-
3
-
-
42049099020
-
Physiology of the prion protein
-
Linden R, Martins VR, Prado MA, Cammarota M, Izquierdo I, Brentani RR. Physiology of the prion protein. Physiol Rev 2008;88:673-728.
-
(2008)
Physiol Rev
, vol.88
, pp. 673-728
-
-
Linden, R.1
Martins, V.R.2
Prado, M.A.3
Cammarota, M.4
Izquierdo, I.5
Brentani, R.R.6
-
4
-
-
74249118091
-
Is indeed, the prion protein a harlequin servant of "many" masters?
-
Sorgato MC, Peggion C, Bertoli A. Is, indeed, the prion protein a harlequin servant of "many" masters? Prion 2009;3:202-205.
-
(2009)
Prion
, vol.3
, pp. 202-205
-
-
Sorgato, M.C.1
Peggion, C.2
Bertoli, A.3
-
5
-
-
61349201380
-
Cellular prion protein mediates impairment of synaptic plasticity by amyloid-beta oligomers
-
Laurén J, Gimbel DA, Nygaard HB, Gilbert JW, Strittmatter SM. Cellular prion protein mediates impairment of synaptic plasticity by amyloid-beta oligomers. Nature 2009;457:1128-1132.
-
(2009)
Nature
, vol.457
, pp. 1128-1132
-
-
Laurén, J.1
Gimbel, D.A.2
Nygaard, H.B.3
Gilbert, J.W.4
Strittmatter, S.M.5
-
6
-
-
0026600865
-
Normal development and behaviour of mice lacking the neuronal cell-surface PrP protein
-
Büeler H, Fischer M, Lang Y, Bluethmann H, Lipp HP, DeArmond S, et al. Normal development and behaviour of mice lacking the neuronal cell-surface PrP protein. Nature 1992;356:577-582.
-
(1992)
Nature
, vol.356
, pp. 577-582
-
-
Büeler, H.1
Fischer, M.2
Lang, Y.3
Bluethmann, H.4
Lipp, H.P.5
DeArmond, S.6
-
7
-
-
0028420937
-
129/Ola mice carrying a null mutation in PrP that abolishes mRNA production are developmentally normal
-
Manson JC, Clarke AR, Hooper ML, Aitchison L, McConnell I, Hope J. 129/Ola mice carrying a null mutation in PrP that abolishes mRNA production are developmentally normal. Mol Neurobiol 1994;8:121-127.
-
(1994)
Mol Neurobiol
, vol.8
, pp. 121-127
-
-
Manson, J.C.1
Clarke, A.R.2
Hooper, M.L.3
Aitchison, L.4
McConnell, I.5
Hope, J.6
-
8
-
-
0036470471
-
Post-natal knockout of prion protein alters hippocampal CA1 properties, but does not result in neurodegeneration
-
Mallucci GR, Ratté S, Asante EA, Linehan J, Gowland I, Jefferys JG, et al. Post-natal knockout of prion protein alters hippocampal CA1 properties, but does not result in neurodegeneration. EMBO J 2002;21:202-210.
-
(2002)
EMBO J
, vol.21
, pp. 202-210
-
-
Mallucci, G.R.1
Ratté, S.2
Asante, E.A.3
Linehan, J.4
Gowland, I.5
Jefferys, J.G.6
-
9
-
-
3042594982
-
Prion protein accumulation and neuroprotection in hypoxic brain damage
-
McLennan NF, Brennan PM, McNeill A, Davies I, Fotheringham A, Rennison KA, et al. Prion protein accumulation and neuroprotection in hypoxic brain damage. Am J Pathol 2004;165:227-235.
-
(2004)
Am J Pathol
, vol.165
, pp. 227-235
-
-
McLennan, N.F.1
Brennan, P.M.2
McNeill, A.3
Davies, I.4
Fotheringham, A.5
Rennison, K.A.6
-
10
-
-
26944462341
-
Aggravation of ischemic brain injury by prion protein deficiency: role of ERK-1/-2 and STAT-1
-
Spudich A, Frigg R, Kilic E, Kilic U, Oesch B, Raeber A, et al. Aggravation of ischemic brain injury by prion protein deficiency: role of ERK-1/-2 and STAT-1. Neurobiol Dis 2005;20:442-449.
-
(2005)
Neurobiol Dis
, vol.20
, pp. 442-449
-
-
Spudich, A.1
Frigg, R.2
Kilic, E.3
Kilic, U.4
Oesch, B.5
Raeber, A.6
-
11
-
-
33646695909
-
Deletion of cellular prion protein results in reduced Akt activation, enhanced postischemic caspasi-3 activation, and exacerbation of ischemic brain injury
-
Weise J, Sandau R, Schwarting S, Crome O, Wrede A, Schulz-Schaeffer W, et al. Deletion of cellular prion protein results in reduced Akt activation, enhanced postischemic caspasi-3 activation, and exacerbation of ischemic brain injury. Stroke 2006;37:1296-1300.
-
(2006)
Stroke
, vol.37
, pp. 1296-1300
-
-
Weise, J.1
Sandau, R.2
Schwarting, S.3
Crome, O.4
Wrede, A.5
Schulz-Schaeffer, W.6
-
12
-
-
0042200243
-
Cellular prion protein ablation impairs behavior as a function of age
-
Coitinho AS, Roesler R, Martins VR, Brentani RR, Izquierdo I. Cellular prion protein ablation impairs behavior as a function of age. NeuroReport 2003;14:1375-1379.
-
(2003)
NeuroReport
, vol.14
, pp. 1375-1379
-
-
Coitinho, A.S.1
Roesler, R.2
Martins, V.R.3
Brentani, R.R.4
Izquierdo, I.5
-
13
-
-
34249947609
-
Motor behavioral and neuropathological deficits in mice deficient for normal prion protein expression
-
Nazor KE, Seward T, Telling GC. Motor behavioral and neuropathological deficits in mice deficient for normal prion protein expression. Biochim Biophys Acta 2007;1772:645-653.
-
(2007)
Biochim Biophys Acta
, vol.1772
, pp. 645-653
-
-
Nazor, K.E.1
Seward, T.2
Telling, G.C.3
-
14
-
-
70350619619
-
Cellular prion protein modulates age-related behavioral and neurochemical alterations in mice
-
Rial D, Duarte FS, Xikota JC, Schmitz AE, Dafrè AL, Figueiredo CP, et al. Cellular prion protein modulates age-related behavioral and neurochemical alterations in mice. Neuroscience 2009;164:896-907.
-
(2009)
Neuroscience
, vol.164
, pp. 896-907
-
-
Rial, D.1
Duarte, F.S.2
Xikota, J.C.3
Schmitz, A.E.4
Dafrè, A.L.5
Figueiredo, C.P.6
-
15
-
-
77649091387
-
Axonal prion protein is required for peripheral myelin maintenance
-
Bremer J, Baumann F, Tiberi C, Wessig C, Fischer H, Schwarz P, et al. Axonal prion protein is required for peripheral myelin maintenance. Nat Neurosci 2010;13:310-318.
-
(2010)
Nat Neurosci
, vol.13
, pp. 310-318
-
-
Bremer, J.1
Baumann, F.2
Tiberi, C.3
Wessig, C.4
Fischer, H.5
Schwarz, P.6
-
16
-
-
84879731350
-
Altered behavioral aspects of aged mice lacking the cellular prion protein
-
Massimino ML, Redaelli M, Bertoli A, Sorgato MC, Mucignat-Caretta C. Altered behavioral aspects of aged mice lacking the cellular prion protein. Physiol Behav 2013;119:86-91.
-
(2013)
Physiol Behav
, vol.119
, pp. 86-91
-
-
Massimino, M.L.1
Redaelli, M.2
Bertoli, A.3
Sorgato, M.C.4
Mucignat-Caretta, C.5
-
17
-
-
20444462264
-
Altered behavioural response to acute stress in mice lacking cellular prion protein
-
Nico PB, de-Paris F, Vinadé ER, Amaral OB, Rockenbach I, Soares BL, et al. Altered behavioural response to acute stress in mice lacking cellular prion protein. Behav Brain Res 2005;162:173-181.
-
(2005)
Behav Brain Res
, vol.162
, pp. 173-181
-
-
Nico, P.B.1
de-Paris, F.2
Vinadé, E.R.3
Amaral, O.B.4
Rockenbach, I.5
Soares, B.L.6
-
18
-
-
0037242707
-
Embryonic activation and developmental expression of the murine prion protein gene
-
Miele G, Alejo Blanco AR, Baybutt H, Horvat S, Manson J, Clinton M. Embryonic activation and developmental expression of the murine prion protein gene. Gene Expr 2003;11:1-12.
-
(2003)
Gene Expr
, vol.11
, pp. 1-12
-
-
Miele, G.1
Alejo Blanco, A.R.2
Baybutt, H.3
Horvat, S.4
Manson, J.5
Clinton, M.6
-
20
-
-
78049403334
-
Cellular prion protein promotes regeneration of adult muscle tissue
-
Stella R, Massimino ML, Sandri M, Sorgato MC, Bertoli A. Cellular prion protein promotes regeneration of adult muscle tissue. Mol Cell Biol 2010;30:4864-4876.
-
(2010)
Mol Cell Biol
, vol.30
, pp. 4864-4876
-
-
Stella, R.1
Massimino, M.L.2
Sandri, M.3
Sorgato, M.C.4
Bertoli, A.5
-
21
-
-
0035873869
-
Imbalance of antioxidant defense in mice lacking cellular prion protein
-
Klamt F, Dal-Pizzol F, Conte da Frota MJ, Walz R, Andrades ME, da Silva EG, et al. Imbalance of antioxidant defense in mice lacking cellular prion protein. Free Radic Biol Med 2001;30:1137-1144.
-
(2001)
Free Radic Biol Med
, vol.30
, pp. 1137-1144
-
-
Klamt, F.1
Dal-Pizzol, F.2
Conte da Frota, M.J.3
Walz, R.4
Andrades, M.E.5
da Silva, E.G.6
-
22
-
-
84913525146
-
The cellular prion protein counteracts cardiac oxidative stress
-
Zanetti F, Carpi A, Menabò R, Giorgio M, Schulz R, Valen G, et al. The cellular prion protein counteracts cardiac oxidative stress. Cardiovasc Res 2014;104:93-102.
-
(2014)
Cardiovasc Res
, vol.104
, pp. 93-102
-
-
Zanetti, F.1
Carpi, A.2
Menabò, R.3
Giorgio, M.4
Schulz, R.5
Valen, G.6
-
23
-
-
0035095576
-
Increased expression of the normal cellular isoform of prion protein in inclusion-body myositis, inflammatory myopathies and denervation atrophy
-
Zanusso G, Vattemi G, Ferrari S, Tabaton M, Pecini E, Cavallaro T, et al. Increased expression of the normal cellular isoform of prion protein in inclusion-body myositis, inflammatory myopathies and denervation atrophy. Brain Pathol 2001;11:182-189.
-
(2001)
Brain Pathol
, vol.11
, pp. 182-189
-
-
Zanusso, G.1
Vattemi, G.2
Ferrari, S.3
Tabaton, M.4
Pecini, E.5
Cavallaro, T.6
-
24
-
-
0034810216
-
Three mouse models of muscular dystrophy: the natural history of strength and fatigue in dystrophin-, dystrophin/utrophin-, and laminin alpha2-deficient mice
-
Connolly AM, Keeling RM, Mehta S, Pestronk A, Sanes JR. Three mouse models of muscular dystrophy: the natural history of strength and fatigue in dystrophin-, dystrophin/utrophin-, and laminin alpha2-deficient mice. Neuromuscul Disord 2001;11:703-712.
-
(2001)
Neuromuscul Disord
, vol.11
, pp. 703-712
-
-
Connolly, A.M.1
Keeling, R.M.2
Mehta, S.3
Pestronk, A.4
Sanes, J.R.5
-
25
-
-
56049126195
-
Akt activation prevents the force drop induced by eccentric contractions in dystrophin-deficient skeletal muscle
-
Blaauw B, Mammucari C, Toniolo L, Agatea L, Abraham R, Sandri M, et al. Akt activation prevents the force drop induced by eccentric contractions in dystrophin-deficient skeletal muscle. Hum Mol Genet 2008;17:3686-3696.
-
(2008)
Hum Mol Genet
, vol.17
, pp. 3686-3696
-
-
Blaauw, B.1
Mammucari, C.2
Toniolo, L.3
Agatea, L.4
Abraham, R.5
Sandri, M.6
-
26
-
-
0027452352
-
Electrophoretic separation of rat skeletal muscle myosin heavy-chain isoforms
-
Talmadge RJ, Roy RR. Electrophoretic separation of rat skeletal muscle myosin heavy-chain isoforms. J Appl Physiol 1993;75:2337-2340.
-
(1993)
J Appl Physiol
, vol.75
, pp. 2337-2340
-
-
Talmadge, R.J.1
Roy, R.R.2
-
27
-
-
69449101150
-
Loss of positive allosteric interactions between neuronal nitric oxide synthase and phosphofructokinase contributes to defects in glycolysis and increased fatigability in muscular dystrophy
-
Wehling-Henricks M1, Oltmann M, Rinaldi C, Myung KH, Tidball JG. Loss of positive allosteric interactions between neuronal nitric oxide synthase and phosphofructokinase contributes to defects in glycolysis and increased fatigability in muscular dystrophy. Hum Mol Genet 2009;18:3439-3451.
-
(2009)
Hum Mol Genet
, vol.18
, pp. 3439-3451
-
-
Wehling-Henricks, M.1
Oltmann, M.2
Rinaldi, C.3
Myung, K.H.4
Tidball, J.G.5
-
28
-
-
84899532964
-
Collagen VI regulates peripheral nerve myelination and function
-
Chen P, Cescon M, Megighian A, Bonaldo P. Collagen VI regulates peripheral nerve myelination and function. FASEB J 2014;28:1145-1156.
-
(2014)
FASEB J
, vol.28
, pp. 1145-1156
-
-
Chen, P.1
Cescon, M.2
Megighian, A.3
Bonaldo, P.4
-
29
-
-
84893366563
-
Long-term measurement of muscle denervation and locomotor behavior in individual wild-type and ALS model mice
-
Akay T. Long-term measurement of muscle denervation and locomotor behavior in individual wild-type and ALS model mice. J Neurophysiol 2014;111:694-703.
-
(2014)
J Neurophysiol
, vol.111
, pp. 694-703
-
-
Akay, T.1
-
30
-
-
5044236743
-
Early abnormalities in sciatic nerve function and structure in a rat model of Charcot-Marie-Tooth type 1A disease
-
Grandis M, Leandri M, Vigo T, Cilli M, Sereda MW, Gherardi G, et al. Early abnormalities in sciatic nerve function and structure in a rat model of Charcot-Marie-Tooth type 1A disease. Exp Neurol 2004;190:213-223.
-
(2004)
Exp Neurol
, vol.190
, pp. 213-223
-
-
Grandis, M.1
Leandri, M.2
Vigo, T.3
Cilli, M.4
Sereda, M.W.5
Gherardi, G.6
-
31
-
-
0031935916
-
Determination of muscle contractile properties: the importance of the nerve
-
Gundersen K. Determination of muscle contractile properties: the importance of the nerve. Acta Physiol Scand 1998;162:333-341.
-
(1998)
Acta Physiol Scand
, vol.162
, pp. 333-341
-
-
Gundersen, K.1
-
32
-
-
0032806450
-
Increased sensitivity to seizures in mice lacking cellular prion protein
-
Walz R, Amaral OB, Rockenbach IC, Roesler R, Izquierdo I, Cavalheiro EA, et al. Increased sensitivity to seizures in mice lacking cellular prion protein. Epilepsia 1999;40:1679-1682.
-
(1999)
Epilepsia
, vol.40
, pp. 1679-1682
-
-
Walz, R.1
Amaral, O.B.2
Rockenbach, I.C.3
Roesler, R.4
Izquierdo, I.5
Cavalheiro, E.A.6
-
33
-
-
1442328250
-
Prions prevent brain damage after experimental brain injury: a preliminary report
-
Hoshino S, Inoue K, Yokoyama T, Kobayashi S, Asakura T, Teramoto A, et al. Prions prevent brain damage after experimental brain injury: a preliminary report. Acta Neurochir Suppl 2003;86:297-299.
-
(2003)
Acta Neurochir Suppl
, vol.86
, pp. 297-299
-
-
Hoshino, S.1
Inoue, K.2
Yokoyama, T.3
Kobayashi, S.4
Asakura, T.5
Teramoto, A.6
-
34
-
-
80052995726
-
Prion protein expression and functional importance in skeletal muscle
-
Smith JD, Moylan JS, Hardin BJ, Chambers MA, Estus S, Telling GC, et al. Prion protein expression and functional importance in skeletal muscle. Antioxid Redox Signal 2011;15:2465-2475.
-
(2011)
Antioxid Redox Signal
, vol.15
, pp. 2465-2475
-
-
Smith, J.D.1
Moylan, J.S.2
Hardin, B.J.3
Chambers, M.A.4
Estus, S.5
Telling, G.C.6
-
35
-
-
0033554306
-
Overview of hereditary neuropathy with liability to pressure palsies
-
Chance PF. Overview of hereditary neuropathy with liability to pressure palsies. Ann NY Acad Sci 1999;883:14-21.
-
(1999)
Ann NY Acad Sci
, vol.883
, pp. 14-21
-
-
Chance, P.F.1
-
36
-
-
0031952546
-
Charcot-Marie-Tooth disease: histopathological features of the peripheral myelin protein (PMP22) duplication (CMT1A) and connexin32 mutations (CMTX1)
-
Sander S, Nicholson GA, Ouvrier RA, McLeod JG, Pollard JD. Charcot-Marie-Tooth disease: histopathological features of the peripheral myelin protein (PMP22) duplication (CMT1A) and connexin32 mutations (CMTX1). Muscle Nerve 1998;21:217-225.
-
(1998)
Muscle Nerve
, vol.21
, pp. 217-225
-
-
Sander, S.1
Nicholson, G.A.2
Ouvrier, R.A.3
McLeod, J.G.4
Pollard, J.D.5
-
37
-
-
16044362374
-
Clinical phenotypes of different MPZ (P0) mutations may include Charcot-Marie-Tooth type 1B, Dejerine-Sottas, and congenital hypomyelination
-
Warner LE, Hilz MJ, Appel SH, Killian JM, Kolodry EH, Karpati G, et al. Clinical phenotypes of different MPZ (P0) mutations may include Charcot-Marie-Tooth type 1B, Dejerine-Sottas, and congenital hypomyelination. Neuron 1996;17:451-460.
-
(1996)
Neuron
, vol.17
, pp. 451-460
-
-
Warner, L.E.1
Hilz, M.J.2
Appel, S.H.3
Killian, J.M.4
Kolodry, E.H.5
Karpati, G.6
-
38
-
-
0036501313
-
Late onset neurological phenotype of the X-ALD gene inactivation in mice: a mouse model for adrenomyeloneuropathy
-
Pujol A, Hindelang C, Callizot N, Bartsch U, Schachner M, Mandel JL. Late onset neurological phenotype of the X-ALD gene inactivation in mice: a mouse model for adrenomyeloneuropathy. Hum Mol Genet 2002;11:499-505.
-
(2002)
Hum Mol Genet
, vol.11
, pp. 499-505
-
-
Pujol, A.1
Hindelang, C.2
Callizot, N.3
Bartsch, U.4
Schachner, M.5
Mandel, J.L.6
-
39
-
-
84870050389
-
Fatigue in immune-mediated neuropathies
-
Merkies IS, Faber CG. Fatigue in immune-mediated neuropathies. Neuromuscul Disord 2012;22(suppl):S203-207.
-
(2012)
Neuromuscul Disord
, vol.22
, pp. S203-S207
-
-
Merkies, I.S.1
Faber, C.G.2
-
40
-
-
84870015962
-
Exploring the experience of fatigue in people with Charcot-Marie-Tooth disease
-
Ramdharry GM, Thornhill A, Mein G, Reilly MM, Marsden JF. Exploring the experience of fatigue in people with Charcot-Marie-Tooth disease. Neuromuscul Disord 2012;22(suppl):S208-213.
-
(2012)
Neuromuscul Disord
, vol.22
, pp. S208-S213
-
-
Ramdharry, G.M.1
Thornhill, A.2
Mein, G.3
Reilly, M.M.4
Marsden, J.F.5
-
41
-
-
80054760368
-
Fiber types in mammalian skeletal muscles
-
Schiaffino S, Reggiani C. Fiber types in mammalian skeletal muscles. Physiol Rev 2011;91:1447-1531.
-
(2011)
Physiol Rev
, vol.91
, pp. 1447-1531
-
-
Schiaffino, S.1
Reggiani, C.2
-
42
-
-
0020541649
-
Adaptation of human skeletal muscle to endurance training of long duration
-
Schantz P, Henriksson J, Jansson E. Adaptation of human skeletal muscle to endurance training of long duration. Clin Physiol 1983;3:141-151.
-
(1983)
Clin Physiol
, vol.3
, pp. 141-151
-
-
Schantz, P.1
Henriksson, J.2
Jansson, E.3
-
43
-
-
0032527977
-
Fast to slow transformation of denervated and electrically stimulated rat muscle
-
Windisch A1, Gundersen K, Szabolcs MJ, Gruber H, Lømo T. Fast to slow transformation of denervated and electrically stimulated rat muscle. J Physiol 1998;510:623-632.
-
(1998)
J Physiol
, vol.510
, pp. 623-632
-
-
Windisch, A.1
Gundersen, K.2
Szabolcs, M.J.3
Gruber, H.4
Lømo, T.5
-
44
-
-
0026607308
-
Myosin heavy chain isoform transition in ageing fast and slow muscles of the rat
-
Sugiura T, Matoba H, Miyata H, Kawai Y, Murakami N. Myosin heavy chain isoform transition in ageing fast and slow muscles of the rat. Acta Physiol Scand 1992;144:419-423.
-
(1992)
Acta Physiol Scand
, vol.144
, pp. 419-423
-
-
Sugiura, T.1
Matoba, H.2
Miyata, H.3
Kawai, Y.4
Murakami, N.5
-
45
-
-
56749177201
-
Nerve-dependent changes in skeletal muscle myosin heavy chain after experimental denervation and cross-reinnervation and in a demyelinating mouse model of Charcot-Marie-Tooth disease type 1A
-
Maggs AM, Huxley C, Hughes SM. Nerve-dependent changes in skeletal muscle myosin heavy chain after experimental denervation and cross-reinnervation and in a demyelinating mouse model of Charcot-Marie-Tooth disease type 1A. Muscle Nerve 2008;38:1572-1584.
-
(2008)
Muscle Nerve
, vol.38
, pp. 1572-1584
-
-
Maggs, A.M.1
Huxley, C.2
Hughes, S.M.3
-
46
-
-
0025380083
-
Evidences for slow to fast changes in the contractile proteins of rat soleus muscle after hindlimb suspension: studies on skinned fibers
-
Stevens L, Mounier Y. Evidences for slow to fast changes in the contractile proteins of rat soleus muscle after hindlimb suspension: studies on skinned fibers. Physiologist 1990;33(suppl):S90-91.
-
(1990)
Physiologist
, vol.33
, pp. S90-S91
-
-
Stevens, L.1
Mounier, Y.2
-
47
-
-
0343133874
-
Changes in muscle strength, muscle fibre size and myofibrillar gene expression after immobilization and retraining in humans
-
Hortobágyi T, Dempsey L, Fraser D, Zheng D, Hamilton G, Lambert J, et al. Changes in muscle strength, muscle fibre size and myofibrillar gene expression after immobilization and retraining in humans. J Physiol 2000;524:293-304.
-
(2000)
J Physiol
, vol.524
, pp. 293-304
-
-
Hortobágyi, T.1
Dempsey, L.2
Fraser, D.3
Zheng, D.4
Hamilton, G.5
Lambert, J.6
|