Spinal muscular atrophy patient-derived motor neurons exhibit hyperexcitability

Scientific Reports

Volumn 5, Issue , 2015, Pages

  Liu, Huisheng ^a   Lu, Jianfeng ^a   Chen, Hong ^a   Du, Zhongwei ^a   Li, Xue Jun ^c   Zhang, Su Chun ^a,b  

^a UNIVERSITY OF WISCONSIN MADISON   (United States)

^b UNIVERSITY OF WISCONSIN SCHOOL OF MEDICINE AND PUBLIC HEALTH   (United States)

^c UNIVERSITY OF CONNECTICUT HEALTH CENTER   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

MESSENGER RNA; SODIUM CHANNEL; SURVIVAL MOTOR NEURON PROTEIN 1;

CELL DIFFERENTIATION; CELL LINE; CYTOLOGY; GENE EXPRESSION PROFILING; GENE EXPRESSION REGULATION; GENETICS; HUMAN; INDUCED PLURIPOTENT STEM CELL; MEMBRANE POTENTIAL; METABOLISM; MOTONEURON; PATHOPHYSIOLOGY; SPINAL MUSCULAR ATROPHY; SYNAPTIC POTENTIAL;

CELL DIFFERENTIATION; CELL LINE; GENE EXPRESSION PROFILING; GENE EXPRESSION REGULATION; HUMANS; INDUCED PLURIPOTENT STEM CELLS; MEMBRANE POTENTIALS; MOTOR NEURONS; MUSCULAR ATROPHY, SPINAL; RNA, MESSENGER; SODIUM CHANNELS; SURVIVAL OF MOTOR NEURON 1 PROTEIN; SYNAPTIC POTENTIALS;

EID: 84937694834     PISSN: None     EISSN: 20452322     Source Type: Journal    
DOI: 10.1038/srep12189     Document Type: Article

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