Autophagy modulators regulate survival motor neuron protein stability in motoneurons

Experimental Neurology

Volumn 283, Issue , 2016, Pages 287-297

  Periyakaruppiah, Ambika ^a   de la Fuente, Sandra ^a   Arumugam, Saravanan ^a   Bahí, Núria ^a   Garcera, Ana ^a   Soler, Rosa M ^a  

^a UNIVERSITY OF LLEIDA   (Spain)

Author keywords

Autophagosome; Autophagy; Calpain; Motoneuron; Rapamycin; Spinal Muscular Atrophy; Survival motor neuron

Indexed keywords

PROTEIN LC3 II; SURVIVAL MOTOR NEURON PROTEIN; UNCLASSIFIED DRUG; BAFILOMYCIN A1; ENZYME INHIBITOR; MACROLIDE; NERVE GROWTH FACTOR; NERVE PROTEIN; SEQUESTOSOME 1; SMN1 PROTEIN, MOUSE; SMN2 PROTEIN, HUMAN; SQSTM1 PROTEIN, HUMAN; SURVIVAL MOTOR NEURON PROTEIN 1; SURVIVAL MOTOR NEURON PROTEIN 2;

ANIMAL CELL; ANIMAL EXPERIMENT; ANIMAL MODEL; ARTICLE; AUTOPHAGOSOME; AUTOPHAGY; CONTROLLED STUDY; DEREGULATION; DEVELOPMENTAL STAGE; DISEASE COURSE; DISEASE SEVERITY; EMBRYO; IN VITRO STUDY; MOTONEURON; MOUSE; NONHUMAN; PRIORITY JOURNAL; PROTEIN STABILITY; SPINAL CORD; SPINAL MUSCULAR ATROPHY; ANIMAL; CELL CULTURE; CELL SURVIVAL; CYTOLOGY; DISEASE MODEL; DRUG EFFECTS; GENE EXPRESSION REGULATION; GENETICS; GROWTH, DEVELOPMENT AND AGING; MAMMALIAN EMBRYO; METABOLISM; NEWBORN; PATHOLOGY; PHYSIOLOGY; TRANSGENIC MOUSE; ULTRASTRUCTURE;

ANIMALS; ANIMALS, NEWBORN; AUTOPHAGY; CELL SURVIVAL; CELLS, CULTURED; DISEASE MODELS, ANIMAL; EMBRYO, MAMMALIAN; ENZYME INHIBITORS; GENE EXPRESSION REGULATION, DEVELOPMENTAL; MACROLIDES; MICE; MICE, TRANSGENIC; MOTOR NEURONS; MUSCULAR ATROPHY, SPINAL; NERVE GROWTH FACTORS; NERVE TISSUE PROTEINS; SEQUESTOSOME-1 PROTEIN; SPINAL CORD; SURVIVAL OF MOTOR NEURON 1 PROTEIN; SURVIVAL OF MOTOR NEURON 2 PROTEIN;

EID: 84977123691     PISSN: 00144886     EISSN: 10902430     Source Type: Journal    
DOI: 10.1016/j.expneurol.2016.06.032     Document Type: Article

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