Ganglioside GM3 is essential for the structural integrity and function of cochlear hair cells

Human Molecular Genetics

Volumn 24, Issue 10, 2015, Pages 2796-2807

[No Author Info available]

Author keywords

[No Author keywords available]

Indexed keywords

ACTIN; GANGLIOSIDE; GANGLIOSIDE GD3; GANGLIOSIDE GM3; MYOSIN VI; TUBULIN; (N-ACETYLNEURAMINYL)-GALACTOSYLGLUCOSYLCERAMIDE N-ACETYLGALACTOSAMINYLTRANSFERASE; HAEMATOSIDE SYNTHETASE; N ACETYLGALACTOSAMINYLTRANSFERASE; SIALYLTRANSFERASE;

ARTICLE; AUDITORY SYSTEM; BRAIN STEM RESPONSE; CELL MEMBRANE; CHILD; CLINICAL ARTICLE; COCHLEA; COCHLEA POTENTIAL; CONFOCAL LASER MICROSCOPY; DISTORTION PRODUCT OTOACOUSTIC EMISSION; ENDOCYTOSIS; EVOKED AUDITORY RESPONSE; EXOCYTOSIS; FEMALE; HAIR CELL; HEARING; HUMAN; INNER HAIR CELL; LIQUID CHROMATOGRAPHY; MALE; MIDDLE EAR; MOLECULAR GENETICS; OUTER HAIR CELL; PHENOTYPE; POSTNATAL DEVELOPMENT; PRESCHOOL CHILD; PRIORITY JOURNAL; SCANNING ELECTRON MICROSCOPY; STEREOCILIUM; WILD TYPE; ANIMAL; COCHLEAR HAIR CELL; DEFICIENCY; EPILEPSY; GENETICS; INFANT; KNOCKOUT MOUSE; MISSENSE MUTATION; MOUSE; PATHOLOGY; PATHOPHYSIOLOGY; PHYSIOLOGY; ULTRASTRUCTURE;

MUS;

ANIMALS; CHILD; CHILD, PRESCHOOL; EPILEPSY; FEMALE; G(M3) GANGLIOSIDE; HAIR CELLS, AUDITORY; HUMANS; INFANT; MALE; MICE; MICE, KNOCKOUT; MUTATION, MISSENSE; N-ACETYLGALACTOSAMINYLTRANSFERASES; SIALYLTRANSFERASES; STEREOCILIA;

EID: 84929773630     PISSN: 09646906     EISSN: 14602083     Source Type: Journal    
DOI: 10.1093/hmg/ddv041     Document Type: Article

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