-
1
-
-
0028625811
-
Protein intake affects phenylalanine requirements and growth of infants with phenylketonuria
-
Acosta PB, Yannicelli S (1994) Protein intake affects phenylalanine requirements and growth of infants with phenylketonuria. Acta Paediatr 83(Supplement 407): 66-67.
-
(1994)
Acta Paediatr.
, vol.83
, Issue.SUPPL. 407
, pp. 66-67
-
-
Acosta, P.B.1
Yannicelli, S.2
-
2
-
-
0031713642
-
Nutrient intake and growth of infants with phenylketonuria undergoing therapy
-
Acosta PB, Yannicelli S, Marriage B, et al (1998) Nutrient intake and growth of infants with phenylketonuria undergoing therapy. J Pediatr Gastroenterol Nutr 27: 287-291.
-
(1998)
J. Pediatr. Gastroenterol. Nutr.
, vol.27
, pp. 287-291
-
-
Acosta, P.B.1
Yannicelli, S.2
Marriage, B.3
-
3
-
-
0034779346
-
Intake and blood levels of fatty acids in treated patients with phenylketonuria
-
Acosta PB, Yannicelli S, Singh R, et al (2001) Intake and blood levels of fatty acids in treated patients with phenylketonuria. J Pediatr Gastroenterol Nutr 33: 253-259.
-
(2001)
J. Pediatr. Gastroenterol. Nutr.
, vol.33
, pp. 253-259
-
-
Acosta, P.B.1
Yannicelli, S.2
Singh, R.3
-
4
-
-
2942545576
-
The addition of fat to a protein substitute designed for children with PKU
-
A compilation of papers from the Sixth International Dietitians Metabolic Meeting, SSIEM, Prague, 2001
-
Cleary M (2001) The addition of fat to a protein substitute designed for children with PKU. A compilation of papers from the Sixth International Dietitians Metabolic Meeting, SSIEM, Prague, 2001, 5-9.
-
(2001)
, pp. 5-9
-
-
Cleary, M.1
-
5
-
-
0025911165
-
Plasma amino acids in adolescents and adults with phenylketonuria on three different levels of protein intake
-
Clemens PC, Heddrich-Ellerbrok M, Wachtel U, Link RM (1991) Plasma amino acids in adolescents and adults with phenylketonuria on three different levels of protein intake. Acta Paediatr 80: 577-580.
-
(1991)
Acta Paediatr.
, vol.80
, pp. 577-580
-
-
Clemens, P.C.1
Heddrich-Ellerbrok, M.2
Wachtel, U.3
Link, R.M.4
-
6
-
-
0003411392
-
-
Committee on Dietary Allowances, Food and Nutrition Board, National Research Council 9th edn. Washington, DC: National Academy Press
-
Committee on Dietary Allowances, Food and Nutrition Board, National Research Council (1980) Recommended Dietary Allowances. 9th edn. Washington, DC: National Academy Press.
-
(1980)
Recommended Dietary Allowances
-
-
-
7
-
-
0003851317
-
Dietary Reference Values for Food, Energy and Nutrients for the United Kingdom
-
Department of Health Report on Health and Social Subjects. No. 41. London: HMSO
-
Department of Health (1991) Dietary Reference Values for Food, Energy and Nutrients for the United Kingdom. Report on Health and Social Subjects. No. 41. London: HMSO.
-
(1991)
-
-
-
9
-
-
0003674969
-
Nutrient and Energy Intakes for the European Community
-
EC Scientific Committee for Food Report (thirty-first series). Luxembourg: Office for Official Publications of the European Communities
-
EC (1993) Scientific Committee for Food Report (thirty-first series). Nutrient and Energy Intakes for the European Community. Luxembourg: Office for Official Publications of the European Communities.
-
(1993)
-
-
-
10
-
-
25544436047
-
Daily phenylalanine variability in adult patients with phenylketonuria
-
(Abstract)
-
François B, Diel M (1998) Daily phenylalanine variability in adult patients with phenylketonuria (Abstract). J Inherit Metab Dis 21(Suppl 2): 11.
-
(1998)
J. Inherit. Metab. Dis.
, vol.21
, Issue.SUPPL. 2
, pp. 11
-
-
François, B.1
Diel, M.2
-
12
-
-
0020656783
-
Comparison of an elemental enteral and polymeric diet in patients with normal gastrointestinal function
-
Jones BJM, Lees R, Andrews J, Frost P, Silk DBA (1983) Comparison of an elemental enteral and polymeric diet in patients with normal gastrointestinal function. Gut 24: 78-84.
-
(1983)
Gut
, vol.24
, pp. 78-84
-
-
Jones, B.J.M.1
Lees, R.2
Andrews, J.3
Frost, P.4
Silk, D.B.A.5
-
13
-
-
0021200956
-
Is phenylalanine requirement in infants and children related to protein intake?
-
Kindt E, Motzfeldt K, Halvorsen S, Lie, SO (1984) Is phenylalanine requirement in infants and children related to protein intake? Br J Nutr 51: 435-442.
-
(1984)
Br. J. Nutr.
, vol.51
, pp. 435-442
-
-
Kindt, E.1
Motzfeldt, K.2
Halvorsen, S.3
Lie, S.O.4
-
14
-
-
2942517374
-
Phenylketonuria
-
Shaw V, Lawson M, eds. 2nd edn. Oxford: Blackwell Science
-
MacDonald A (2001) Phenylketonuria. In Shaw V, Lawson M, eds. Clinical Paediatric Dietetics, 2nd edn. Oxford: Blackwell Science, 235-253.
-
(2001)
Clinical Paediatric Dietetics
, pp. 235-253
-
-
MacDonald, A.1
-
15
-
-
0030048431
-
Factors affecting the variation in plasma phenylalanine in patients with phenylketonuria on diet
-
MacDonald A, Rylance G, Hall SK, Asplin D, Booth IW (1996) Factors affecting the variation in plasma phenylalanine in patients with phenylketonuria on diet. Arch Dis Child 74: 412-417.
-
(1996)
Arch. Dis. Child.
, vol.74
, pp. 412-417
-
-
MacDonald, A.1
Rylance, G.2
Hall, S.K.3
Asplin, D.4
Booth, I.W.5
-
16
-
-
0030723113
-
Abnormal feeding behaviours in phenylketonuria
-
MacDonald A, Harris G, Rylance G, Asplin D, Booth IW (1997) Abnormal feeding behaviours in phenylketonuria. J Hum Nutr Diet 10: 163-170.
-
(1997)
J. Hum. Nutr. Diet.
, vol.10
, pp. 163-170
-
-
MacDonald, A.1
Harris, G.2
Rylance, G.3
Asplin, D.4
Booth, I.W.5
-
17
-
-
0031953295
-
Does a single plasma phenylalanine predict quality of control in phenylketonuria?
-
MacDonald A, Rylance GW, Asplin D, Hall SK, Booth IW (1998) Does a single plasma phenylalanine predict quality of control in phenylketonuria? Arch Dis Child 78: 122-126.
-
(1998)
Arch. Dis. Child.
, vol.78
, pp. 122-126
-
-
MacDonald, A.1
Rylance, G.W.2
Asplin, D.3
Hall, S.K.4
Booth, I.W.5
-
18
-
-
2942600880
-
PKU gel: A new protein substitute
-
[Abstract]. 28th Annual Conference of NSPKU, 2-4 March, Margate
-
MacDonald A, Rylance G, Asplin D, Hall SK (2001) PKU gel: a new protein substitute [Abstract]. 28th Annual Conference of NSPKU, 2-4 March, Margate, 9-10.
-
(2001)
, pp. 9-10
-
-
MacDonald, A.1
Rylance, G.2
Asplin, D.3
Hall, S.K.4
-
19
-
-
0042420698
-
Administration of protein substitute and quality of control in phenylketonuria: A randomized study
-
MacDonald A, Rylance G, Davies P, Asplin D, Hall SK, Booth IW (2003a) Administration of protein substitute and quality of control in phenylketonuria: a randomized study. J Inherit Metab Dis 26: 319-326.
-
(2003)
J. Inherit. Metab. Dis.
, vol.26
, pp. 319-326
-
-
MacDonald, A.1
Rylance, G.2
Davies, P.3
Asplin, D.4
Hall, S.K.5
Booth, I.W.6
-
20
-
-
0037383731
-
Are tablets a practical source of protein substitute in phenylketonuria:?
-
MacDonald A, Ferguson C, Rylance G, et al (2003b) Are tablets a practical source of protein substitute in phenylketonuria:? Arch Dis Child 88: 327-329.
-
(2003)
Arch. Dis. Child.
, vol.88
, pp. 327-329
-
-
MacDonald, A.1
Ferguson, C.2
Rylance, G.3
-
21
-
-
2942512654
-
The efficacy and acceptability of protein substitute tablets (Phlexy-10 tablets) in PKU
-
A compilation of papers from the Seventh International Metabolic Dietitians Meeting, SSIEM, Dublin, 2002
-
MacDonald A, Cochrane B, Asplin D, et al (2003c). The efficacy and acceptability of protein substitute tablets (Phlexy-10 tablets) in PKU. A compilation of papers from the Seventh International Metabolic Dietitians Meeting, SSIEM, Dublin, 2002, 34-37.
-
(2003)
, pp. 34-37
-
-
MacDonald, A.1
Cochrane, B.2
Asplin, D.3
-
22
-
-
2942568160
-
A new, low volume protein substitute for teenagers and adults with PKU
-
(in press)
-
MacDonald A, Lilburn M, Cochrane B, et al (2004) A new, low volume protein substitute for teenagers and adults with PKU. J Inherit Metab Dis (in press).
-
(2004)
J. Inherit. Metab. Dis.
-
-
MacDonald, A.1
Lilburn, M.2
Cochrane, B.3
-
23
-
-
0027533685
-
Recommendations on the dietary management of phenylketonuria
-
MRC Medical Research Council Working Party on Phenylketonuria
-
MRC (1993) Medical Research Council Working Party on Phenylketonuria. Recommendations on the dietary management of phenylketonuria. Arch Dis Child 68: 426-427.
-
(1993)
Arch. Dis. Child.
, vol.68
, pp. 426-427
-
-
-
24
-
-
84916525886
-
The influence of glucose on amino acid metabolism
-
Munro HN, Thomson WST (1953) The influence of glucose on amino acid metabolism. Metabolism 2: 354-361.
-
(1953)
Metabolism
, vol.2
, pp. 354-361
-
-
Munro, H.N.1
Thomson, W.S.T.2
-
25
-
-
0008089896
-
Phenylketonuria treated with a high phenylalanine intake and casein-hydrolysate/amino acid mixtures
-
June 24
-
O'Daly S (1961) Phenylketonuria treated with a high phenylalanine intake and casein-hydrolysate/amino acid mixtures. Lancet June 24: 1379-1383.
-
(1961)
Lancet
, pp. 1379-1383
-
-
O'Daly, S.1
-
26
-
-
0030808328
-
Treatment products and approaches for phenylketonuria: Improved palatability and flexibility demonstrate safety, efficacy and acceptance in US clinical trials
-
Prince AP, McMurry MP, Buist NRM (1997) Treatment products and approaches for phenylketonuria: improved palatability and flexibility demonstrate safety, efficacy and acceptance in US clinical trials. J Inherit Metab Dis 20: 486-498.
-
(1997)
J. Inherit. Metab. Dis.
, vol.20
, pp. 486-498
-
-
Prince, A.P.1
McMurry, M.P.2
Buist, N.R.M.3
-
27
-
-
0029786624
-
Recommendations for protein and amino acid intake in phenylketonuria patients
-
Przyrembel H (1996) Recommendations for protein and amino acid intake in phenylketonuria patients. Eur J Pediatr 155: S130-S131.
-
(1996)
Eur. J. Pediatr.
, vol.155
-
-
Przyrembel, H.1
-
28
-
-
0028999278
-
Nutrient intake and food consumption of adolescents and young adults with phenylketonuria
-
Schulz B, Bremer, HJ (1995) Nutrient intake and food consumption of adolescents and young adults with phenylketonuria. Acta Paediatr 84: 743-748.
-
(1995)
Acta Paediatr.
, vol.84
, pp. 743-748
-
-
Schulz, B.1
Bremer, H.J.2
-
29
-
-
0028633591
-
Influence of single dose amino acid mixtures on the nitrogen retention in patients with phenylketonuria
-
Schoeffer A, Herrmann M-E, Brösicke HG, Mönch E (1994) Influence of single dose amino acid mixtures on the nitrogen retention in patients with phenylketonuria. J Nutr Med 4: 415-418.
-
(1994)
J. Nutr. Med.
, vol.4
, pp. 415-418
-
-
Schoeffer, A.1
Herrmann, M.-E.2
Brösicke, H.G.3
Mönch, E.4
-
31
-
-
0028346377
-
Growth in patients with phenylketonuria
-
Weglage J, Bramswig JH, Koch HG, Karassalidou S, Ullrich K (1994) Growth in patients with phenylketonuria. Eur J Pediatr 153: 537-538.
-
(1994)
Eur. J. Pediatr.
, vol.153
, pp. 537-538
-
-
Weglage, J.1
Bramswig, J.H.2
Koch, H.G.3
Karassalidou, S.4
Ullrich, K.5
-
32
-
-
0003526098
-
Energy and Protein Requirements
-
World Health Organization Report of a Joint FAO/WHO/UNU Expert Consultation: WHO Technical Report Series No. 522. Geneva: WHO
-
World Health Organization (1973) Energy and Protein Requirements. Report of a Joint FAO/WHO/UNU Expert Consultation: WHO Technical Report Series No. 522. Geneva: WHO.
-
(1973)
-
-
-
33
-
-
0003526098
-
Energy and Protein Requirements
-
World Health Organization Report of a Joint FAO/WHO/UNU Expert Consultation: WHO Technical Report Series. No. 724. Geneva: WHO
-
World Health Organization (1985) Energy and Protein Requirements. Report of a Joint FAO/WHO/UNU Expert Consultation: WHO Technical Report Series. No. 724. Geneva: WHO.
-
(1985)
-
-
-
35
-
-
0347157135
-
Phenylketonuria with a study of the effect upon it of glutamic acid
-
Woolf LI, Vulliamy DG (1951) Phenylketonuria with a study of the effect upon it of glutamic acid. Arch Dis Child 26: 487-494.
-
(1951)
Arch. Dis. Child.
, vol.26
, pp. 487-494
-
-
Woolf, L.I.1
Vulliamy, D.G.2
-
36
-
-
0002424530
-
Treatment of phenylketonuria with a diet low in phenylalanine
-
Jan. 8
-
Woolf LI, Griffiths R, Moncrieff A (1955). Treatment of phenylketonuria with a diet low in phenylalanine. Br Med J Jan. 8: 57-64.
-
(1955)
Br. Med. J.
, pp. 57-64
-
-
Woolf, L.I.1
Griffiths, R.2
Moncrieff, A.3
|