-
1
-
-
34547638271
-
Ultrasensitive detection of scrapie prion protein using seeded conversion of recombinant prion protein
-
Atarashi, R., Moore, R. A., Sim, V. L., Hughson, A. G., Dorward, D. W., Onwubiko, H. A., Priola, S. A. & Caughey, B. (2007). Ultrasensitive detection of scrapie prion protein using seeded conversion of recombinant prion protein. Nat Methods 4, 645-650.
-
(2007)
Nat Methods
, vol.4
, pp. 645-650
-
-
Atarashi, R.1
Moore, R.A.2
Sim, V.L.3
Hughson, A.G.4
Dorward, D.W.5
Onwubiko, H.A.6
Priola, S.A.7
Caughey, B.8
-
2
-
-
40149090017
-
Simplified ultrasensitive prion detection by recombinant PrP conversion with shaking
-
Atarashi, R., Wilham, J. M., Christensen, L., Hughson, A. G., Moore, R. A., Johnson, L. M., Onwubiko, H. A., Priola, S. A. & Caughey, B. (2008). Simplified ultrasensitive prion detection by recombinant PrP conversion with shaking. Nat Methods 5, 211-212.
-
(2008)
Nat Methods
, vol.5
, pp. 211-212
-
-
Atarashi, R.1
Wilham, J.M.2
Christensen, L.3
Hughson, A.G.4
Moore, R.A.5
Johnson, L.M.6
Onwubiko, H.A.7
Priola, S.A.8
Caughey, B.9
-
3
-
-
79751535822
-
Ultrasensitive human prion detection in cerebrospinal fluid by realtime quaking-induced conversion
-
Authors other
-
Atarashi, R., Satoh, K., Sano, K., Fuse, T., Yamaguchi, N., Ishibashi, D., Matsubara, T., Nakagaki, T., Yamanaka, H. & other authors (2011). Ultrasensitive human prion detection in cerebrospinal fluid by realtime quaking-induced conversion. Nat Med 17, 175-178.
-
(2011)
Nat Med
, vol.17
, pp. 175-178
-
-
Atarashi, R.1
Satoh, K.2
Sano, K.3
Fuse, T.4
Yamaguchi, N.5
Ishibashi, D.6
Matsubara, T.7
Nakagaki, T.8
Yamanaka, H.9
-
4
-
-
77955344991
-
Defining sporadic Creutzfeldt-Jakob disease strains and their transmission properties
-
Bishop, M. T., Will, R. G. & Manson, J. C. (2010). Defining sporadic Creutzfeldt-Jakob disease strains and their transmission properties. Proc Natl Acad Sci U S A 107, 12005-12010.
-
(2010)
Proc Natl Acad Sci U S A
, vol.107
, pp. 12005-12010
-
-
Bishop, M.T.1
Will, R.G.2
Manson, J.C.3
-
5
-
-
33747040538
-
Iatrogenic Creutzfeldt-Jakob disease: The waning of an era
-
Brown, P., Brandel, J. P., Preece, M. & Sato, T. (2006). Iatrogenic Creutzfeldt-Jakob disease: the waning of an era. Neurology 67, 389-393.
-
(2006)
Neurology
, vol.67
, pp. 389-393
-
-
Brown, P.1
Brandel, J.P.2
Preece, M.3
Sato, T.4
-
6
-
-
67650747654
-
Getting a grip on prions: Oligomers, amyloids, and pathological membrane interactions
-
Caughey, B., Baron, G. S., Chesebro, B. & Jeffrey, M. (2009). Getting a grip on prions: oligomers, amyloids, and pathological membrane interactions. Annu Rev Biochem 78, 177-204.
-
(2009)
Annu Rev Biochem
, vol.78
, pp. 177-204
-
-
Caughey, B.1
Baron, G.S.2
Chesebro, B.3
Jeffrey, M.4
-
7
-
-
77956270117
-
Superoxide dismutase 1 and tgSOD1 mouse spinal cord seed fibrils, suggesting a propagative cell death mechanism in amyotrophic lateral sclerosis
-
Chia, R., Tattum, M. H., Jones, S., Collinge, J., Fisher, E. M. & Jackson, G. S. (2010). Superoxide dismutase 1 and tgSOD1 mouse spinal cord seed fibrils, suggesting a propagative cell death mechanism in amyotrophic lateral sclerosis. PLoS ONE 5, e10627.
-
(2010)
PLoS ONE
, vol.5
-
-
Chia, R.1
Tattum, M.H.2
Jones, S.3
Collinge, J.4
Fisher, E.M.5
Jackson, G.S.6
-
8
-
-
79951802675
-
Comparison of the level, distribution and form of disease-associated prion protein in variant and sporadic Creutzfeldt-Jakob diseased brain using conformation-dependent immunoassay and Western blot
-
Choi, Y. P., Gröner, A., Ironside, J. W. & Head, M. W. (2011). Comparison of the level, distribution and form of disease-associated prion protein in variant and sporadic Creutzfeldt-Jakob diseased brain using conformation-dependent immunoassay and Western blot. J Gen Virol 92, 727-732.
-
(2011)
J Gen Virol
, vol.92
, pp. 727-732
-
-
Choi, Y.P.1
Gröner, A.2
Ironside, J.W.3
Head, M.W.4
-
9
-
-
38049170554
-
Prion detection by an amyloid seeding assay
-
Colby, D. W., Zhang, Q., Wang, S., Groth, D., Legname, G., Riesner, D. & Prusiner, S. B. (2007). Prion detection by an amyloid seeding assay. Proc Natl Acad Sci U S A 104, 20914-20919.
-
(2007)
Proc Natl Acad Sci U S A
, vol.104
, pp. 20914-20919
-
-
Colby, D.W.1
Zhang, Q.2
Wang, S.3
Groth, D.4
Legname, G.5
Riesner, D.6
Prusiner, S.B.7
-
10
-
-
0141514771
-
Sporadic and familial CJD: Classification and characterisation
-
Gambetti, P., Kong, Q., Zou, W., Parchi, P. & Chen, S. G. (2003). Sporadic and familial CJD: classification and characterisation. Br Med Bull 66, 213-239.
-
(2003)
Br Med Bull
, vol.66
, pp. 213-239
-
-
Gambetti, P.1
Kong, Q.2
Zou, W.3
Parchi, P.4
Chen, S.G.5
-
11
-
-
33748369869
-
Creutzfeldt-Jakob disease and blood transfusion: Results of the UK Transfusion Medicine Epidemiological Review study
-
Hewitt, P. E., Llewelyn, C. A., Mackenzie, J. & Will, R. G. (2006). Creutzfeldt-Jakob disease and blood transfusion: results of the UK Transfusion Medicine Epidemiological Review study. Vox Sang 91, 221-230.
-
(2006)
Vox Sang
, vol.91
, pp. 221-230
-
-
Hewitt, P.E.1
Llewelyn, C.A.2
Mackenzie, J.3
Will, R.G.4
-
12
-
-
31144463958
-
Pathogenesis and prevalence of variant Creutzfeldt-Jakob disease
-
Hilton, D. A. (2006). Pathogenesis and prevalence of variant Creutzfeldt-Jakob disease. J Pathol 208, 134-141.
-
(2006)
J Pathol
, vol.208
, pp. 134-141
-
-
Hilton, D.A.1
-
13
-
-
68149100194
-
Prion diseases
-
8th edn, Edited by S. Love, D. N. Louis & D. W. Ellison. London: Hodder and Arnold
-
Ironside, J. W., Ghetti, B., Head, M. W., Piccardo, P. & Will, R. G. (2008). Prion diseases. In Greenfield's Neuropathology, Vol. 2. 8th edn, pp. 1197-1273. Edited by S. Love, D. N. Louis & D. W. Ellison. London: Hodder and Arnold.
-
(2008)
Greenfield's Neuropathology
, vol.2
, pp. 1197-1273
-
-
Ironside, J.W.1
Ghetti, B.2
Head, M.W.3
Piccardo, P.4
Will, R.G.5
-
14
-
-
34548394607
-
In vitro amplification and detection of variant Creutzfeldt-Jakob disease PrPSc
-
Jones, M., Peden, A. H., Prowse, C. V., Gröner, A., Manson, J. C., Turner, M. L., Ironside, J. W., MacGregor, I. R. & Head, M. W. (2007). In vitro amplification and detection of variant Creutzfeldt-Jakob disease PrPSc. J Pathol 213, 21-26.
-
(2007)
J Pathol
, vol.213
, pp. 21-26
-
-
Jones, M.1
Peden, A.H.2
Prowse, C.V.3
Gröner, A.4
Manson, J.C.5
Turner, M.L.6
Ironside, J.W.7
Macgregor, I.R.8
Head, M.W.9
-
15
-
-
57149144250
-
Effects of human PrPSc type and PRNP genotype in an in-vitro conversion assay
-
Jones, M., Peden, A. H., Wight, D., Prowse, C., Macgregor, I., Manson, J., Turner, M., Ironside, J. W. & Head, M.W. (2008). Effects of human PrPSc type and PRNP genotype in an in-vitro conversion assay. Neuroreport 19, 1783-1786.
-
(2008)
Neuroreport
, vol.19
, pp. 1783-1786
-
-
Jones, M.1
Peden, A.H.2
Wight, D.3
Prowse, C.4
Macgregor, I.5
Manson, J.6
Turner, M.7
Ironside, J.W.8
Head, M.W.9
-
16
-
-
58849146750
-
Human platelets as a substrate source for the in vitro amplification of the abnormal prion protein (PrP) associated with variant Creutzfeldt-Jakob disease
-
Jones, M., Peden, A. H., Yull, H., Wight, D., Bishop, M. T., Prowse, C. V., Turner, M. L., Ironside, J. W., MacGregor, I. R. & Head, M. W. (2009a). Human platelets as a substrate source for the in vitro amplification of the abnormal prion protein (PrP) associated with variant Creutzfeldt-Jakob disease. Transfusion 49, 376-384.
-
(2009)
Transfusion
, vol.49
, pp. 376-384
-
-
Jones, M.1
Peden, A.H.2
Yull, H.3
Wight, D.4
Bishop, M.T.5
Prowse, C.V.6
Turner, M.L.7
Ironside, J.W.8
Macgregor, I.R.9
Head, M.W.10
-
17
-
-
73949119010
-
Molecular model of prion transmission to humans
-
Jones, M., Wight, D., Barron, R., Jeffrey, M., Manson, J., Prowse, C., Ironside, J. W. & Head, M. W. (2009b). Molecular model of prion transmission to humans. Emerg Infect Dis 15, 2013-2016.
-
(2009)
Emerg Infect Dis
, vol.15
, pp. 2013-2016
-
-
Jones, M.1
Wight, D.2
Barron, R.3
Jeffrey, M.4
Manson, J.5
Prowse, C.6
Ironside, J.W.7
Head, M.W.8
-
18
-
-
78651235125
-
The application of in vitro cell-free conversion systems to human prion diseases
-
Jones, M., Peden, A. H., Head, M. W. & Ironside, J. W. (2011). The application of in vitro cell-free conversion systems to human prion diseases. Acta Neuropathol 121, 135-143.
-
(2011)
Acta Neuropathol
, vol.121
, pp. 135-143
-
-
Jones, M.1
Peden, A.H.2
Head, M.W.3
Ironside, J.W.4
-
19
-
-
1142273431
-
Possible transmission of variant Creutzfeldt-Jakob disease by blood transfusion
-
Llewelyn, C. A., Hewitt, P. E., Knight, R. S., Amar, K., Cousens, S., Mackenzie, J. & Will, R. G. (2004). Possible transmission of variant Creutzfeldt-Jakob disease by blood transfusion. Lancet 363, 417-421.
-
(2004)
Lancet
, vol.363
, pp. 417-421
-
-
Llewelyn, C.A.1
Hewitt, P.E.2
Knight, R.S.3
Amar, K.4
Cousens, S.5
Mackenzie, J.6
Will, R.G.7
-
20
-
-
0035902492
-
Probing the mechanism of insulin fibril formation with insulin mutants
-
Nielsen, L., Frokjaer, S., Brange, J., Uversky, V. N. & Fink, A. L. (2001). Probing the mechanism of insulin fibril formation with insulin mutants. Biochemistry 40, 8397-8409.
-
(2001)
Biochemistry
, vol.40
, pp. 8397-8409
-
-
Nielsen, L.1
Frokjaer, S.2
Brange, J.3
Uversky, V.N.4
Fink, A.L.5
-
21
-
-
70349211719
-
Human variant Creutzfeldt-Jakob disease and sheep scrapie PrPres detection using seeded conversion of recombinant prion protein
-
Orrú, C. D., Wilham, J. M., Hughson, A. G., Raymond, L. D., McNally, K. L., Bossers, A., Ligios, C. & Caughey, B. (2009). Human variant Creutzfeldt-Jakob disease and sheep scrapie PrPres detection using seeded conversion of recombinant prion protein. Protein Eng Des Sel 22, 515-521.
-
(2009)
Protein Eng Des Sel
, vol.22
, pp. 515-521
-
-
Orrú, C.D.1
Wilham, J.M.2
Hughson, A.G.3
Raymond, L.D.4
McNally, K.L.5
Bossers, A.6
Ligios, C.7
Caughey, B.8
-
22
-
-
79960163849
-
Prion disease blood test using immunoprecipitation and improved quaking-induced conversion
-
Orrú, C. D., Wilham, J. M., Raymond, L. D., Kuhn, F., Schroeder, B., Raeber, A. J. & Caughey, B. (2011). Prion disease blood test using immunoprecipitation and improved quaking-induced conversion. MBio 2, e00078-11.
-
(2011)
MBio
, vol.2
-
-
Orrú, C.D.1
Wilham, J.M.2
Raymond, L.D.3
Kuhn, F.4
Schroeder, B.5
Raeber, A.J.6
Caughey, B.7
-
23
-
-
0032816292
-
Classification of sporadic Creutzfeldt-Jakob disease based on molecular and phenotypic analysis of 300 subjects
-
Authors other
-
Parchi, P., Giese, A., Capellari, S., Brown, P., Schulz-Schaeffer, W., Windl, O., Zerr, I., Budka, H., Kopp, N. & other authors (1999). Classification of sporadic Creutzfeldt-Jakob disease based on molecular and phenotypic analysis of 300 subjects. Ann Neurol 46, 224-233.
-
(1999)
Ann Neurol
, vol.46
, pp. 224-233
-
-
Parchi, P.1
Giese, A.2
Capellari, S.3
Brown, P.4
Schulz-Schaeffer, W.5
Windl, O.6
Zerr, I.7
Budka, H.8
Kopp, N.9
-
24
-
-
77957660770
-
Agent strain variation in human prion disease: Insights from a molecular and pathological review of the National Institutes of Health series of experimentally transmitted disease
-
Parchi, P., Cescatti, M., Notari, S., Schulz-Schaeffer, W. J., Capellari, S., Giese, A., Zou, W. Q., Kretzschmar, H., Ghetti, B. & Brown, P. (2010). Agent strain variation in human prion disease: insights from a molecular and pathological review of the National Institutes of Health series of experimentally transmitted disease. Brain 133, 3030-3042.
-
(2010)
Brain
, vol.133
, pp. 3030-3042
-
-
Parchi, P.1
Cescatti, M.2
Notari, S.3
Schulz-Schaeffer, W.J.4
Capellari, S.5
Giese, A.6
Zou, W.Q.7
Kretzschmar, H.8
Ghetti, B.9
Brown, P.10
-
25
-
-
4043157677
-
Preclinical vCJD after blood transfusion in a PRNP codon 129 heterozygous patient
-
Peden, A. H., Head, M. W., Ritchie, D. L., Bell, J. E. & Ironside, J. W. (2004). Preclinical vCJD after blood transfusion in a PRNP codon 129 heterozygous patient. Lancet 364, 527-529.
-
(2004)
Lancet
, vol.364
, pp. 527-529
-
-
Peden, A.H.1
Head, M.W.2
Ritchie, D.L.3
Bell, J.E.4
Ironside, J.W.5
-
26
-
-
57149132410
-
Advances in the development of a screening test for variant Creutzfeldt-Jakob disease
-
Peden, A. H., Head, M. W., Jones, M., MacGregor, I. R., Turner, M. L. & Ironside, J. W. (2008). Advances in the development of a screening test for variant Creutzfeldt-Jakob disease. Expert Opin Med Diagn 2, 207-219.
-
(2008)
Expert Opin Med Diagn
, vol.2
, pp. 207-219
-
-
Peden, A.H.1
Head, M.W.2
Jones, M.3
Macgregor, I.R.4
Turner, M.L.5
Ironside, J.W.6
-
27
-
-
77749322732
-
Variant CJD infection in the spleen of a neurologically asymptomatic UK adult patient with haemophilia
-
Peden, A., McCardle, L., Head, M. W., Love, S., Ward, H. J., Cousens, S. N., Keeling, D. M., Millar, C. M., Hill, F. G. & Ironside, J. W. (2010). Variant CJD infection in the spleen of a neurologically asymptomatic UK adult patient with haemophilia. Haemophilia 16, 296-304.
-
(2010)
Haemophilia
, vol.16
, pp. 296-304
-
-
Peden, A.1
McCardle, L.2
Head, M.W.3
Love, S.4
Ward, H.J.5
Cousens, S.N.6
Keeling, D.M.7
Millar, C.M.8
Hill, F.G.9
Ironside, J.W.10
-
29
-
-
0031720905
-
Eight prion strains have PrPSc molecules with different conformations
-
Safar, J., Wille, H., Itri, V., Groth, D., Serban, H., Torchia, M., Cohen, F. E. & Prusiner, S. B. (1998). Eight prion strains have PrPSc molecules with different conformations. Nat Med 4, 1157-1165.
-
(1998)
Nat Med
, vol.4
, pp. 1157-1165
-
-
Safar, J.1
Wille, H.2
Itri, V.3
Groth, D.4
Serban, H.5
Torchia, M.6
Cohen, F.E.7
Prusiner, S.B.8
-
30
-
-
20044383009
-
Diagnosis of human prion disease
-
Authors other
-
Safar, J. G., Geschwind, M. D., Deering, C., Didorenko, S., Sattavat, M., Sanchez, H., Serban, A., Vey, M., Baron, H. & other authors (2005). Diagnosis of human prion disease. Proc Natl Acad Sci U S A 102, 3501-3506.
-
(2005)
Proc Natl Acad Sci U S A
, vol.102
, pp. 3501-3506
-
-
Safar, J.G.1
Geschwind, M.D.2
Deering, C.3
Didorenko, S.4
Sattavat, M.5
Sanchez, H.6
Serban, A.7
Vey, M.8
Baron, H.9
-
31
-
-
24644448839
-
The most infectious prion protein particles
-
Silveira, J. R., Raymond, G. J., Hughson, A. G., Race, R. E., Sim, V. L., Hayes, S. F. & Caughey, B. (2005). The most infectious prion protein particles. Nature 437, 257-261.
-
(2005)
Nature
, vol.437
, pp. 257-261
-
-
Silveira, J.R.1
Raymond, G.J.2
Hughson, A.G.3
Race, R.E.4
Sim, V.L.5
Hayes, S.F.6
Caughey, B.7
-
32
-
-
57449084177
-
An update on the assessment and management of the risk of transmission of variant Creutzfeldt-Jakob disease by blood and plasma products
-
Turner, M. L. & Ludlam, C. A. (2009). An update on the assessment and management of the risk of transmission of variant Creutzfeldt-Jakob disease by blood and plasma products. Br J Haematol 144, 14-23.
-
(2009)
Br J Haematol
, vol.144
, pp. 14-23
-
-
Turner, M.L.1
Ludlam, C.A.2
-
33
-
-
78651249792
-
Rapid end-point quantitation of prion seeding activity with sensitivity comparable to bioassays
-
Wilham, J.M., Orrú, C. D., Bessen, R. A., Atarashi, R., Sano, K., Race, B., Meade-White, K. D., Taubner, L. M., Timmes, A. & Caughey, B. (2010). Rapid end-point quantitation of prion seeding activity with sensitivity comparable to bioassays. PLoS Pathog 6, e1001217.
-
(2010)
PLoS Pathog
, vol.6
-
-
Wilham, J.M.1
Orrú, C.D.2
Bessen, R.A.3
Atarashi, R.4
Sano, K.5
Race, B.6
Meade-White, K.D.7
Taubner, L.M.8
Timmes, A.9
Caughey, B.10
-
34
-
-
77957713851
-
Variant CJD: Where has it gone, or has it?
-
Will, B. (2010). Variant CJD: where has it gone, or has it? Pract Neurol 10, 250-251.
-
(2010)
Pract Neurol
, vol.10
, pp. 250-251
-
-
Will, B.1
-
35
-
-
33845227845
-
Clinical presentation and pre-mortem diagnosis of variant Creutzfeldt-Jakob disease associated with blood transfusion: A case report
-
Authors other
-
Wroe, S. J., Pal, S., Siddique, D., Hyare, H., Macfarlane, R., Joiner, S., Linehan, J. M., Brandner, S., Wadsworth, J. D. & other authors (2006). Clinical presentation and pre-mortem diagnosis of variant Creutzfeldt-Jakob disease associated with blood transfusion: a case report. Lancet 368, 2061-2067.
-
(2006)
Lancet
, vol.368
, pp. 2061-2067
-
-
Wroe, S.J.1
Pal, S.2
Siddique, D.3
Hyare, H.4
Macfarlane, R.5
Joiner, S.6
Linehan, J.M.7
Brandner, S.8
Wadsworth, J.D.9
-
36
-
-
30344438495
-
Detection of type 1 prion protein in variant Creutzfeldt-Jakob disease
-
Yull, H. M., Ritchie, D. L., Langeveld, J. P., van Zijderveld, F. G., Bruce, M. E., Ironside, J. W. & Head, M. W. (2006). Detection of type 1 prion protein in variant Creutzfeldt-Jakob disease. Am J Pathol 168, 151-157.
-
(2006)
Am J Pathol
, vol.168
, pp. 151-157
-
-
Yull, H.M.1
Ritchie, D.L.2
Langeveld, J.P.3
van Zijderveld, F.G.4
Bruce, M.E.5
Ironside, J.W.6
Head, M.W.7
|