An isogenetic myoblast expression screen identifies DUX4-mediated FSHD-associated molecular pathologies

EMBO Journal

Volumn 27, Issue 20, 2008, Pages 2766-2779

  Bosnakovski, Darko ^a   Xu, Zhaohui ^b   Ji Gang, Eun ^b   Galindo, Cristi L ^b   Liu, Mingju ^b   Simsek, Tugba ^b   Garner, Harold R ^b   Agha Mohammadi, Siamak ^c   Tassin, Alexandra ^d   Coppée, Frédérique ^d   Belayew, Alexandra ^d   Perlingeiro, Rita R ^a   Kyba, Michael ^a  

^a UNIVERSITY OF MINNESOTA MEDICAL SCHOOL   (United States)

^b UNIVERSITY OF TEXAS SOUTHWESTERN MEDICAL CENTER   (United States)

^c UNIVERSITY OF PITTSBURGH SCHOOL OF MEDICINE   (United States)

^d UNIVERSITY OF MONS   (Belgium)

Author keywords

Cassette exchange; DUX4; Facioscapulohumeral muscular dystrophy; Myoblast

Indexed keywords

HOMEODOMAIN PROTEIN; MYOD PROTEIN; PROTEIN DUX4; TRANSCRIPTION FACTOR PAX3; TRANSCRIPTION FACTOR PAX4; UNCLASSIFIED DRUG;

ARTICLE; CONTROLLED STUDY; FASCIOSCAPULOHUMERAL MUSCULAR DYSTROPHY; GENE DELETION; GENE EXPRESSION; GENETIC ANALYSIS; MUSCULAR DYSTROPHY; MYOBLAST; NONHUMAN; PHENOTYPE; PRIORITY JOURNAL;

ANIMALS; CELL DIFFERENTIATION; CLONING, MOLECULAR; GENE DELETION; GENE EXPRESSION REGULATION; GLUTATHIONE; HOMEODOMAIN PROTEINS; MICE; MUSCULAR DYSTROPHY, FACIOSCAPULOHUMERAL; MYOBLASTS; OXIDATION-REDUCTION; PAIRED BOX TRANSCRIPTION FACTORS; PAX7 TRANSCRIPTION FACTOR; PHENOTYPE; TRANSGENES;

EID: 54349088194     PISSN: 02614189     EISSN: 14602075     Source Type: Journal    
DOI: 10.1038/emboj.2008.201     Document Type: Article

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