Thioethers as markers of hydrogen sulfide production in homocystinurias

Biochimie

Volumn 126, Issue , 2016, Pages 14-20

  Kožich, Viktor ^a   Krijt, Jakub ^a   Sokolová, Jitka ^a   Melenovská, Petra ^a   Ješina, Pavel ^a   Vozdek, Roman ^a,c   Majtán, Tomáš ^b   Kraus, Jan P ^b  

^a Charles University in Prague and General University Hospital in Prague   (Czech Republic)

^b University of Colorado Denver and Children s Hospital Colorado   (United States)

^c UNIVERSITY OF CALIFORNIA   (United States)

Author keywords

Cystathionine; Cystathionine beta synthase; Gamma cystathionase; Homolanthionine; Hydrogen sulfide; Lanthionine

Indexed keywords

BIOLOGICAL MARKER; CYSTATHIONINE; CYSTEINE; HOMOCYSTEINE; HYDROGEN SULFIDE; LANTHIONINE; SULFIDE; ALANINE; CYSTATHIONINE BETA SYNTHASE;

ARTICLE; BLOOD SAMPLING; CLINICAL ARTICLE; CONTROLLED STUDY; ELECTROSPRAY MASS SPECTROMETRY; ENZYME ACTIVITY; FIBROBLAST CULTURE; HOMOCYSTINURIA; HUMAN; HUMAN CELL; IN VITRO STUDY; IN VIVO STUDY; LIMIT OF DETECTION; METABOLISM; QUADRUPOLE MASS SPECTROMETRY; REVERSED PHASE HIGH PERFORMANCE LIQUID CHROMATOGRAPHY; SIGNAL NOISE RATIO; TANDEM MASS SPECTROMETRY; ANALOGS AND DERIVATIVES; CELL CULTURE; FEMALE; FIBROBLAST; MALE; PATHOLOGY;

ALANINE; CELLS, CULTURED; CYSTATHIONINE; CYSTATHIONINE BETA-SYNTHASE; FEMALE; FIBROBLASTS; HOMOCYSTINURIA; HUMANS; HYDROGEN SULFIDE; MALE; SULFIDES;

EID: 84955324857     PISSN: 03009084     EISSN: 61831638     Source Type: Journal    
DOI: 10.1016/j.biochi.2016.01.001     Document Type: Article

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