Model systems of DUX4 expression recapitulate the transcriptional profile of FSHD cells

Human Molecular Genetics

Volumn 25, Issue 20, 2016, Pages 4419-4431

  Jagannathan, Sujatha ^a   Shadle, Sean C ^b   Resnick, Rebecca ^b   Snider, Lauren ^a   Tawil, Rabi N ^c   van der Maarel, Silvère M ^d   Bradley, Robert K ^a   Tapscott, Stephen J ^a  

^a Fred Hutchinson Cancer Research Center   (United States)

^b UNIVERSITY OF WASHINGTON   (United States)

^c UNIVERSITY OF ROCHESTER MEDICAL CENTER   (United States)

^d LEIDEN UNIVERSITY MEDICAL CENTER   (Netherlands)

Author keywords

[No Author keywords available]

Indexed keywords

DOXYCYCLINE; PUROMYCIN; RNA; TRANSCRIPTION FACTOR; TRANSCRIPTION FACTOR DUX4; UNCLASSIFIED DRUG; DUX4 PROTEIN, HUMAN; HOMEODOMAIN PROTEIN; TRANSCRIPTOME;

ARTICLE; CELL DIFFERENTIATION; CLONAL CELL LINE; CODON; CONTROLLED STUDY; CORRELATIONAL STUDY; EXTRACELLULAR MATRIX; FACIOSCAPULOHUMERAL MUSCULAR DYSTROPHY; GENE EXPRESSION; GENE INDUCTION; GENE SILENCING; HUMAN; HUMAN CELL; INNATE IMMUNITY; MUSCLE CELL; MUSCLE DEVELOPMENT; MUSCLE FUNCTION; MYOBLAST; PATHOPHYSIOLOGY; POLYADENYLATION; PRIORITY JOURNAL; PROTEIN EXPRESSION; RNA EXTRACTION; RNA SEQUENCE; SKELETAL MUSCLE CELL; BIOLOGICAL MODEL; CELL CULTURE; GENE EXPRESSION PROFILING; GENE EXPRESSION REGULATION; GENETICS; METABOLISM; MUTATION; SEQUENCE ANALYSIS;

CELLS, CULTURED; GENE EXPRESSION PROFILING; GENE EXPRESSION REGULATION; HOMEODOMAIN PROTEINS; HUMANS; MODELS, BIOLOGICAL; MUSCLE FIBERS, SKELETAL; MUSCULAR DYSTROPHY, FACIOSCAPULOHUMERAL; MUTATION; MYOBLASTS; SEQUENCE ANALYSIS, RNA; TRANSCRIPTOME;

EID: 85002032285     PISSN: 09646906     EISSN: 14602083     Source Type: Journal    
DOI: 10.1093/hmg/ddw271     Document Type: Article

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