Rapidly progressive dementia with thalamic degeneration and peculiar cortical prion protein immunoreactivity, but absence of proteinase K resistant PrP: A new disease entity?

Acta Neuropathologica Communications

Volumn 2, Issue 1, 2014, Pages

  Kovacs, Gabor G ^a   Peden, Alexander ^b   Weis, Serge ^c   Höftberger, Romana ^a   Berghoff, Anna S ^a   Yull, Helen ^b   Ströbel, Thomas ^a   Koppi, Stefan ^d   Katzenschlager, Regina ^e   Langenscheidt, Dieter ^d   Assar, Hamid ^c   Zaruba, Elisabeth ^f   Gröner, Albrecht ^g   Voigtländer, Till ^a   Puska, Gina ^h   Hametner, Eva ⁱ   Grams, Astrid ⁱ   Muigg, Armin ⁱ   Knoflach, Michael ⁱ   László, Lajos ^h   Ironside, James W ^b   Head, Mark W ^b   Budka, Herbert ^a,j   more..

^a MEDICAL UNIVERSITY OF VIENNA   (Austria)

^b UNIVERSITY OF EDINBURGH   (United Kingdom)

^c KEPLER UNIVERSITY HOSPITAL   (Austria)

^d Department of Neurology ^*  (Austria)

^e DANUBE HOSPITAL   (Austria)

^f General Hospital Hietzing with Neurological Center Rosenhugel   (Austria)

^g CSL BEHRING GMBH   (Germany)

^h EÖTVÖS LORÁND UNIVERSITY   (Hungary)

ⁱ UNIVERSITY HOSPITAL INNSBRUCK   (Austria)

^j UNIVERSITY HOSPITAL ZURICH   (Switzerland)

more..

Author keywords

Conformational assay; Prion protein; Prionopathy; Protease sensitive PrPSc; Thalamic degeneration

Indexed keywords

PRION; PROTEINASE K;

AGED; BRAIN CORTEX; CASE REPORT; DEGENERATIVE DISEASE; DEMENTIA; DISEASE COURSE; FEMALE; HUMAN; MALE; METABOLISM; MIDDLE AGED; PATHOLOGY; PATHOPHYSIOLOGY; PRION; THALAMUS; VERY ELDERLY;

AGED; AGED, 80 AND OVER; CEREBRAL CORTEX; DEMENTIA; DISEASE PROGRESSION; ENDOPEPTIDASE K; FEMALE; HUMANS; MALE; MIDDLE AGED; NEURODEGENERATIVE DISEASES; PRIONS; THALAMUS;

EID: 85005846684     PISSN: None     EISSN: 20515960     Source Type: Journal    
DOI: 10.1186/20515960172     Document Type: Article

References (46)

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