-
2
-
-
84907971646
-
Recent advances in the management of cystic fibrosis
-
2 Davies, J.C., Ebdon, A.M., Orchard, C., Recent advances in the management of cystic fibrosis. Arch Dis Child 99 (2014), 1033–1036.
-
(2014)
Arch Dis Child
, vol.99
, pp. 1033-1036
-
-
Davies, J.C.1
Ebdon, A.M.2
Orchard, C.3
-
3
-
-
84959465154
-
UK Cystic Fibrosis Registry 2014 Annual Data Report
-
The Cystic Fibrosis Trust UK
-
3 Siobhan, C., Rebecca, C., Vian, R.H., UK Cystic Fibrosis Registry 2014 Annual Data Report., 2015, The Cystic Fibrosis Trust, UK.
-
(2015)
-
-
Siobhan, C.1
Rebecca, C.2
Vian, R.H.3
-
4
-
-
84859620802
-
Cystic fibrosis: a mucosal immunodeficiency syndrome
-
4 Cohen, T.S., Prince, A., Cystic fibrosis: a mucosal immunodeficiency syndrome. Nat Med 18 (2012), 509–519.
-
(2012)
Nat Med
, vol.18
, pp. 509-519
-
-
Cohen, T.S.1
Prince, A.2
-
5
-
-
84880046935
-
Early lung disease in cystic fibrosis
-
5 Grasemann, H., Ratjen, F., Early lung disease in cystic fibrosis. Lancet Respir Med 1 (2013), 148–157.
-
(2013)
Lancet Respir Med
, vol.1
, pp. 148-157
-
-
Grasemann, H.1
Ratjen, F.2
-
6
-
-
84902602970
-
Multi-country estimate of different manifestations of aspergillosis in cystic fibrosis
-
6 Armstead, J., Morris, J., Denning, D.W., Multi-country estimate of different manifestations of aspergillosis in cystic fibrosis. PLoS One, 9, 2014, e98502.
-
(2014)
PLoS One
, vol.9
, pp. e98502
-
-
Armstead, J.1
Morris, J.2
Denning, D.W.3
-
7
-
-
84856793307
-
Cystic fibrosis transmembrane conductance regulator regulates epithelial cell response to Aspergillus and resultant pulmonary inflammation
-
7 Chaudhary, N., Datta, K., Askin, F.B., Staab, J.F., Marr, K.A., Cystic fibrosis transmembrane conductance regulator regulates epithelial cell response to Aspergillus and resultant pulmonary inflammation. Am J Respir Crit Care Med 185 (2012), 301–310.
-
(2012)
Am J Respir Crit Care Med
, vol.185
, pp. 301-310
-
-
Chaudhary, N.1
Datta, K.2
Askin, F.B.3
Staab, J.F.4
Marr, K.A.5
-
8
-
-
84894094805
-
Pretransplant Aspergillus colonization of cystic fibrosis patients and the incidence of post-lung transplant invasive aspergillosis
-
8 Luong, M.L., Chaparro, C., Stephenson, A., Rotstein, C., Singer, L.G., Waters, V., et al. Pretransplant Aspergillus colonization of cystic fibrosis patients and the incidence of post-lung transplant invasive aspergillosis. Transplantion 97 (2014), 351–357.
-
(2014)
Transplantion
, vol.97
, pp. 351-357
-
-
Luong, M.L.1
Chaparro, C.2
Stephenson, A.3
Rotstein, C.4
Singer, L.G.5
Waters, V.6
-
9
-
-
34548452140
-
Post-operative infections in cystic fibrosis and non-cystic fibrosis patients after lung transplantation
-
9 Bonvillain, R.W., Valentine, V.G., Lombard, G., LaPlace, S., Dhillon, G., Wang, G., Post-operative infections in cystic fibrosis and non-cystic fibrosis patients after lung transplantation. J Heart Lung Transp 26 (2007), 890–897.
-
(2007)
J Heart Lung Transp
, vol.26
, pp. 890-897
-
-
Bonvillain, R.W.1
Valentine, V.G.2
Lombard, G.3
LaPlace, S.4
Dhillon, G.5
Wang, G.6
-
10
-
-
67449104896
-
Occurrence and relevance of filamentous fungi in respiratory secretions of patients with cystic fibrosis–a review
-
10 Pihet, M., Carrere, J., Cimon, B., Chabasse, D., Delhaes, L., Symoens, F., et al. Occurrence and relevance of filamentous fungi in respiratory secretions of patients with cystic fibrosis–a review. Med Mycol 47 (2009), 387–397.
-
(2009)
Med Mycol
, vol.47
, pp. 387-397
-
-
Pihet, M.1
Carrere, J.2
Cimon, B.3
Chabasse, D.4
Delhaes, L.5
Symoens, F.6
-
11
-
-
84876985774
-
What is the clinical significance of filamentous fungi positive sputum cultures in patients with cystic fibrosis?
-
11 Liu, J.C., Modha, D.E., Gaillard, E.A., What is the clinical significance of filamentous fungi positive sputum cultures in patients with cystic fibrosis?. J Cyst Fibros 12 (2013), 187–193.
-
(2013)
J Cyst Fibros
, vol.12
, pp. 187-193
-
-
Liu, J.C.1
Modha, D.E.2
Gaillard, E.A.3
-
12
-
-
0032916340
-
Aspergillus fumigatus and aspergillosis
-
12 Latge, J.P., Aspergillus fumigatus and aspergillosis. Clin Microbiol Rev 12 (1999), 310–350.
-
(1999)
Clin Microbiol Rev
, vol.12
, pp. 310-350
-
-
Latge, J.P.1
-
13
-
-
84867033879
-
Effects of Aspergillus fumigatus colonization on lung function in cystic fibrosis
-
13 Speirs, J.J., van der Ent, C.K., Beekman, J.M., Effects of Aspergillus fumigatus colonization on lung function in cystic fibrosis. Curr Opin Pulm Med 18 (2012), 632–638.
-
(2012)
Curr Opin Pulm Med
, vol.18
, pp. 632-638
-
-
Speirs, J.J.1
van der Ent, C.K.2
Beekman, J.M.3
-
14
-
-
84901641154
-
Fungi in the cystic fibrosis lung: bystanders or pathogens?
-
14 Chotirmally, S.H., McElavaney, N.G., Fungi in the cystic fibrosis lung: bystanders or pathogens?. Int J Biochem Cell Biol 52 (2014), 161–173.
-
(2014)
Int J Biochem Cell Biol
, vol.52
, pp. 161-173
-
-
Chotirmally, S.H.1
McElavaney, N.G.2
-
15
-
-
33746324245
-
Aspergillus bronchitis in cystic fibrosis
-
15 Shoseyov, D., Brownlee, K.G., Conway, S.P., Kerem, E., Aspergillus bronchitis in cystic fibrosis. Chest 130 (2006), 222–226.
-
(2006)
Chest
, vol.130
, pp. 222-226
-
-
Shoseyov, D.1
Brownlee, K.G.2
Conway, S.P.3
Kerem, E.4
-
16
-
-
84883228378
-
Novel immunologic classification of aspergillosis in adult cystic fibrosis
-
16 Baxter, C.G., Dunn, G., Jones, A.M., Webb, K., Gore, R., Richardson, M.D., et al. Novel immunologic classification of aspergillosis in adult cystic fibrosis. J Allergy Clin Immunol 132 (2013), 560–566.
-
(2013)
J Allergy Clin Immunol
, vol.132
, pp. 560-566
-
-
Baxter, C.G.1
Dunn, G.2
Jones, A.M.3
Webb, K.4
Gore, R.5
Richardson, M.D.6
-
17
-
-
84881021238
-
Allergic bronchopulmonary aspergillosis: review of literature and proposal of new diagnostic and classification criteria
-
17 Agarwal, R., Chakrabarti, A., Shah, A., Gupta, D., Meis, J.F., Guleria, R., et al. Allergic bronchopulmonary aspergillosis: review of literature and proposal of new diagnostic and classification criteria. Clin Exp Allergy 43 (2013), 850–873.
-
(2013)
Clin Exp Allergy
, vol.43
, pp. 850-873
-
-
Agarwal, R.1
Chakrabarti, A.2
Shah, A.3
Gupta, D.4
Meis, J.F.5
Guleria, R.6
-
18
-
-
0029928073
-
Clinical significance of the recovery of Aspergillus species from the respiratory secretions of cystic fibrosis patients
-
18 Milla, C.E., Wielinski, C.L., Regelmann, W.E., Clinical significance of the recovery of Aspergillus species from the respiratory secretions of cystic fibrosis patients. Pediatr Pulmonol 21 (1996), 6–10.
-
(1996)
Pediatr Pulmonol
, vol.21
, pp. 6-10
-
-
Milla, C.E.1
Wielinski, C.L.2
Regelmann, W.E.3
-
19
-
-
84856968847
-
Radiological abnormalities associated with Aspergillus colonization in a cystic fibrosis population
-
19 McMahon, M.A., Chotirmall, S.H., McCullagh, B., Branagan, P., McElvaney, N.G., Logan, P.M., Radiological abnormalities associated with Aspergillus colonization in a cystic fibrosis population. Eur J Radiol 81 (2012), e197–202.
-
(2012)
Eur J Radiol
, vol.81
, pp. e197-202
-
-
McMahon, M.A.1
Chotirmall, S.H.2
McCullagh, B.3
Branagan, P.4
McElvaney, N.G.5
Logan, P.M.6
-
20
-
-
79957529529
-
Aspergillus fumigatus colonization in cystic fibrosis: implications for lung function?
-
20 de Vrankrijker, A.M., van der Ent, C.K., van Berkhout, F.T., Stellato, R.K., Willems, R.J., Bonten, M.J., et al. Aspergillus fumigatus colonization in cystic fibrosis: implications for lung function?. Clin Microbiol Infect 17 (2011), 1381–1386.
-
(2011)
Clin Microbiol Infect
, vol.17
, pp. 1381-1386
-
-
de Vrankrijker, A.M.1
van der Ent, C.K.2
van Berkhout, F.T.3
Stellato, R.K.4
Willems, R.J.5
Bonten, M.J.6
-
21
-
-
77956111173
-
Risk factors for Aspergillus colonization and allergic bronchopulmonary aspergillosis in children with cystic fibrosis
-
21 Jubin, V., Ranque, S., Stremler le Bel, N., Sarles, J., Dubus, J.C., Risk factors for Aspergillus colonization and allergic bronchopulmonary aspergillosis in children with cystic fibrosis. Pediatr Pulmonol 45 (2010), 764–771.
-
(2010)
Pediatr Pulmonol
, vol.45
, pp. 764-771
-
-
Jubin, V.1
Ranque, S.2
Stremler le Bel, N.3
Sarles, J.4
Dubus, J.C.5
-
22
-
-
74949096500
-
The effect of chronic infection with Aspergillus fumigatus on lung function and hospitalization in patients with cystic fibrosis
-
22 Amin, R., Dupuis, A., Aaron, S.D., Ratjen, F., The effect of chronic infection with Aspergillus fumigatus on lung function and hospitalization in patients with cystic fibrosis. Chest 137 (2010), 171–176.
-
(2010)
Chest
, vol.137
, pp. 171-176
-
-
Amin, R.1
Dupuis, A.2
Aaron, S.D.3
Ratjen, F.4
-
23
-
-
78649943740
-
Lack of standardization in the procedures for mycological examination of sputum samples from CF patients: a possible cause for variations in the prevalence of filamentous fungi
-
23 Borman, A.M., Palmer, M.D., Delhaes, L., Carrere, J., Favennec, L., Ranque, S., et al. Lack of standardization in the procedures for mycological examination of sputum samples from CF patients: a possible cause for variations in the prevalence of filamentous fungi. Med Mycol 48 (2010), S88–S97.
-
(2010)
Med Mycol
, vol.48
, pp. S88-S97
-
-
Borman, A.M.1
Palmer, M.D.2
Delhaes, L.3
Carrere, J.4
Favennec, L.5
Ranque, S.6
-
24
-
-
84929340326
-
Lung microbiota across age and disease stage in cystic fibrosis
-
24 Coburn, B., Wang, P.W., Diaz Caballero, J., Clark, S.T., Brahma, V., Donaldson, S., et al. Lung microbiota across age and disease stage in cystic fibrosis. Sci Rep, 5, 2015, 10241.
-
(2015)
Sci Rep
, vol.5
, pp. 10241
-
-
Coburn, B.1
Wang, P.W.2
Diaz Caballero, J.3
Clark, S.T.4
Brahma, V.5
Donaldson, S.6
-
25
-
-
0028077051
-
Development of immune responses to Aspergillus at an early age in children with cystic fibrosis
-
25 El-Dahr, J.M., Fink, R., Selden, R., Arruda, L.K., Platts-Mills, T.A., Heymann, P.W., Development of immune responses to Aspergillus at an early age in children with cystic fibrosis. Am J Respir Crit Care Med 150 (1994), 1513–1518.
-
(1994)
Am J Respir Crit Care Med
, vol.150
, pp. 1513-1518
-
-
El-Dahr, J.M.1
Fink, R.2
Selden, R.3
Arruda, L.K.4
Platts-Mills, T.A.5
Heymann, P.W.6
-
26
-
-
84902550971
-
Aspergillus sensitization or carriage in cystic fibrosis patients
-
26 Fillaux, J., Bremont, F., Murris, M., Cassaing, S., Tetu, L., Segonds, C., et al. Aspergillus sensitization or carriage in cystic fibrosis patients. Pediatr Infect Dis J 33 (2014), 680–686.
-
(2014)
Pediatr Infect Dis J
, vol.33
, pp. 680-686
-
-
Fillaux, J.1
Bremont, F.2
Murris, M.3
Cassaing, S.4
Tetu, L.5
Segonds, C.6
-
27
-
-
0035076336
-
Molecular epidemiology of airway colonisation by Aspergillus fumigatus in cystic fibrosis patients
-
27 Cimon, B., Symoens, F., Zouhair, R., Chabasse, D., Nolard, N., Defontaine, A., et al. Molecular epidemiology of airway colonisation by Aspergillus fumigatus in cystic fibrosis patients. J Med Microbiol 50 (2001), 367–374.
-
(2001)
J Med Microbiol
, vol.50
, pp. 367-374
-
-
Cimon, B.1
Symoens, F.2
Zouhair, R.3
Chabasse, D.4
Nolard, N.5
Defontaine, A.6
-
28
-
-
84860484915
-
The airway microbiota in cystic fibrosis: a complex fungal and bacterial community–implications for therapeutic management
-
28 Delhaes, L., Monchy, S., Frealle, E., Hubans, C., Salleron, J., Leroy, S., et al. The airway microbiota in cystic fibrosis: a complex fungal and bacterial community–implications for therapeutic management. PLoS One, 7, 2012, e36313.
-
(2012)
PLoS One
, vol.7
, pp. e36313
-
-
Delhaes, L.1
Monchy, S.2
Frealle, E.3
Hubans, C.4
Salleron, J.5
Leroy, S.6
-
29
-
-
80052014087
-
Inflammatory responses to individual microorganisms in the lungs of children with cystic fibrosis
-
29 Gangell, C., Gard, S., Douglas, T., Park, J., de Klerk, N., Keil, T., et al. Inflammatory responses to individual microorganisms in the lungs of children with cystic fibrosis. Clin Infect Dis 53 (2011), 425–432.
-
(2011)
Clin Infect Dis
, vol.53
, pp. 425-432
-
-
Gangell, C.1
Gard, S.2
Douglas, T.3
Park, J.4
de Klerk, N.5
Keil, T.6
-
30
-
-
34247161953
-
Neutrophilic inflammation as a major determinant in the progression of cystic fibrosis
-
30 Tirouvanziam, R., Neutrophilic inflammation as a major determinant in the progression of cystic fibrosis. Drug News Perspect 19 (2006), 609–614.
-
(2006)
Drug News Perspect
, vol.19
, pp. 609-614
-
-
Tirouvanziam, R.1
-
31
-
-
80051572617
-
Infection, inflammation, and lung function decline in infants with cystic fibrosis
-
31 Pillarisetti, N., Williamson, E., Linnane, B., Skoric, B., Robertson, C.F., Robinson, P., et al. Infection, inflammation, and lung function decline in infants with cystic fibrosis. Am J Respir Crit Care Med 184 (2011), 75–81.
-
(2011)
Am J Respir Crit Care Med
, vol.184
, pp. 75-81
-
-
Pillarisetti, N.1
Williamson, E.2
Linnane, B.3
Skoric, B.4
Robertson, C.F.5
Robinson, P.6
-
32
-
-
84860456588
-
Treatment of Aspergillus fumigatus in patients with cystic fibrosis: a randomized, placebo-controlled pilot study
-
32 Aaron, S.D., Vandemheen, K.L., Freitag, A., Pedder, L., Camerom, W., Lavoie, A., et al. Treatment of Aspergillus fumigatus in patients with cystic fibrosis: a randomized, placebo-controlled pilot study. PLoS One, 7, 2012, e36077.
-
(2012)
PLoS One
, vol.7
, pp. e36077
-
-
Aaron, S.D.1
Vandemheen, K.L.2
Freitag, A.3
Pedder, L.4
Camerom, W.5
Lavoie, A.6
-
33
-
-
84870889954
-
Aspergillus bronchitis without significant immunocompromise
-
33 Chrdle, A., Mustakim, S., Bright-Thomas, R.J., Baxter, C.G., Felton, T., Denning, D.W., Aspergillus bronchitis without significant immunocompromise. Ann N Y Acad Sci 1272 (2012), 73–85.
-
(2012)
Ann N Y Acad Sci
, vol.1272
, pp. 73-85
-
-
Chrdle, A.1
Mustakim, S.2
Bright-Thomas, R.J.3
Baxter, C.G.4
Felton, T.5
Denning, D.W.6
-
34
-
-
0033806235
-
Allergic bronchopulmonary aspergillosis in cystic fibrosis. A European epidemiological study. Epidemiologic Registry of Cystic Fibrosis
-
34 Mastella, G., Rainisio, M., Harms, H.K., Hodson, M.E., Koch, C., Navarro, J., et al. Allergic bronchopulmonary aspergillosis in cystic fibrosis. A European epidemiological study. Epidemiologic Registry of Cystic Fibrosis. Eur Respir J 16 (2000), 464–471.
-
(2000)
Eur Respir J
, vol.16
, pp. 464-471
-
-
Mastella, G.1
Rainisio, M.2
Harms, H.K.3
Hodson, M.E.4
Koch, C.5
Navarro, J.6
-
35
-
-
59349114291
-
Diagnosing allergic bronchopulmonary aspergillosis in children with cystic fibrosis
-
35 Thia, L.P., Balfour Lynn, I.M., Diagnosing allergic bronchopulmonary aspergillosis in children with cystic fibrosis. Paediatr Respir Rev 10 (2009), 37–42.
-
(2009)
Paediatr Respir Rev
, vol.10
, pp. 37-42
-
-
Thia, L.P.1
Balfour Lynn, I.M.2
-
36
-
-
84947433926
-
Prevalence of Aspergillus sensitization and allergic bronchopulmonary aspergillosis in cystic fibrosis: systematic review and meta-analysis
-
36 Maturu, V.N., Agarwal, R., Prevalence of Aspergillus sensitization and allergic bronchopulmonary aspergillosis in cystic fibrosis: systematic review and meta-analysis. Clin Exp Allergy 45 (2015), 1765–1778.
-
(2015)
Clin Exp Allergy
, vol.45
, pp. 1765-1778
-
-
Maturu, V.N.1
Agarwal, R.2
-
37
-
-
84867780388
-
Assessment of Aspergillus sensitization or persistent carriage as a factor in lung function impairment in cystic fibrosis patients
-
37 Fillaux, J., Bremont, F., Murris, M., Cassaing, S., Rittie, J.L., Tetu, L., et al. Assessment of Aspergillus sensitization or persistent carriage as a factor in lung function impairment in cystic fibrosis patients. Scand J Infect Dis 44 (2012), 842–847.
-
(2012)
Scand J Infect Dis
, vol.44
, pp. 842-847
-
-
Fillaux, J.1
Bremont, F.2
Murris, M.3
Cassaing, S.4
Rittie, J.L.5
Tetu, L.6
-
38
-
-
0030919614
-
Sensitization to Aspergillus fumigatus and lung function in children with cystic fibrosis
-
38 Wojnarowski, C., Eichler, I., Fartner, C., Götz, M., Renner, S., Koller, D.Y., et al. Sensitization to Aspergillus fumigatus and lung function in children with cystic fibrosis. Am J Respir Crit Care Med 155 (1997), 1902–1907.
-
(1997)
Am J Respir Crit Care Med
, vol.155
, pp. 1902-1907
-
-
Wojnarowski, C.1
Eichler, I.2
Fartner, C.3
Götz, M.4
Renner, S.5
Koller, D.Y.6
-
39
-
-
33845542156
-
Effect of allergic bronchopulmonary aspergillosis on lung function in children with cystic fibrosis
-
39 Kraemer, R., Delosea, N., Ballinari, P., Gallati, S., Crameri, R., Effect of allergic bronchopulmonary aspergillosis on lung function in children with cystic fibrosis. Am J Respir Crit Care Med 174 (2006), 1211–1220.
-
(2006)
Am J Respir Crit Care Med
, vol.174
, pp. 1211-1220
-
-
Kraemer, R.1
Delosea, N.2
Ballinari, P.3
Gallati, S.4
Crameri, R.5
-
40
-
-
32244443965
-
Allergic bronchopulmonary aspergillosis in paediatric cystic fibrosis patients
-
40 de Almeida, M.B., Bussamra, M.H., Rodrigues, J.C., Allergic bronchopulmonary aspergillosis in paediatric cystic fibrosis patients. Paediatr Respir Rev 7 (2006), 67–72.
-
(2006)
Paediatr Respir Rev
, vol.7
, pp. 67-72
-
-
de Almeida, M.B.1
Bussamra, M.H.2
Rodrigues, J.C.3
-
41
-
-
77958113699
-
Allergic bronchopulmonary aspergillosis and Aspergillus infection in cystic fibrosis
-
41 Moss, R.B., Allergic bronchopulmonary aspergillosis and Aspergillus infection in cystic fibrosis. Curr Opin Pulm Med 16 (2010), 598–603.
-
(2010)
Curr Opin Pulm Med
, vol.16
, pp. 598-603
-
-
Moss, R.B.1
-
42
-
-
84964313843
-
Antifungal therapies for allergic bronchopulmonary aspergillosis in people with cystic fibrosis
-
42 Elphick, H.E., Southern, K.W., Antifungal therapies for allergic bronchopulmonary aspergillosis in people with cystic fibrosis. Cochrane Database Syst Rev, 11, 2014, CD002204.
-
(2014)
Cochrane Database Syst Rev
, vol.11
, pp. CD002204
-
-
Elphick, H.E.1
Southern, K.W.2
-
43
-
-
84906254100
-
Antifungal treatment in allergic bronchopulmonary aspergillosis with and without cystic fibrosis: a systematic review
-
43 Moreira, A.S., Silva, D., Ferreira, A.R., Delgado, L., Antifungal treatment in allergic bronchopulmonary aspergillosis with and without cystic fibrosis: a systematic review. Clin Exp Allergy 44 (2014), 1210–1227.
-
(2014)
Clin Exp Allergy
, vol.44
, pp. 1210-1227
-
-
Moreira, A.S.1
Silva, D.2
Ferreira, A.R.3
Delgado, L.4
-
44
-
-
29544437697
-
Voriconazole therapy in children with cystic fibrosis
-
44 Hilliard, T., Edwards, S., Buchdahl, R., Francis, J., Rosenthal, M., Balfour-Lynn, I., et al. Voriconazole therapy in children with cystic fibrosis. J Cyst Fibros 4 (2005), 215–220.
-
(2005)
J Cyst Fibros
, vol.4
, pp. 215-220
-
-
Hilliard, T.1
Edwards, S.2
Buchdahl, R.3
Francis, J.4
Rosenthal, M.5
Balfour-Lynn, I.6
-
45
-
-
84863307371
-
The oral corticosteroid-sparing effect of omalizumab in children with severe asthma
-
45 Brodlie, M., McKean, M.C., Moss, S., Spencer, D.A., The oral corticosteroid-sparing effect of omalizumab in children with severe asthma. Arch Dis Child 97 (2012), 604–609.
-
(2012)
Arch Dis Child
, vol.97
, pp. 604-609
-
-
Brodlie, M.1
McKean, M.C.2
Moss, S.3
Spencer, D.A.4
-
46
-
-
84898600933
-
Omalizumab therapy for allergic bronchopulmonary aspergillosis in children with cystic fibrosis: a synthesis of published evidence
-
46 Tanou, K., Zintzaras, E., Kaditis, A.G., Omalizumab therapy for allergic bronchopulmonary aspergillosis in children with cystic fibrosis: a synthesis of published evidence. Pediatr Pulmonol 49 (2014), 503–507.
-
(2014)
Pediatr Pulmonol
, vol.49
, pp. 503-507
-
-
Tanou, K.1
Zintzaras, E.2
Kaditis, A.G.3
-
47
-
-
0029758131
-
A 12-year longitudinal study of Aspergillus sensitivity in patients with cystic fibrosis
-
47 Hutcheson, P.S., Knutsen, A.P., Rejent, A.J., Slavin, R.G., A 12-year longitudinal study of Aspergillus sensitivity in patients with cystic fibrosis. Chest 110 (1996), 363–366.
-
(1996)
Chest
, vol.110
, pp. 363-366
-
-
Hutcheson, P.S.1
Knutsen, A.P.2
Rejent, A.J.3
Slavin, R.G.4
-
48
-
-
84878668026
-
Immune response, diagnosis and treatment of allergic bronchopulmonary aspergillosis in cystic fibrosis lung disease
-
48 Eickmeier, O., Rieber, N., Eckrich, J., Hector, A., Graeppler-Mainka, U., Hartl, D., Immune response, diagnosis and treatment of allergic bronchopulmonary aspergillosis in cystic fibrosis lung disease. Curr Pharm Des 19 (2013), 3669–3678.
-
(2013)
Curr Pharm Des
, vol.19
, pp. 3669-3678
-
-
Eickmeier, O.1
Rieber, N.2
Eckrich, J.3
Hector, A.4
Graeppler-Mainka, U.5
Hartl, D.6
-
49
-
-
84876802220
-
Cystic fibrosis transmembrane conductance regulator recruitment to phagosomes in neutrophils
-
49 Zhou, Y., Song, K., Painter, R.G., Aiken, M., Reiser, J., Stanton, B.A., et al. Cystic fibrosis transmembrane conductance regulator recruitment to phagosomes in neutrophils. J Innate Imm 5 (2013), 219–230.
-
(2013)
J Innate Imm
, vol.5
, pp. 219-230
-
-
Zhou, Y.1
Song, K.2
Painter, R.G.3
Aiken, M.4
Reiser, J.5
Stanton, B.A.6
-
50
-
-
84903119926
-
Detection of CFTR protein in human leukocytes by flow cytometry
-
50 Johansson, J., Vezzalini, M., Verze, G., Caldrer, S., Bolognin, S., Buffelli, M., et al. Detection of CFTR protein in human leukocytes by flow cytometry. Cytom A 85 (2014), 611–620.
-
(2014)
Cytom A
, vol.85
, pp. 611-620
-
-
Johansson, J.1
Vezzalini, M.2
Verze, G.3
Caldrer, S.4
Bolognin, S.5
Buffelli, M.6
-
51
-
-
84901631277
-
Current concepts of immune dysregulation in cystic fibrosis
-
51 Rieber, N., Hector, A., Carevic, M., Hartl, D., Current concepts of immune dysregulation in cystic fibrosis. Int J Biochem Cell Biol 52 (2014), 108–112.
-
(2014)
Int J Biochem Cell Biol
, vol.52
, pp. 108-112
-
-
Rieber, N.1
Hector, A.2
Carevic, M.3
Hartl, D.4
-
52
-
-
84861780622
-
Immune responses in cystic fibrosis: are they intrinsically defective?
-
52 Ratner, D., Mueller, C., Immune responses in cystic fibrosis: are they intrinsically defective?. Am J Respir Cell Mol Biol 46 (2012), 715–722.
-
(2012)
Am J Respir Cell Mol Biol
, vol.46
, pp. 715-722
-
-
Ratner, D.1
Mueller, C.2
-
53
-
-
34347396792
-
Is cystic fibrosis a TH17 disease?
-
53 Dubin, P.J., McAllister, F., Kolls, J.K., Is cystic fibrosis a TH17 disease?. Inflamm Res 56 (2007), 221–227.
-
(2007)
Inflamm Res
, vol.56
, pp. 221-227
-
-
Dubin, P.J.1
McAllister, F.2
Kolls, J.K.3
-
54
-
-
0031035884
-
Nasal and bronchoalveolar lavage fluid cytokines in early cystic fibrosis
-
54 Noah, T.L., Black, H.R., Cheng, P.W., Wood, R.E., Leigh, M.W., Nasal and bronchoalveolar lavage fluid cytokines in early cystic fibrosis. J Infect Dis 175 (1997), 638–647.
-
(1997)
J Infect Dis
, vol.175
, pp. 638-647
-
-
Noah, T.L.1
Black, H.R.2
Cheng, P.W.3
Wood, R.E.4
Leigh, M.W.5
-
55
-
-
0032770489
-
Quantitation of inflammatory responses to bacteria in young cystic fibrosis and control patients
-
55 Muhlebach, M.S., Stewart, P.W., Leigh, M.W., Noah, T.L., Quantitation of inflammatory responses to bacteria in young cystic fibrosis and control patients. Am J Respir Crit Care Med 160 (1999), 186–191.
-
(1999)
Am J Respir Crit Care Med
, vol.160
, pp. 186-191
-
-
Muhlebach, M.S.1
Stewart, P.W.2
Leigh, M.W.3
Noah, T.L.4
-
56
-
-
0028784322
-
Inflammatory cytokines in cystic fibrosis lungs
-
56 Bonfield, T.L., Panuska, J.R., Konstan, M.W., Hilliard, K.A., Hilliard, J.B., Ghnaim, H., et al. Inflammatory cytokines in cystic fibrosis lungs. Am J Respir Crit Care Med 152 (1995), 2111–2118.
-
(1995)
Am J Respir Crit Care Med
, vol.152
, pp. 2111-2118
-
-
Bonfield, T.L.1
Panuska, J.R.2
Konstan, M.W.3
Hilliard, K.A.4
Hilliard, J.B.5
Ghnaim, H.6
-
57
-
-
0028914085
-
Early pulmonary inflammation in infants with cystic fibrosis
-
57 Khan, T.Z., Wagener, J.S., Bost, T., Martinez, J., Accurso, F.J., Riches, D.W., Early pulmonary inflammation in infants with cystic fibrosis. Am J Respir Crit Care Med 151 (1995), 1075–1082.
-
(1995)
Am J Respir Crit Care Med
, vol.151
, pp. 1075-1082
-
-
Khan, T.Z.1
Wagener, J.S.2
Bost, T.3
Martinez, J.4
Accurso, F.J.5
Riches, D.W.6
-
58
-
-
45949103092
-
The role of chloride anion and CFTR in killing of Pseudomonas aeruginosa by normal and CF neutrophils
-
58 Painter, R.G., Bonvillain, R.W., Valentine, V.G., Lombard, G.A., LaPlace, S.G., Nauseef, W.M., et al. The role of chloride anion and CFTR in killing of Pseudomonas aeruginosa by normal and CF neutrophils. J Leuk Biol 83 (2008), 1345–1353.
-
(2008)
J Leuk Biol
, vol.83
, pp. 1345-1353
-
-
Painter, R.G.1
Bonvillain, R.W.2
Valentine, V.G.3
Lombard, G.A.4
LaPlace, S.G.5
Nauseef, W.M.6
-
59
-
-
79956194922
-
Dysfunctional CFTR alters the bactericidal activity of human macrophages against Pseudomonas aeruginosa
-
59 Del Porto, P., Cifani, N., Guarnieri, S., Di Domenico, E.G., Mariggiò, M.A., Spadaro, F., et al. Dysfunctional CFTR alters the bactericidal activity of human macrophages against Pseudomonas aeruginosa. PLoS One, 6, 2011, e19970.
-
(2011)
PLoS One
, vol.6
, pp. e19970
-
-
Del Porto, P.1
Cifani, N.2
Guarnieri, S.3
Di Domenico, E.G.4
Mariggiò, M.A.5
Spadaro, F.6
-
60
-
-
79959572825
-
Abnormal trafficking and degradation of TLR4 underlie the elevated inflammatory response in cystic fibrosis
-
60 Bruscia, E.M., Zhang, P.X., Satoh, A., Caputo, C., Medzhitov, R., Shenoy, A., et al. Abnormal trafficking and degradation of TLR4 underlie the elevated inflammatory response in cystic fibrosis. J Immunol 186 (2011), 6990–6998.
-
(2011)
J Immunol
, vol.186
, pp. 6990-6998
-
-
Bruscia, E.M.1
Zhang, P.X.2
Satoh, A.3
Caputo, C.4
Medzhitov, R.5
Shenoy, A.6
-
61
-
-
80051554943
-
Lack of cystic fibrosis transmembrane conductance regulator in CD3+ lymphocytes leads to aberrant cytokine secretion and hyperinflammatory adaptive immune responses
-
61 Mueller, C., Braag, S.A., Keeler, A., Hodges, C., Drumm, M., Flotte, T.R., Lack of cystic fibrosis transmembrane conductance regulator in CD3+ lymphocytes leads to aberrant cytokine secretion and hyperinflammatory adaptive immune responses. Am J Respir Cell Mol Bio 44 (2011), 922–929.
-
(2011)
Am J Respir Cell Mol Bio
, vol.44
, pp. 922-929
-
-
Mueller, C.1
Braag, S.A.2
Keeler, A.3
Hodges, C.4
Drumm, M.5
Flotte, T.R.6
-
62
-
-
73249114731
-
Rescue of CF airway epithelial cell function in vitro by a CFTR potentiator, VX-770
-
62 Van Goor, F., Hadida, S., Grootenhuis, P.D., Burton, B., Cao, D., Neuberger, T., et al. Rescue of CF airway epithelial cell function in vitro by a CFTR potentiator, VX-770. Proc Natl Acad Sci USA 106 (2009), 18825–18830.
-
(2009)
Proc Natl Acad Sci USA
, vol.106
, pp. 18825-18830
-
-
Van Goor, F.1
Hadida, S.2
Grootenhuis, P.D.3
Burton, B.4
Cao, D.5
Neuberger, T.6
-
63
-
-
80455162465
-
A CFTR potentiator in patients with cystic fibrosis and the G551D mutation
-
63 Ramsey, B.W., Davies, J., McElvaney, N.G., Tullis, E., Bell, S.C., Drevinek, P., et al. A CFTR potentiator in patients with cystic fibrosis and the G551D mutation. N Engl J Med 365 (2011), 1663–1672.
-
(2011)
N Engl J Med
, vol.365
, pp. 1663-1672
-
-
Ramsey, B.W.1
Davies, J.2
McElvaney, N.G.3
Tullis, E.4
Bell, S.C.5
Drevinek, P.6
-
64
-
-
84878970875
-
Efficacy and safety of ivacaftor in patients aged 6 to 11 years with cystic fibrosis with a G551D mutation
-
64 Davies, J.C., Wainwright, C.E., Canny, G.J., Chilvers, M.A., Howenstine, M.S., Munck, A., et al. Efficacy and safety of ivacaftor in patients aged 6 to 11 years with cystic fibrosis with a G551D mutation. Am J Respir Crit Care Med 187 (2013), 1219–1225.
-
(2013)
Am J Respir Crit Care Med
, vol.187
, pp. 1219-1225
-
-
Davies, J.C.1
Wainwright, C.E.2
Canny, G.J.3
Chilvers, M.A.4
Howenstine, M.S.5
Munck, A.6
-
65
-
-
84935511737
-
Pseudomonas aeruginosa in cystic fibrosis patients with G551D-CFTR treated with ivacaftor
-
65 Heltshe, S.L., Mayer-Hamblett, N., Burns, J.L., Khan, U., Baines, A., Ramsey, B.W., et al. Pseudomonas aeruginosa in cystic fibrosis patients with G551D-CFTR treated with ivacaftor. Clin Infect Dis 60 (2015), 703–712.
-
(2015)
Clin Infect Dis
, vol.60
, pp. 703-712
-
-
Heltshe, S.L.1
Mayer-Hamblett, N.2
Burns, J.L.3
Khan, U.4
Baines, A.5
Ramsey, B.W.6
-
66
-
-
84905992903
-
A neutrophil intrinsic impairment affecting Rab27a and degranulation in cystic fibrosis is corrected by CFTR potentiator therapy
-
66 Pohl, K., Hayes, E., Keenan, J., Henry, M., Meleady, P., Molloy, K., et al. A neutrophil intrinsic impairment affecting Rab27a and degranulation in cystic fibrosis is corrected by CFTR potentiator therapy. Blood 124 (2014), 999–1009.
-
(2014)
Blood
, vol.124
, pp. 999-1009
-
-
Pohl, K.1
Hayes, E.2
Keenan, J.3
Henry, M.4
Meleady, P.5
Molloy, K.6
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