-
1
-
-
0032513942
-
Clinical outcome in relation to care in centres specialising in cystic fibrosis: Cross sectional study
-
Mahadeva R, Webb K, Westerbeek RC, et al. Clinical outcome in relation to care in centres specialising in cystic fibrosis: cross sectional study. BMJ 1998; 316: 1771-1775.
-
(1998)
BMJ
, vol.316
, pp. 1771-1775
-
-
Mahadeva, R.1
Webb, K.2
Westerbeek, R.C.3
-
2
-
-
67650712233
-
Lung disease at diagnosis in infants with cystic fibrosis detected by newborn screening
-
Sly PD, Brennan S, Gangell C, et al. Lung disease at diagnosis in infants with cystic fibrosis detected by newborn screening. Am J Respir Crit Care Med 2009; 180: 146-152.
-
(2009)
Am J Respir Crit Care Med
, vol.180
, pp. 146-152
-
-
Sly, P.D.1
Brennan, S.2
Gangell, C.3
-
3
-
-
70349831005
-
Bronchiectasis in infants and preschool children diagnosed with cystic fibrosis after newborn screening
-
Stick SM, Brennan S, Murray C, et al. Bronchiectasis in infants and preschool children diagnosed with cystic fibrosis after newborn screening. J Pediatr 2009; 155: 623-628.
-
(2009)
J Pediatr
, vol.155
, pp. 623-628
-
-
Stick, S.M.1
Brennan, S.2
Murray, C.3
-
4
-
-
28344451370
-
Lower airway inflammation in infants with cystic fibrosis detected by newborn screening
-
Armstrong DS, Hook SM, Jamsen KM, et al. Lower airway inflammation in infants with cystic fibrosis detected by newborn screening. Pediatr Pulmonol 2005; 40: 500-510.
-
(2005)
Pediatr Pulmonol
, vol.40
, pp. 500-510
-
-
Armstrong, D.S.1
Hook, S.M.2
Jamsen, K.M.3
-
5
-
-
84878000440
-
Risk factors for bronchiectasis in children with cystic fibrosis
-
Sly PD, Gangell CL, Chen L, et al. Risk factors for bronchiectasis in children with cystic fibrosis. N Engl J Med 2013; 368: 1963-1970.
-
(2013)
N Engl J Med
, vol.368
, pp. 1963-1970
-
-
Sly, P.D.1
Gangell, C.L.2
Chen, L.3
-
7
-
-
80053063761
-
The role of matrix metalloproteinases in cystic fibrosis lung disease
-
Gaggar A, Hector A, Bratcher PE, et al. The role of matrix metalloproteinases in cystic fibrosis lung disease. Eur Respir J 2011; 38: 721-727.
-
(2011)
Eur Respir J
, vol.38
, pp. 721-727
-
-
Gaggar, A.1
Hector, A.2
Bratcher, P.E.3
-
8
-
-
79960153872
-
Biological role of matrix metalloproteinases: A critical balance
-
Löffek S, Schilling O, Franzke C-W. Biological role of matrix metalloproteinases: a critical balance. Eur Respir J 2011; 38: 191-208.
-
(2011)
Eur Respir J
, vol.38
, pp. 191-208
-
-
Löffek, S.1
Schilling, O.2
Franzke, C.-W.3
-
9
-
-
0242487715
-
Structural basis of matrix metalloproteinases and tissue inhibitors of metalloproteinases
-
Maskos K, Bode W. Structural basis of matrix metalloproteinases and tissue inhibitors of metalloproteinases. Mol Biotechnol 2003; 25: 241-266.
-
(2003)
Mol Biotechnol
, vol.25
, pp. 241-266
-
-
Maskos, K.1
Bode, W.2
-
10
-
-
0029162022
-
Imbalance between 95kDa type IV collagenase and tissue inhibitor of metalloproteinases in sputum of patients with cystic fibrosis
-
Delacourt C, Le Bourgeois M, D'Ortho MP, et al. Imbalance between 95kDa type IV collagenase and tissue inhibitor of metalloproteinases in sputum of patients with cystic fibrosis. Am J Respir Crit Care Med 1995; 152: 765-774.
-
(1995)
Am J Respir Crit Care Med
, vol.152
, pp. 765-774
-
-
Delacourt, C.1
Le Bourgeois, M.2
D'Ortho, M.P.3
-
11
-
-
0036845446
-
Matrix metalloproteases in BAL fluid of patients with cystic fibrosis and their modulation by treatment with dornase alpha
-
Ratjen F, Hartog C-M, Paul K, et al. Matrix metalloproteases in BAL fluid of patients with cystic fibrosis and their modulation by treatment with dornase alpha. Thorax 2002; 57: 930-934.
-
(2002)
Thorax
, vol.57
, pp. 930-934
-
-
Ratjen, F.1
Hartog, C.-M.2
Paul, K.3
-
12
-
-
16244368754
-
Induced sputum matrix metalloproteinase-9 correlates with lung function and airway inflammation in children with cystic fibrosis
-
Sagel SD, Kapsner RK, Osberg I. Induced sputum matrix metalloproteinase-9 correlates with lung function and airway inflammation in children with cystic fibrosis. Pediatr Pulmonol 2005; 39: 224-232.
-
(2005)
Pediatr Pulmonol
, vol.39
, pp. 224-232
-
-
Sagel, S.D.1
Kapsner, R.K.2
Osberg, I.3
-
13
-
-
34447522038
-
Matrix metalloprotease-9 dysregulation in lower airway secretions of cystic fibrosis patients
-
Gaggar A, Li Y, Weathington N, et al. Matrix metalloprotease-9 dysregulation in lower airway secretions of cystic fibrosis patients. Am J Physiol Lung Cell Mol Physiol 2007; 293: L96-L104.
-
(2007)
Am J Physiol Lung Cell Mol Physiol
, vol.293
, pp. L96-L104
-
-
Gaggar, A.1
Li, Y.2
Weathington, N.3
-
14
-
-
36048972322
-
Airway remodelling in children with cystic fibrosis
-
Hilliard TN, Regamey N, Shute JK, et al. Airway remodelling in children with cystic fibrosis. Thorax 2007; 62: 1074-1080.
-
(2007)
Thorax
, vol.62
, pp. 1074-1080
-
-
Hilliard, T.N.1
Regamey, N.2
Shute, J.K.3
-
15
-
-
84926134611
-
An observational study of matrix metalloproteinase (MMP)-9 in cystic fibrosis
-
Devereux G, Steele S, Jagelman T, et al. An observational study of matrix metalloproteinase (MMP)-9 in cystic fibrosis. J Cyst Fibros 2014; 13: 557-563.
-
(2014)
J Cyst Fibros
, vol.13
, pp. 557-563
-
-
Devereux, G.1
Steele, S.2
Jagelman, T.3
-
16
-
-
0024323967
-
Activation of matrix metalloproteinase 3 (stromelysin) and matrix metalloproteinase 2 ('gelatinase') by human neutrophil elastase and cathepsin G
-
Okada Y, Nakanishi I. Activation of matrix metalloproteinase 3 (stromelysin) and matrix metalloproteinase 2 ('gelatinase') by human neutrophil elastase and cathepsin G. FEBS Lett 1989; 249: 353-356.
-
(1989)
FEBS Lett
, vol.249
, pp. 353-356
-
-
Okada, Y.1
Nakanishi, I.2
-
17
-
-
0034783941
-
Activation of progelatinase A (MMP-2) by neutrophil elastase, cathepsin G, and proteinase-3: A role for inflammatory cells in tumor invasion and angiogenesis
-
Shamamian P, Schwartz JD, Pocock BJ, et al. Activation of progelatinase A (MMP-2) by neutrophil elastase, cathepsin G, and proteinase-3: a role for inflammatory cells in tumor invasion and angiogenesis. J Cell Physiol 2001; 189: 197-206.
-
(2001)
J Cell Physiol
, vol.189
, pp. 197-206
-
-
Shamamian, P.1
Schwartz, J.D.2
Pocock, B.J.3
-
18
-
-
77951951482
-
Human neutrophil elastase-mediated cleavage sites of MMP-9 and TIMP-1: Implications to cystic fibrosis proteolytic dysfunction
-
Jackson PL, Xu X, Wilson L, et al. Human neutrophil elastase-mediated cleavage sites of MMP-9 and TIMP-1: implications to cystic fibrosis proteolytic dysfunction. Mol Med 2010; 16: 159-166.
-
(2010)
Mol Med
, vol.16
, pp. 159-166
-
-
Jackson, P.L.1
Xu, X.2
Wilson, L.3
-
19
-
-
66749185766
-
Association of lower airway inflammation with physiologic findings in young children with cystic fibrosis
-
Peterson-Carmichael SL, Harris WT, Goel R, et al. Association of lower airway inflammation with physiologic findings in young children with cystic fibrosis. Pediatr Pulmonol 2009; 44: 503-511.
-
(2009)
Pediatr Pulmonol
, vol.44
, pp. 503-511
-
-
Peterson-Carmichael, S.L.1
Harris, W.T.2
Goel, R.3
-
20
-
-
0033985571
-
Bronchoalveolar lavage in children. ERS Task Force on bronchoalveolar lavage in children. European Respiratory Society
-
De Blic J, Midulla F, Barbato A, et al. Bronchoalveolar lavage in children. ERS Task Force on bronchoalveolar lavage in children. European Respiratory Society. Eur Respir J 2000; 15: 217-231.
-
(2000)
Eur Respir J
, vol.15
, pp. 217-231
-
-
De Blic, J.1
Midulla, F.2
Barbato, A.3
-
21
-
-
77956897106
-
Stability of interleukin 8 and neutrophil elastase in bronchoalveolar lavage fluid following long-term storage
-
Berry LJ, Sheil B, Garratt L, et al. Stability of interleukin 8 and neutrophil elastase in bronchoalveolar lavage fluid following long-term storage. J Cyst Fibros 2010; 9: 346-350.
-
(2010)
J Cyst Fibros
, vol.9
, pp. 346-350
-
-
Berry, L.J.1
Sheil, B.2
Garratt, L.3
-
22
-
-
70349095833
-
Alveolar macrophages and CC chemokines are increased in children with cystic fibrosis
-
Brennan S, Sly PD, Gangell CL, et al. Alveolar macrophages and CC chemokines are increased in children with cystic fibrosis. Eur Respir J 2009; 34: 655-661.
-
(2009)
Eur Respir J
, vol.34
, pp. 655-661
-
-
Brennan, S.1
Sly, P.D.2
Gangell, C.L.3
-
23
-
-
80053331188
-
The airway epithelium is a direct source of matrix degrading enzymes in bronchiolitis obliterans syndrome
-
Banerjee B, Ling K-M, Sutanto EN, et al. The airway epithelium is a direct source of matrix degrading enzymes in bronchiolitis obliterans syndrome. J Heart Lung Transplant 2011; 30: 1175-1185.
-
(2011)
J Heart Lung Transplant
, vol.30
, pp. 1175-1185
-
-
Banerjee, B.1
Ling, K.-M.2
Sutanto, E.N.3
-
24
-
-
84893700542
-
Heterogeneity of serum gelatinases MMP-2 and MMP-9 isoforms and charge variants
-
Rossano R, Larocca M, Riviello L, et al. Heterogeneity of serum gelatinases MMP-2 and MMP-9 isoforms and charge variants. J Cell Mol Med 2014; 18: 242-252.
-
(2014)
J Cell Mol Med
, vol.18
, pp. 242-252
-
-
Rossano, R.1
Larocca, M.2
Riviello, L.3
-
25
-
-
84860463028
-
Matrix metalloproteinase-9 activity detected in body fluids is the result of two different enzyme forms
-
Bellini T, Trentini A, Manfrinato MC, et al. Matrix metalloproteinase-9 activity detected in body fluids is the result of two different enzyme forms. J Biochem 2012; 151: 493-499.
-
(2012)
J Biochem
, vol.151
, pp. 493-499
-
-
Bellini, T.1
Trentini, A.2
Manfrinato, M.C.3
-
26
-
-
12344258657
-
Zymographic techniques for the analysis of matrix metalloproteinases and their inhibitors
-
Snoek-van Beurden PAM, Von den Hoff JW. Zymographic techniques for the analysis of matrix metalloproteinases and their inhibitors. Biotechniques 2005; 38: 73-83.
-
(2005)
Biotechniques
, vol.38
, pp. 73-83
-
-
Beurden PAM, S.1
Von Den Hoff, J.W.2
-
27
-
-
52949084668
-
Progress in matrix metalloproteinase research
-
Murphy G, Nagase H. Progress in matrix metalloproteinase research. Mol Aspects Med 2008; 29: 290-308.
-
(2008)
Mol Aspects Med
, vol.29
, pp. 290-308
-
-
Murphy, G.1
Nagase, H.2
-
28
-
-
69549105799
-
Serum matrix metalloproteinases in adult CF patients: Relation to pulmonary exacerbation
-
Roderfeld M, Rath T, Schulz R, et al. Serum matrix metalloproteinases in adult CF patients: relation to pulmonary exacerbation. J Cyst Fibros 2009; 8: 338-347.
-
(2009)
J Cyst Fibros
, vol.8
, pp. 338-347
-
-
Roderfeld, M.1
Rath, T.2
Schulz, R.3
-
29
-
-
84905992903
-
A neutrophil intrinsic impairment affecting Rab27a and degranulation in cystic fibrosis is corrected by CFTR potentiator therapy
-
Pohl K, Hayes E, Keenan J, et al. A neutrophil intrinsic impairment affecting Rab27a and degranulation in cystic fibrosis is corrected by CFTR potentiator therapy. Blood 2014; 124: 999-1009.
-
(2014)
Blood
, vol.124
, pp. 999-1009
-
-
Pohl, K.1
Hayes, E.2
Keenan, J.3
-
30
-
-
79955489997
-
Innate inflammatory responses of pediatric cystic fibrosis airway epithelial cells: Effects of nonviral and viral stimulation
-
Sutanto EN, Kicic A, Foo CJ, et al. Innate inflammatory responses of pediatric cystic fibrosis airway epithelial cells: effects of nonviral and viral stimulation. Am J Respir Cell Mol Biol 2011; 44: 761-767.
-
(2011)
Am J Respir Cell Mol Biol
, vol.44
, pp. 761-767
-
-
Sutanto, E.N.1
Kicic, A.2
Foo, C.J.3
-
31
-
-
84876531002
-
The level of p38α mitogen-activated protein kinase activation in airway epithelial cells determines the onset of innate immune responses to planktonic and biofilm Pseudomonas aeruginosa
-
Beaudoin T, LaFayette S, Roussel L, et al. The level of p38α mitogen-activated protein kinase activation in airway epithelial cells determines the onset of innate immune responses to planktonic and biofilm Pseudomonas aeruginosa. J Infect Dis 2013; 207: 1544-1555.
-
(2013)
J Infect Dis
, vol.207
, pp. 1544-1555
-
-
Beaudoin, T.1
LaFayette, S.2
Roussel, L.3
-
32
-
-
84899791723
-
Lack of neutrophil elastase reduces inflammation, mucus hypersecretion, and emphysema, but not mucus obstruction, in mice with cystic fibrosis-like lung disease
-
Gehrig S, Duerr J, Weitnauer M, et al. Lack of neutrophil elastase reduces inflammation, mucus hypersecretion, and emphysema, but not mucus obstruction, in mice with cystic fibrosis-like lung disease. Am J Respir Crit Care Med 2014; 189: 1082-1092.
-
(2014)
Am J Respir Crit Care Med
, vol.189
, pp. 1082-1092
-
-
Gehrig, S.1
Duerr, J.2
Weitnauer, M.3
-
33
-
-
84862776813
-
Progression of early structural lung disease in young children with cystic fibrosis assessed using CT
-
Mott LS, Park J, Murray CP, et al. Progression of early structural lung disease in young children with cystic fibrosis assessed using CT. Thorax 2012; 67: 509-516.
-
(2012)
Thorax
, vol.67
, pp. 509-516
-
-
Mott, L.S.1
Park, J.2
Murray, C.P.3
-
34
-
-
33846570486
-
Human airway surface epithelial regeneration is delayed and abnormal in cystic fibrosis
-
Hajj R, Lesimple P, Nawrocki-Raby B, et al. Human airway surface epithelial regeneration is delayed and abnormal in cystic fibrosis. J Pathol 2007; 211: 340-350.
-
(2007)
J Pathol
, vol.211
, pp. 340-350
-
-
Hajj, R.1
Lesimple, P.2
Nawrocki-Raby, B.3
-
35
-
-
0032189325
-
Matrilysin expression and function in airway epithelium
-
Dunsmore SE, Saarialho-Kere UK, Roby JD, et al. Matrilysin expression and function in airway epithelium. J Clin Invest 1998; 102: 1321-1331.
-
(1998)
J Clin Invest
, vol.102
, pp. 1321-1331
-
-
Dunsmore, S.E.1
Saarialho-Kere, U.K.2
Roby, J.D.3
-
36
-
-
84914143169
-
Airway mucus obstruction triggers macrophage activation and matrix metalloproteinase 12-dependent emphysema
-
Trojanek JB, Cobos-Correa A, Diemer S, et al. Airway mucus obstruction triggers macrophage activation and matrix metalloproteinase 12-dependent emphysema. Am J Respir Cell Mol Biol 2014; 51: 709-720.
-
(2014)
Am J Respir Cell Mol Biol
, vol.51
, pp. 709-720
-
-
Trojanek, J.B.1
Cobos-Correa, A.2
Diemer, S.3
-
37
-
-
80355148573
-
A therapeutic role for matrix metalloproteinase inhibitors in lung diseases?
-
Vandenbroucke RE, Dejonckheere E, Libert C. A therapeutic role for matrix metalloproteinase inhibitors in lung diseases? Eur Respir J 2011; 38: 1200-1214.
-
(2011)
Eur Respir J
, vol.38
, pp. 1200-1214
-
-
Vandenbroucke, R.E.1
Dejonckheere, E.2
Libert, C.3
-
38
-
-
0025374923
-
Neutrophil elastase cleaves C3bi on opsonized Pseudomonas as well as CR1 on neutrophils to create a functionally important opsonin receptor mismatch
-
Tosi MF, Zakem H, Berger M. Neutrophil elastase cleaves C3bi on opsonized Pseudomonas as well as CR1 on neutrophils to create a functionally important opsonin receptor mismatch. J Clin Invest 1990; 86: 300-308.
-
(1990)
J Clin Invest
, vol.86
, pp. 300-308
-
-
Tosi, M.F.1
Zakem, H.2
Berger, M.3
-
39
-
-
0033045546
-
Neutrophil elastase increases MUC5AC mRNA and protein expression in respiratory epithelial cells
-
Voynow JA, Young LR, Wang Y, et al. Neutrophil elastase increases MUC5AC mRNA and protein expression in respiratory epithelial cells. Am J Physiol 1999; 276: L835-L843.
-
(1999)
Am J Physiol
, vol.276
, pp. L835-L843
-
-
Voynow, J.A.1
Young, L.R.2
Wang, Y.3
-
40
-
-
33846907545
-
α1-Antitrypsin inhalation reduces airway inflammation in cystic fibrosis patients
-
Griese M, Latzin P, Kappler M, et al. α1-Antitrypsin inhalation reduces airway inflammation in cystic fibrosis patients. Eur Respir J 2007; 29: 240-250.
-
(2007)
Eur Respir J
, vol.29
, pp. 240-250
-
-
Griese, M.1
Latzin, P.2
Kappler, M.3
|