.39
, pp. 745-749
-
-
Garnier-Sagne, I.1
Leblanc, J.C.2
Verger, P.3
-
27
-
-
0142243163
-
Introduction to the Monte Carlo project and the approach to validation of conceptual models of dietary exposure to selected food chemicals
-
Oct
-
Gibney MJ, Van der Voet H. 2003. Introduction to the Monte Carlo project and the approach to validation of conceptual models of dietary exposure to selected food chemicals. Food Addit Contam. 20(Suppl 1) Oct:S1–S7.
-
(2003)
Food Addit Contam
, vol.20
, pp. S1-S7
-
-
Gibney, M.J.1
Van der Voet, H.2
-
28
-
-
0033857660
-
Breakfast cereal consumption in young children: associations with non-milk extrinsic sugars and caries experience: further analysis of data from the UK National Diet and Nutrition Survey of children aged 1.5±4.5 years
-
Gibson SA. 1999. Breakfast cereal consumption in young children: associations with non-milk extrinsic sugars and caries experience: further analysis of data from the UK National Diet and Nutrition Survey of children aged 1.5±4.5 years. Public Health Nutr. 3:227–232.
-
(1999)
Public Health Nutr
, vol.3
, pp. 227-232
-
-
Gibson, S.A.1
-
29
-
-
0142150056
-
Validation analysis of probabilistic models of dietary exposure to food additives
-
Gilsenan MB, Thompson RL, Lambe J, Gibney MJ. 2003. Validation analysis of probabilistic models of dietary exposure to food additives. Food Addit Contam. 20:S61–S72.
-
(2003)
Food Addit Contam
, vol.20
, pp. S61-S72
-
-
Gilsenan, M.B.1
Thompson, R.L.2
Lambe, J.3
Gibney, M.J.4
-
31
-
-
0003703337
-
National Diet and Nutrition Survey: children aged 1.5 to 4.5 years. Vol. 2
-
London: HMSO
-
Hinds K, Gregory JR. 1995. National Diet and Nutrition Survey: children aged 1.5 to 4.5 years. Vol. 2. Report of the Dental Survey. London: HMSO.
-
(1995)
Report of the Dental Survey
-
-
Hinds, K.1
Gregory, J.R.2
-
32
-
-
84857437425
-
Dietary intake of artificial sweeteners by the Belgian population
-
2011, Nov
-
Huvaere K, Vandevijvere S, Hasni M, Vinkx C, Van Loco J. Dietary intake of artificial sweeteners by the Belgian population. 2012. Food Addit Contam Part A Chem Anal Control Expo Risk Assess. 29(1):54–65. 2011 Nov 17. doi:10.1080/19440049.2011.627572.Epub
-
(2012)
Food Addit Contam Part A Chem Anal Control Expo Risk Assess
, vol.29
, Issue.1
, pp. 54-65
-
-
Huvaere, K.1
Vandevijvere, S.2
Hasni, M.3
Vinkx, C.4
Van Loco, J.5
-
33
-
-
19244377281
-
Estimated intake of the artificial sweeteners acesulfame-K, aspartame, cyclamate and saccharin in a group of Swedish diabetics
-
Ilbäck N-G, Alzin M, Jahrl S, Enghardt-Barbieri H, Busk L. 2003. Estimated intake of the artificial sweeteners acesulfame-K, aspartame, cyclamate and saccharin in a group of Swedish diabetics. Food Addit Contam. 20:99–114.
-
(2003)
Food Addit Contam
, vol.20
, pp. 99-114
-
-
Ilbäck, N.-G.1
Alzin, M.2
Jahrl, S.3
Enghardt-Barbieri, H.4
Busk, L.5
-
34
-
-
84930944562
-
Assessing and reporting uncertainties in dietary exposure analysis: mapping of uncertainties in a tiered approach
-
Review
-
Kettler S, Kennedy M, McNamara C, Oberdörfer R, O’Mahony C, Schnabel J, Smith B, Sprong C, Faludi R, Tennant D. 2015. Assessing and reporting uncertainties in dietary exposure analysis: mapping of uncertainties in a tiered approach. Food Chem Toxicol. 82:79–95. Review.
-
(2015)
Food Chem Toxicol
, vol.82
, pp. 79-95
-
-
Kettler, S.1
Kennedy, M.2
McNamara, C.3
Oberdörfer, R.4
O’Mahony, C.5
Schnabel, J.6
Smith, B.7
Sprong, C.8
Faludi, R.9
Tennant, D.10
-
35
-
-
0036183324
-
The use of food consumption data in assessments of exposure to food chemicals, including the application of probabilistic modeling
-
Lambe J. 2002. The use of food consumption data in assessments of exposure to food chemicals, including the application of probabilistic modeling. Proc Nutr Soc. 61:11–18.
-
(2002)
Proc Nutr Soc
, vol.61
, pp. 11-18
-
-
Lambe, J.1
-
36
-
-
33745790867
-
Protein substitute dosage in PKU: how much do young patients need?
-
accessed, 2006, Mar
-
MacDonald A, Chakrapani A, Hendriksz C, Daly A, Davies P, Asplin D, Hall K, Booth IW. 2006. Protein substitute dosage in PKU: how much do young patients need? Arch Dis Child. 91(7):588–593. accessed 2006 Mar 17.
-
(2006)
Arch Dis Child
, vol.91
, Issue.7
, pp. 588-593
-
-
MacDonald, A.1
Chakrapani, A.2
Hendriksz, C.3
Daly, A.4
Davies, P.5
Asplin, D.6
Hall, K.7
Booth, I.W.8
-
37
-
-
2942622419
-
Protein substitutes for PKU: what’s new?
-
MacDonald A, Daly A, Davies P, Asplin D, Hall SK, Rylance G, Chakrapani A. 2004. Protein substitutes for PKU: what’s new? J Inherit Metab Dis. 27(3):363–371.
-
(2004)
J Inherit Metab Dis
, vol.27
, Issue.3
, pp. 363-371
-
-
MacDonald, A.1
Daly, A.2
Davies, P.3
Asplin, D.4
Hall, S.K.5
Rylance, G.6
Chakrapani, A.7
-
39
-
-
84961198706
-
Dietary intake of four artificial sweeteners by Irish pre-school children
-
Epub 2016 Mar 4
-
Martyn DM, Nugent AP, McNulty BA, O’Reilly E, Tlustos C, Walton J, Flynn A, Gibney MJ. 2016. Dietary intake of four artificial sweeteners by Irish pre-school children. Food Addit Contam Part Chem Anal Control Expo Risk Assess. 33 4:592–602. Epub 2016 Mar 4. doi:10.1080/19440049.2016.1152880
-
(2016)
Food Addit Contam Part Chem Anal Control Expo Risk Assess
, vol.33
, pp. 592-602
-
-
Martyn, D.M.1
Nugent, A.P.2
McNulty, B.A.3
O’Reilly, E.4
Tlustos, C.5
Walton, J.6
Flynn, A.7
Gibney, M.J.8
-
40
-
-
0142150059
-
Design, development and validation of software for modelling dietary exposure to food chemicals and nutrients
-
McNamara C, Naddy B, Rohan D, Sexton J. 2003. Design, development and validation of software for modelling dietary exposure to food chemicals and nutrients. Food Addit Contam. 20:S8–S26.
-
(2003)
Food Addit Contam
, vol.20
, pp. S8-S26
-
-
McNamara, C.1
Naddy, B.2
Rohan, D.3
Sexton, J.4
-
41
-
-
0027533685
-
-
Medical Research Council Working Party on Phenylketonuria Recommendations on the dietary management of phenylketonuria. 1993. Arch Dis Child. 68:426–427.
-
(1993)
Arch Dis Child
, vol.68
, pp. 426-427
-
-
-
43
-
-
33644547369
-
Understanding the origin of flavor preferences
-
Mennella JA, Beauchamp GK. 2005. Understanding the origin of flavor preferences. Chem Senses. 30(Suppl.1):i242–i243.
-
(2005)
Chem Senses
, vol.30
, pp. i242-i243
-
-
Mennella, J.A.1
Beauchamp, G.K.2
-
47
-
-
84989260665
-
Probabilistic modelling to assess exposure to three artificial sweeteners of young Irish patients aged 1–3 years with PKU and CMPA
-
O’Sullivan AJ, Pigat S, O’Mahony C, Gibney MJ, McKevitt AI. 2016. Probabilistic modelling to assess exposure to three artificial sweeteners of young Irish patients aged 1–3 years with PKU and CMPA. Food Addit Contam: Part A. 33(11):1660–1671.
-
(2016)
Food Addit Contam: Part A
, vol.33
, Issue.11
, pp. 1660-1671
-
-
O’Sullivan, A.J.1
Pigat, S.2
O’Mahony, C.3
Gibney, M.J.4
McKevitt, A.I.5
-
48
-
-
85030714711
-
-
[accessed, 2017, Mar, ]
-
OMIM® - Online Mendelian Inheritance in Man®. 2017. # 261600 PHENYLKETONURIA; PKU. [accessed 2017 Mar 17]. http://omim.org/entry/261600#142.
-
(2017)
# 261600 PHENYLKETONURIA; PKU
-
-
-
50
-
-
34848850451
-
The PAH gene, phenylketonuria, and a paradigm shift
-
Scriver CR. 2007. The PAH gene, phenylketonuria, and a paradigm shift. Hum Mutat. 28:831–845.
-
(2007)
Hum Mutat
, vol.28
, pp. 831-845
-
-
Scriver, C.R.1
-
51
-
-
0019137917
-
Phenylketonuria: epitome of human biochemical genetics
-
Scriver CR, Clow CL. 1980. Phenylketonuria: epitome of human biochemical genetics. New Eng J Med. 303:1336–1342 and 1394–1400.
-
(1980)
New Eng J Med
, vol.303
-
-
Scriver, C.R.1
Clow, C.L.2
-
52
-
-
0033676463
-
Risk factors for poor iron status in British toddlers: further analysis of data from the National Diet and Nutrition Survey of children aged 1.5±4.5 years
-
Thane CW, Walmsley CM, Bates CJ, Prentice A, Cole TJ. 2000. Risk factors for poor iron status in British toddlers: further analysis of data from the National Diet and Nutrition Survey of children aged 1.5±4.5 years. Public Health Nutr. 3:433–440.
-
(2000)
Public Health Nutr
, vol.3
, pp. 433-440
-
-
Thane, C.W.1
Walmsley, C.M.2
Bates, C.J.3
Prentice, A.4
Cole, T.J.5
-
53
-
-
84890803876
-
Estimation of the dietary intake of 13 priority additives in France, Italy, the UK and Ireland as part of the FACET project
-
Vin K, Connolly A, McCaffrey T, McKevitt A, O’Mahony C, Prieto M, Tennant D, Hearty A, Volatier JL. 2013. Estimation of the dietary intake of 13 priority additives in France, Italy, the UK and Ireland as part of the FACET project. Food Addit Contam Part A Chem Anal Control Expo Risk Assess. 30(12):2050–2080.
-
(2013)
Food Addit Contam Part A Chem Anal Control Expo Risk Assess
, vol.30
, Issue.12
, pp. 2050-2080
-
-
Vin, K.1
Connolly, A.2
McCaffrey, T.3
McKevitt, A.4
O’Mahony, C.5
Prieto, M.6
Tennant, D.7
Hearty, A.8
Volatier, J.L.9
-
54
-
-
0142017677
-
-
Geneva: WHO, [accessed, 2012, Oct, ]
-
[WHO] World Health Organization. 2003. Adherence to long term therapies: evidence for action. Geneva: WHO. [accessed 2012 Oct 25]. http://www.who.int/chp/knowledge/publications/adherence_introduction.pdf.
-
(2003)
Adherence to long term therapies: evidence for action
-
-
|