Molecular insights into cell toxicity of a novel familial amyloidogenic variant of β2-microglobulin

Journal of Cellular and Molecular Medicine

Volumn 20, Issue 8, 2016, Pages 1443-1456

  Leri, Manuela ^a   Bemporad, Francesco ^a   Oropesa Nuñez, Reinier ^b   Canale, Claudio ^b   Calamai, Martino ^c,d   Nosi, Daniele ^a   Ramazzotti, Matteo ^a   Giorgetti, Sofia ^e   Pavone, Francesco S ^c   Bellotti, Vittorio ^e,f   Stefani, Massimo ^a,g   Bucciantini, Monica ^a,g  

^a UNIVERSITY OF FLORENCE   (Italy)

^b ISTITUTO ITALIANO DI TECNOLOGIA   (Italy)

^c UNIVERSITY OF FLORENCE   (Italy)

^d ISTITUTO NAZIONALE DI OTTICA   (Italy)

^e UNIVERSITY OF PAVIA   (Italy)

^f UNIVERSITY COLLEGE LONDON   (United Kingdom)

^g Centro Interuniversitario per lo Studio delle Malattie Neurodegenerative (CIMN)   (Italy)

Author keywords

amyloid cytotoxicity; GM1 ganglioside; membrane bilayers; protein misfolding; systemic amyloidosis

Indexed keywords

AMYLOID PROTEIN; BETA 2 MICROGLOBULIN; CONGO RED; GANGLIOSIDE GM1; QUANTUM DOT; REACTIVE OXYGEN METABOLITE; THIOFLAVINE;

AMYLOIDOSIS; ARTICLE; CELL DEATH; CELL VIABILITY; CIRCULAR DICHROISM; CYTOTOXICITY; DIFFUSION COEFFICIENT; ELASTICITY; HUMAN; HUMAN CELL; IMMUNOFLUORESCENCE; LIGHT SCATTERING; LIPID VESICLE; PRIORITY JOURNAL; PROTEIN FOLDING; QUANTITATIVE ANALYSIS; T CELL DEPLETION; TRANSMISSION ELECTRON MICROSCOPY;

EID: 84979086201     PISSN: 15821838     EISSN: None     Source Type: Journal    
DOI: 10.1111/jcmm.12833     Document Type: Article

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