In Vitro and In Vivo Modeling of Spinal and Bulbar Muscular Atrophy

Journal of Molecular Neuroscience

Volumn 58, Issue 3, 2016, Pages 365-373

  Pennuto, Maria ^a   Basso, Manuela ^a  

^a UNIVERSITY OF TRENTO   (Italy)

Author keywords

Androgen receptor; Cell models; Knock in mice; Mouse models; Muscle cells; Neuronal cells; Spinal and bulbar muscular atrophy; Transgenic mice

Indexed keywords

POLYGLUTAMINE; ANDROGEN RECEPTOR; PEPTIDE;

FRUIT FLY MODEL; HUMAN; IN VITRO STUDY; IN VIVO STUDY; KENNEDY DISEASE; MOTONEURON; NONHUMAN; PC12 CELL LINE; REVIEW; TRANSGENIC MOUSE; ANIMAL; DISEASE MODEL; FEMALE; GENETICS; MALE; METABOLISM; PATHOLOGY; PRIMARY CELL CULTURE; PROCEDURES; TRINUCLEOTIDE REPEAT;

ANIMALS; BULBO-SPINAL ATROPHY, X-LINKED; DISEASE MODELS, ANIMAL; FEMALE; HUMANS; MALE; PEPTIDES; PRIMARY CELL CULTURE; RECEPTORS, ANDROGEN; TRINUCLEOTIDE REPEAT EXPANSION;

EID: 84961168768     PISSN: 08958696     EISSN: 15591166     Source Type: Journal    
DOI: 10.1007/s12031-015-0677-4     Document Type: Review

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